title: Clouston syndrome associated with eccrine syringofibroadenoma.
abstract: Eccrine syringofibroadenoma is a rare benign neoplasia derived from acrosyryngium cells of the eccrine sudoriferous glands. It affects the extremities of elderly individuals as solitary tumors, or may also present as multiple lesions. There are controversies about the pathogenesis and differentiation of the tumor. Eccrine syringofibroadenoma has been associated with subjacent conditions, such as for example, hypohidrotic ectodermic dysplasias. The authors describe a case report of a patient with Clouston Syndrome, who presented papules and nodules in extremities, clinically and histologically compatible with eccrine syringofibroadenoma. There are only three cases described in the literature, associated with Clouston Syndrome, and this is the fourth case.
authors.affiliation: Universidade Estadual do Sudoeste da Bahia, Jequié, BA, Brazil.
authors.forename: Ana Carolina Dias Viana de
authors.initials: AC
authors.lastname: Andrade
authors.affiliation: Centro Municipal de Atenção Especializada, Vitória da Conquista, BA, Brazil.
authors.forename: Denise Cardoso
authors.initials: DC
authors.lastname: Vieira
authors.affiliation: Universidade Federal do Rio de Janeiro, Rio de Janeiro, Brazil.
authors.forename: Olga Maria Oiticica
authors.initials: OM
authors.lastname: Harris
authors.affiliation: Universidade Estadual do Sudoeste da Bahia, Jequié, BA, Brazil.
authors.forename: Matheus Melo
authors.initials: MM
authors.lastname: Pithon
mesh_terms: D000328:Adult; D000505:Alopecia / Q000473:pathology; D001706:Biopsy; D004439:Eccrine Glands / Q000473:pathology*; D004476:Ectodermal Dysplasia / Q000150:complications* / Q000473:pathology; D005260:Female; D018226:Fibroadenoma / Q000150:complications* / Q000473:pathology; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000473:pathology; D013544:Sweat Gland Neoplasms / Q000150:complications* / Q000473:pathology