title: [Hemiconvulsion-hemiplegia-epilepsy syndrome in a girl with adrenogenital syndrome].
abstract: Hemiconvulsion-hemiplegia-epilepsy (HHE) syndrome is a very rare condition caused by a fever-associated status epilepticus causing various degrees of hemiplegia and secondary epilepsy affecting children under the age of four. The aetiology is not fully understood. We report a case of a two-year-old girl with adrenogenital syndrome presenting with HHE syndrome in the course of a bacterial septicaemia.
authors.affiliation: Dronningens Tværgade 46, 2.-3., 1302 København K. maikenvest@hotmail.com.
authors.forename: Maiken
authors.initials: M
authors.lastname: Vestergaard
authors.forename: Peter
authors.initials: P
authors.lastname: Uldall
mesh_terms: D047808:Adrenogenital Syndrome / Q000150:complications; D002675:Child, Preschool; D004827:Epilepsy / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000188:drug therapy; D005260:Female; D005334:Fever / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy; D006429:Hemiplegia / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000188:drug therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D011859:Radiography; D013226:Status Epilepticus / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000188:drug therapy; D013577:Syndrome