title: Cochlear implantation in patients with Cogan syndrome: long-term results.
abstract: The objective of this study was to evaluate the long-term outcomes of patients with Cogan syndrome (CS) who have undergone cochlear implantation. Subjects consisted of 12 cochlear implant users with a typical form of CS. Measures included word and sentence recognition scores. The speech recognition performance was rated before cochlear implantation and at 1 and 5 years after implantation. The speech materials were presented in quiet only condition. The mean 12-month post-operative word and sentence recognition scores were 91.4 and 93.1%, respectively. Five years after implantation, the group means for word and sentence recognition tests were 94 and 96.3%, respectively. No patients in this series experienced flap complication or other local or systemic complications. This long-term study on 12 subjects with CS over 5 years of cochlear implant use reveals that cochlear implantation is safe in the long term and provides excellent and stable hearing results.
authors.affiliation: Department of Clinical and Experimental Medicine, Unit of Audiology and Pediatric Otorhinolaryngology, University-Hospital of Parma, Via Gramsci 14, 43123, Parma, Italy. andreabacciu@yahoo.it.
authors.forename: Andrea
authors.initials: A
authors.lastname: Bacciu
authors.affiliation: Department of Clinical and Experimental Medicine, Unit of Audiology and Pediatric Otorhinolaryngology, University-Hospital of Parma, Via Gramsci 14, 43123, Parma, Italy.
authors.forename: Enrico
authors.initials: E
authors.lastname: Pasanisi
authors.affiliation: Department of Clinical and Experimental Medicine, Unit of Audiology and Pediatric Otorhinolaryngology, University-Hospital of Parma, Via Gramsci 14, 43123, Parma, Italy.
authors.forename: Filippo
authors.initials: F
authors.lastname: Di Lella
authors.affiliation: Department of Clinical and Experimental Medicine, Unit of Audiology and Pediatric Otorhinolaryngology, University-Hospital of Parma, Via Gramsci 14, 43123, Parma, Italy.
authors.forename: Maurizio
authors.initials: M
authors.lastname: Guida
authors.affiliation: Department of Clinical and Experimental Medicine, Unit of Audiology and Pediatric Otorhinolaryngology, University-Hospital of Parma, Via Gramsci 14, 43123, Parma, Italy.
authors.forename: Salvatore
authors.initials: S
authors.lastname: Bacciu
authors.affiliation: Department of Clinical and Experimental Medicine, Unit of Audiology and Pediatric Otorhinolaryngology, University-Hospital of Parma, Via Gramsci 14, 43123, Parma, Italy.
authors.forename: Vincenzo
authors.initials: V
authors.lastname: Vincenti
mesh_terms: D000293:Adolescent; D000328:Adult; D019929:Cochlear Implantation; D003054:Cochlear Implants; D055952:Cogan Syndrome / Q000601:surgery*; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000601:surgery*; D006801:Humans; D008297:Male; D008875:Middle Aged; D009999:Ossification, Heterotopic / Q000601:surgery; D012533:Scala Tympani; D013067:Speech Perception; D055815:Young Adult
keywords: Cochlear implant; Cogan syndrome; Deafness; Ossified cochlea; Results