Systemic panniculitis-like T-cell lymphoma with involvement of mesenteric fat and subcutis.
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is an uncommon non-Hodgkins primary cutaneous lymphoma that typically presents as subcutaneous nodules on the extremities or trunk. Here, we report an unusual case of systemic panniculitic T-cell lymphoma with predominantly mesenteric extra-cutaneous involvement and an aggressive clinical course with histopathologic and immunophenotypic features that mimic SPTCL. This case serves to expand the body of literature regarding systemic SPTCL-like disorders with prominent extra-cutaneous involvement.
Department of Pathology, Stanford University Medical School, Stanford, CA, USA.
Laura
L
Lester
Mark
M
Ewalt
Roger
R
Warnke
Jinah
J
Kim
D000328:Adult; D003937:Diagnosis, Differential; D006801:Humans; D016399:Lymphoma, T-Cell / Q000473:pathology*; D016410:Lymphoma, T-Cell, Cutaneous / Q000473:pathology*; D008297:Male; D015434:Panniculitis / Q000473:pathology*; D011379:Prognosis; D012878:Skin Neoplasms / Q000473:pathology; D050151:Subcutaneous Fat / Q000473:pathology*
SLE; T-cell receptor; cutaneous T-cell lymphoma; cutaneous lymphoma; rearrangement