title: [Idiopathic interstitial pneumonias].
abstract: Idiopathic interstitial pneumonias represent approximately 30% of all interstitial lung diseases. The new classification of idiopathic interstitial pneumonias published in 2013 distinguishes 6 major entities, including chronic fibrosing forms (idiopathic pulmonary fibrosis and nonspecific interstitial pneumonia), acute/subacute forms (cryptogenic organizing pneumonia and acute interstitial pneumonia) and smoking-related disorders (respiratory bronchiolitis interstitial lung disease and desquamative interstitial pneumonia). Pleuroparenchymal fibroelastosis is individualized as a new rare clinco-pathologic entity. For cases not fitting any specific clinic- pathological category, a pragmatic classification based on disease behavior is proposed.
authors.forename: Romain
authors.initials: R
authors.lastname: Lazor
authors.forename: Igor
authors.initials: I
authors.lastname: Letovanec
authors.forename: Catherine
authors.initials: C
authors.lastname: Beigelman
mesh_terms: D030342:Genetic Diseases, Inborn / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D006801:Humans; D054988:Idiopathic Interstitial Pneumonias / Q000145:classification / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D054990:Idiopathic Pulmonary Fibrosis / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D017563:Lung Diseases, Interstitial / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D014029:Tobacco Use Disorder / Q000150:complications