title: Upper respiratory system involvement as the only manifestation of granulomatosis with polyangiitis in a child with marfan phenotype.
abstract: We report a 9-year old girl with an unusual presentation of granulomatosis with polyangiitis in association with Marfan phenotype. The patient presented with recurrent sinusitis, epistaxis, hearing loss and hyperplastic gingivitis, without any signs or symptoms of major organ involvement.
authors.affiliation: Department of Allergy and Clinical Immunology, Namazi Hospital, Shiraz University of Medical Sciences, Shiraz, Iran.
authors.forename: Reza
authors.initials: R
authors.lastname: Amin
authors.affiliation: Department of Allergy and Clinical Immunology, Namazi Hospital, Shiraz University of Medical Sciences, Shiraz, Iran.
authors.forename: Soheila
authors.initials: S
authors.lastname: Alyasin
authors.affiliation: Department of Allergy and Clinical Immunology, Namazi Hospital, Shiraz University of Medical Sciences, Shiraz, Iran.
authors.forename: Tooba
authors.initials: T
authors.lastname: Momen
authors.affiliation: Department of Allergy and Clinical Immunology, Namazi Hospital, Shiraz University of Medical Sciences, Shiraz, Iran.
authors.forename: Maryam
authors.initials: M
authors.lastname: Khoshkhouy
authors.affiliation: Department of Allergy and Clinical Immunology, Namazi Hospital, Shiraz University of Medical Sciences, Shiraz, Iran.
authors.forename: Sepideh
authors.initials: S
authors.lastname: Darougar
keywords: Epistaxis; Granulomatosis with Polyangiitis; Hyperplastic gingivitis; Marfan Syndrome; Sinusitis