title: [Aberrant right subclavian artery in children examined at the National Institute of Cardiology Ignacio Chavez (1992-2012)].
abstract: OBJECTIVE
  Congenital vascular malformations of the major arteries in the chest have been classified into 5 groups: 1) double aortic arch; 2) right aortic arch with left ligament or persistent ductus arteriosus; 3) aberrant subclavian artery; 4) aberrant left pulmonary artery, and 5) anomalous innominate artery. We reviewed the patients with aberrant right subclavian artery and their treatment.
  
  
  METHODS
  We studied retrospectively the records of 29 patients with aberrant right subclavian artery in childhood, from January 1992 to December 2012, analyzing the following variables: age at onset, clinical manifestations, associated cardiovascular defects, diagnosis and surgical approach method.
  
  
  RESULTS
  We found that most patients have an asymptomatic course, only 31% of them course with symptoms during the first year of life, with an incidental diagnosis of 35% during catheterization or other imaging studies. Patent ductus arteriosus was the most frequently associated congenital malformation, with 13%. Down's syndrome was found in 21%. The most common treatment was surgical section of the aberrant subclavian artery to release the esophagus.
  
  
  CONCLUSIONS
  This vascular abnormality must be suspected in those patients with dysphagia, dyspnea, chest pain during feeding or breathing difficulties. A significant number of patients are not diagnosed in time, some reach adulthood without a diagnosis. This malformation is often found in imaging studies when evaluating the aorta or in a gastroesophageal reflux study, in which the barium bolus reveals the extrinsic compression of the esophagus.
authors.affiliation: Departamento de Cardiología Pediátrica, Instituto Nacional de Cardiología Ignacio Chávez, México, D. F., México. Electronic address: dr.rmijangos@gmail.com.
authors.forename: Roberto
authors.initials: R
authors.lastname: Mijangos-Vázquez
authors.affiliation: Departamento de Cardiología Pediátrica, Instituto Nacional de Cardiología Ignacio Chávez, México, D. F., México.
authors.forename: Emilia
authors.initials: E
authors.lastname: Patiño-Bahena
authors.affiliation: Departamento de Cardiología Pediátrica, Instituto Nacional de Cardiología Ignacio Chávez, México, D. F., México.
authors.forename: Alfonso
authors.initials: A
authors.lastname: Martínez-García
authors.affiliation: Departamento de Ecocardiografía, Instituto Nacional de Cardiología Ignacio Chávez, México, D. F., México.
authors.forename: Juan
authors.initials: J
authors.lastname: Herrera
authors.affiliation: Departamento de Cardiología Pediátrica, Instituto Nacional de Cardiología Ignacio Chávez, México, D. F., México.
authors.forename: Juan
authors.initials: J
authors.lastname: Calderón-Colmenero
authors.affiliation: Departamento de Cardiología Pediátrica, Instituto Nacional de Cardiología Ignacio Chávez, México, D. F., México.
authors.forename: Alfonso
authors.initials: A
authors.lastname: Buendía-Hernández
authors.affiliation: Departamento de Inmunología, Instituto Nacional de Cardiología Ignacio Chávez, México, D.F., México.
authors.forename: María Elena
authors.initials: ME
authors.lastname: Soto-López
mesh_terms: D000047:Academies and Institutes; D000783:Aneurysm / Q000175:diagnosis* / Q000601:surgery*; D002309:Cardiology; D018376:Cardiovascular Abnormalities / Q000175:diagnosis* / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D003680:Deglutition Disorders / Q000175:diagnosis* / Q000601:surgery*; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D012189:Retrospective Studies; D013348:Subclavian Artery / Q000002:abnormalities* / Q000601:surgery
keywords: Aberrant right subclavian artery; Aortic arch; Arco aórtico; Arteria subclavia derecha aberrante; Malformaciones vasculares; Mexico; México; Vascular lesions