Pentology of Fallot's presenting with complete heart block.
A 17-year-old male patient presented with cyanosis, repeated squatting since childhood and haemoptysis since the past 1 month. He had central cyanosis with clubbing. Cardiovasular examination revealed ejection systolic murmur in the pulmonary area with single S2. ECG showed right ventricular hypertrophy (RVH) with right atrial enlargement and first-degree heart block. Two-dimensional echo showed ventricular septal defect, overriding aorta, RVH, right ventricular enlargement (RVE) and right atrial enlargement with infundibular and valvular pulmonary stenosis and 1.9 cm ostium secondum atrial septal defect. There was no evidence of atrioventricular canal defect. The patient was diagnosed with pentology of Fallots. Follow-up ECG showed complete heart block (CHB) that again reverted to first-degree heart block. A diagnosis of pentology of Fallot with intermittent CHB was made with an awake heart rate of 50/min. This case report shows association of CHB with tetralogy of Fallot.
Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India.
Rishi
R
Sethi
Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India.
Rashi
R
Khare
Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India.
Akshyaya
A
Pradhan
Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India.
Varun Shankar
VS
Narain
D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000293:Adolescent; D054537:Atrioventricular Block / Q000175:diagnosis*; D003490:Cyanosis / Q000175:diagnosis / Q000209:etiology; D003937:Diagnosis, Differential; D018618:Echocardiography, Doppler, Color / Q000379:methods; D019560:Echocardiography, Three-Dimensional / Q000379:methods; D004562:Electrocardiography / Q000379:methods; D004636:Emergency Service, Hospital; D006330:Heart Defects, Congenital / Q000175:diagnosis*; D006337:Heart Murmurs / Q000150:complications / Q000175:diagnosis; D006339:Heart Rate; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging; D006801:Humans; D017380:Hypertrophy, Right Ventricular / Q000000981:diagnostic imaging; D008297:Male; D008991:Monitoring, Physiologic / Q000379:methods; D011379:Prognosis; D013902:Radiography, Thoracic / Q000379:methods; D013771:Tetralogy of Fallot / Q000175:diagnosis; D016312:Treatment Refusal; D014286:Trilogy of Fallot / Q000175:diagnosis