title: Oral findings in a family with Tuberous sclerosis complex.
abstract: Tuberous sclerosis complex (TSC) is an autosomal dominant disorder with a multisystemic character that may present alterations in multiple organ systems, including oral manifestations. This case report describes a family (mother and two sons) with TSC that underwent a multidisciplinary approach, emphasizing their oral manifestations and highlights the adequate approach taken. The children presented many and distinct features of TSC in different systems; however the family revealed similar oral manifestations. The oral findings were dental enamel pits on permanent teeth and spread gingival fibromas on both jaws. The dental planning was the same for all three patients and included guidelines on oral hygiene and dietary habits, fluoride therapy and a preventive approach through six-month reevaluations. In multisystemic disorders, early multidisciplinary action is vital to provide comprehensive care and reduce or even prevent complications from the condition, thus ensuring the patient's quality of life.
authors.affiliation: PhD Student, Department of Pediatric Dentistry and Orthodontics, School of Dentistry, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Rio de Janeiro, Brazil.|Assistant Professor, Department of Specific Trainning, Universidade Federal Fluminense, Nova Friburgo, Rio de Janeiro, Brazil.
authors.forename: Michelle Mikhael
authors.initials: MM
authors.lastname: Ammari
authors.affiliation: Full Professor, Department of Pediatric Dentistry and Orthodontics, School of Dentistry, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Rio de Janeiro, Brazil.
authors.forename: Ivete Pomarico
authors.initials: IP
authors.lastname: Ribeiro de Souza
authors.affiliation: Full Professor, Department of Pediatric Dentistry and Orthodontics, School of Dentistry, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Rio de Janeiro, Brazil.
authors.forename: Lucianne Cople
authors.initials: LC
authors.lastname: Maia
authors.affiliation: Associate Professor, Department of Pediatric Dentistry and Orthodontics, School of Dentistry, Universidade Federal do Rio de Janeiro, Rio de Janeiro, Rio de Janeiro, Brazil.
authors.forename: Laura Guimarães
authors.initials: LG
authors.lastname: Primo
keywords: case report; oral manifestations; tuberous sclerosis