title: Liver fibrosis in primary intestinal lymphangiectasia: An undervalued topic.
abstract: The relationship between primary intestinal lymphangiectasia (PIL) and liver fibrosis is an emerging topic with many obscure aspects due to the rarity of the disorder. A recent paper reported that a six-month low-fat diet improved liver fibrosis. We report the case of a 17-year-old girl affected by PIL whose hepatic fibrosis progressively worsened within one year, despite dietetic support. This and the previous case report describe extraordinary events, which do not allow clear-cut clinical aspects to be established. Nevertheless, both cases suggest that in patients with PIL, it is necessary to closely monitor liver morphology with in-depth investigations including not only ultrasonography, but also elastography.
authors.affiliation: Raffaele Licinio, Mariabeatrice Principi, Enzo Ierardi, Alfredo Di Leo, Gastroenterology Unit, Department of Emergency and Organ Transplantation, University of Bari, Cesare, 70124 Bari, Italy.
authors.forename: Raffaele
authors.initials: R
authors.lastname: Licinio
authors.affiliation: Raffaele Licinio, Mariabeatrice Principi, Enzo Ierardi, Alfredo Di Leo, Gastroenterology Unit, Department of Emergency and Organ Transplantation, University of Bari, Cesare, 70124 Bari, Italy.
authors.forename: Mariabeatrice
authors.initials: M
authors.lastname: Principi
authors.affiliation: Raffaele Licinio, Mariabeatrice Principi, Enzo Ierardi, Alfredo Di Leo, Gastroenterology Unit, Department of Emergency and Organ Transplantation, University of Bari, Cesare, 70124 Bari, Italy.
authors.forename: Enzo
authors.initials: E
authors.lastname: Ierardi
authors.affiliation: Raffaele Licinio, Mariabeatrice Principi, Enzo Ierardi, Alfredo Di Leo, Gastroenterology Unit, Department of Emergency and Organ Transplantation, University of Bari, Cesare, 70124 Bari, Italy.
authors.forename: Alfredo
authors.initials: A
authors.lastname: Di Leo
keywords: Hepatic transient elastography; Liver fibrosis; Low-fat diet; Primary intestinal lymphangiectasia