title: Thoracoabdominal aortic repair in a patient with Ehlers-Danlos syndrome.
abstract: Type IV Ehlers-Danlos syndrome is a life-threatening inherited disorder of connective tissue associated with multiple aneurysm formation. Thoracoabdominal aortic repair in these patients has rarely been performed. We report the case of a 13-year-old patient with Ehlers-Danlos syndrome who had multiple aortic operations from the ascending aorta to the thoracoabdominal aorta.
authors.affiliation: Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan. Electronic address: tfukui.cvs@gmail.com.
authors.forename: Toshihiro
authors.initials: T
authors.lastname: Fukui
authors.affiliation: Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan.
authors.forename: Daisuke
authors.initials: D
authors.lastname: Hiraoka
authors.affiliation: Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan.
authors.forename: Tomoya
authors.initials: T
authors.lastname: Uchimuro
authors.affiliation: Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan.
authors.forename: Tomoki
authors.initials: T
authors.lastname: Shimokawa
authors.affiliation: Department of Cardiovascular Surgery, Sakakibara Heart Institute, Tokyo, Japan.
authors.forename: Shuichiro
authors.initials: S
authors.lastname: Takanashi
authors.affiliation: Department of Pediatric Cardiac Surgery, Sakakibara Heart Institute, Tokyo, Japan.
authors.forename: Yukihiro
authors.initials: Y
authors.lastname: Takahashi
mesh_terms: D000293:Adolescent; D017542:Aneurysm, Ruptured / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D001011:Aorta / Q000601:surgery*; D017545:Aortic Aneurysm, Thoracic / Q000000981:diagnostic imaging / Q000209:etiology / Q000601:surgery*; D001027:Aortography / Q000379:methods; D019917:Blood Vessel Prosthesis Implantation / Q000009:adverse effects / Q000379:methods*; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000175:diagnosis; D005500:Follow-Up Studies; D006801:Humans; D007564:Japan; D008297:Male; D012086:Reoperation / Q000706:statistics & numerical data; D018570:Risk Assessment; D016896:Treatment Outcome