title: Regional anaesthesia in a Duchenne muscular dystrophy patient for upper extremity amputation.
abstract: Duchenne muscular dystrophy (DMD) is the most common of the neuromuscular disorders. DMD is usually a challenge for the anaesthesiologist, with poor cardiac function, a high risk of developing rhabdomyolysis, and the probable life-threatening complications of general anaesthesia. To avoid possible morbidity associated with general anaesthesia, we applied a supraclavicular blockade. In this report, we present a 17-year-old DMD patient with a massive rhabdomyosarcoma, for whom a left arm amputation was indicated. In the post-operative period, a malignant hyperthermia-like reaction occurred, which resolved in a short time. We suggest a regional blockade as a safer alternative to general anaesthesia for the management of high risk DMD patients during orthopedic procedures.
authors.affiliation: Department of Anesthesiology, İstanbul University İstanbul Faculty of Medicine, İstanbul, Turkey.
authors.forename: Mehmet İlke
authors.initials: Mİ
authors.lastname: Büget
authors.affiliation: Department of Orthopaedics and Traumatology, İstanbul University İstanbul Faculty of Medicine, İstanbul, Turkey.
authors.forename: İlker
authors.initials: İ
authors.lastname: Eren
authors.affiliation: Department of Anesthesiology, İstanbul University İstanbul Faculty of Medicine, İstanbul, Turkey.
authors.forename: Süleyman
authors.initials: S
authors.lastname: Küçükay
mesh_terms: D000293:Adolescent; D000671:Amputation, Surgical; D000779:Anesthetics, Local / Q000008:administration & dosage; D001132:Arm / Q000601:surgery*; D001917:Brachial Plexus; D002045:Bupivacaine / Q000008:administration & dosage; D006801:Humans; D008297:Male; D020388:Muscular Dystrophy, Duchenne; D009407:Nerve Block; D010149:Postoperative Pain / Q000517:prevention & control*; D012208:Rhabdomyosarcoma / Q000601:surgery*
chemical_list: D000779:Anesthetics, Local; D002045:Bupivacaine