title: Pulmonary artery rupture after bilateral pulmonary artery banding in a neonate with Loeys-Dietz syndrome and an interrupted aortic arch complex: report of a case.
abstract: Loeys-Dietz syndrome (LDS) is a recognized connective tissue disorder characterized by progressive aortic aneurysm and dissection. Patients are at high risk of aortic dissection or rupture at an early age, but to our knowledge, surgery on the great arteries has never been attempted in the neonatal period. We report a case of LDS with dilated pulmonary arteries and an interrupted aortic arch complex in a neonate. We performed bilateral pulmonary artery banding, but 12 days after the procedure, the infant died of rupture of the distal portion of the banding sites following massive dilatation.
authors.affiliation: Department of Cardiovascular Surgery, Osaka Medical Center, and Research Institute for Maternal and Child Health, Izumi, Osaka, Japan, h.ozawa@f7.dion.ne.jp.
authors.forename: Hideto
authors.initials: H
authors.lastname: Ozawa
authors.forename: Hiroaki
authors.initials: H
authors.lastname: Kawata
authors.forename: Shigemitsu
authors.initials: S
authors.lastname: Iwai
authors.forename: Sanae
authors.initials: S
authors.lastname: Yamauchi
authors.forename: Tomomitsu
authors.initials: T
authors.lastname: Kanaya
authors.forename: Hidefumi
authors.initials: H
authors.lastname: Kishimoto
mesh_terms: D001015:Aortic Arch Syndromes / Q000150:complications / Q000601:surgery; D004108:Dilatation, Pathologic; D004310:Double Outlet Right Ventricle / Q000150:complications / Q000601:surgery; D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D055947:Loeys-Dietz Syndrome / Q000150:complications / Q000601:surgery*; D008297:Male; D011651:Pulmonary Artery / Q000473:pathology / Q000601:surgery*; D012306:Risk; D014656:Vascular Surgical Procedures / Q000379:methods*