title: Herlyn-Werner-Wunderlich syndrome: a very rare urogenital anomaly in a teenage girl.
abstract: BACKGROUND
  Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon variant of Müllerian duct anomalies, consisting of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents in a post-pubertal adolescent or adult woman in whom hematometrocolpos produces a pronounced mass effect and pain on the side of the obstructed hemivagina.
  
  
  METHODS
  We report the case of a 13-year-old girl who presented to the emergency radiology department with sudden onset of severe pain at the right lower quadrant of the abdomen; imaging confirmed the diagnosis of HWW syndrome. WHY SHOULD AN EMERGENCY PHYSICIAN BE AWARE OF THIS?: When unilateral renal agenesis and uterus didelphys coexist, the first thing that the physician should remember is to confirm or refute the presence of a blind vagina for diagnosis of HWW syndrome.
authors.affiliation: Department of Radiology, Ataturk University, School of Medicine, Erzurum, Turkey.
authors.forename: Leyla
authors.initials: L
authors.lastname: Karaca
authors.affiliation: Department of Radiology, Ataturk University, School of Medicine, Erzurum, Turkey.
authors.forename: Berhan
authors.initials: B
authors.lastname: Pirimoglu
authors.affiliation: Department of Radiology, Ataturk University, School of Medicine, Erzurum, Turkey.
authors.forename: Ummugulsum
authors.initials: U
authors.lastname: Bayraktutan
authors.affiliation: Department of Radiology, Ataturk University, School of Medicine, Erzurum, Turkey.
authors.forename: Hayri
authors.initials: H
authors.lastname: Ogul
authors.affiliation: Department of Pediatric Surgery, Ataturk University, School of Medicine, Erzurum, Turkey.
authors.forename: Akgun
authors.initials: A
authors.lastname: Oral
authors.affiliation: Department of Radiology, Ataturk University, School of Medicine, Erzurum, Turkey.
authors.forename: Mecit
authors.initials: M
authors.lastname: Kantarci
mesh_terms: D000006:Abdomen, Acute / Q000209:etiology; D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000293:Adolescent; D000013:Congenital Abnormalities / Q000175:diagnosis*; D005260:Female; D006801:Humans; D052202:Hydrocolpos / Q000150:complications / Q000175:diagnosis*; D007668:Kidney / Q000002:abnormalities*; D007674:Kidney Diseases / Q000151:congenital* / Q000175:diagnosis; D008279:Magnetic Resonance Imaging; D013577:Syndrome; D014599:Uterus / Q000002:abnormalities*; D014621:Vagina / Q000002:abnormalities*
keywords: Herlyn Werner Wunderlich syndrome; Müllerian duct anomalies; hematocolpos; renal agenesis