title: ALCAPA and massive pulmonary atelectasis: how a stent in the airway can be life-saving.
abstract: Anomalous left coronary artery from pulmonary artery (ALCAPA) is a rare congenital anomaly in which left coronary artery arises from the pulmonary artery resulting in progressive myocardial ischemia and dysfunction of the left ventricle. We report a case of ALCAPA with severe cardiac and respiratory failure and huge heart dilation compressing the left main bronchus and preventing from an effective ventilation. Emergency bronchial stenting allowed to improve left lung atelectasis, reduce pulmonary hypertension, resume anterograde left coronary artery perfusion and stabilize cardiovascular conditions to undertake a successful surgical correction.
authors.affiliation: Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy. Electronic address: p.serio@meyer.it.
authors.forename: Paola
authors.initials: P
authors.lastname: Serio
authors.affiliation: Pediatric Cardiology Unit, Meyer Children Hospital, Florence, Italy.
authors.forename: Enrico
authors.initials: E
authors.lastname: Chiappa
authors.affiliation: Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy; Department of Paediatrics, Parma Children Hospital, Parma, Italy.
authors.forename: Valentina
authors.initials: V
authors.lastname: Fainardi
authors.affiliation: Pediatric Cardiology Unit, Meyer Children Hospital, Florence, Italy.
authors.forename: Silvia
authors.initials: S
authors.lastname: Favilli
authors.affiliation: Pediatric Cardiac Surgery, Heart Hospital, G. Monasterio Tuscany Foundation, Massa, Italy.
authors.forename: Bruno
authors.initials: B
authors.lastname: Murzi
authors.affiliation: Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy.
authors.forename: Roberto
authors.initials: R
authors.lastname: Baggi
authors.affiliation: Pediatric Cardiac Surgery, Heart Hospital, G. Monasterio Tuscany Foundation, Massa, Italy.
authors.forename: Luigi
authors.initials: L
authors.lastname: Arcieri
authors.affiliation: Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy; Department of Anesthesia and Intensive Care, Ospedale Riuniti di Foggia, Foggia, Italy.
authors.forename: Roberto
authors.initials: R
authors.lastname: Leone
authors.affiliation: Respiratory Endoscopy Unit, Department of Paediatric Anesthesia and Intensive Care, Meyer Children Hospital, Florence, Italy.
authors.forename: Lorenzo
authors.initials: L
authors.lastname: Mirabile
mesh_terms: D063748:Bland White Garland Syndrome / Q000150:complications*; D001980:Bronchi; D005260:Female; D006333:Heart Failure / Q000209:etiology / Q000628:therapy*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology / Q000628:therapy; D007223:Infant; D001261:Pulmonary Atelectasis / Q000209:etiology / Q000628:therapy*; D012131:Respiratory Insufficiency / Q000209:etiology / Q000628:therapy*; D015607:Stents
keywords: Airway stent; Alcapa syndrome; Atelectasis; Cardiac arrest; Respiratory distress; Stent