title: Failure to wean caused by cryptogenic fibrosing pleuritis and bilateral lung trapping: case report.
abstract: OBJECTIVE
  Cryptogenic fibrosing pleuritis is an extremely rare disease, which can affect both lungs from a very young age. The most common finding is severe lung restriction resulting in both hypoxemic and ventilatory failure.
  
  
  METHODS
  Male patient, 26 year old with acute deterioration of chronic respiratory failure. Following admission prolonged mechanical ventilation was necessary. An atypical clinical presentation made the diagnosis difficult, but eventually cryptogenic fibrosing pleuritis and lung fibrosis were established.
  
  
  CONCLUSIONS
  The prognostic outcome of patients with the final diagnosis of cryptogenic fibrosing pleuritis is extremely poor, especially in an advanced phase of this disease. We recommend early treatment with corticosteroids or surgical pleural decortication.
authors.forename: Elsemiek
authors.initials: E
authors.lastname: Verweel
authors.forename: Jos le
authors.initials: Jl
authors.lastname: Noble
authors.forename: Christine Groeninx-van
authors.initials: CG
authors.lastname: Zoelen
authors.forename: Alex
authors.initials: A
authors.lastname: Maat
authors.forename: Willy
authors.initials: W
authors.lastname: Thijsse
authors.forename: Patricia
authors.initials: P
authors.lastname: Gerritsen
authors.forename: Jan
authors.initials: J
authors.lastname: Bakker