title: [Sexual activity and quality of life in patients with Mayer-Rokitansky-Kuster-Hauser syndrome].
abstract: OBJECTIVE
  This study evaluated the sexual activity and the quality of life in patients with a Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome.
  
  
  METHODS
  The study is based on a series of patients hospitalized for the treatment of MRKH syndrome in CMCO between 1997 and 2010. Through the medical reports, we recovered information about the pathology, the treatment given and the psychological support proposed to or wished by the patients. The patients also had to answer a questionnary concerning the quality of the informations they received about the treatment, the different types of supports proposed and wanted, their life as a couple and how they communicated about their disease.
  
  
  RESULTS
  Eleven medical reports have been reviewed. The patients were aged 21 in average at the moment of the treatment. Three patients had some associated malformations. Different methods of treatment were represented (Frank's method, Vecchietti's technique, sigmoid vaginoplasty, McIndoe's technique). Sexual intercourse was assessed as satisfactory by 4 patients. In 8 cases, the partner accepted well the pathology. Only 4 out of the eleven medical reports mentioned a psychological support. Nine out of the eleven patients accepted to answer the questionnary.
  
  
  CONCLUSIONS
  The review of the literature and our own results show that the patients with MRKH syndrome have a real need for psychological support. They are able to have sexual intercourse that is satisfactory in the domains of excitation, lubrification and desire, especially after treatment. The main problem is the inability to bear children, a problem which might by solved by the future researches about uterus graft and the evolution of the laws concerning gestational surrogacy.
authors.affiliation: Service de gynécologie-obstétrique, hôpital de Hautepierre, 1, avenue Molière, 67100 Strasbourg, France. Electronic address: yves.delaine@neuf.fr.
authors.forename: M
authors.initials: M
authors.lastname: Delaine
authors.affiliation: Service de gynécologie-obstétrique, CMCO, 19, rue Louis-Pasteur, 67300 Schiltigheim, France.
authors.forename: J
authors.initials: J
authors.lastname: Ohl
mesh_terms: D058489:46, XX Disorders of Sex Development / Q000503:physiopathology* / Q000523:psychology* / Q000601:surgery; D003075:Coitus; D000013:Congenital Abnormalities / Q000503:physiopathology* / Q000523:psychology* / Q000601:surgery; D005260:Female; D006801:Humans; D009095:Mullerian Ducts / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery; D011788:Quality of Life; D019651:Plastic Surgery Procedures; D012189:Retrospective Studies; D012725:Sexual Behavior; D012944:Social Support; D011795:Surveys and Questionnaires; D014621:Vagina / Q000601:surgery; D055815:Young Adult
keywords: Activité sexuelle; Agénésie vaginale; Aspect psychologique; MRKH; Mayer-Rokitansky-Kuster-Hauser syndrome; Neovagina; Néovagin; Psychological support; Sexual intercourse; Syndrome de Mayer-Rokitansky-Kuster-Hauser; Vaginal agenesis