title: Ipsilateral cochlear implantation in patients with sporadic vestibular schwannoma in the only or best hearing ear and in patients with NF2.
abstract: The aim of this study was to evaluate the cochlear implant (CI) performances in neurofibromatosis type 2 (NF2) patients with bilateral vestibular schwannoma (VS) and in patients with sporadic VS in the only or better hearing ear. All patients with bilateral VS or sporadic VS in the only or better hearing ear who underwent cochlear implantation, either simultaneous to VS surgery or staged after treatment for VS, in the tumor side were chosen for the study. Postimplantation audiometric scores (sound detection, closed-set and open-set discrimination scores) and device use patterns were the main outcome measures. 15 patients were implanted. Eight patients (53 %) were NF2 and seven patients had VS in the only or better hearing ear. One patient was explanted for cerebrospinal fluid leak. In the CI-only condition, the other 14 patients obtained sound detection, 64 % of them achieving open-set discrimination (mean 70 ± 38 %) and 85 % achieving closed-set discrimination (mean 41 ± 33 %). At the last follow-up 10 patients (67 %) were using the CI. Cochlear implantation provides hearing in particular cases of patients with bilateral VS or VS in the only or better hearing ear. As long as anatomic preservation of the cochlear nerve is achieved, cochlear implantation may offer improvement in communication skills for most patients.
authors.affiliation: Department of Otolaryngology, IdiPaz Research Institute, "La Paz" University Hospital, Paseo de La Castellana 261, 28046, Madrid, Spain. luikilassa@yahoo.com.
authors.forename: Luis
authors.initials: L
authors.lastname: Lassaletta
authors.affiliation: Department of Otolaryngology, "Gregorio Marañon" University Hospital, C/Doctor Esquerdo 46, 28007, Madrid, Spain.
authors.forename: Miguel
authors.initials: M
authors.lastname: Aristegui
authors.affiliation: Department of Otolaryngology, "Rey Juan Carlos" Hospital, C/ Gladiolo, s/n, 28933, Móstoles, Madrid, Spain.
authors.forename: Marimar
authors.initials: M
authors.lastname: Medina
authors.affiliation: Department of Otolaryngology, "Gregorio Marañon" University Hospital, C/Doctor Esquerdo 46, 28007, Madrid, Spain.
authors.forename: Gracia
authors.initials: G
authors.lastname: Aranguez
authors.affiliation: Department of Otolaryngology, IdiPaz Research Institute, "La Paz" University Hospital, Paseo de La Castellana 261, 28046, Madrid, Spain.
authors.forename: Rosa M
authors.initials: RM
authors.lastname: Pérez-Mora
authors.affiliation: Department of Otology and Skull Base Surgery, Gruppo Otologico Piacenza-Rome, University of Chieti, Chieti. Via Emmanueli 42, 29121, Piacenza, Italy.
authors.forename: Maurizio
authors.initials: M
authors.lastname: Falcioni
authors.affiliation: Department of Otolaryngology, IdiPaz Research Institute, "La Paz" University Hospital, Paseo de La Castellana 261, 28046, Madrid, Spain.
authors.forename: Javier
authors.initials: J
authors.lastname: Gavilán
authors.affiliation: Department of Neuroradiology, University of Parma, Parma, Italy.
authors.forename: Paolo
authors.initials: P
authors.lastname: Piazza
authors.affiliation: Department of Otology and Skull Base Surgery, Gruppo Otologico Piacenza-Rome, University of Chieti, Chieti. Via Emmanueli 42, 29121, Piacenza, Italy.
authors.forename: Mario
authors.initials: M
authors.lastname: Sanna
mesh_terms: D000328:Adult; D000368:Aged; D001299:Audiometry; D019929:Cochlear Implantation; D005260:Female; D006309:Hearing / Q000502:physiology*; D006801:Humans; D008297:Male; D008875:Middle Aged; D016518:Neurofibromatosis 2 / Q000150:complications*; D009464:Neuroma, Acoustic / Q000601:surgery*; D012189:Retrospective Studies; D055815:Young Adult
keywords: Cochlear implantation; Hearing outcome; Neurofibromatosis type 2; Vestibular schwannoma