Dome-shaped macula associated with Best vitelliform macular dystrophy.
OBJECTIVE
Dome-shaped macula (DSM) has been described recently as an inward convexity of the macula typical of myopic eyes detectable on spectral-domain optical coherence tomography (SD-OCT). The authors describe a case of monolateral DSM associated with Best vitelliform macular dystrophy (VMD).


METHODS
Case report.


RESULTS
A 60-year-old man already diagnosed with VMD in vitelliruptive stage underwent SD-OCT that revealed the typical vitelliform material accumulation associated in the left eye with a convex elevation of the macula. No change was registered over a 1-year follow-up.


CONCLUSIONS
This is the first report describing a monolateral DSM associated with VMD. Dome-shaped macula could be considered as a nonspecific scleral alteration, probably due to increased scleral thickness, which can accompany many retinal disorders.
Department of Ophthalmology, University Vita-Salute, San Raffaele Scientific Institute, Milan - Italy.
Maurizio
M
Battaglia Parodi
Ilaria
I
Zucchiatti
Francesco
F
Fasce
Maria Lucia
ML
Cascavilla
Maria Vittoria
MV
Cicinelli
Francesco
F
Bandello
D000075002:Bestrophins; D018118:Chloride Channels / Q000235:genetics; D004585:Electrooculography; D005136:Eye Proteins / Q000235:genetics; D005451:Fluorescein Angiography; D006801:Humans; D008266:Macula Lutea / Q000473:pathology*; D008297:Male; D008875:Middle Aged; D041623:Tomography, Optical Coherence / Q000379:methods; D014792:Visual Acuity / Q000502:physiology; D057826:Vitelliform Macular Dystrophy / Q000175:diagnosis* / Q000235:genetics
C113133:BEST1 protein, human; D000075002:Bestrophins; D018118:Chloride Channels; D005136:Eye Proteins