title: [Mid-aortic syndrome in 2-year old boy presenting with severe left ventricular dysfunction; report of a case].
abstract: Mid aortic syndrome is uncommon acquired or congenital condition characterized by segmental narrowing of the abdominal or distal descending thoracic aorta. If left untreated, it result in life threatening complications. We described the case of 2-year-old boy admitted to our hospital for hypertension and heart failure. Diagnosis of mid aortic syndrome was made with severe stenosis in distal descending aorta. With consideration of growth, we avoided bypass grafting and implantation with prothesic graft. For severe adhesion, we performed patch aortoplasty with 0.4 mm expanded polytetrafluoroethylene (ePTFE) patch. Postoperative course was unevetful. His blood pressure and left ventricular function was normalized. He was discharged on the 20st day after the surgery.
authors.affiliation: Department of Cardiovascular Surgery, Saitama Children's Medical Center, Saitama, Japan.
authors.forename: Kouichi
authors.initials: K
authors.lastname: Muramatsu
authors.forename: Gen
authors.initials: G
authors.lastname: Shinohara
authors.forename: Koji
authors.initials: K
authors.lastname: Nomura
mesh_terms: D001013:Aorta, Thoracic / Q000601:surgery; D001018:Aortic Diseases / Q000150:complications / Q000601:surgery*; D001024:Aortic Valve Stenosis / Q000601:surgery; D002675:Child, Preschool; D003251:Constriction, Pathologic; D006801:Humans; D008297:Male; D014656:Vascular Surgical Procedures; D018754:Ventricular Dysfunction / Q000150:complications*