title: Photoletter to the editor: A neurocutaneous rarity: phacomatosis pigmentokeratotica.
abstract: Phacomatosis pigmentokeratotica is characterized by the coexistence of nevus sebaceus, papular nevus spilus and associated neurologic abnormalities. We report a case of phacomatosis pigmentokeratotica in a 28-year-old male who presented with palmar-plantar dysesthesia and ipsilateral brain hemiatrophy. As a characteristic neuroimaging finding of the disorder, we found multiple hypointense lesions involving the ipsilateral hemisphere.
authors.affiliation: Neurology Division, University Hospital, Faculty of Medicine, Federal University of Juiz de Fora (UFJF), Juiz de Fora, Minas Gerais, Brazil;
authors.forename: Thiago Cardoso
authors.initials: TC
authors.lastname: Vale
authors.affiliation: Neurology Division, University Hospital, Faculty of Medicine, Federal University of Minas Gerais (UFMG), Belo Horizonte, Minas Gerais, Brazil;
authors.forename: David Márcio Barbosa
authors.initials: DM
authors.lastname: Santos
authors.affiliation: Neurology Division, University Hospital, Faculty of Medicine, Federal University of Minas Gerais (UFMG), Belo Horizonte, Minas Gerais, Brazil;
authors.forename: Ricardo Oliveira
authors.initials: RO
authors.lastname: Maciel
authors.affiliation: Neurology Division, Department of Internal Medicine, Faculty of Medicine, Federal University of Minas Gerais (UFMG), Belo Horizonte, Minas Gerais, Brazil;
authors.forename: Francisco
authors.initials: F
authors.lastname: Cardoso
authors.affiliation: Department of Dermatology, Freiburg University Medical Center, Freiburg, Germany.
authors.forename: Rudolf
authors.initials: R
authors.lastname: Happle
keywords: atrophy; bones; congenital abnormalities; dysesthesia; neuropathy; nevus sebaceous; nevus spilus; unilateral