title: Primary vulvar lymphangioma circumscriptum: a case report and review of literature.
abstract: OBJECTIVE
  To add a new case of primary vulvar lymphangioma circumscriptum to the literature and to review the current literature.
  
  
  METHODS
  We searched the PubMed/MEDLINE databases for previous case reports using the key words "vulvar lymphangioma circumscriptum" and "primary vulvar lymphangioma circumscriptum."
  
  
  RESULTS
  We found 21 cases of primary vulvar lymphangioma circumscriptum reported until 2013. Mean age was 32 years (range = 3-76 y), and 62 % of the cases had been treated surgically.
  
  
  CONCLUSIONS
  The treatment of primary vulvar lymphangioma circumscriptum is mainly surgery. Depending on the age of the patient and the extent of lesion, surgical treatment might be in the form of the local excision, labiectomy, or vulvectomy.
authors.affiliation: Departments of 1Obstetrics and Gynecology and 2Pathology, Faculty of Medicine, University of Ondokuz Mayis, Samsun, Turkey.
authors.forename: Arif
authors.initials: A
authors.lastname: Kokcu
authors.forename: Seher
authors.initials: S
authors.lastname: Sari
authors.forename: Mehmet
authors.initials: M
authors.lastname: Kefeli
mesh_terms: D000293:Adolescent; D000328:Adult; D000368:Aged; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008202:Lymphangioma / Q000175:diagnosis* / Q000473:pathology* / Q000601:surgery; D008875:Middle Aged; D014846:Vulvar Neoplasms / Q000175:diagnosis* / Q000473:pathology* / Q000601:surgery; D055815:Young Adult