title: Successful implantation of a dual-chamber pacemaker in an ELBW infant for long QT syndrome.
abstract: Long QT syndromes encompass the most prevalent group of ion channelopathies. Long QT syndromes are predominantly familial and predispose the affected individual to ventricular arrhythmias and sudden death. Permanent pacemaker insertion for long QT syndrome is discouraged apart from younger patients exhibiting 2:1 atrioventricular block. However, permanent pacemaker insertion is a relatively common procedure in neonates with atrioventricular block, and dual-chamber permanent pacemaker insertion in low birth weight infants is challenging. We describe the management of long QT syndrome - type 2 - presenting in an extremely preterm neonate including epicardial, dual-chamber permanent pacemaker insertion.
authors.affiliation: 1Department of Paediatric Cardiology,Murdoch Children's Research Institute and University of Melbourne,Royal Children's Hospital,Melbourne,Australia.
authors.forename: Brian
authors.initials: B
authors.lastname: McCrossan
authors.affiliation: 2Department of Paediatric Cardiac Surgery,Royal Children's Hospital,Melbourne,Australia.
authors.forename: Yves
authors.initials: Y
authors.lastname: d'Udekem
authors.affiliation: 1Department of Paediatric Cardiology,Murdoch Children's Research Institute and University of Melbourne,Royal Children's Hospital,Melbourne,Australia.
authors.forename: Andrew Mark
authors.initials: AM
authors.lastname: Davis
authors.affiliation: 1Department of Paediatric Cardiology,Murdoch Children's Research Institute and University of Melbourne,Royal Children's Hospital,Melbourne,Australia.
authors.forename: Andreas
authors.initials: A
authors.lastname: Pflaumer
mesh_terms: D002304:Cardiac Pacing, Artificial / Q000379:methods*; D004562:Electrocardiography; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D007230:Infant, Low Birth Weight; D008133:Long QT Syndrome / Q000503:physiopathology / Q000628:therapy*; D016896:Treatment Outcome
keywords: low birth weight