title: Recurrent arterial aneurysm rupture of the upper extremity in a patient with vascular-type Ehlers-Danlos syndrome.
abstract: Arterial aneurysm rupture is one of the most critical complications in patients with vascular-type Ehlers-Danlos syndrome (vEDS). Here, we report a case of recurrent aneurysm rupture successfully treated by endovascular embolization. A 38-year old woman who underwent brachial artery ligation for a ruptured aneurysm was diagnosed postoperatively with vEDS. Impending rupture of a collateral artery aneurysm was encountered 5 months after the initial open surgery. Endovascular embolization with a liquid embolic agent was successfully performed. Given that arterial rupture can occur repeatedly in patients with vEDS, careful life-long follow-up is necessary.
authors.affiliation: Department of Cardiovascular Surgery, Japanese Red Cross Okayama Hospital, Okayama, Japan.
authors.forename: Koji
authors.initials: K
authors.lastname: Nakanishi
authors.affiliation: Department of Radiology, Japanese Red Cross Okayama Hospital, Okayama, Japan.
authors.forename: Nobuhisa
authors.initials: N
authors.lastname: Tajiri
authors.affiliation: Department of Cardiovascular Surgery, National Hospital Organization Okayama Medical Center, Okayama, Japan.
authors.forename: Mikizo
authors.initials: M
authors.lastname: Nakai
authors.affiliation: Department of Cardiovascular Dynamics, National Cerebral and Cardiovascular Center, Osaka, Japan shujismz@ri.ncvc.go.jp.
authors.forename: Shuji
authors.initials: S
authors.lastname: Shimizu
mesh_terms: D000328:Adult; D017542:Aneurysm, Ruptured / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D001916:Brachial Artery / Q000000981:diagnostic imaging / Q000601:surgery; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000175:diagnosis; D004621:Embolization, Therapeutic; D005260:Female; D006801:Humans; D008026:Ligation; D012008:Recurrence; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D034941:Upper Extremity / Q000098:blood supply*
keywords: Brachial artery aneurysm; Ehlers–Danlos syndrome; Endovascular treatment; Liquid embolic agent; Open surgery