title: Upper urinary tract abnormalities: a case of bilateral kidneys within a left-sided omphalocele.
abstract: Children with omphalocele, exstrophy, imperforate anus, and spinal defects complex present with the most severe form of birth defects in the exstrophy-epispadias spectrum. Prenatal diagnosis is difficult, but improved survival over the past several decades makes understanding the potential anatomic manifestations imperative for expeditious and appropriate surgical care. The upper urinary tract is often normal in children with omphalocele, exstrophy, imperforate anus, and spinal defects complex, but malposition of one of the kidneys has previously been reported. We present the first case of bilateral kidney herniation into the omphalocele sac.
authors.affiliation: Division of Urology, Department of Surgery, Tripler Army Medical Center, Honolulu, HI. Electronic address: Raffaella.Derosa.mil@mail.mil.
authors.forename: Raffaella
authors.initials: R
authors.lastname: DeRosa
authors.affiliation: Department of Urologic Oncology, Memorial Sloan Kettering Cancer Center, New York, NY; Urology Service, Department of Surgery, New York, NY.
authors.forename: John E
authors.initials: JE
authors.lastname: Musser
authors.affiliation: Department of Radiology, Tripler Army Medical Center, Honolulu, HI.
authors.forename: Veronica J
authors.initials: VJ
authors.lastname: Rooks
authors.affiliation: Department of Radiology, Womack Army Medical Center, Fort Bragg, NC.
authors.forename: John
authors.initials: J
authors.lastname: McPherson
authors.affiliation: Division of Urology, Department of Surgery, Tripler Army Medical Center, Honolulu, HI.
authors.forename: Leah P
authors.initials: LP
authors.lastname: McMann
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis; D001006:Anus, Imperforate / Q000150:complications; D017809:Fatal Outcome; D006554:Hernia, Umbilical / Q000150:complications*; D006801:Humans; D007231:Infant, Newborn; D007668:Kidney / Q000002:abnormalities*; D013116:Spinal Cord / Q000002:abnormalities; D014551:Urinary Tract / Q000002:abnormalities*