title: Basaloid Squamous Carcinoma of Skin Associated with Xeroderma Pigmentosum in an 8-year-old Child: A Rare Entity.
abstract: Xeroderma pigmentosum (XP) is a rare autosomal recessive genodermatosis associated with hypersensitivity to ultraviolet (UV) light, due to defects in deoxyribonucleic acid (DNA) repair. Basaloid squamous cell carcinoma is a rare aggressive variant of squamous cell carcinoma. Patients with XP are at increased risk of developing cutaneous malignancy and are commonly associated with squamous carcinoma. We report an extremely rare case of 8-year-old child with XP along with basaloidsquamous carcinoma of skin; and review of literature related to it.
authors.affiliation: Department of Head and Neck Oncology, Dr. B Borooah Cancer Institute, Guwahati, Assam, India.
authors.forename: Tashnin
authors.initials: T
authors.lastname: Rahman
authors.affiliation: Department of Pathology, Dr. B Borooah Cancer Institute, Guwahati, Assam, India.
authors.forename: Jagannath D
authors.initials: JD
authors.lastname: Sharma
authors.affiliation: Department of Head and Neck Oncology, Dr. B Borooah Cancer Institute, Guwahati, Assam, India.
authors.forename: Manigreeva
authors.initials: M
authors.lastname: Krishnatreya
authors.affiliation: Department of Head and Neck Oncology, Dr. B Borooah Cancer Institute, Guwahati, Assam, India.
authors.forename: Amal C
authors.initials: AC
authors.lastname: Kataki
keywords: Basaloid squamous carcinoma; cutaneous malignancy; xeroderma pigmentosum