title: Hyperautofluorescent macular ring in a series of patients with enhanced S-cone syndrome.
abstract: The authors describe fundus autofluorescence (AF) and spectral-domain optical coherence tomography (SD-OCT) findings in three patients with enhanced S-cone syndrome and their correlation around the hyperautofluorescent ring border. Patients had AF imaging in combination with SD-OCT line-scans through the fovea, at the posterior pole, and at a temporal locus centered on the ring border. All eyes demonstrated a macular ring of high-intensity AF. The inner segment ellipsoid band showed thinning and disorganization toward the ring border, where it was lost.
authors.forename: Rony
authors.initials: R
authors.lastname: Gelman
authors.forename: Jonathan P
authors.initials: JP
authors.lastname: Greenberg
authors.forename: Tobias
authors.initials: T
authors.lastname: Duncker
authors.forename: Huy V
authors.initials: HV
authors.lastname: Nguyen
authors.forename: Lawrence A
authors.initials: LA
authors.lastname: Yannuzzi
authors.forename: Stephen H
authors.initials: SH
authors.lastname: Tsang
mesh_terms: D000328:Adult; D002648:Child; D004596:Electroretinography; D015785:Eye Diseases, Hereditary / Q000175:diagnosis* / Q000503:physiopathology; D005260:Female; D005451:Fluorescein Angiography; D006801:Humans; D008062:Lipofuscin / Q000378:metabolism; D008297:Male; D020419:Photoreceptor Cells, Vertebrate / Q000473:pathology*; D012162:Retinal Degeneration / Q000175:diagnosis* / Q000503:physiopathology; D055213:Retinal Pigment Epithelium / Q000378:metabolism / Q000473:pathology*; D041623:Tomography, Optical Coherence; D014786:Vision Disorders / Q000175:diagnosis* / Q000503:physiopathology; D014792:Visual Acuity; D058609:Visual Field Tests; D014794:Visual Fields
chemical_list: D008062:Lipofuscin