title: A case of Parry-Romberg syndrome and alien hand.
abstract: Parry-Romberg syndrome (PRS) is a rare condition characterised by progressive hemi-facial atrophy. Here we present a PRS case with alien-hand syndrome, which has not previously been described in adult onset disease. On the basis of the presumed auto-immune pathology of PRS we justify the treatment strategy we successfully used in this patient. A review of the literature was extensively done for understanding the history of alien hand sign over the years.
authors.affiliation: Department of Neurology, Harrogate District Foundation Trust, Harrogate, UK.
authors.forename: Gurjit
authors.initials: G
authors.lastname: Chokar
authors.affiliation: Unit NINT Neuroimaging and Neurointervention, Department of Neurological and Sensorineural Sciences, Azienda Ospedaliera Universitaria Senese, "Santa Maria alle Scotte" General Hospital, Viale Mario Bracci, 16, 53100 Siena, Italy.
authors.forename: Alfonso
authors.initials: A
authors.lastname: Cerase
authors.affiliation: Department of Rheumatology, Harrogate District Foundation Trust, Harrogate, UK.
authors.forename: Andrew
authors.initials: A
authors.lastname: Gough
authors.affiliation: Department of Neurophysiology, York Teaching Hospital, York, UK.
authors.forename: Sibte
authors.initials: S
authors.lastname: Hasan
authors.affiliation: Department of Radiology, Harrogate District Foundation Trust, UK.
authors.forename: David
authors.initials: D
authors.lastname: Scullion
authors.affiliation: Department of Psychiatry, Harrogate District Foundation Trust, UK.
authors.forename: Hany
authors.initials: H
authors.lastname: El-Sayeh
authors.affiliation: Department of Neurology, Harrogate District Foundation Trust, Harrogate, UK. Electronic address: rosaria.buccoliero@hdft.nhs.uk.
authors.forename: Rosaria
authors.initials: R
authors.lastname: Buccoliero
mesh_terms: D000328:Adult; D055964:Alien Limb Phenomenon / Q000150:complications* / Q000473:pathology; D005150:Facial Hemiatrophy / Q000150:complications* / Q000473:pathology; D005260:Female; D015600:Glasgow Coma Scale; D006801:Humans; D008279:Magnetic Resonance Imaging
keywords: Alien limb; Immunosuppression; MRI scan; Parry–Romberg syndrome; Status epilepticus; Vasculitis