title: Perirenal lymphangiomatosis.
abstract: Lymphangioma is a rare, benign mesenchymal neoplasm, which is characterized by numerous intercommunicating cystic spaces containing lymphatic fluid. It is considered a congenital disease resulting from the obstruction of regional lymph drainage during the developmental period. Lymphangioma may be focal/unilateral or diffuse/bilateral, and in the latter case, it is referred to as lymphangiomatosis. Here, we report a case of a 38-year-old man with perirenal lymphangiomatosis. The patient's chief complaint was left flank pain, and left pleural effusion was found on radiological examination. After radical nephrectomy, the pathological examinations revealed that the kidney was enclosed by a multicystic mass with intrarenal cystic dilatations. We report the case and discuss the management of perirenal lymphangiomatosis with a literature review.
authors.affiliation: Department of Urology, Pusan National University Hospital, Busan, Korea.
authors.forename: Tae Gyeong
authors.initials: TG
authors.lastname: Jeon
authors.affiliation: Department of Urology, Pusan National University Hospital, Busan, Korea.
authors.forename: Do Hoon
authors.initials: do H
authors.lastname: Kong
authors.affiliation: Department of Urology, Pusan National University Hospital, Busan, Korea.
authors.forename: Hyun Jun
authors.initials: HJ
authors.lastname: Park
authors.affiliation: Department of Radiology, Pusan National University Hospital, Busan, Korea.
authors.forename: Suk
authors.initials: S
authors.lastname: Kim
authors.affiliation: Department of Pathology, Pusan National University Hospital, Busan, Korea.
authors.forename: Won Young
authors.initials: WY
authors.lastname: Park
authors.affiliation: Department of Urology, Dong-A University Medical Center, Busan, Korea.
authors.forename: Soo Dong
authors.initials: SD
authors.lastname: Kim
authors.affiliation: Department of Urology, Pusan National University Hospital, Busan, Korea.
authors.forename: Hong Koo
authors.initials: HK
authors.lastname: Ha
keywords: Kidney; Lymphangioma; Lymphatic diseases; Neoplasms