Bullous mastocytosis in a 3-month-old infant.
Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation and accumulation of mast cells in one or more organ systems including the skin, bone marrow, liver, spleen, lymph nodes and gastrointestinal tract. An infant presenting with bullous lesions is an even rarer clinical presentation of cutaneous mastocytosis. The symptoms and complications are mostly in proportion to the mast cell degranulation in tissues. Management is focused on preventing and treating this event. We report a three-month-old infant with bullous mastocytosis to enhance awareness about this rare diagnosis.
Department of Dermatology, All India Institute of Medical Sciences, Bhopal, Madhya Pradesh, India.
Dinesh Prasad
DP
Asati
Consultant Dermatologist, Centre for Skin Diseases and Laser Treatment, Bhopal, Madhya Pradesh, India.
Anurag
A
Tiwari
Infantile bullous mastocytosis; mast cells; urticaria pigmentosa