title: Pemphigus. S2 Guideline for diagnosis and treatment--guided by the European Dermatology Forum (EDF) in cooperation with the European Academy of Dermatology and Venereology (EADV).
abstract: BACKGROUND
  Pemphigus encompasses a group of life-threatening autoimmune bullous diseases characterized by blisters and erosions of the mucous membranes and skin. Before the era of immunosuppressive treatment, the prognosis of pemphigus was almost fatal. Due to its rarity, only few prospective controlled therapeutic trials are available.
  
  
  OBJECTIVE
  For this reason, a group of European dermatologists with a long-standing interest and expertise in basic and clinical pemphigus research has sought to define diagnostic and therapeutic guidelines for the management of patients with pemphigus.
  
  
  RESULTS
  This group identified the statements of major agreement or disagreement regarding the diagnostic and therapeutic management of pemphigus. The revised final version of the pemphigus guideline was finally passed on to the European Dermatology Forum (EDF) for a final consensus with the European Academy of Dermatology and Venereology (EADV) and the European Union of Medical Specialists (UEMS).
authors.affiliation: Department of Dermatology, Philipps-University Marburg, Marburg, Germany.
authors.forename: M
authors.initials: M
authors.lastname: Hertl
authors.forename: H
authors.initials: H
authors.lastname: Jedlickova
authors.forename: S
authors.initials: S
authors.lastname: Karpati
authors.forename: B
authors.initials: B
authors.lastname: Marinovic
authors.forename: S
authors.initials: S
authors.lastname: Uzun
authors.forename: S
authors.initials: S
authors.lastname: Yayli
authors.forename: D
authors.initials: D
authors.lastname: Mimouni
authors.forename: L
authors.initials: L
authors.lastname: Borradori
authors.forename: C
authors.initials: C
authors.lastname: Feliciani
authors.forename: D
authors.initials: D
authors.lastname: Ioannides
authors.forename: P
authors.initials: P
authors.lastname: Joly
authors.forename: C
authors.initials: C
authors.lastname: Kowalewski
authors.forename: G
authors.initials: G
authors.lastname: Zambruno
authors.forename: D
authors.initials: D
authors.lastname: Zillikens
authors.forename: M F
authors.initials: MF
authors.lastname: Jonkman
mesh_terms: D005060:Europe; D006801:Humans; D010392:Pemphigus / Q000175:diagnosis* / Q000628:therapy*