title: A rare case of biventricular outflow obstruction with intact ventricular septum.
abstract: We report a case of pulmonary atresia with intact ventricular septum and aortic valve stenosis in a neonate. This combination is extremely rare. Cardiac catheterization was performed at 2 days of age, which confirmed the prenatal echocardiographic diagnosis and identified associated moderate aortic valve stenosis. Soon after the examination, an urgent surgical intervention was required due to uncontrollable circulatory instability. The baby underwent a successful Fontan-type repair achieved by surgical management only.
authors.affiliation: Department of Cardiovascular Surgery, Kinki University School of Medicine, Nara Hospital, Nara, Japan Yocky2001@aol.com.
authors.forename: Shinya
authors.initials: S
authors.lastname: Yokoyama
authors.affiliation: Department of Cardiovascular Surgery, Kinki University School of Medicine, Nara Hospital, Nara, Japan.
authors.forename: Shigeo
authors.initials: S
authors.lastname: Nagasaka
authors.affiliation: Department of Cardiovascular Surgery, Kinki University School of Medicine, Nara Hospital, Nara, Japan.
authors.forename: Kozo
authors.initials: K
authors.lastname: Kaneda
authors.affiliation: Department of Cardiovascular Surgery, Kinki University School of Medicine, Nara Hospital, Nara, Japan.
authors.forename: Noboru
authors.initials: N
authors.lastname: Nishiwaki
mesh_terms: D001024:Aortic Valve Stenosis / Q000000981:diagnostic imaging / Q000601:surgery*; D004452:Echocardiography; D018729:Fontan Procedure / Q000379:methods*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D018633:Pulmonary Atresia / Q000000981:diagnostic imaging / Q000601:surgery*; D016896:Treatment Outcome; D054088:Ventricular Septum / Q000000981:diagnostic imaging*
keywords: Aortic valve stenosis; cardiac catheterization; infant; newborn; prenatal; pulmonary atresia; pulmonary valve stenosis; ultrasonography