title: Urological surgery in epidermolysis bullosa: tactical planning for surgery and anesthesia.
abstract: Epidermolysis bullosa (EB) is characterized by extreme fragility of the skin and mucosae. Anesthetic and surgical techniques have to be adapted to those children and routine practice may not be adequate. Urological problems are relatively common, but surgical techniques adapted to those children have not been well debated and only low evidence is available to this moment. Herein we discuss the specifics of anesthetic and surgical techniques chosen to treat a six year old EB male presenting with symptomatic phimosis.
authors.affiliation: Department of Pediatric Surgery, Hospital Universitário Antônio Pedro, RJ, Brazil.
authors.forename: Lisieux Eyer de
authors.initials: LE
authors.lastname: Jesus
authors.affiliation: Department of Pediatric Surgery, Hospital Universitário Antônio Pedro, RJ, Brazil.
authors.forename: Maira
authors.initials: M
authors.lastname: Rangel
authors.affiliation: Department of Pediatric Surgery, Hospital Universitário Antônio Pedro, RJ, Brazil.
authors.forename: Ronaldo S
authors.initials: RS
authors.lastname: Moura-Filho
authors.affiliation: Department of Anesthesiology, Hospital Universitário Antônio Pedro, RJ, Brazil.
authors.forename: Glória
authors.initials: G
authors.lastname: Novaes
authors.affiliation: Department of Dermatology, Hospital Universitário Antônio Pedro, RJ, Brazil.
authors.forename: Ada
authors.initials: A
authors.lastname: Quattrino
authors.affiliation: Department of Pediatrics, Hospital Universitário Antônio Pedro, RJ, Brazil.
authors.forename: Angelica F
authors.initials: AF
authors.lastname: Aguas
mesh_terms: D000768:Anesthesia, General / Q000379:methods*; D002648:Child; D016108:Epidermolysis Bullosa Dystrophica / Q000150:complications / Q000601:surgery*; D006801:Humans; D008297:Male; D010688:Phimosis / Q000209:etiology / Q000601:surgery*; D053831:Surgical Fixation Devices; D016896:Treatment Outcome; D013521:Urologic Surgical Procedures, Male / Q000295:instrumentation / Q000379:methods*