title: Intraosseous pseudotumour in a child with mild hemophilia B: report of a rare case and brief review of literature.
abstract: Hemophilic pseudotumor is a rare, but well-known, complication of hemophilia occurring in 1-2 % of individuals with a severe factor VIII or IX deficiency. The hemophilic pseudotumor is defined as an encapsulated hematoma that increases of volume progressively by episodes of recurrent hemorrhage; usually originate in soft tissues or in subperiosteal or intraosseous areas. Very seldom, patient with mild form of hemophilia present with intraosseous pseudotumor. This report describe an 11-year-old boy with mild factor IX deficiency (17 % of normal factor IX activity), who developed a pseudotumor of the femur.
authors.affiliation: Department of Paediatric Medicine, NRS Medical College and Hospital, 138, AJC Bose Road, Kolkata, 700014 West Bengal India.
authors.forename: Radheshyam
authors.initials: R
authors.lastname: Purkait
authors.affiliation: Department of Paediatric Medicine, NRS Medical College and Hospital, 138, AJC Bose Road, Kolkata, 700014 West Bengal India.
authors.forename: Aritra
authors.initials: A
authors.lastname: Mukherji
authors.affiliation: Department of Haematology, NRS Medical College and Hospital, 138, AJC Bose Road, Kolkata, 700014 West Bengal India.
authors.forename: Tuphan Kanti
authors.initials: TK
authors.lastname: Dolai
authors.affiliation: Department of Radiology, NRS Medical College and Hospital, 138, AJC Bose Road, Kolkata, 700014 West Bengal India.
authors.forename: Ramchandra
authors.initials: R
authors.lastname: Bhadra
keywords: Factor IX concentrates; Hemophilia B; Intraosseous pseudotumour