title: Shone variant with large eustachian valve: implication for repair and heart transplantation.
abstract: We present a case of a neonate with Shone complex in addition to the underdevelopment of the right ventricle associated with dysplasia and stenosis of the tricuspid valve. Because of lack of effective surgical options, the patient was transplanted at the age of 8days. A gradient was noted in the postoperative period across the inferior vena cava anastomosis. At reoperation, a prominent myxomatous Eustachian valve was resected. We believe the large Eustachian valve was likely responsible for the right-sided pathology.
authors.affiliation: UAB Department of Pathology. Electronic address: slitovsk@uab.edu.
authors.forename: Silvio H
authors.initials: SH
authors.lastname: Litovsky
authors.affiliation: Children's of Alabama Department of Pathology and Laboratory Medicine.
authors.forename: David R
authors.initials: DR
authors.lastname: Kelly
authors.affiliation: UAB Pediatric Cardiology.
authors.forename: Mark A
authors.initials: MA
authors.lastname: Law
authors.affiliation: UAB Cardiothoracic Surgery.
authors.forename: Robert J
authors.initials: RJ
authors.lastname: Dabal
authors.affiliation: Children's of Alabama Department of Pathology and Laboratory Medicine.
authors.forename: Richard L
authors.initials: RL
authors.lastname: Daniel
authors.affiliation: Children's of Alabama Department of Pathology and Laboratory Medicine.
authors.forename: Dava Sue
authors.initials: DS
authors.lastname: Cleveland
authors.affiliation: UAB Pediatric Cardiology.
authors.forename: F Bennet
authors.initials: FB
authors.lastname: Pearce
mesh_terms: D006330:Heart Defects, Congenital / Q000473:pathology* / Q000601:surgery*; D016027:Heart Transplantation; D006801:Humans; D007231:Infant, Newborn; D008297:Male
keywords: Eustachian valve; Heart transplant; Right ventricle; Shone’s syndrome