title: Giant “Panfacial” Chordoma  Involving Skull Base With  Intracranial Invasion.
abstract: Chordomas are rare, low-grade, primary malignant bone tumor arising from primitive notochord remnants of the axial skeleton. They rarely occur in an extraosseus craniofacial location such as nasopharynx, nasal septum, paranasal sinuses, and orbits. We report here an extreme case of "panfacial" chordoma involving middle and anterior skull base with intracranial invasion, which reached considerable size because of a delay in diagnosis and treatment. In this case, a wide surgical excision was performed to improve quality of life.
authors.forename: Andrea
authors.initials: A
authors.lastname: Cassoni
authors.forename: Valentina
authors.initials: V
authors.lastname: Terenzi
authors.forename: Andrea
authors.initials: A
authors.lastname: Battisti
authors.forename: Paolo
authors.initials: P
authors.lastname: Priore
authors.forename: Marco
authors.initials: M
authors.lastname: Della Monaca
authors.lastname: Sandro Bosco
authors.forename: Paolo
authors.initials: P
authors.lastname: Bianco
authors.forename: Valentino
authors.initials: V
authors.lastname: Valentini
mesh_terms: D001932:Brain Neoplasms / Q000175:diagnosis / Q000601:surgery; D002817:Chordoma / Q000175:diagnosis* / Q000601:surgery; D057210:Delayed Diagnosis; D005147:Facial Bones / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D009361:Neoplasm Invasiveness; D011788:Quality of Life; D019651:Plastic Surgery Procedures / Q000379:methods; D019292:Skull Base Neoplasms / Q000175:diagnosis* / Q000601:surgery; D012888:Skull Neoplasms / Q000175:diagnosis* / Q000601:surgery; D014057:Tomography, X-Ray Computed / Q000379:methods; D055815:Young Adult