title: Angiomyolipoma of the helix without signs of systemic involvement: successful surgical approach.
abstract: Cutaneous angiomyolipoma (AMP) of the ear is an extremely rare benign mesenchymal tumour. Angiomyolipomas are the most common benign tumour of the kidney and could be associated in 20&#x0025; of the cases with the tuberous sclerosis complex (TBC), in which condition, most of the patients have several angiomyolipomas affecting both of the kidneys. We report the rare case of a 66-year-old female who had an asymptomatic, solitary, nodule on the helix of the right ear for several years, which was histologically assessed as angiomyolipoma. There were no clinical signs of the tuberous sclerosis complex (TBC) or renal AML. A surgical excision was performed with an excellent therapeutic result. In contrast to renal AMLs or PEComas, which are often invasive and may involve regional nodes, cutaneous AMLs are solitary, non-invasive, and not associated with tuberous sclerosis, and are curable by simple elliptical excision.
authors.affiliation: Policlinic for Dermatology and Venereology, Saint Kliment Ohridski University, Medical Faculty, University Hospital Lozenetz, Sofia, Bulgaria.
authors.forename: G
authors.initials: G
authors.lastname: Tchernev
authors.affiliation: Department of General and Clinical Pathology, Medical Faculty, Saint Kliment Ohridski University Sofia, Bulgaria.
authors.forename: S
authors.initials: S
authors.lastname: Philipov
authors.affiliation: Department of General and Clinical Pathology, Medical Faculty, Trakia University, Stara Zagora, Bulgaria.
authors.forename: J
authors.initials: J
authors.lastname: Ananiev
authors.affiliation: Department of General and Clinical Pathology, Medical Faculty, Trakia University, Stara Zagora, Bulgaria.
authors.forename: M
authors.initials: M
authors.lastname: Gulubova
authors.affiliation: Onkoderma- Policlinic for Dermatology and Dermatologic Surgery, General Skobelev 26 Sofia, Bulgaria.
authors.forename: A A
authors.initials: AA
authors.lastname: Chokoeva
authors.affiliation: Department of Medicine and Science of Aging G. DAnnunzio University, Chieti, Italy.
authors.forename: C
authors.initials: C
authors.lastname: Tana
authors.affiliation: Department of Dermatology and Allergology, Hospital Dresden-Friedrichstadt, Academic Teaching Hospital of the Technical University of Dresden, Dresden, Germany.
authors.forename: U
authors.initials: U
authors.lastname: Wollina
mesh_terms: D000368:Aged; D018207:Angiomyolipoma / Q000473:pathology / Q000601:surgery*; D004428:Ear Neoplasms / Q000473:pathology / Q000601:surgery*; D005260:Female; D006801:Humans; D012878:Skin Neoplasms / Q000473:pathology / Q000601:surgery*