title: Successful Bentall procedure in a patient with a Fontan circulation.
abstract: A 33-year old male patient with absent left atrioventricular connection and double outlet left ventricle developed severe aortic root dilatation and aortic regurgitation. He had undergone initial banding of the pulmonary trunk and atrial septectomy, eventually followed by the bidirectional Glenn procedure. At the time of the total cavopulmonary connection (at 27 years of age), his ascending aorta was plicated and wrapped. Subsequently, the aortic root below the wrapped ascending aorta showed further dilatation. The Bentall procedure was successfully carried out.
authors.affiliation: Heart Division, Royal Brompton Hospital, London, UK Department of Thoracic and Cardiovascular Sciences, University of Padua, Padua, Italy.
authors.forename: Veronica
authors.initials: V
authors.lastname: Spadotto
authors.affiliation: Heart Division, Royal Brompton Hospital, London, UK Congenital Heart Disease Center, Nara Medical University, Nara, Japan humed@me.com.
authors.forename: Hideki
authors.initials: H
authors.lastname: Uemura
authors.affiliation: Heart Division, Royal Brompton Hospital, London, UK.
authors.forename: Anselm
authors.initials: A
authors.lastname: Uebing
mesh_terms: D000015:Abnormalities, Multiple; D000328:Adult; D001011:Aorta / Q000473:pathology / Q000503:physiopathology / Q000601:surgery*; D001014:Aortic Aneurysm / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology / Q000601:surgery*; D001021:Aortic Valve / Q000503:physiopathology / Q000601:surgery*; D001022:Aortic Valve Insufficiency / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology / Q000601:surgery*; D001807:Blood Vessel Prosthesis; D019917:Blood Vessel Prosthesis Implantation / Q000295:instrumentation; D004108:Dilatation, Pathologic; D018729:Fontan Procedure; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D006350:Heart Valve Prosthesis; D019918:Heart Valve Prosthesis Implantation / Q000295:instrumentation; D006352:Heart Ventricles / Q000002:abnormalities / Q000601:surgery*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D011474:Prosthesis Design; D012086:Reoperation; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
keywords: Aortic root dilatation; Bentall; Fontan