title: Maffucci syndrome and intracranial chondrosarcomas: a case report featuring spontaneous resolution of sixth nerve palsy.
abstract: Maffucci syndrome is a rare disease process characterized by enchondromatosis with cutaneous hemangiomatosis. We report a 20-year-old woman with Maffucci syndrome with a 5-day history of diplopia. She was found to have a left sixth nerve palsy due to a parasellar chondrosarcoma. Three weeks later, the patient's diplopia spontaneously resolved. This unusual clinical course prompted us to review frequency of sixth nerve palsy with skull base neoplasms and the phenomenon of spontaneous resolution of diplopia.
authors: Section of Ophthalmology (MM, FC, RY), Department of Surgery, University of Calgary, Calgary, Alberta, Canada; Departments of Clinical Neurosciences (FC) and Radiology (DB), University of Calgary, Calgary Alberta, Canada; and Mitchell Eye Centre, Southern Alberta Eye Center, Calgary, Alberta, Canada.
authors: Monique
authors: M
authors: Munro
authors: Fiona
authors: F
authors: Costello
authors: David
authors: D
authors: Burrowes
authors: Ryan
authors: R
authors: Yau
mesh_terms: D020434:Abducens Nerve Diseases / Q000150:complications*; D001921:Brain / Q000473:pathology*; D002813:Chondrosarcoma / Q000150:complications*; D004687:Enchondromatosis / Q000150:complications*; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D009418:S100 Proteins / Q000378:metabolism; D055815:Young Adult
chemical_list: D009418:S100 Proteins