title: Generalized odontodysplasia in a 5-year-old patient with Hallermann-Streiff syndrome: clinical aspects, cone beam computed tomography findings, and conservative clinical approach.
abstract: This article aims to report the main clinical aspects, cone beam computed tomography (CBCT) findings, and conservative oral rehabilitation in a child born from a consanguineous marriage who presented with Hallermann-Streiff syndrome (HSS) and generalized odontodysplasia. A 5-year-old girl presented with a diagnosis of HSS for oral evaluation. Radiographically, all teeth showed wide pulp chambers and roots with thin dentinal walls and open apices, resembling ghost teeth and indicating a diagnosis of odontodysplasia. Oral rehabilitation consisted of partial dentures that were regularly adjusted to conform the device with the pattern of growth and development of the child. CBCT scan provided great insight into HSS, allowing a detailed view of the morphologic aspects and associated trabecular bone pattern. Treatment of these 2 rare conditions in young children must consider the stage of growth and development. Although extremely rare in HSS, odontodysplasia should be investigated and conservatively managed in young children.
authors.affiliation: PhD student, Postgraduate Program in Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil.
authors.forename: Juliana Ximenes
authors.initials: JX
authors.lastname: Damasceno
authors.affiliation: PhD student, Postgraduate Program in Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil.
authors.forename: José Luciano Pimenta
authors.initials: JL
authors.lastname: Couto
authors.affiliation: PhD student, Postgraduate Program in Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil.
authors.forename: Karla Shangela da Silva
authors.initials: KS
authors.lastname: Alves
authors.affiliation: Associate Professor, Division of Orthodontics and Pediatric Dentistry, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil.
authors.forename: Cauby Maia
authors.initials: CM
authors.lastname: Chaves
authors.affiliation: Adjunct Professor, Division of Oral Radiology, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil.
authors.forename: Fábio Wildson Gurgel
authors.initials: FW
authors.lastname: Costa
authors.affiliation: Adjunct Professor, Division of Oral Radiology, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil.
authors.forename: Alynne de Menezes Vieira
authors.initials: Ade M
authors.lastname: Pimenta
authors.affiliation: Associate Professor, Division of Orthodontics and Pediatric Dentistry, Department of Clinical Dentistry, Federal University of Ceará, Fortaleza, Ceará, Brazil. Electronic address: cfontele@ufc.br.
authors.forename: Cristiane Sá Roriz
authors.initials: CS
authors.lastname: Fonteles
mesh_terms: D002675:Child, Preschool; D054893:Cone-Beam Computed Tomography; D005260:Female; D006210:Hallermann's Syndrome / Q000150:complications* / Q000000981:diagnostic imaging* / Q000628:therapy; D006801:Humans; D018126:Odontodysplasia / Q000000981:diagnostic imaging* / Q000209:etiology* / Q000628:therapy; D011862:Radiography, Panoramic