title: Otodental syndrome: a case presentation in a 6-year old child.
abstract: BACKGROUND
  Otodental syndrome is a rare condition characterised by globodontia, and sensorineural high frequency hearing loss. To date, only 20 cases of otodental syndrome have been reported.
  
  
  METHODS
  A 6 year-old girl presented with a chief complaint of delay in the eruption of primary canines. Following clinical, radiographic and audiologic evaluations, the patient was diagnosed with otodental syndrome.
  
  
  CONCLUSIONS
  Globodontia is a diagnostic feature of the otodental syndrome, which often provides the path to discovery of the associated hearing loss. Missing teeth, arch-size discrepancies, chewing problems and teething disturbances are the other major complications.
authors.affiliation: Başkent University Faculty of Dentistry, Paediatric Dentistry, Bağl?ca, Turkey.
authors.forename: S B
authors.initials: SB
authors.lastname: Cehreli
authors.affiliation: Deceased, Former Head Louisiana State University Health Sciences Center.
authors.forename: R B
authors.initials: RB
authors.lastname: Brannon
authors.affiliation: Louisiana State University Health Sciences Center, School of Dentistry, Department of Pediatric Dentistry.
authors.forename: R J
authors.initials: RJ
authors.lastname: Musselman
authors.affiliation: Başkent University Faculty of Dentistry, Paediatric Dentistry, Bağl?ca, Turkey.
authors.forename: R E
authors.initials: RE
authors.lastname: Tirali
authors.affiliation: Başkent University Faculty of Medicine, Department of Paediatrics, Bağl?ca, Turkey.
authors.forename: M
authors.initials: M
authors.lastname: Derbent
mesh_terms: D002648:Child; D002872:Chromosome Deletion; D025063:Chromosome Disorders / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000503:physiopathology; D002880:Chromosomes, Human, Pair 11 / Q000000981:diagnostic imaging; D003103:Coloboma / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000503:physiopathology; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000503:physiopathology; D006801:Humans; D011862:Radiography, Panoramic; D014071:Tooth Abnormalities / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000503:physiopathology