title: Chest wall reconstruction in Marfan syndrome following aortic root replacement.
abstract: Chest wall and spine deformities are common in Marfan syndrome, and often coexist with cardiac defects. Surgery is often needed to both the aortic root and the anterior chest wall, and early spinal surgery is not uncommon. We describe a case of severe thoracic cage deformity with aortic root dilatation, which was managed by a staged approach, with a very good final result.
authors.affiliation: Department of Cardiothoracic Surgery, Great Ormond Street Hospital for Children, London, UK.
authors.forename: Laurynas
authors.initials: L
authors.lastname: Bezuska
authors.affiliation: Department of Cardiothoracic Surgery, Great Ormond Street Hospital for Children, London, UK.
authors.forename: Shaffi
authors.initials: S
authors.lastname: Mussa
authors.affiliation: Department of Cardiothoracic Surgery, Great Ormond Street Hospital for Children, London, UK prathinaga@gmail.com.
authors.forename: Nagarajan
authors.initials: N
authors.lastname: Muthialu
mesh_terms: D000293:Adolescent; D001014:Aortic Aneurysm / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D019917:Blood Vessel Prosthesis Implantation; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008382:Marfan Syndrome / Q000150:complications* / Q000175:diagnosis; D010027:Osteotomy; D066166:Pectus Carinatum / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D019651:Plastic Surgery Procedures; D019616:Thoracic Surgical Procedures; D016896:Treatment Outcome
keywords: Aorta; Dilatation; Funnel chest; Marfan syndrome; pathologic; thoracic