title: Anaesthesia for emergency ventriculo-peritoneal shunt in an adolescent with Noonan's syndrome.
abstract: A 15-year-old boy with Noonan's syndrome was admitted for emergency ventriculo-peritoneal shunt. Intraoperative course was complicated by hypertensive urgency, which was effectively managed with high doses of esmolol (500 μg/kg/min). Difficult airway was anticipated due to presence of webbed neck and facial dysmorphism. Tracheal intubation was however successfully accomplished with the aid of a bougie. This report thus highlights the unique anaesthetic problems encountered during anaesthetic management of such a case, which is worth sharing.
authors.affiliation: Department of Anaesthesia and Intensive Care, Lady Hardinge Medical College, New Delhi, India.
authors.forename: Tanvir
authors.initials: T
authors.lastname: Samra
authors.affiliation: Department of Anaesthesia and Intensive Care, Ram Manohar Lohia Hospital, New Delhi, India.
authors.forename: Neerja
authors.initials: N
authors.lastname: Banerjee
keywords: Hypertension; Noonan syndrome; hypertrophic cardiomyopathy; paediatric anaesthesia; scoliosis