title: Giant retroperitoneal leiomyosarcoma. Multiorgan block removal.
abstract: BACKGROUND
  Retroperitoneal tumors are rare, mostly malignant. Locally aggressive, and more frequent in women in their 5th decade of life. Its symptoms are nonspecific, including abdominal pain and palpable mass. To diagnosis is helpful computed tomography and biopsy. It needs surgery for absolute healing.
  
  
  METHODS
  67 years old man was admitted with back pain and fever. Abdominal imaging tests showed a 15cm abdominal mass without clear organodependencia. Endoscopy with biopsies evidenced mesenchymal neoplasia of undetermined origin. In surgery we confirm its resecability and was necessary multiorgan resection. Pathologic diagnosis: well differentiated retroperitoneal leiomyosarcoma. Started adjuvant radiotherapy. In subsequent tests showed the presence of liver metastases.
  
  
  CONCLUSIONS
  Retroperitoneal tumors are developed from nerve, vascular, muscular, connective, supportive and fibroareolar tissue from this space. Its size does not modificate survival or resectability. We used TC and biopsy for its diagnose. Adjuvant therapy does not affect survival or quality of life, surgery remains the only curative option. Locoregional recurrence is the most influential figure in the prognosis. A large percentage of patients required a second surgery (between 45 and 82%).
  
  
  CONCLUSIONS
  The only curative option of retroperitoneal sarcomas is surgery, which usually requires multiple organ resection. Chemotherapy and radiotherapy are mostly a surgical supplement. Chemotherapy has not shown significant increase in survival.
authors.affiliation: Hospital of Jerez de la Frontera, N-IVa Road s/n, Jerez, Cadiz, Spain. Electronic address: fasismateo@gmail.com.
authors.forename: F
authors.initials: F
authors.lastname: Mateo Vallejo
authors.affiliation: Hospital of Jerez de la Frontera, N-IVa Road s/n, Jerez, Cadiz, Spain.
authors.forename: M R
authors.initials: MR
authors.lastname: Dominguez Reinado
authors.affiliation: Hospital of Jerez de la Frontera, N-IVa Road s/n, Jerez, Cadiz, Spain.
authors.forename: C
authors.initials: C
authors.lastname: Medina Achirica
authors.affiliation: Hospital of Jerez de la Frontera, N-IVa Road s/n, Jerez, Cadiz, Spain.
authors.forename: M
authors.initials: M
authors.lastname: Diaz Oteros
authors.affiliation: Hospital of Jerez de la Frontera, N-IVa Road s/n, Jerez, Cadiz, Spain.
authors.forename: J L
authors.initials: JL
authors.lastname: Esteban Ramos
authors.affiliation: Hospital of Jerez de la Frontera, N-IVa Road s/n, Jerez, Cadiz, Spain.
authors.forename: S
authors.initials: S
authors.lastname: Melero Brenes
keywords: Leiomyosarcoma; Multiorgan resection; Retroperitoneal