title: Rare orbital cystic lesions in children.
abstract: OBJECTIVE
  To analyze the clinical features, imaging findings and surgical management of rare orbital cystic lesions in children.
  
  
  METHODS
  Clinical records of 5 Chinese children with rare orbital cystic lesions including cystic teratoma, congenital cystic eye, optic nerve sheath cyst, parasitic cyst, and meningoencephalocele were reviewed. Their clinical history, symptoms and signs, ultrasonography or computed tomography/magnetic resonance imaging (CT/MRI), surgical management were presented in detail.
  
  
  RESULTS
  Among the 5 patients, 2 were male and 3 female. The right orbit was involved in 2 patients and the left orbit in 3 patients. Ages ranged from 2 months to 11 years (mean, 4.2 years). Cystic teratoma showed a well-outlined cystic mass with a focal bone-like structure (or calcific densities) in their lumens as revealed with CT scan. Congenital cystic eye was a rare ocular malformation that existed at birth and showed a cystic lesion with no definite ocular structures in the orbit. With MRI examination, the optic nerve sheath cyst demonstrated a clear figure of the central optic nerve and the surrounding sheath cyst. Patients with parasitic cysts usually had frequent animal contact and high levels of blood eosinophils. Meningoencephalocele, the herniation into the orbit of brain tissue, had the typical CT/MRI features, with bone defect and soft tissue mass in the orbit and a homogenous appearance that was isodense with brain.
  
  
  CONCLUSIONS
  Besides common dermoid/epidermoid cyst, rare orbital cystic lesions such as cystic teratoma, congenital cystic eye, optic nerve sheath cyst, parasitic cyst, and meningoencephalocele should be considered in children.
authors.affiliation: The State Key Laboratory of Ophthalmology, Zhongshan Ophthalmic Center, Sun Yat-sen University, Guangzhou, 510060, People's Republic of China. Electronic address: yanjh2011@126.com.
authors.forename: Jianhua
authors.initials: J
authors.lastname: Yan
authors.affiliation: The State Key Laboratory of Ophthalmology, Zhongshan Ophthalmic Center, Sun Yat-sen University, Guangzhou, 510060, People's Republic of China.
authors.forename: Yongping
authors.initials: Y
authors.lastname: Li
authors.affiliation: The State Key Laboratory of Ophthalmology, Zhongshan Ophthalmic Center, Sun Yat-sen University, Guangzhou, 510060, People's Republic of China.
authors.forename: Qiwen
authors.initials: Q
authors.lastname: Chen
authors.affiliation: The State Key Laboratory of Ophthalmology, Zhongshan Ophthalmic Center, Sun Yat-sen University, Guangzhou, 510060, People's Republic of China.
authors.forename: Xuelian
authors.initials: X
authors.lastname: Ye
authors.affiliation: The State Key Laboratory of Ophthalmology, Zhongshan Ophthalmic Center, Sun Yat-sen University, Guangzhou, 510060, People's Republic of China.
authors.forename: Jianqun
authors.initials: J
authors.lastname: Li
mesh_terms: D002648:Child; D003560:Cysts / Q000151:congenital / Q000000981:diagnostic imaging*; D004443:Echinococcosis / Q000000981:diagnostic imaging; D004677:Encephalocele / Q000000981:diagnostic imaging; D005124:Eye Abnormalities / Q000000981:diagnostic imaging; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D008588:Meningocele / Q000000981:diagnostic imaging; D009901:Optic Nerve Diseases / Q000000981:diagnostic imaging; D009915:Orbit / Q000002:abnormalities; D009916:Orbital Diseases / Q000151:congenital / Q000000981:diagnostic imaging* / Q000469:parasitology; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging*; D035583:Rare Diseases; D012189:Retrospective Studies; D013724:Teratoma / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed / Q000379:methods; D014463:Ultrasonography / Q000379:methods
keywords: Congenital cystic eye; Meningoencephalocele; Optic nerve sheath cyst; Orbital cyst; Parasitic cyst; Teratoma