Retinitis pigmentosa associated with progressive hemifacial atrophy (parry-romberg syndrome).
OBJECTIVE
The Parry-Romberg syndrome, or progressive hemifacial atrophy, is a slowly progressive marked facial deformity because of atrophy of subcutaneous fat and skin, cartilage, and bone wasting. Various ocular findings may be present in approximately 40% of cases of progressive hemifacial atrophy. We describe a novel case of a 42-year-old woman with progressive hemifacial atrophy and bilateral retinal dystrophy consistent with retinitis pigmentosa.


METHODS
Case report and literature review.


RESULTS
Clinical features, fundus photographs, visual fields, and electroretinographic findings are reported.


CONCLUSIONS
Progressive hemifacial atrophy can occur with retinitis pigmentosa.
From the Departments of *Ophthalmology and †Biological Structure, University of Washington School of Medicine, Seattle, Washington.
Daniel B
DB
Moore
Sandeep
S
Randhawa
Russell N
RN
Van Gelder