title: Coexistence of autosomal dominant polycystic kidney disease and amyloidosis in a patient with nephrotic-range proteinuria.
abstract: Autosomal dominant polycystic kidney disease (ADPKD) is an inherited disorder characterized by the development and growth of cysts in the kidneys. Non-nephritic-range proteinuria is a common presentation in ADPKD patients; however, nephrotic syndrome is a rare coincidence. A 52-year-old man is described who was diagnosed with secondary amyloidosis with ADPKD. To our knowledge, this is the first case of amyloidosis associated with frequently infected renal cysts. Patients with ADPKD who show massive proteinuria should be investigated in terms of concomitant glomerular disease.
authors.affiliation: Department of Nephrology, Ankara Numune Research and Education Hospital, Ankara, Turkey. drezgi_76@hotmail.com.
authors.forename: Ezgi Coskun
authors.initials: EC
authors.lastname: Yenigun
authors.forename: Fatih
authors.initials: F
authors.lastname: Dede
authors.forename: Nihal
authors.initials: N
authors.lastname: Ozkayar
authors.forename: Didem
authors.initials: D
authors.lastname: Turgut
authors.forename: Serhan Vahit
authors.initials: SV
authors.lastname: Piskinpasa
authors.forename: Ramazan
authors.initials: R
authors.lastname: Ozturk
authors.forename: Eyup
authors.initials: E
authors.lastname: Koc
authors.forename: Ali Riza
authors.initials: AR
authors.lastname: Odabas
mesh_terms: D000686:Amyloidosis / Q000150:complications*; D006801:Humans; D008297:Male; D008875:Middle Aged; D009404:Nephrotic Syndrome / Q000209:etiology*; D016891:Polycystic Kidney, Autosomal Dominant / Q000150:complications*; D011507:Proteinuria / Q000209:etiology*