title: A case of atypical teratoid/rhabdoid tumor in the internal auditory canal.
abstract: OBJECTIVE
  The case of a thirteen-year-old woman showing an atypical teratoid/rhabdoid tumor (AT/RT) primarily occurred in the internal auditory canal was presented.
  
  
  RESULTS
  There was a delay in diagnosing AT/RT because of the first histological diagnosis of benign neurofibroma. If we had changed the surgical approach to one which was middle cranial fossa-based or translabyrinthine in the second or third operation, we might have reached an earlier final diagnosis. Although we faced a dilemma about whether to sacrifice facial nerve function for dissection of the tumor, we should have considered the possibility of malignancy at an earlier stage.
  
  
  CONCLUSIONS
  This is a case report of AT/RT in the internal auditory canal presenting with progressive hearing loss as the initial symptom. Although no previous reports of AT/RT primarily occurring in the internal auditory canal are existent, this rare form of the disease should be considered in future evaluations as a differential diagnosis for internal auditory canal tumor.
authors.affiliation: Department of Otolaryngology of the Kitasato University Hospital, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa 252-0374, Japan. Electronic address: ytomoko@med.kitasato-u.ac.jp.
authors.forename: Tomoko
authors.initials: T
authors.lastname: Yamaguchi
authors.affiliation: Department of Neurosurgery of the Kitasato University Hospital, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa 252-0374, Japan.
authors.forename: Hidehiro
authors.initials: H
authors.lastname: Oka
authors.affiliation: Department of Neurosurgery of the Kitasato University Hospital, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa 252-0374, Japan.
authors.forename: Chihiro
authors.initials: C
authors.lastname: Kijima
authors.affiliation: Department of Otolaryngology of the Kitasato University Hospital, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa 252-0374, Japan.
authors.forename: Hajime
authors.initials: H
authors.lastname: Sano
authors.affiliation: Department of Otolaryngology of the Kitasato University Hospital, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa 252-0374, Japan.
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Watanabe
authors.affiliation: Department of Otolaryngology of the Kitasato University Hospital, 1-15-1 Kitasato, Minami, Sagamihara, Kanagawa 252-0374, Japan.
authors.forename: Makito
authors.initials: M
authors.lastname: Okamoto
mesh_terms: D000293:Adolescent; D004428:Ear Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D007758:Ear, Inner / Q000473:pathology* / Q000601:surgery; D005158:Facial Paralysis / Q000175:diagnosis* / Q000209:etiology; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis* / Q000209:etiology; D006801:Humans; D008279:Magnetic Resonance Imaging; D018335:Rhabdoid Tumor / Q000150:complications / Q000175:diagnosis* / Q000601:surgery; D013724:Teratoma / Q000150:complications / Q000175:diagnosis* / Q000601:surgery
keywords: Facial palsy; Internal auditory canal tumor; Rapidly progressive hearing loss