title: Journey to chew: a case of maxillary duplication and bony syngnathia.
abstract: Tessier no 3 cleft, bony syngnathia, and maxillary duplication are rare as independent anomalies and have never been reported together in a single case. Here we present a patient with congenital bony syngnathia, maxillary duplication, and a Tessier no. 3 nasal cleft. Other abnormalities included situs inversus, dextrocardia, coarctation of the aorta, left choanal stenosis, left coloboma, and hypertelorbitism. Given the unique presentation, we present our early surgical management to this complex problem.
authors.affiliation: Plastic Surgery, UT Houston, Houston, TX, USA. Electronic address: spatel17@gmail.com.
authors.forename: Shitel D
authors.initials: SD
authors.lastname: Patel
authors.affiliation: Oral and Maxillofacial Surgery, UT Houston, Houston, TX, USA.
authors.forename: Susana
authors.initials: S
authors.lastname: Porras
authors.affiliation: University of Missouri, Kansas City School of Medicine, Children's Mercy Hospital, Kansas City, USA.
authors.forename: Michael
authors.initials: M
authors.lastname: Lypka
mesh_terms: D001017:Aortic Coarctation / Q000175:diagnosis; D058747:CHARGE Syndrome / Q000175:diagnosis; D002754:Choanal Atresia / Q000175:diagnosis; D003103:Coloboma / Q000175:diagnosis; D003914:Dextrocardia / Q000175:diagnosis; D003937:Diagnosis, Differential; D006801:Humans; D006972:Hypertelorism / Q000175:diagnosis; D007231:Infant, Newborn; D008297:Male; D008334:Mandible / Q000002:abnormalities*; D008437:Maxilla / Q000002:abnormalities*; D009666:Nose / Q000002:abnormalities; D012857:Situs Inversus / Q000175:diagnosis
keywords: Bony sygnathia; Fat grafting; Maxillary duplication; Tessier 3 cleft