title: Factor XIII deficiency in Henoch-Schönlein purpura - report on two cases and literature review.
abstract: Factor XIII (FXIII) deficiency is a rare, inherited or acquired coagulation disorder that potentially precipitates fatal haemorrhage. We report two consecutive pediatric patients with Henoch-Schönlein purpura (HSP) and symptomatic decrease in FXIII. The possible FXIII deficiency should be kept in mind by every doctor taking care of patients with HSP, in spite of normal value of routine coagulation tests.
authors.affiliation: Department of Pediatrics, Oncology, Hematology and Diabetology, Medical university of Lodz, 36/50 Sporna St. 91-738 Lodz, Poland, phone +48 505-979-152, +48 42 617-77-50, fax: +48 42 617 77 98, e-mail: anna.hogendorf@gmail.com.
authors.forename: Anna
authors.initials: A
authors.lastname: Hogendorf
authors.forename: Wojciech
authors.initials: W
authors.lastname: Młynarski
mesh_terms: D015746:Abdominal Pain / Q000209:etiology; D002648:Child; D002675:Child, Preschool; D005177:Factor XIII Deficiency / Q000150:complications* / Q000175:diagnosis*; D005260:Female; D006470:Hemorrhage / Q000209:etiology; D006801:Humans; D011695:IgA Vasculitis / Q000150:complications*; D008297:Male