title: Interradicular dentin dysplasia associated with amelogenesis imperfecta with taurodontism or trichodentoosseous syndrome: a diagnostic dilemma.
abstract: Amelogenesis imperfecta is a hereditary disorder with diverse clinical presentation, where enamel is the tissue that is primarily affected either quantitatively or qualitatively. Hypomaturation/hypoplastic amelogenesis imperfecta with taurodontism is a rare variant of amelogenesis imperfecta which is often confused with trichodentoosseous syndrome. We report a rare case of hereditary enamel defect with taurodontism associated with interradicular dentin dysplasia.
authors.affiliation: Department of Oral Pathology, SDM College of Dental Sciences and Hospital, Dharwad, Karnataka, India.
authors.forename: Veda
authors.initials: V
authors.lastname: Hegde
authors.forename: K
authors.initials: K
authors.lastname: Srikanth
mesh_terms: D000328:Adult; D000566:Amelogenesis; D019465:Craniofacial Abnormalities / Q000175:diagnosis* / Q000473:pathology; D003744:Dental Enamel Hypoplasia / Q000175:diagnosis* / Q000473:pathology; D003786:Dental Pulp Cavity / Q000002:abnormalities* / Q000473:pathology; D003805:Dentin Dysplasia / Q000473:pathology*; D006201:Hair Diseases / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008297:Male; D014071:Tooth Abnormalities / Q000150:complications* / Q000473:pathology