title: Hirschsprung's disease in twin to twin transfusion syndrome: a case report.
abstract: Twin to twin transfusion syndrome (TTTS) is caused by aberrant vascular connections between infant twins and results in high morbidity and mortality in the perinatal period. In donor infants with TTTS and symptoms of intestinal obstruction, small-bowel lesions have been reported in most cases. We report on a 33(+6) gestational wk donor infant with TTTS who had intermittent obstructive episodes, including delayed meconium passage and colonic dilatation on abdominal X-ray. The diagnosis of Hirschsprung's disease was based on a lateral pelvic film with a reversed rectosigmoid ratio. A subsequent barium colon study and rectal suction biopsy indicated a short segment aganglionosis of the colon.
authors.affiliation: Hye Won Park, Byung Ok Kwak, Min Hee Kim, Department of Pediatrics, Konkuk University Medical Center, Konkuk University School of Medicine, Seoul 143-729, South Korea.
authors.forename: Hye Won
authors.initials: HW
authors.lastname: Park
authors.affiliation: Hye Won Park, Byung Ok Kwak, Min Hee Kim, Department of Pediatrics, Konkuk University Medical Center, Konkuk University School of Medicine, Seoul 143-729, South Korea.
authors.forename: Min Jeng
authors.initials: MJ
authors.lastname: Cho
authors.affiliation: Hye Won Park, Byung Ok Kwak, Min Hee Kim, Department of Pediatrics, Konkuk University Medical Center, Konkuk University School of Medicine, Seoul 143-729, South Korea.
authors.forename: Wook Youn
authors.initials: WY
authors.lastname: Kim
authors.affiliation: Hye Won Park, Byung Ok Kwak, Min Hee Kim, Department of Pediatrics, Konkuk University Medical Center, Konkuk University School of Medicine, Seoul 143-729, South Korea.
authors.forename: Byung Ok
authors.initials: BO
authors.lastname: Kwak
authors.affiliation: Hye Won Park, Byung Ok Kwak, Min Hee Kim, Department of Pediatrics, Konkuk University Medical Center, Konkuk University School of Medicine, Seoul 143-729, South Korea.
authors.forename: Min Hee
authors.initials: MH
authors.lastname: Kim
mesh_terms: D000328:Adult; D001466:Barium Sulfate; D001706:Biopsy; D003125:Colostomy; D003287:Contrast Media; D003937:Diagnosis, Differential; D005260:Female; D005330:Fetofetal Transfusion / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D005769:Gastrointestinal Motility; D005865:Gestational Age; D006627:Hirschsprung Disease / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007150:Immunohistochemistry; D007231:Infant, Newborn; D007415:Intestinal Obstruction / Q000209:etiology / Q000503:physiopathology; D008297:Male; D011237:Predictive Value of Tests; D011247:Pregnancy; D059285:Pregnancy, Twin; D016896:Treatment Outcome
chemical_list: D003287:Contrast Media; D001466:Barium Sulfate
keywords: Aganglionosis; Delayed meconium passage; Donor; Hirschsprung’s disease; Twin to twin transfusion syndrome