title: Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome).
abstract: Frontometaphyseal dysplasia (FMD), also called Gorlin-Cohen syndrome, is a rare hereditary X-linked dominant craniotubular bone disorder. The presentation describes the airway management of a 2-year-old child suffering from FMD with significant retrognathia, posted for major long bone corrective osteotomy. Induction with a combination of dexmedetomidine and ketamine preceded a successful endotracheal intubation under spontaneous ventilation.
authors.affiliation: Department of Anesthesiology, Indira Gandhi Institute of Child Health, Bangalore, Karnataka, India.
authors.forename: Anuradha
authors.initials: A
authors.lastname: Ganigara
authors.affiliation: Department of Anesthesiology, Indira Gandhi Institute of Child Health, Bangalore, Karnataka, India.
authors.forename: Madhavi
authors.initials: M
authors.lastname: Nishtala
authors.affiliation: Department of Anesthesiology, Indira Gandhi Institute of Child Health, Bangalore, Karnataka, India.
authors.forename: Yabagodu Rama Vakoda
authors.initials: YR
authors.lastname: Chandrika
authors.affiliation: Department of Anesthesiology, Indira Gandhi Institute of Child Health, Bangalore, Karnataka, India.
authors.forename: Kunigal Ravishankar
authors.initials: KR
authors.lastname: Chandrakala
keywords: Dexmedetomidine; difficult airway; frontometaphyseal dysplasia; ketamine