title: Cochlear implantation in children with auditory neuropathy spectrum disorders.
abstract: OBJECTIVE
  To present the outcomes of cochlear implantation (CI) in children with auditory neuropathy spectrum disorders (ANSD).
  
  
  METHODS
  The pre- and post-CI hearing outcomes in children with ANSD were retrospectively evaluated. Performance was assessed with categories of auditory performance (CAP) and the Manchester spoken language development scale (MSLDS).
  
  
  RESULTS
  Full data were available in 27 implanted children with ANSD with average age at implantation 35.4 months (range 19-68 months). Nine children were implanted bilaterally, while 13 were bimodal. The pre-CI CAP and MSLDS scores were 2.5 (range 0-5) and 2.5 (range 0-6), while the post-CI scores 5.8 (range 2-9) and 7.7 (range 3-10), respectively.
  
  
  CONCLUSIONS
  Although the outcome of CI in children with ANSD might vary, it is favourable in most of the cases. CI seems a justified hearing rehabilitation option for children with ANSD and limited benefits from conventional hearing aids.
authors.forename: Georgios
authors.initials: G
authors.lastname: Kontorinis
authors.forename: Simon K W
authors.initials: SK
authors.lastname: Lloyd
authors.forename: Lise
authors.initials: L
authors.lastname: Henderson
authors.forename: Deanne
authors.initials: D
authors.lastname: Jayewardene-Aston
authors.forename: Kerri
authors.initials: K
authors.lastname: Milward
authors.forename: Iain A
authors.initials: IA
authors.lastname: Bruce
authors.forename: Martin
authors.initials: M
authors.lastname: O'Driscoll
authors.forename: Kevin
authors.initials: K
authors.lastname: Green
authors.forename: Simon R M
authors.initials: SR
authors.lastname: Freeman
mesh_terms: D001072:Apraxias / Q000175:diagnosis* / Q000628:therapy; D001321:Autistic Disorder / Q000175:diagnosis* / Q000628:therapy; D002648:Child; D002675:Child, Preschool; D019929:Cochlear Implantation / Q000379:methods*; D003054:Cochlear Implants; D003072:Cognition Disorders / Q000175:diagnosis* / Q000628:therapy; D015331:Cohort Studies; D005260:Female; D005500:Follow-Up Studies; D006313:Hearing Loss, Central / Q000175:diagnosis* / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D012189:Retrospective Studies; D018570:Risk Assessment; D012720:Severity of Illness Index; D013577:Syndrome; D013997:Time Factors; D016896:Treatment Outcome
keywords: Auditory neuropathy; Cochlear implant; Cochleovestibular nerve; Cognitive disorders; Dyssynchrony; Hearing aids