title: An Unusual Case of Severe Stenosis of the Coronary Sinus Ostium in Association With Double Inlet Left Ventricle.
abstract: We present a patient with complex single ventricle physiology who was subsequently diagnosed with atresia of the coronary sinus ostium in the setting of myocardial dysfunction following operative palliation. Although a rare cardiac defect, awareness is important as the coronary venous system will often drain to a left superior vena cava (LSVC). If the LSVC is ligated without knowing of this defect, cardiac dysfunction and death can occur.
authors: Department of Pediatrics, Division of Cardiology, Medical College of Wisconsin, Milwaukee, WI, USA phidestrand@chw.org.
authors: Pip M
authors: PM
authors: Hidestrand
authors: Department of Pediatrics, Division of Cardiology, Medical College of Wisconsin, Milwaukee, WI, USA.
authors: Edward C
authors: EC
authors: Kirkpatrick
authors: Department of Surgery, Division of Cardiothoracic Surgery, Medical College of Wisconsin, Milwaukee, WI, USA.
authors: Michael E
authors: ME
authors: Mitchell
mesh_terms: D006328:Cardiac Catheterization; D054326:Coronary Sinus / Q000000981:diagnostic imaging*; D023921:Coronary Stenosis / Q000175:diagnosis / Q000209:etiology*; D006330:Heart Defects, Congenital / Q000150:complications* / Q000175:diagnosis; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D008297:Male
keywords: congenital heart disease; congenital heart surgery; coronary sinus; univentricular heart