title: Functioning endometrium and endometrioma in a patient with mayer-rokitanski-kuster-hauser syndrome.
abstract: Mayer-Rokitanski-Kuster-Hauser (MRKH) syndrome is a rare disease. A 27-year-old woman was admitted for primary amenorrhea and cyclic pelvic pain. Magnetic resonance imaging (MRI) revealed bilateral Müllerian remnants with functioning endometrium and a pelvic mass considered to be an endometriotic cyst. Bilateral Müllerian remnants were removed, and right ovarian cystectomy was performed at laparoscopic surgery. Accurate evaluation before the operation and informed consent are necessary to treat patients with MRKH syndrome.
authors.affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.
authors.forename: Yasushi
authors.initials: Y
authors.lastname: Kawano
authors.affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.
authors.forename: Tomoko
authors.initials: T
authors.lastname: Hirakawa
authors.affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.
authors.forename: Masakazu
authors.initials: M
authors.lastname: Nishida
authors.affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.
authors.forename: Akitoshi
authors.initials: A
authors.lastname: Yuge
authors.affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.
authors.forename: Mitsutake
authors.initials: M
authors.lastname: Yano
authors.affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.
authors.forename: Kaei
authors.initials: K
authors.lastname: Nasu
authors.affiliation: Department of Obstetrics and Gynecology, Faculty of Medicine, Oita University, Yufu, Oita, Japan.
authors.forename: Hisashi
authors.initials: H
authors.lastname: Narahara
keywords: Mayer-Rokitanski-Kuster-Hauser syndrome; endometriosis; vaginal agenesis