title: [Hemiconvulsion-hemiplegia-epilepsy syndrome].
abstract: Hemiconvulsion-hemiplegia-epilepsy syndrome is a rare consequence of a status epilepticus in the course of a febrile illness in children under the age of four years. Various degrees of hemiplegia and within a variable interval, subsequent epilepsia follows. Neuroimaging show unilateral cytotoxic oedema at the initial convulsive state, followed by severe chronic atrophy of the affected hemisphere. The aetiology remains unclear. Several mechanisms may contribute to this condition. To improve the outcome, further studies are needed and early diagnosis is essential.
authors.affiliation: Dronningens Tværgade 46, 2.-3., 1302 København K. maikenvest@hotmail.com.
authors.forename: Maiken
authors.initials: M
authors.lastname: Vestergaard
authors.forename: Peter
authors.initials: P
authors.lastname: Uldall
mesh_terms: D001921:Brain / Q000000981:diagnostic imaging / Q000503:physiopathology; D002675:Child, Preschool; D004827:Epilepsy / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000188:drug therapy; D005334:Fever / Q000150:complications / Q000175:diagnosis; D006429:Hemiplegia / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000188:drug therapy; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D011859:Radiography; D035583:Rare Diseases; D013226:Status Epilepticus / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000188:drug therapy; D013577:Syndrome