title: An unusual cause of duodenal obstruction: mesenteric fibromatosis in a patient with type I Mayer-Rokitansky-Kuster-Hauser syndrome.
abstract: Patients with mesenteric fibromatosis (MF) are clinically asymptomatic, with little or no focal symptoms until later in their course, at which time they complain of pain, abdominal discomfort, constipation, vomiting, abdominal mass, weight loss, and symptoms due to organ compression. Generally, it occurs as an abdominal mass but may also present in many different ways. In some cases, trauma, previous abdominal surgery, and hormonal stimulation (such as estrogen) may play a role in onset of this neoplasm. Patients with Mayer-Rokitansky-Kuster-Hauser syndrome present primary amenorrhea and may have some other anomalies, including hearing defects, heart defects, skeletal deformities, and genital neoplastic diseases. We diagnosed duodenal obstruction due to MF in a patient with type I Mayer-Rokitansky-Kuster-Hauser syndrome.
authors.affiliation: Division of Nephrology, Department of Internal Medicine, Mersin University Faculty of Medicine, Mersin, Turkey.
authors.forename: Kenan
authors.initials: K
authors.lastname: Turgutalp
authors.forename: Feray
authors.initials: F
authors.lastname: Tabakan
authors.forename: Tuğba
authors.initials: T
authors.lastname: Kara
authors.forename: Ozlem
authors.initials: O
authors.lastname: Gübür
authors.forename: Engin
authors.initials: E
authors.lastname: Altıntaş
authors.forename: Ozgür
authors.initials: O
authors.lastname: Türkmenoğlu
authors.forename: Onur
authors.initials: O
authors.lastname: Ozhan
authors.forename: Ahmet
authors.initials: A
authors.lastname: Kıykım
authors.forename: F Demir
authors.initials: FD
authors.lastname: Apaydın
mesh_terms: D058489:46, XX Disorders of Sex Development / Q000150:complications*; D000328:Adult; D000013:Congenital Abnormalities; D004380:Duodenal Obstruction / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D005260:Female; D005350:Fibroma / Q000150:complications / Q000473:pathology* / Q000601:surgery; D006801:Humans; D007580:Jejunal Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D009095:Mullerian Ducts / Q000002:abnormalities*