title: Pediatric split liver transplantation after Fontan procedure in left isomerism combined with biliary atresia: a case report.
abstract: LI is a subset of the heterotaxy syndrome and a rare birth defect that involves the heart and other organs. It can be combined with extracardiac abnormalities, especially BA. CHD can be associated with LI in up to 15% of cases, although it is rare in BA. Pediatric LT for a child with ESLD due to BA combined with LI and CHD is a challenging issue for a transplant surgeon. Herein, we report a successful split LT on a three-yr-old boy with LI who survived after a Fontan procedure due to single ventricle, but who suffered from HPS associated with BA.
authors.affiliation: Department of Surgery, Seoul National University College of Medicine, Seoul, Korea.
authors.forename: Joong Kee
authors.initials: JK
authors.lastname: Youn
authors.forename: Jeong-Moo
authors.initials: JM
authors.lastname: Lee
authors.forename: Nam-Joon
authors.initials: NJ
authors.lastname: Yi
authors.forename: Young Rok
authors.initials: YR
authors.lastname: Choi
authors.forename: Suk-Won
authors.initials: SW
authors.lastname: Suh
authors.forename: Tae
authors.initials: T
authors.lastname: You
authors.forename: Kwang-Woong
authors.initials: KW
authors.lastname: Lee
authors.forename: Chul-Woo
authors.initials: CW
authors.lastname: Jung
authors.forename: Ji-Won
authors.initials: JW
authors.lastname: Lee
authors.forename: Eun-Jung
authors.initials: EJ
authors.lastname: Bae
authors.forename: Jae Sung
authors.initials: JS
authors.lastname: Ko
authors.forename: Woong-Han
authors.initials: WH
authors.lastname: Kim
authors.forename: Kwi-Won
authors.initials: KW
authors.lastname: Park
authors.forename: Kyung-Suk
authors.initials: KS
authors.lastname: Suh
mesh_terms: D001656:Biliary Atresia / Q000150:complications / Q000601:surgery*; D002675:Child, Preschool; D018729:Fontan Procedure; D020065:Hepatopulmonary Syndrome / Q000209:etiology / Q000601:surgery; D059446:Heterotaxy Syndrome / Q000601:surgery*; D006801:Humans; D016031:Liver Transplantation / Q000379:methods*; D008297:Male
keywords: Fontan operation; biliary atresia; hepatopulmonary syndrome; left isomerism; liver transplantation