title: Ventricular tachycardia an atypical presentation of Ebstein's disease.
abstract: Ebstein's anomaly (EA) is a rare congenital malformation, characterized by an apical displacement and dysplasia of the septal leaflet of the tricuspid valve with a right ventricular atrialization compromising its function. This malformation includes electrical conduction abnormalities, and very rarely ventricular arrhythmias. We report the case of a 22-year-old male, presenting with dizziness and palpitations. The electrocardiogram showed a sustained monomorphic ventricular tachycardia (SMVT). The presentation of the disease with ventricular tachycardia associated with hemodynamic instability is extremely rare. We placed a surgical implantable cardiac defibrillator when the diagnosis of EA, SMVT, and right ventricular systolic impairment was confirmed.
authors.affiliation: Department of Cardiology and Physiology, Faculty of Medicine, Universidad Abierta Interamericana, Buenos Aires, Argentina. E-mail. gpbaztarrica@yahoo.com.
authors.forename: Gabriel E
authors.initials: GE
authors.lastname: Baztarrica
authors.forename: Gastón G
authors.initials: GG
authors.lastname: Sereno
authors.forename: Sebastían A
authors.initials: SA
authors.lastname: Villecco
authors.forename: Rafael
authors.initials: R
authors.lastname: Porcile
mesh_terms: D004244:Dizziness / Q000209:etiology; D004437:Ebstein Anomaly / Q000150:complications / Q000175:diagnosis*; D004452:Echocardiography; D004562:Electrocardiography; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D017180:Tachycardia, Ventricular / Q000175:diagnosis* / Q000209:etiology; D055815:Young Adult