title: Desmoplastic infantile ganglioglioma: Report of an unusual case with a cranial defect.
abstract: Desmoplastic infantile ganglioglioma (DIG) is a rare tumor that typically occurs in infants under the age of 24 months. These tumors commonly have a good prognosis after surgical resection despite their aggressive radiological appearances. Clinical signs are due to the large size of the tumor and include increased head circumference, bulging fontanel, sunset sign and seizures. We report an unusual DIG case who presented with parietal bulging associated with a bony defect. The patient was thought to have a leptomeningeal cystic formation, but on his cranial magnetic resonance imaging (MRI), we observed a centrally and homogeneously gadolinium-enhanced lesion fixed to the dura by its solid component. A surgical gross total resection was performed, and no residual tumor was observed on follow-up.
authors.affiliation: Department of Neurosurgery, Dr. Lutfi Kirdar Training and Research Hospital, Istanbul, Turkey.
authors.forename: Recep
authors.initials: R
authors.lastname: Basaran
authors.affiliation: Department of Pediatric Hematology-Oncology, School of Medicine, Bezmi Alem Foundation University, Istanbul, Turkey.
authors.forename: Fatma Betul
authors.initials: FB
authors.lastname: Cakir
authors.affiliation: Department of Neurosurgery, Goztepe Training and Research Hospital, Istanbul Medeniyet University, Istanbul, Turkey.
authors.forename: Nejat
authors.initials: N
authors.lastname: Isik
authors.affiliation: Department of Pathology, School of Medicine, Acibadem University, Istanbul, Turkey.
authors.forename: Aydin
authors.initials: A
authors.lastname: Sav
authors.affiliation: Department of Neurosurgery, School of Medicine, Medipol University, Istanbul, Turkey.
authors.forename: Ilhan
authors.initials: I
authors.lastname: Elmaci
keywords: Bony defect; desmoplastic; ganglioglioma; pediatric; skull deformation; supratentorial tumor