title: Persistent mullerian duct syndrome: A case report and review of the literature.
abstract: Persistent mullerian duct syndrome (PMDS) is usually an accidental finding either during orchipexy or during routine inguinal hernia repair in male patients presenting with maldescended or crytorchid testes. It is caused by a defect in the mullerian inhibiting substance system. Intraoperatively, mullerian remnants consisting of an infantile uterus and fallopian tubes are usually found. Familiarity with PMDS is necessary to diagnose the condition. We report a case of PMDS in a 14-year-old male presenting with bilateral undescended testes.
authors.affiliation: Department of Pathology, PES Institute of Medical Sciences and Research, Kuppam, Andhra Pradesh, India.
authors.forename: Vaibhav J
authors.initials: VJ
authors.lastname: Nayak
authors.affiliation: Department of Pathology, PES Institute of Medical Sciences and Research, Kuppam, Andhra Pradesh, India.
authors.forename: Akshatha S
authors.initials: AS
authors.lastname: Kamath
authors.affiliation: BGS Global Hospitals, Bangalore, Karnataka, India.
authors.forename: Manjunath Hanumanthappa
authors.initials: MH
authors.lastname: Krishnappa
authors.affiliation: Department of Pathology, PES Institute of Medical Sciences and Research, Kuppam, Andhra Pradesh, India.
authors.forename: Sunil Kumar
authors.initials: SK
authors.lastname: Bylappa
keywords: Hernia uteri inguinale; mullerian inhibiting substance; mullerian remnants; persistent mullerian duct syndrome