title: Coronary-pulmonary artery fistula in tetralogy of Fallot with pulmonary atresia.
abstract: Surgical correction of patients with tetralogy of Fallot with pulmonary atresia is now one of the routine procedures performed by pediatric cardiac surgeons. In one variant, the pulmonary arterial supply is derived from a fistulous communication from the coronary arteries. This rare and interesting situation poses a diagnostic and therapeutic dilemma, as well as providing specific management challenges to the surgical team. Here, we discuss important aspects of this rare variant, specifically its morphology, presentation, evaluation and management.
authors.affiliation: Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi, India sachintalwar@hotmail.com.
authors.forename: Sachin
authors.initials: S
authors.lastname: Talwar
authors.affiliation: Institute of Genetic Medicine, Newcastle upon Tyne, UK.
authors.forename: Robert H
authors.initials: RH
authors.lastname: Anderson
authors.affiliation: Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Vikas Kumar
authors.initials: VK
authors.lastname: Keshri
authors.affiliation: Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Shiv Kumar
authors.initials: SK
authors.lastname: Choudhary
authors.affiliation: Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Gurpreet Singh
authors.initials: GS
authors.lastname: Gulati
authors.affiliation: Cardiothoracic Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Balram
authors.initials: B
authors.lastname: Airan
mesh_terms: D001159:Arterio-Arterial Fistula / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D017023:Coronary Angiography / Q000379:methods; D003326:Coronary Circulation; D003330:Coronary Vessel Anomalies / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D006439:Hemodynamics; D006801:Humans; D011237:Predictive Value of Tests; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery; D018633:Pulmonary Atresia / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D011652:Pulmonary Circulation; D013771:Tetralogy of Fallot / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
keywords: Arterio-arterial fistula; congenital; fistula; heart defects; pulmonary atresia; tetralogy of Fallot