title: [Pelvic inflammatory disease due to Herlyn-Werner-Wunderlich syndrome].
abstract: BACKGROUND
  Herlyn-Werner-Wunderlich syndrome is a congenital urogenital malformation that is associated with a uterus didelphys and a longitudinal vaginal septum, resulting in a blind hemivagina and ipsilateral renal agenesis. Clinical presentation is highly variable, delaying diagnosis and leading to important complications.
  
  
  METHODS
  We present the case of a 13-year-old female who was diagnosed with Herlyn-Werner-Wunderlich syndrome following an acute abdomen due to a right tubo-ovarian abscess. She had a vaginal septum giving rise to a right blind hemivagina. It was microperforated, causing intermittent genital bleeding. This hematocolpos was colonized by microorganisms that ascended to the pelvic cavity, causing right tuboovarian abscess. Nuclear magnetic resonance imaging provided theWernermost diagnostic information. We performed a vaginal septum resection, and both hemiuteros communicated with a single vagina, resulting in an asymptomatic patient.
  
  
  CONCLUSIONS
  Herlyn-Werner-Wunderlich syndrome is a little known entity and can be presented atypically, resulting in diagnostic difficulty and treatment delay. It is important to be aware of this syndrome in order to avoid irreversible complications.
authors.affiliation: Servicio de Ginecología y Obstetricia del Hospital General Universitario de Ciudad Real, Ciudad Real, Spain. trini17med@hotmail.com.
authors.forename: Maria Trinidad
authors.initials: MT
authors.lastname: Alumbreros-Andújar
authors.affiliation: Servicio de Ginecología y Obstetricia del Hospital General Universitario de Ciudad Real, Ciudad Real, Spain.
authors.forename: Esther Vanesa
authors.initials: EV
authors.lastname: Aguilar-Galán
authors.affiliation: Servicio de Ginecología y Obstetricia del Hospital General Universitario de Ciudad Real, Ciudad Real, Spain.
authors.forename: Celia
authors.initials: C
authors.lastname: Pérez-Parra
authors.affiliation: Servicio de Ginecología y Obstetricia del Hospital General Universitario de Ciudad Real, Ciudad Real, Spain.
authors.forename: Carmen
authors.initials: C
authors.lastname: Céspedes-Casas
authors.affiliation: Servicio de Ginecología y Obstetricia del Hospital General Universitario de Ciudad Real, Ciudad Real, Spain.
authors.forename: Mercedes
authors.initials: M
authors.lastname: Ramírez-Gómez
authors.affiliation: Servicio de Ginecología y Obstetricia del Hospital General Universitario de Ciudad Real, Ciudad Real, Spain.
authors.forename: Ana
authors.initials: A
authors.lastname: González-López
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000196:embryology / Q000601:surgery; D000038:Abscess / Q000209:etiology; D000293:Adolescent; D005184:Fallopian Tube Diseases / Q000209:etiology; D005260:Female; D006399:Hematocolpos / Q000209:etiology; D006801:Humans; D007668:Kidney / Q000002:abnormalities* / Q000196:embryology; D008279:Magnetic Resonance Imaging; D009095:Mullerian Ducts / Q000002:abnormalities / Q000473:pathology; D010049:Ovarian Diseases / Q000209:etiology; D000292:Pelvic Inflammatory Disease / Q000209:etiology*; D013577:Syndrome; D014599:Uterus / Q000002:abnormalities* / Q000196:embryology; D014621:Vagina / Q000002:abnormalities* / Q000196:embryology / Q000601:surgery
keywords: Herlyn-Wener-Wunderlich; OHVIRA; hematocolpos