title: Computed tomography and magnetic resonance imaging of multiple focal nodular hyperplasias of the liver with congenital absence of the portal vein in a Chinese girl: case report and review of the literature.
abstract: BACKGROUND
  Patients with congenital absence of the portal vein (CAPV) often suffer from additional medical complications such as hepatic tumors and cardiac malformations.
  
  
  METHODS
  Congenital absence of the portal vein (CAPV) is a rare malformation. We present a case of a 16-year-old Chinese girl with CAPV with multiple pathology-proven hepatic focal nodular hyperplasias (FNHs) and ventricular septal defect (VSD). The CT and MRI features of this case are described, and previously reported cases are reviewed.
  
  
  CONCLUSIONS
  CAPV is a rare congenital anomaly and in such patients, clarifying the site of portosystemic shunts, liver disease, and other anomalies is critical for appropriate treatment selection and accurate prognosis determination. Close follow-up, including laboratory testing and radiologic imaging, is recommended for all CAPV patients.
authors.affiliation: Department of Radiology, PLA General Hospital, #28 Fuxing Road, Beijing, 100853, China. zkbeir@163.com.
authors.forename: Kun
authors.initials: K
authors.lastname: Zhang
authors.affiliation: Department of Radiology, PLA General Hospital, #28 Fuxing Road, Beijing, 100853, China. wangqingjun77@163.com.
authors.forename: Qingjun
authors.initials: Q
authors.lastname: Wang
authors.affiliation: Department of Radiology, PLA General Hospital, #28 Fuxing Road, Beijing, 100853, China. wanghaiyi301@126.com.
authors.forename: Haiyi
authors.initials: H
authors.lastname: Wang
authors.affiliation: Department of Radiology, PLA General Hospital, #28 Fuxing Road, Beijing, 100853, China. yehuiyi301@aliyun.com.
authors.forename: Huiyi
authors.initials: H
authors.lastname: Ye
authors.affiliation: Department of Pathology, PLA General Hospital, #28 Fuxing Road, Beijing, 100853, China. guoaitao301@126.com.
authors.forename: Aitao
authors.initials: A
authors.lastname: Guo
authors.affiliation: Department of Hepatobiliary Surgery, PLA General Hospital, #28 Fuxing Road, Beijing, 100853, China. duanweidong301@126.com.
authors.forename: Weidong
authors.initials: W
authors.lastname: Duan
mesh_terms: D005260:Female; D020518:Focal Nodular Hyperplasia / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D008113:Liver Neoplasms / Q000098:blood supply* / Q000473:pathology*; D008279:Magnetic Resonance Imaging / Q000379:methods; D064847:Multimodal Imaging; D011169:Portal Vein / Q000002:abnormalities* / Q000601:surgery*; D014057:Tomography, X-Ray Computed / Q000379:methods