title: Cord compression due to extradural thoracic nerve root hemangioblastoma.
abstract: Hemangioblastomas (HGBs) are benign tumors that occur sporadically or as part of von Hippel-Lindau (VHL) disease. 6-8% of spinal HGBs are extramedullary in location, and basically referred to as HGB of the spinal nerve root. Purely extradural (ED) location is the rarest form of these tumors. We report a case of a non-VHL patient with large thoracic ED HGB, who presented with myelopathy due to cord compression. We emphasize the importance of correct pre-operative diagnosis as well as pre-operative embolization in order to reach the goal of complete tumor resection with minimal complications. We also review the relevant literature and summarize the few case reports of this unique tumor.
authors.affiliation: Department of Neurosurgery, Beilinson Hospital, Rabin Medical Center , Petah Tiqva , Israel.
authors.forename: Yosef
authors.initials: Y
authors.lastname: Laviv
authors.forename: Zvi Harry
authors.initials: ZH
authors.lastname: Rappaport
mesh_terms: D000368:Aged; D005260:Female; D018325:Hemangioblastoma / Q000150:complications* / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D006801:Humans; D013117:Spinal Cord Compression / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D013126:Spinal Nerve Roots / Q000601:surgery*; D013900:Thoracic Nerves / Q000473:pathology; D016896:Treatment Outcome; D006623:von Hippel-Lindau Disease / Q000150:complications / Q000175:diagnosis / Q000601:surgery*
keywords: embolization; spinal cord compression; spinal tumor; thoracic spine