title: Sinus histiocytosis with massive lymphadenopathy: a "massive" misnomer.
abstract: Sinus histiocytosis with massive lymphadenopathy also known as Rosai-Dorfman disease is a rare, benign, histiocytic disorder of unknown origin characterized by lymphadenopathy. Since its original description by Rosai and Dorfman in 1969, small number of cases has been reported; hence no specific diagnostic criteria and treatment guidelines have been suggested. The purpose of this article is to present and discuss a case of Rosai Dorfman Syndrome in 4-year-old child diagnosed with the help of Fine Needle Aspiration Cytology. The swelling resolved over a period of 18 months without any recurrence in 2-year follow-up period. This case report highlights the role of Fine Needle Aspiration Cytology in the diagnosis of Rosai-Dorfman disease and the importance of regular follow ups using a careful wait and watch approach in its management. The report also briefly discusses the various dilemmas associated with its diagnosis and treatment.
authors.affiliation: Unit of Pedodontics and Preventive Dentistry, Oral Health Sciences Center, Post-Graduate Institute of Medical Education and Research, Chandigarh, India.
authors.forename: Divesh
authors.initials: D
authors.lastname: Sardana
authors.forename: Ashima
authors.initials: A
authors.lastname: Goyal
authors.forename: Krishan
authors.initials: K
authors.lastname: Gauba
mesh_terms: D044963:Biopsy, Fine-Needle / Q000379:methods; D002675:Child, Preschool; D019468:Disease Management; D015618:Histiocytosis, Sinus / Q000175:diagnosis / Q000473:pathology*; D006801:Humans; D008297:Male; D012008:Recurrence
keywords: Rosai-Dorfman disease; lymphadenopathy; massive; sinus histiocytosis