title: Epidermal nevus syndrome and dysplatic kidney disease.
abstract: Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with Wilms' tumor. According to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders.
authors.affiliation: Department of Pediatric Nephrology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran. anickavar@yahoo.com.
authors.forename: Azar
authors.initials: A
authors.lastname: Nickavar
authors.affiliation: Department of Dermatology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran. anickavar@yahoo.com.
authors.forename: Najmessadat
authors.initials: N
authors.lastname: Atefi
authors.affiliation: Department of Pathology, Razi Dermatology Hospital, Tehran University of Medical Sciences, Tehran, Iran. anickavar@yahoo.com.
authors.forename: Kambiz
authors.initials: K
authors.lastname: Kamyab Hesari
mesh_terms: D002675:Child, Preschool; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology*; D008297:Male; D021782:Multicystic Dysplastic Kidney / Q000503:physiopathology*; D009506:Nevus / Q000473:pathology; D013577:Syndrome; D009396:Wilms Tumor / Q000473:pathology*