title: Headache and the pseudotumor cerebri syndrome.
abstract: Pseudotumor cerebri syndrome (PTCS) refers to the primary and secondary disorders that cause elevated intracranial pressure without an intracranial mass lesion, ventriculomegaly, or central nervous system infection or malignancy. Headache is the most frequent symptom of PTCS, but there is considerable overlap between the headache features of raised intracranial pressure and the headache features of primary headache disorders. We review headache subtypes that occur in PTCS, non-headache features that help distinguish PTCS from other headache types, changes to the diagnostic criteria for PTCS with and without papilledema, and headache treatment strategies as they apply to PTCS.
authors.affiliation: Departments of Neurology and Ophthalmology, University of Pennsylvania, 51 N. 39th Street, Suite 501, Philadelphia, PA, 19104, USA, robert.mallery@uphs.upenn.edu.
authors.forename: Robert M
authors.initials: RM
authors.lastname: Mallery
authors.forename: Deborah I
authors.initials: DI
authors.lastname: Friedman
authors.forename: Grant T
authors.initials: GT
authors.lastname: Liu
mesh_terms: D000086:Acetazolamide / Q000627:therapeutic use; D001416:Back Pain / Q000209:etiology / Q000503:physiopathology* / Q000628:therapy; D003937:Diagnosis, Differential; D004232:Diuretics / Q000627:therapeutic use; D005632:Fructose / Q000031:analogs & derivatives / Q000627:therapeutic use; D005665:Furosemide / Q000627:therapeutic use; D020773:Headache Disorders / Q000209:etiology / Q000503:physiopathology* / Q000628:therapy; D006801:Humans; D019586:Intracranial Hypertension / Q000150:complications / Q000503:physiopathology* / Q000628:therapy; D008881:Migraine Disorders / Q000209:etiology / Q000503:physiopathology* / Q000628:therapy; D018696:Neuroprotective Agents / Q000627:therapeutic use; D010211:Papilledema / Q000150:complications / Q000503:physiopathology; D011559:Pseudotumor Cerebri / Q000150:complications / Q000503:physiopathology* / Q000628:therapy; D014012:Tinnitus / Q000209:etiology / Q000503:physiopathology; D000077236:Topiramate; D014786:Vision Disorders / Q000209:etiology / Q000503:physiopathology*; D061217:Weight Reduction Programs
chemical_list: D004232:Diuretics; D018696:Neuroprotective Agents; D000077236:Topiramate; D005632:Fructose; D005665:Furosemide; D000086:Acetazolamide
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