title: Septum primum atrial septal defect in an infant with hypoplastic left heart syndrome.
abstract: Hypoplastic left heart syndrome (HLHS) is a form of congenital heart disease characterized by severe underdevelopment of the left heart, leading to inadequate systemic blood flow. Several different atrial septal morphologies are observed in HLHS, most commonly a secundum atrial septal defect, patent foramen ovale, intact septum, and leftward displacement of the superior attachment of the septum primum. It has been postulated that atrial septal development is associated with the development of the left heart. We present a case of a newborn infant with HLHS and the unusual finding of a primum ASD.
authors.affiliation: Division of Pediatric Cardiology, Mayo Clinic, Rochester, Minnesota, USA.
authors.forename: Robert W
authors.initials: RW
authors.lastname: Loar
authors.affiliation: Division of Cardiovascular Surgery, Mayo Clinic, Rochester, Minnesota, USA.
authors.forename: Harold M
authors.initials: HM
authors.lastname: Burkhart
authors.affiliation: Division of Pediatric Cardiology, Mayo Clinic, Rochester, Minnesota, USA.
authors.forename: Nathaniel W
authors.initials: NW
authors.lastname: Taggart
mesh_terms: D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging* / Q000601:surgery*; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000000981:diagnostic imaging* / Q000601:surgery*; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000000981:diagnostic imaging* / Q000601:surgery*; D007231:Infant, Newborn; D016896:Treatment Outcome; D014463:Ultrasonography