title: Multiple aortic operations in loeys-dietz syndrome: report of 2 cases.
abstract: Due to its low prevalence and because there is lack of awareness about it, Loeys-Dietz syndrome is often mis-diagnosed as Marfan syndrome, which has similar skeletal abnormalities and aortic pathology. However, the differential diagnosis between these two connective tissue diseases is critical because they correspond to different surgical indications and surgical decision-making. We report two cases of successful thoracoabdominal aortic replacement in patients with previously undiagnosed Loeys-Dietz syndrome.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine.
authors.forename: Kwon Joong
authors.initials: KJ
authors.lastname: Na
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine.
authors.forename: Kay-Hyun
authors.initials: KH
authors.lastname: Park
keywords: Aorta, surgery; Aortic aneurysm; Loeys-Dietz syndrome; Marfan syndrome