title: Percutaneous device occlusion of hepatocardiac venous collateral via left transhepatic access in a patient with heterotaxy syndrome following Fontan procedure.
abstract: Venovenous collateral vessels are a common cause for desaturation in patients who have undergone a Fontan procedure. We describe a patient with heterotaxy syndrome (leftward pointing apex) and complex single ventricle with Fontan physiology that was desaturated due to a hepatocardiac vein. The vessel was entered via a left transhepatic access and was successfully occluded using an Amplatzer Vascular Plug.
authors.affiliation: Department of Cardiology, Cook Children's Medical Center, Fort Worth, Texas.
authors.forename: James A
authors.initials: JA
authors.lastname: Kuo
mesh_terms: D000293:Adolescent; D006328:Cardiac Catheterization / Q000295:instrumentation*; D003097:Collateral Circulation; D004621:Embolization, Therapeutic / Q000295:instrumentation*; D004867:Equipment Design; D005260:Female; D018729:Fontan Procedure / Q000009:adverse effects*; D006325:Heart Atria; D006503:Hepatic Veins; D059446:Heterotaxy Syndrome / Q000601:surgery*; D006801:Humans; D011183:Postoperative Complications; D055989:Septal Occluder Device
keywords: Fontan procedure; cyanosis; therapeutic embolization