title: Sturge-weber syndrome: a report of 14 cases.
abstract: Sturge-Weber-Krabe syndrome (SWS), also known as encephalotrigeminalangiomatosis and named the forthfacomatosis, recall the names of the authors who first describedit in its basic clinical, radiological andanatomopathological aspects. We report here 14 cases of Sturge-Weber disease. In 6 of these, despite what had been previously described in literature, an extension of the angioma has been noted in other parts of the body. The study of these subjects stresses not only the need for a pharmacological/neuropsychomotor intervention, but alsothe need of a psychotherapeutic approach, for the emotional and affective implications thatcould derive from this syndrome. The reported cases are similar to those presented in literature for their main features. In particular, two elements are interesting: i) the exceptional diffusion of the red nevousto the whole hemicorpo; and ii) the evaluation of the way the patients live the disease, which has not beenpreviously considered in literature. We can conclude that SWS is a multisystem disorder that requires the neurologist to be aware of the possible endocrine, psychiatric, ophthalmological, and other medical issues that can arise and impact on the neurological status of the patients.
authors.affiliation: Department of Psychology, University of Palermo , Italy.
authors.forename: Lucia
authors.initials: L
authors.lastname: Parisi
authors.affiliation: Department of Psychology, University of Palermo , Italy.
authors.forename: Teresa
authors.initials: T
authors.lastname: Di Filippo
authors.affiliation: Department of Psychology, University of Palermo , Italy.
authors.forename: Sabina
authors.initials: S
authors.lastname: La Grutta
authors.affiliation: Psychiatric Clinic, University of Palermo , Italy.
authors.forename: Rosa
authors.initials: R
authors.lastname: Lo Baido
authors.affiliation: Department of Psychology, University of Palermo , Italy.
authors.forename: Maria Stella
authors.initials: MS
authors.lastname: Epifanio
authors.affiliation: Clinic of Child and Adolescent Neuropsychiatry, Second University of Naples , Italy.
authors.forename: Maria
authors.initials: M
authors.lastname: Esposito
authors.affiliation: Clinic of Child and Adolescent Neuropsychiatry, Second University of Naples , Italy.
authors.forename: Marco
authors.initials: M
authors.lastname: Carotenuto
authors.affiliation: Department of Psychology, University of Palermo , Italy.
authors.forename: Michele
authors.initials: M
authors.lastname: Roccella
keywords: Sturge-Weber syndrome; encephalotrigeminalangiomatosis; epilepsy; neurocutaneous syndrome