title: Primary desmoplastic small round cell tumor of the duodenum.
abstract: The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.
authors.forename: Qi
authors.initials: Q
authors.lastname: Liu
authors.forename: Nan
authors.initials: N
authors.lastname: Liu
authors.affiliation: General Surgery Department, Qian Wei Hospital of Jilin province, Changchun City, Jilin Province, China. 797980@sina.com.
authors.forename: DeXing
authors.initials: D
authors.lastname: Chen
mesh_terms: D000293:Adolescent; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000008:administration & dosage*; D017024:Chemotherapy, Adjuvant; D058405:Desmoplastic Small Round Cell Tumor / Q000000981:diagnostic imaging / Q000188:drug therapy* / Q000473:pathology; D004379:Duodenal Neoplasms / Q000000981:diagnostic imaging / Q000188:drug therapy* / Q000473:pathology; D004386:Duodenum / Q000473:pathology / Q000601:surgery; D005260:Female; D006801:Humans; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography