title: [Pulmonary reperfusion syndrome after pulmonary stent implants in a patient with vascular tortuosity syndrome].
abstract: Vascular tortuosity syndrome is a rare genetic disorder that causes tortuosity and stenosis of the pulmonary, systemic and / or coronary circulations. As a result of treatment of pulmonary stenosis, symptoms of pulmonary edema, known as lung reperfusion syndrome, may occur. The case is presented of an adolescent patient with vascular tortuosity syndrome who presented with a pulmonary reperfusion syndrome after multiple stent implants in the left pulmonary artery. After the procedure, the patient immediately developed an acute pulmonary edema with severe clinical deterioration, which required assistance with extracorporeal membrane oxygenation for recovery.
authors.affiliation: Servicio de Pediatría, Hospital Universitario 12 de Octubre, Madrid, España. Electronic address: mberenguer_p@hotmail.com.
authors.forename: M
authors.initials: M
authors.lastname: Berenguer Potenciano
authors.affiliation: Servicio de Pediatría, Hospital Universitario 12 de Octubre, Madrid, España.
authors.forename: S
authors.initials: S
authors.lastname: Piris Borregas
authors.affiliation: Instituto Pediátrico del Corazón, Hospital Universitario 12 de Octubre, Madrid, España.
authors.forename: A
authors.initials: A
authors.lastname: Mendoza Soto
authors.affiliation: Instituto Pediátrico del Corazón, Hospital Universitario 12 de Octubre, Madrid, España.
authors.forename: J M
authors.initials: JM
authors.lastname: Velasco Bayon
authors.affiliation: Servicio de Pediatría, Hospital Universitario 12 de Octubre, Madrid, España.
authors.forename: A
authors.initials: A
authors.lastname: Caro Barri
mesh_terms: D000293:Adolescent; D001158:Arteries / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D007593:Joint Instability / Q000601:surgery*; D008297:Male; D011183:Postoperative Complications / Q000209:etiology*; D011654:Pulmonary Edema / Q000209:etiology*; D012873:Skin Diseases, Genetic / Q000601:surgery*; D015607:Stents / Q000009:adverse effects*; D054079:Vascular Malformations / Q000601:surgery*; D014656:Vascular Surgical Procedures / Q000009:adverse effects*
keywords: Arterial tortuosity syndrome; Daño por reperfusión pulmonar; Edema pulmonar; Lung reperfusion injury; Pulmonary edema; Síndrome de tortuosidad vascular