title: Anesthesia for a patient with Fanconi anemia for developmental dislocation of the hip: a case report.
abstract: Fanconi anemia is a rare autosomal recessive inherited bone marrow failure syndrome with congenital and hematological abnormalities. Literature regarding the anesthetic management in these patients is limited. A management of a developmental dislocation of the hip was described in a patient with fanconi anemia. Because of the heterogeneous nature, a patient with fanconi anemia should be established thorough preoperative evaluation in order to diagnose on clinical features. In conclusion, we preferred caudal anesthesia in this patient with fanconi anemia without thrombocytopenia, because of avoiding from N2O, reducing amount of anesthetic, existing microcephaly, hypothyroidism and elevated liver enzymes, providing postoperative analgesia, and reducing amount of analgesic used postoperatively.
authors.affiliation: Department of Anesthesiology and Intensive Care, Bezmialem Vakif University Medical School, Istanbul, Turkey. Electronic address: drzdogan@yahoo.com.
authors.forename: Zafer
authors.initials: Z
authors.lastname: Dogan
authors.affiliation: Department of Anesthesiology and Intensive Care, Kahramanmaras Sutcu Imam University, Medical School, Kahramanmaras, Turkey.
authors.forename: Huseyin
authors.initials: H
authors.lastname: Yildiz
authors.affiliation: Department of Anesthesiology and Intensive Care, Kahramanmaras Sutcu Imam University, Medical School, Kahramanmaras, Turkey.
authors.forename: Ismail
authors.initials: I
authors.lastname: Coskuner
authors.affiliation: Department of Orthopedics and Traumatology, Kahramanmaras Sutcu Imam University, Medical School, Kahramanmaras, Turkey.
authors.forename: Murat
authors.initials: M
authors.lastname: Uzel
authors.affiliation: Department of Pediatrics, Kahramanmaras Sutcu Imam University, Medical School, Kahramanmaras, Turkey.
authors.forename: Mesut
authors.initials: M
authors.lastname: Garipardic
mesh_terms: D000700:Analgesics / Q000008:administration & dosage / Q000627:therapeutic use; D000763:Anesthesia, Caudal / Q000379:methods*; D002675:Child, Preschool; D005199:Fanconi Anemia / Q000503:physiopathology / Q000601:surgery*; D005260:Female; D006618:Hip Dislocation, Congenital / Q000209:etiology / Q000601:surgery*; D006801:Humans; D010149:Postoperative Pain / Q000188:drug therapy
chemical_list: D000700:Analgesics
keywords: Caudal anesthesia; Developmental dislocation of the hip; Fanconi anemia