Anesthetic considerations in Sheldon-Hall syndrome.
Arthrogryposis is characterized by multiple, nonprogressive joint contractures which may be caused by maternal disorders such as oligohydramnios as well as fetal akinesia resulting from primary disorders of muscle, connective tissue, or neurologic tissue. Its prevalence is about 1 : 3000. Distal arthrogryposis (DA) is a heterogenous group of genetic disorders with a characteristic flexion of the joints of the hands and feet divided into different types with additional features. Sheldon-Hall Syndrome (SHS), also known as distal arthrogryposis type 2A (DA2A), has some nonorthopedic features of specific importance to anesthetic care.
Thomas Anthony
TA
Anderson
James R
JR
Kasser
Robert S
RS
Holzman
D000015:Abnormalities, Multiple; D000732:Androstanols / Q000627:therapeutic use*; D018686:Anesthetics, Intravenous; D001176:Arthrogryposis; D002675:Child, Preschool; D003025:Clubfoot / Q000601:surgery; D005283:Fentanyl; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods*; D008297:Male; D008723:Methohexital; D003473:Neuromuscular Nondepolarizing Agents / Q000627:therapeutic use*; D000077123:Rocuronium; D014071:Tooth Abnormalities / Q000601:surgery
D000732:Androstanols; D018686:Anesthetics, Intravenous; D003473:Neuromuscular Nondepolarizing Agents; D008723:Methohexital; D005283:Fentanyl; D000077123:Rocuronium