Parry-romberg syndrome: a case of late onset with rapid progression.
Parry-Romberg syndrome (PRS) or progressive hemifacial atrophy is rare, poorly understood condition with an unclear aetiology and characterized by slow and progressive atrophy affecting one side of the face. PRS is a syndrome with diverse presentation and the most common early sign is a painless cleft, the "coup de sabre" near the midline of the face which marks the boundary between the normal and atrophic tissues. Characteristically, the atrophy starts in the first decade of life and progresses slowly for several years before it becomes quiescent. This article describes a case of PRS in a 19-year-old female patient affecting the right side of the face which is unique in the fact that it had a late onset with rapid progression.
Reader, Department of Oral Surgery, Thai Moogambigai Dental College , Chennai, India .
Senthil
S
Kumar
Senior Lecturer, Department of Oral Pathology, S.R.M Dental College , Chennai, India .
Dinesh
D
Kumar
Professor, Department of Oral Pathology, S.R.M Dental college , Chennai, India .
Ramesh
R
Kumar
Professor and Head, Department of Oral Pathology, S.R.M Dental College , Chennai, India .
Rajkumar
Dean and Head, Department of Orthodontics, Thai Moogambigai Dental College , Chennai, India .
Ramachandra
R
Prabhakar
Facial hemiatrophy; Parry-romberg syndrome; Progressive hemifacial atrophy