title: Diagnosis and management of idiopathic pulmonary fibrosis: French practical guidelines.
abstract: Idiopathic pulmonary fibrosis (IPF) is the most frequent chronic idiopathic interstitial pneumonia in adults. The management of rare diseases in France has been organised by a national plan for rare diseases, which endorsed a network of expert centres for rare diseases throughout France. This article is an overview of the executive summary of the French guidelines for the management of IPF, an initiative that emanated from the French National Reference Centre and the Network of Regional Competence Centres for Rare Lung Diseases. This review aims at providing pulmonologists with a document that: 1) combines the current available evidence; 2) reviews practical modalities of diagnosis and management of IPF; and 3) is adapted to everyday medical practice. The French practical guidelines result from the combined efforts of a coordination committee, a writing committee and a multidisciplinary review panel, following recommendations from the Haute Autorité de Santé. All recommendations included in this article received at least 90% agreement by the reviewing panel. Herein, we summarise the main conclusions and practical recommendations of the French guidelines.
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section vincent.cottin@chu-lyon.fr.
authors.forename: Vincent
authors.initials: V
authors.lastname: Cottin
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Bruno
authors.initials: B
authors.lastname: Crestani
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Dominique
authors.initials: D
authors.lastname: Valeyre
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Benoit
authors.initials: B
authors.lastname: Wallaert
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Jacques
authors.initials: J
authors.lastname: Cadranel
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Jean-Charles
authors.initials: JC
authors.lastname: Dalphin
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Philippe
authors.initials: P
authors.lastname: Delaval
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Dominique
authors.initials: D
authors.lastname: Israel-Biet
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Romain
authors.initials: R
authors.lastname: Kessler
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Martine
authors.initials: M
authors.lastname: Reynaud-Gaubert
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Bernard
authors.initials: B
authors.lastname: Aguilaniu
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Benoit
authors.initials: B
authors.lastname: Bouquillon
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Philippe
authors.initials: P
authors.lastname: Carré
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Claire
authors.initials: C
authors.lastname: Danel
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Jean-Baptiste
authors.initials: JB
authors.lastname: Faivre
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Gilbert
authors.initials: G
authors.lastname: Ferretti
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Nicolas
authors.initials: N
authors.lastname: Just
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Serge
authors.initials: S
authors.lastname: Kouzan
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: François
authors.initials: F
authors.lastname: Lebargy
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Sylvain
authors.initials: S
authors.lastname: Marchand-Adam
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Bruno
authors.initials: B
authors.lastname: Philippe
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Grégoire
authors.initials: G
authors.lastname: Prévot
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Bruno
authors.initials: B
authors.lastname: Stach
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Françoise
authors.initials: F
authors.lastname: Thivolet-Béjui
authors.affiliation: For a full list of the authors affiliations see the Acknowledgements section.
authors.forename: Jean-François
authors.initials: JF
authors.lastname: Cordier
mesh_terms: D032921:Consensus; D003952:Diagnostic Imaging / Q000592:standards; D019317:Evidence-Based Medicine / Q000592:standards; D005602:France / Q000453:epidemiology; D006801:Humans; D054990:Idiopathic Pulmonary Fibrosis / Q000175:diagnosis* / Q000453:epidemiology / Q000628:therapy*; D011237:Predictive Value of Tests; D015272:Pulmonary Medicine / Q000592:standards*; D012307:Risk Factors; D016896:Treatment Outcome