title: Vascular malformation and common keratinocytic nevus of the soft type: phacomatosis pigmentovascularis revisited.
abstract: Phacomatosis pigmentovascularis is a rare syndrome characterized by the coexistence of a pigmented nevus and a cutaneous vascular malformation. We report a 5-year-old boy with all the typical findings of phacomatosis pigmentovascularis type Ia. Although its existence according to the traditional classification has been questioned, this case represents a very rare association of a capillary vascular malformation and a common keratinocytic nevus of the soft type.
authors.affiliation: Department of Dermatology and Venereology, Hospital de Curry Cabral, Centro Hospitalar de Lisboa Central, Rua da Beneficência, No. 8, 1069-166 Lisboa, Portugal.
authors.forename: André
authors.initials: A
authors.lastname: Laureano
authors.affiliation: Department of Dermatology and Venereology, Hospital de Curry Cabral, Centro Hospitalar de Lisboa Central, Rua da Beneficência, No. 8, 1069-166 Lisboa, Portugal.
authors.forename: Rodrigo
authors.initials: R
authors.lastname: Carvalho
authors.affiliation: Department of Dermatology and Venereology, Hospital de Curry Cabral, Centro Hospitalar de Lisboa Central, Rua da Beneficência, No. 8, 1069-166 Lisboa, Portugal.
authors.forename: Cristina
authors.initials: C
authors.lastname: Amaro
authors.affiliation: Department of Dermatology and Venereology, Hospital de Curry Cabral, Centro Hospitalar de Lisboa Central, Rua da Beneficência, No. 8, 1069-166 Lisboa, Portugal.
authors.forename: Isabel
authors.initials: I
authors.lastname: Freitas
authors.affiliation: Department of Dermatology and Venereology, Hospital de Curry Cabral, Centro Hospitalar de Lisboa Central, Rua da Beneficência, No. 8, 1069-166 Lisboa, Portugal.
authors.forename: Jorge
authors.initials: J
authors.lastname: Cardoso