[Progressive pigmented purpuric dermatosis in young children].
BACKGROUND
Pigmented purpuric dermatosis (or Schamberg's disease) is characterized by chronic macular purpura and capillaritis. It is more common in young adult males and adolescents and is generally localized on the lower limbs. In this article, we report on five young children with generalized Schamberg's disease.


METHODS
Five children (aged 13 months to 5 years) were included in this retrospective study. Time to consultation delay ranged from 15 days to 1 year.


RESULTS
All patients presented asymptomatic generalized macular purpura. Skin biopsies were performed in 4 cases and were characteristic. The results of coagulation tests and complete blood counts were within the normal range in all patients. The clinical course was chronic, with periods of improvement and worsening. No treatment was prescribed.


CONCLUSIONS
Schamberg's disease is uncommon in childhood. Our observations suggest that this diagnosis is not exceptional. Clinical appearance, setting and normal blood count values are sufficient to enable a diagnosis to be made. The clinical course is generally chronic, and as yet no treatments have demonstrated efficacy.
Service de dermatologie, CHU l'Archet 2, 151, route Saint-Antoine-de-Ginestière, 06200 Nice, France; Hôpital pédiatrique, CHU Lenval, 57, avenue de la Californie, 06200 Nice, France. Electronic address: annelaure.herisse@gmail.com.
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Hérissé
Service de dermatologie, CHU l'Archet 2, 151, route Saint-Antoine-de-Ginestière, 06200 Nice, France; Hôpital pédiatrique, CHU Lenval, 57, avenue de la Californie, 06200 Nice, France.
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Chiaverini
Unité de dermatologie pédiatrique, CHU Pellegrin-Enfants, place Amélie-Raba-Léon, 33076 Bordeaux cedex, France.
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Boralevi
Service de dermatologie, CHU Clocheville, 49, boulevard Beranger, 37044 Tours, France.
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Maruani
Service de dermatologie, centre hospitalier Lyon Sud - Pierre-Bénite, 165, chemin du Grand-Revoyet, 69495 Pierre-Bénite cedex, France.
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Phan
Service de dermatologie, CHU l'Archet 2, 151, route Saint-Antoine-de-Ginestière, 06200 Nice, France.
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Lacour
D002675:Child, Preschool; D018450:Disease Progression; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D011693:Purpura / Q000276:immunology / Q000473:pathology*; D012189:Retrospective Studies
Capillarite purpurique diffuse; Children; Enfant; Maladie de Schamberg; Pigmented purpuric dermatosis; Schamberg's disease