title: Ehlers-Danlos syndrome.
abstract: Ehlers-Danlos syndrome (EDS) is a generalized disorder of one element of connective tissue manifesting clinically by fragility and hyperelasticity of the skin and joint laxity. It is a hereditary disorder, the inheritance being usually autosomal dominant with low penetrance. Autosomal recessive and X-linked recessive varieties are also known. First described by Hippocrates in 4(th) century B.C., the various clinical types with variable penetrance have been described lately. The number of cases EDS reported in the literature is very meagre. With the available information only about six publications of classic EDS in siblings had been reported in Indian literature.
authors.affiliation: Department of Dermatology, Venereology and leprosy, Dr. Prabhakar Kore Medical Hospital and Research Centre, KLE University, Belgaum, Karnataka, India.
authors.forename: Farhana Tahseen
authors.initials: FT
authors.lastname: Taj
authors.affiliation: Department of Dermatology, Venereology and leprosy, Dr. Prabhakar Kore Medical Hospital and Research Centre, KLE University, Belgaum, Karnataka, India.
authors.forename: Vijaya V
authors.initials: VV
authors.lastname: Sajjan
authors.affiliation: Department of Dermatology, Venereology and leprosy, Dr. Prabhakar Kore Medical Hospital and Research Centre, KLE University, Belgaum, Karnataka, India.
authors.forename: Dolly
authors.initials: D
authors.lastname: Singh
keywords: Cigarette paper scarring; Gorlin's sign; Reverse Namaskar sign