Relaxing retinectomy for tractional retinal detachment with retinal capillary hemangiomas in genotypically confirmed von hippel-lindau disease.
OBJECTIVE
To report the outcome of tractional retinal detachment with retinal capillary hemangiomas after pars plana vitrectomy (PPV) and relaxing retinectomy in genotypically confirmed von Hippel-Lindau disease (VHL).


METHODS
Interventional case report of a 28-year-old patient with multiple and large retinal capillary hemangiomas underwent PPV combined with relaxing retinectomy.


RESULTS
Over the next several weeks, the retina recovered to reattachment and remained this way for 2 years. In excised angiomas, the finding of a missense Arg167Trp mutation and immunohistochemistry staining confirmed the diagnosis of VHL.


CONCLUSIONS
Patients with tractional retinal detachment with hemangiomas secondary to VHL may benefit from PPV with relaxing retinectomy.
From the *Department of Ophthalmology, Shin Kong Wu Ho-Su Memorial Hospital, Taipei, Taiwan; † School of Medicine, Fu Jen Catholic University, Taipei, Taiwan; ‡Institute of Clinical Medicine and School of Medicine, National Yang-Ming University, Taipei, Taiwan; §Department of Ophthalmology, College of Medicine, National Taiwan University, Taipei, Taiwan; ¶School of Nutrition and Health Sciences, Taipei Medical University, Taipei, Taiwan; and Departments of **Pediatrics ††Pathology, Shin Kong Wu Ho-Su Memorial Hospital, Taipei, Taiwan.
Chi-Hsien
CH
Peng
Cheng-Kuo
CK
Cheng
Sing-Chung
SC
Li
Shu-Chi
SC
Mu
Chin-Cheng
CC
Lee