title: Extraskeletal myxoid chondrosarcoma of the thigh in a child: a case report.
abstract: Extraskeletal myxoid chondrosarcoma (EMC) is aggressive in children. The condition in children differs to that in adults and to skeletal myxoid chondrosarcoma. We report on a 9-year-old girl with EMC in her left thigh. She underwent above-knee amputation. Five months later, a small mass was noted at the right lower lobe of the lung. The patient underwent one course of ifosfamide, carboplatin, and etoposide chemotherapy, followed by resection of the mass and 8 more courses of chemotherapy. At the 2-year follow-up, she was in remission radiologically.
authors.affiliation: Department of Pathology, Faculty of Medicine and Health Sciences, Universiti Malaysia Sarawak, Kuching, Sarawak, Malaysia.
authors.forename: Zainal Abidin
authors.initials: ZA
authors.lastname: Ibrahim
authors.affiliation: Department of Orthopedics, Faculty of Medicine and Health Sciences, Universiti Malaysia Sarawak, Kuching, Sarawak, Malaysia.
authors.forename: Wai Hoong
authors.initials: WH
authors.lastname: Chan
authors.affiliation: Sibu Specialist Medical Centre, Sarawak, Malaysia.
authors.forename: Siong Lung
authors.initials: SL
authors.lastname: Wong
authors.affiliation: Pediatrics Department, Sabah Women and Children's Hospital, Kota Kinabalu, Sabah, Malaysia.
authors.forename: Eng Joe
authors.initials: EJ
authors.lastname: Ong
authors.affiliation: Department of Pathology, Faculty of Medicine and Health Sciences, Universiti Malaysia Sarawak, Kuching, Sarawak, Malaysia.
authors.forename: M Zulkarnaen A
authors.initials: MZ
authors.lastname: Narihan
mesh_terms: D000671:Amputation, Surgical; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D016190:Carboplatin / Q000008:administration & dosage; D002648:Child; D002813:Chondrosarcoma / Q000556:secondary / Q000601:surgery*; D005047:Etoposide / Q000008:administration & dosage; D005260:Female; D006801:Humans; D007069:Ifosfamide / Q000008:administration & dosage; D008175:Lung Neoplasms / Q000556:secondary / Q000628:therapy*; D018204:Neoplasms, Connective and Soft Tissue / Q000556:secondary / Q000601:surgery*; D012983:Soft Tissue Neoplasms / Q000473:pathology / Q000601:surgery*; D013848:Thigh
chemical_list: D005047:Etoposide; D016190:Carboplatin; D007069:Ifosfamide
keywords: chondrosarcoma, extraskeletal myxoid; paediatrics; thigh