Colovaginoplasty in a case of mayer-rokitansky-kuster-hauser syndrome.
Mayer-Rokitansky-Kuster-Hauser Syndrome (MRKHS) is characterized by various abnormalities of paramesonephric duct structures; vaginal aplasia being the commonest anomaly in the spectrum. We report a 17-year-old girl; a case of MRKHS with vaginal agenesis. The cervix was present but atretic; uterus, fallopian tubes and ovaries were normal. There were no associated renal or skeletal defects. Colovaginoplasty was done to bridge the gap between uterus and introitus. Postoperatively, small part of colovaginoplasty flap became necrotic posteriorly, which was ultimately managed by insetting of labial flap.
Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health Lahore, Pakistan.
Muhammad
M
Saleem
Department of Pediatric Surgery, Sheikh Zayed Hospital Rahim Yar Khan, Pakistan.
Muhammad Zafar
MZ
Iqbal
Department of Pediatric Surgery, Sheikh Zayed Hospital Rahim Yar Khan, Pakistan.
Mazher Rafee
MR
Jam
Department of Pediatric Surgery, Sheikh Zayed Hospital Rahim Yar Khan, Pakistan.
Mushtaq
M
Ahmad
Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health Lahore, Pakistan.
Bilal
B
Mirza
Colovaginoplasty; Mayer-Rokitansky-Kuster-Hauser Syndrome; Vaginal agenesis