title: Spinal intradural extramedullary cavernous angioma presenting with superficial siderosis and hydrocephalus: a case report and review of the literature.
abstract: A 36-year-old man with progressive hearing impairment visited our hospital complaining of a severe headache. A neurological examination revealed bilateral sensorineural hearing impairment, mild ataxia, hyperreflexia and mild cognitive dysfunction. Brain MRI demonstrated hydrocephalus and typical hypointensity rimming the brain surface on T2(*)-weighted images. The patient was diagnosed as having superficial siderosis. Spinal MRI disclosed the presence of a lumbar intradural extramedullary mass. The surgically resected tumor was histologically found to be a cavernous angioma. Superficial siderosis is an important cause of hearing loss. With respect to the detection of disorders underlying this pathological condition, MRI examinations, including those of the brain and whole spinal cord, are recommended.
authors.affiliation: Department of Neurology and Rheumatology, Shinshu University School of Medicine, Japan.
authors.forename: Nagaaki
authors.initials: N
authors.lastname: Katoh
authors.forename: Takuhiro
authors.initials: T
authors.lastname: Yoshida
authors.forename: Takeshi
authors.initials: T
authors.lastname: Uehara
authors.forename: Kiyoshi
authors.initials: K
authors.lastname: Ito
authors.forename: Kazuhiro
authors.initials: K
authors.lastname: Hongo
authors.forename: Shu-ichi
authors.initials: S
authors.lastname: Ikeda
mesh_terms: D000328:Adult; D006319:Hearing Loss, Sensorineural / Q000209:etiology; D006392:Hemangioma, Cavernous / Q000150:complications* / Q000473:pathology*; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology*; D008279:Magnetic Resonance Imaging; D008297:Male; D012806:Siderosis / Q000209:etiology* / Q000473:pathology; D013116:Spinal Cord / Q000473:pathology*