title: [Pheochromocytoma and paraganglioma in childhood: a report of 2 cases report].
abstract: Pheochromocytomas and paragangliomas are rare neuroendocrine tumors in children and most of them are sporadic. However, they represent the most common endocrine tumor in childhood, and hereditary tumor syndromes are most relevant in these age. Advances in genetic, biochemistry and imaging techniques have revised the management of these tumors; thus A biochemical study should be always initiated once the clinical diagnosis is suspected, followed by imaging and molecular studies, particularly in the context of known familial disease. The diagnostic and therapeutic features are reviewed after the presentation of two clinical cases, where the second one is a patient with type 1 Neurofibromatosis.
authors.affiliation: Servicio de Pediatría, Unidad de Oncología Pediátrica, Complejo Hospitalario de Navarra, Pamplona, Navarra, España. Electronic address: arantxamosquera@hotmail.com.
authors.forename: A
authors.initials: A
authors.lastname: Mosquera Gorostidi
authors.affiliation: Servicio de Pediatría, Unidad de Oncología Pediátrica, Complejo Hospitalario de Navarra, Pamplona, Navarra, España.
authors.forename: A
authors.initials: A
authors.lastname: Justo Ranera
authors.affiliation: Servicio de Pediatría, Unidad de Oncología Pediátrica, Complejo Hospitalario de Navarra, Pamplona, Navarra, España.
authors.forename: S E
authors.initials: SE
authors.lastname: Zakirian Denis
authors.affiliation: Servicio de Pediatría, Unidad de Oncología Pediátrica, Complejo Hospitalario de Navarra, Pamplona, Navarra, España.
authors.forename: N
authors.initials: N
authors.lastname: González Temprano
authors.affiliation: Servicio de Pediatría, Unidad de Oncología Pediátrica, Complejo Hospitalario de Navarra, Pamplona, Navarra, España.
authors.forename: M
authors.initials: M
authors.lastname: Sagaseta de Ilúrdoz Uranga
authors.affiliation: Servicio de Pediatría, Unidad de Oncología Pediátrica, Complejo Hospitalario de Navarra, Pamplona, Navarra, España.
authors.forename: J
authors.initials: J
authors.lastname: Molina Garicano
mesh_terms: D000293:Adolescent; D000310:Adrenal Gland Neoplasms / Q000175:diagnosis / Q000628:therapy; D005260:Female; D006801:Humans; D010235:Paraganglioma / Q000175:diagnosis / Q000628:therapy; D010673:Pheochromocytoma / Q000175:diagnosis / Q000628:therapy
keywords: Catecholamines; Catecolaminas; Children; Feocromocitoma; Metanefrinas; Metanephrines; Paraganglioma; Pediátricos; Pheochromocytoma