title: A familial poikiloderma-like cutaneous amyloidosis.
abstract: Familial poikiloderma-like cutaneous amyloidosis(FPLCA) is a rare, generalized but genetic dyschromic skin disorder characterized by amyloid deposits in dermis due to defective DNA repair secondary to sunlight damage. Clinically, it presents with diffuse brownish pigmentation with hypo-pigmented macules and many brownish scattered lichenoid papules with normal developmental milestones. The condition is autosomal dominant with incomplete penetrance. We are here reporting a rare familial case of FPLCA with a review of the literature.
authors.affiliation: Department of Dermatology, S. Nijlingappa Medical College, Bagalkot, Karnataka, India.
authors.forename: Mahesh
authors.initials: M
authors.lastname: Unni
authors.affiliation: Department of Dermatology, S. Nijlingappa Medical College, Bagalkot, Karnataka, India.
authors.forename: Balachandra
authors.initials: B
authors.lastname: Ankad
authors.affiliation: Department of Dermatology, S. Nijlingappa Medical College, Bagalkot, Karnataka, India.
authors.forename: Varna
authors.initials: V
authors.lastname: Naidu
authors.affiliation: Department of Dermatology, S. Nijlingappa Medical College, Bagalkot, Karnataka, India.
authors.forename: Km
authors.initials: K
authors.lastname: Sudakar Rao
keywords: Familial case; generalized macular amyloidosis; poikiloderma appearance