title: Persistent primitive hepatic venous plexus with Scimitar syndrome: description of a case and review of the literature.
abstract: Persistent primitive hepatic venous plexus is an anomaly of the systemic venous return characterised by postnatal persistence of the foetal intrahepatic venous drainage. Scimitar syndrome is a condition that consists of partial anomalous pulmonary venous return of the right pulmonary venous drainage into the systemic veins, associated with pulmonary artery hypoplasia with the underdeveloped right lung, pulmonary sequestration, and cardiac malposition. Both conditions are rare and together have been rarely described in the literature. We report the first case of this combination of lesions imaged by cardiac magnetic resonance imaging with a three-dimensional reconstruction and reviewed the literature to characterise this uncommon combination.
authors.affiliation: Department of Pediatrics,Division of Pediatric Cardiology,University of Iowa Children's Hospital,Carver College of Medicine,Iowa City,Iowa,United States of America.
authors.forename: M Santiago
authors.initials: MS
authors.lastname: Restrepo
authors.affiliation: Department of Pediatrics,Division of Pediatric Cardiology,University of Iowa Children's Hospital,Carver College of Medicine,Iowa City,Iowa,United States of America.
authors.forename: Osamah
authors.initials: O
authors.lastname: Aldoss
authors.affiliation: Department of Pediatrics,Division of Pediatric Cardiology,University of Iowa Children's Hospital,Carver College of Medicine,Iowa City,Iowa,United States of America.
authors.forename: Benton
authors.initials: B
authors.lastname: Ng
mesh_terms: D000015:Abnormalities, Multiple; D006328:Cardiac Catheterization; D004452:Echocardiography; D005260:Female; D006503:Hepatic Veins / Q000002:abnormalities*; D006801:Humans; D008279:Magnetic Resonance Imaging; D013902:Radiography, Thoracic; D012587:Scimitar Syndrome / Q000175:diagnosis*; D055815:Young Adult
keywords: Persistent primitive hepatic venous plexus; Scimitar syndrome; partial anomalous pulmonary venous return