title: Double-valve surgery in Shprintzen-Goldberg syndrome.
abstract: We describe the challenging case of a 28-year-old Jehovah's Witness patient who presented with symptomatic mitral and tricuspid valve disease and Shprintzen-Goldberg syndrome. This is the first reported double-valve surgery in such a patient who, apart from chest deformity, had a small body size, severe lung disease, difficult airway and vascular access, and to add to the complexity, refused blood and blood product use. The patient underwent a successful mitral valve replacement and tricuspid valve repair through a right thoracotomy. Apart from atrial fibrillation, he had a smooth hospital course and was discharged home on postoperative day 9.
authors.affiliation: Department of Cardiac Surgery, Ottawa Heart Institute, Ottawa, Canada Cardiothoracic Surgery Department, Tanta University, Tanta, Egypt.
authors.forename: Elsayed
authors.initials: E
authors.lastname: Elmistekawy
authors.affiliation: Department of Anesthesia, Ottawa Heart Institute, Ottawa, Canada.
authors.forename: Christopher C
authors.initials: CC
authors.lastname: Hudson
authors.affiliation: Cardiology Department, Health Science Center, St. John's, Newfoundland, Canada.
authors.forename: Anne
authors.initials: A
authors.lastname: Williams
authors.affiliation: Department of Cardiac Surgery, Ottawa Heart Institute, Ottawa, Canada tmesana@ottawaheart.ca.
authors.forename: Thierry
authors.initials: T
authors.lastname: Mesana
mesh_terms: D000328:Adult; D000889:Anti-Arrhythmia Agents / Q000627:therapeutic use; D054119:Arachnodactyly / Q000150:complications* / Q000175:diagnosis; D001281:Atrial Fibrillation / Q000188:drug therapy / Q000209:etiology; D058385:Cardiac Valve Annuloplasty / Q000009:adverse effects; D003398:Craniosynostoses / Q000150:complications* / Q000175:diagnosis; D019918:Heart Valve Prosthesis Implantation / Q000009:adverse effects; D006801:Humans; D033221:Jehovah's Witnesses; D008297:Male; D008382:Marfan Syndrome / Q000150:complications* / Q000175:diagnosis; D008943:Mitral Valve / Q000601:surgery*; D008944:Mitral Valve Insufficiency / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D012068:Religion and Medicine; D013908:Thoracotomy; D013997:Time Factors; D016896:Treatment Outcome; D014261:Tricuspid Valve / Q000601:surgery*; D014262:Tricuspid Valve Insufficiency / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*
chemical_list: D000889:Anti-Arrhythmia Agents
keywords: Heart valve prosthesis; Jehovah’s Witnesses; Shprintzen-Goldberg syndrome