title: Intraosseous pseudotumor in a child with hypofibrinogenemia.
abstract: Intraosseous pseudotumor (i.e. chronic, encapsulated, hemorrhagic fluid collection that can be seen in any portion of the tubular bones) is an uncommon complication of severe hemophilia; however, it can occur with other rare bleeding disorders. We present the case of an 11-year-old girl with hypofibrinogenemia who had multiple intramedullary lesions that were consistent with intramedullary pseudotumor associated with this rare bleeding disorder. Percutaneous biopsy of a pseudotumor is contraindicated due to the high prevalence of complications, including life-threatening bleeding. Therefore, radiologists should make the diagnosis with characteristic MR imaging findings in a patient with a severe coagulation disorder.
authors.affiliation: Department of Pediatric Radiology, Hacettepe University Medical School, Fakülteler Mah. Dirim sok 22/3, Cebeci, 06590, Ankara, Turkey, drhnozcan@yahoo.com.
authors.forename: H Nursun
authors.initials: HN
authors.lastname: Ozcan
authors.forename: Fatma Bilge
authors.initials: FB
authors.lastname: Ergen
authors.forename: Ustun
authors.initials: U
authors.lastname: Aydingoz
mesh_terms: D000347:Afibrinogenemia / Q000150:complications / Q000151:congenital* / Q000473:pathology / Q000628:therapy; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods*; D010014:Osteolysis / Q000209:etiology* / Q000473:pathology* / Q000628:therapy