title: Christ-Siemens-Touraine Syndrome with Self-mutilation Habit: An Unusual Presentation.
abstract: Ectodermal dysplasia exhibits a classic triad of hypohidrosis, hypotrichosis, and hypodontia. Self- mutilation could be due to organic or functional causes. The occurrence of selfmutilation with functional cause represents a diagnostic challenge to practitioners. In most of the instances dentists are the first to recognize patient with ectodermal dysplasia as they report primarily with a complaint of missing teeth. The most common type is hypohidrotic ectodermal dysplasia (Christ-Siemens-Touraine syndrome). A thorough knowledge of this disease with multidisciplinary approach aids in successful outcome of the treatment. This is an unusual case report of Christ-Siemens-Touraine syndrome with selfmutilation.
authors.affiliation: Assistant Professor.
authors.forename: Gurusamy
authors.initials: G
authors.lastname: Kayalvizhi
authors.affiliation: Assistant Professor, Department of Pedodontics and Preventive Dentistry, MR Ambedkar Dental College, Bangalore-560005 Karnataka, India.
authors.forename: R
authors.initials: R
authors.lastname: Neeraja
keywords: Christ-Siemens-Touraine syndrome; Ectodermal dysplasia; Hypodontia; Hypohidrotic; Prosthetic treatment.; Self- mutilation