title: Dentinogenesis imperfecta type I: A case report with literature review on nomenclature system.
abstract: Dentinogenesis imperfecta (DI) is an inherited disorder affecting dentin. Defective dentin formation results in discolored teeth that are prone to attrition and fracture. Mutation in dentin sialophosphoprotein (DSPP) has been found to cause the dentin disorders DI - I and II (shields II and III). Early diagnosis and treatment of DI is recommended as it may prevent or intercept deterioration of the teeth and occlusion and improve esthetics. Here, we report a case with characteristic clinical, radiological and histological features of DI-I. The etiology and classification followed in literature is confusing since dentinoenamel junction (DEJ) in DI seems to be structurally and functionally normal and DI is clearly a disorder distinct from osteogenesis imperfecta (OI), but we still relate etiology of DI to DEJ and follow Shields classification. Therefore, we have briefly reviewed etiology and nomenclature system of DI.
authors.affiliation: Department of Oral Medicine and Radiodiagnosis, Krishnadevaraya College of Dental Sciences and Hospital, Bangalore, Karnataka, India.
authors.forename: D
authors.initials: D
authors.lastname: Devaraju
authors.affiliation: Department of Oral Medicine and Radiodiagnosis, MS Ramaiah Dental College and Hospital, Bangalore, Karnataka, India.
authors.forename: Bk Yashoda
authors.initials: BY
authors.lastname: Devi
authors.affiliation: Department of Oral Medicine and Radiodiagnosis, Krishnadevaraya College of Dental Sciences and Hospital, Bangalore, Karnataka, India.
authors.forename: Vijeev
authors.initials: V
authors.lastname: Vasudevan
authors.affiliation: Department of Oral Medicine and Radiodiagnosis, Krishnadevaraya College of Dental Sciences and Hospital, Bangalore, Karnataka, India.
authors.forename: V
authors.initials: V
authors.lastname: Manjunath
keywords: Dentin; odontoblasts; reciprocal induction