[Adult Sturge-Weber syndrome without facial hemangioma: report of one case].
Sturge-Weber syndrome (SWS) is characterized by angiomas affecting the ophthalmic division of the trigeminal nerve, epilepsy, intellectual impairment, hemiplegia and glaucoma. We report a patient who developed SWS without facial hemangioma (SWS type III) in his adulthood. The patient presented with repeated episodes of headache since age 37 year. He manifested first attack of seizure at the age 47 year followed by aphasia and right upper limb palsy. Brain CT scan revealed right parietal-occipital calcification, brain CT angiography showed right temporal lobe and occipital lobe vascular malformation, and MRI showed leptomeningeal enhancement in the riht cerebral piamater. The seizure was controlled with antiepileptic drugs and reviewed in routine follow up.
Department of Ophthalmology, Shaoxing Peoples Hospital, Shaoxing 312000, China;College of Optometry, Wenzhou Medical University, Wenzhou 325027, China.
Rong
R
Zhang
Department of Ophthalmology, Shaoxing Peoples Hospital, Shaoxing 312000, China;College of Optometry, Wenzhou Medical University, Wenzhou 325027, China.
Wei
W
Chen
Department of Neurosurgery, Second Affiliated Hospital, Zhejiang University School of Medicine, Hangzhou 310009, China.
Qiang
Q
Hu
Department of Neurosurgery, Second Affiliated Hospital, Zhejiang University School of Medicine, Hangzhou 310009, China.
Sudeep
S
Shrestha
D000328:Adult; D000792:Angiography; D000927:Anticonvulsants / Q000627:therapeutic use; D001921:Brain / Q000473:pathology; D004827:Epilepsy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D012640:Seizures / Q000188:drug therapy; D013341:Sturge-Weber Syndrome / Q000473:pathology*
D000927:Anticonvulsants