title: Subcutaneous panniculitis like T cell lymphoma associated with erythromelalgia.
abstract: Erythromelalgia is a rare disorder that simulates a small fiber neuropathy and patients often have painful erythematous extremities during episodes. It is of two types: A primary or inherited form that is sometimes associated with a Na channel mutation or a secondary disorder associated with an underlying systemic disorder. We present a 19-year-old boy who presented to us with erythromelalgia and a febrile illness with systemic rash. Detailed work-up revealed another unusual condition: Subcutaneous panniculitis like T cell lymphoma (SPTCL). This is the first report of an association of erythromelalgia with SPTCL.
authors.affiliation: Department of Rheumatology, Lourdes Hospital, Kochi, Kerala, India.
authors.forename: J
authors.initials: J
authors.lastname: Thomas
authors.forename: B V
authors.initials: BV
authors.lastname: Maramattom
authors.forename: P M
authors.initials: PM
authors.lastname: Kuruvilla
authors.forename: J
authors.initials: J
authors.lastname: Varghese
mesh_terms: D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D003520:Cyclophosphamide / Q000627:therapeutic use; D003937:Diagnosis, Differential; D004317:Doxorubicin / Q000627:therapeutic use; D004916:Erythromelalgia / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D005076:Exanthema / Q000209:etiology; D006801:Humans; D016399:Lymphoma, T-Cell / Q000175:diagnosis* / Q000188:drug therapy / Q000191:economics; D008297:Male; D015434:Panniculitis / Q000175:diagnosis* / Q000188:drug therapy / Q000191:economics; D011241:Prednisone / Q000627:therapeutic use; D012878:Skin Neoplasms / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D012883:Skin Ulcer / Q000209:etiology; D016896:Treatment Outcome; D014750:Vincristine / Q000627:therapeutic use; D055815:Young Adult
chemical_list: D014750:Vincristine; D004317:Doxorubicin; D003520:Cyclophosphamide; D011241:Prednisone