title: Primary Pulmonary Ewing's Sarcoma: Rare Cause of Superior Vena Cava Syndrome in Children.
abstract: Ewing's sarcoma is a common malignant bone tumour presenting in children and young adults. Rarely extra- skeletal soft tissues and visceral organs can also be the site of origin of Ewing's sarcoma. Primary pulmonary Ewing's sarcoma is an extremely rare malignancy which occurs in the paediatric population. We report an unusual case of primary pulmonary Ewing's sarcoma in a nine year old girl who presented with features of superior vena cava syndrome in the emergency department. The diagnosis was confirmed pathologically both by light microscopy and immunohistochemistry. The patient was put on chemotherapy and surgery was planned but the patient expired within three days of starting chemotherapy.
authors.affiliation: Associate Professor, Department of Radiology, Dr. Ram Manohar Lohia Hospital and PGIMER , New Delhi, India .
authors.forename: Shibani
authors.initials: S
authors.lastname: Mehra
authors.affiliation: Senior Resident, Department of Radiology, Dr. Ram Manohar Lohia Hospital and PGIMER , New Delhi, India .
authors.forename: Swapndeep Singh
authors.initials: SS
authors.lastname: Atwal
authors.affiliation: Professor and Head of Department, Department of Radiology, Dr. Ram Manohar Lohia Hospital and PGIMER , New Delhi, India .
authors.forename: Umesh Chandra
authors.initials: UC
authors.lastname: Garga
keywords: Children; Ewing’s sarcoma; Pulmonary; Superior vena cava (SVC) syndrome