title: Hallervorden-Spatz syndrome: a rare cause of extrapyramidal manifestations.
abstract: Hallervorden-Spatz syndrome is a rare neurodegenerative disease of autosomal recessive inheritance which presents in childhood or early adulthood with dystonia, dysarthria, rigidity and choreoathetosis. Here we present an unusual case of atypical Hallervorden-Spatz syndrome with onset during adolescence and rapid progression in a young female patient who showed the characteristic "eye of the tiger" appearance on magnetic resonance imaging [MRI] of brain. This reporting intends to highlight Hallervorden-Spatz syndrome as a rare cause of extrapyramidal manifestations and the interesting radiologic picture of the disease.
authors.affiliation: Department of General Medicine, JIPMER, Dhanvantarinagar, Puducherry- 605 006, INDIA.
authors.forename: Kv
authors.initials: K
authors.lastname: Vinod
authors.affiliation: Department of General Medicine, JIPMER, Dhanvantarinagar, Puducherry- 605 006, INDIA.
authors.forename: S
authors.initials: S
authors.lastname: Giridharan
authors.affiliation: Department of General Medicine, JIPMER, Dhanvantarinagar, Puducherry- 605 006, INDIA.
authors.forename: Tk
authors.initials: T
authors.lastname: Dutta
keywords: dystonia; extrapyramidal; eye of the tiger; neurodegeneration; pantothenate kinase 2