title: A case of periampullary adenocarcinoma in neurofibromatosis type 1.
abstract: Neurofibromatosis type 1 (NF-1) is an autosomal dominant genetic disorder with a known predisposition to gastrointestinal neoplasms such as stromal tumors and carcinoids. Adenocarcinomas (ACs) of the gastrointestinal tract are relatively rare in patients with NF-1, especially those found in the periampullary region. We present a case report of periampullary adenocarcinoma in a 56-year-old woman with NF-1 who presented with abdominal pain and obstructive jaundice.
authors.affiliation: 1 Department of Medicine, 2 Department of Medical Oncology, 3 Department of Surgery, 4 Department of Pathology, 5 Department of Medicine, Division of Gastroenterology and Hepatology, Thomas Jefferson University Hospital, Philadelphia, PA, USA.
authors.forename: C Andrew
authors.initials: CA
authors.lastname: Kistler
authors.affiliation: 1 Department of Medicine, 2 Department of Medical Oncology, 3 Department of Surgery, 4 Department of Pathology, 5 Department of Medicine, Division of Gastroenterology and Hepatology, Thomas Jefferson University Hospital, Philadelphia, PA, USA.
authors.forename: Jennifer M
authors.initials: JM
authors.lastname: Johnson
authors.affiliation: 1 Department of Medicine, 2 Department of Medical Oncology, 3 Department of Surgery, 4 Department of Pathology, 5 Department of Medicine, Division of Gastroenterology and Hepatology, Thomas Jefferson University Hospital, Philadelphia, PA, USA.
authors.forename: Jordan M
authors.initials: JM
authors.lastname: Winter
authors.affiliation: 1 Department of Medicine, 2 Department of Medical Oncology, 3 Department of Surgery, 4 Department of Pathology, 5 Department of Medicine, Division of Gastroenterology and Hepatology, Thomas Jefferson University Hospital, Philadelphia, PA, USA.
authors.forename: Jeffrey P
authors.initials: JP
authors.lastname: Baliff
authors.affiliation: 1 Department of Medicine, 2 Department of Medical Oncology, 3 Department of Surgery, 4 Department of Pathology, 5 Department of Medicine, Division of Gastroenterology and Hepatology, Thomas Jefferson University Hospital, Philadelphia, PA, USA.
authors.forename: Ali A
authors.initials: AA
authors.lastname: Siddiqui
authors.affiliation: 1 Department of Medicine, 2 Department of Medical Oncology, 3 Department of Surgery, 4 Department of Pathology, 5 Department of Medicine, Division of Gastroenterology and Hepatology, Thomas Jefferson University Hospital, Philadelphia, PA, USA.
authors.forename: Ashwin R
authors.initials: AR
authors.lastname: Sama
keywords: Periampullary adenocarcinoma (AC); neurofibromatosis type 1 (NF-1)