title: Christmas disease: diagnosis and management of a haemorrhagic diathesis following dentofacial trauma.
abstract: Haemorrhagic diathesis has been of much concern to health professionals including dentists. It is not infrequent that a dentist becomes the first person to diagnose a bleeding disorder while performing dental treatment. Haemophilia is an X linked disorder with a frequency of about 1:10,000 births. Haemophilia B is much less common than haemophilia A, and affects only 1:300,000 males born alive. The clinical features of haemophilia B are very similar to those of haemophilia A with a prolongation of activated partial thromboplastin time. This case report describes the dental management of a patient with an uncommon haematological disorder, namely, factor IX deficiency, which remained undiagnosed until the patient had to undergo dentofacial trauma with unexpected severe haemorrhage. Preventive dentistry remains vital to young haemophiliacs. Surgical dental procedures may be performed for haemophiliacs but they must be judiciously coordinated by dental and medical health professionals.
authors.affiliation: Department of Pedodontics, Bharati Vidyapeeth Deemed University Dental College and Hospital, Sangli, Maharashtra, India.
authors.forename: Sridevi B
authors.initials: SB
authors.lastname: Tamagond
authors.affiliation: Department of Conservative Dentistry, Bharati Vidyapeeth Deemed University Dental College and Hospital, Sangli, Maharashtra, India.
authors.forename: Santosh I
authors.initials: SI
authors.lastname: Hugar
authors.affiliation: Department of Pedodontics, Bharati Vidyapeeth Deemed University Dental College and Hospital, Sangli, Maharashtra, India.
authors.forename: Anil
authors.initials: A
authors.lastname: Patil
authors.affiliation: Department of Pedodontics, Bharati Vidyapeeth Deemed University Dental College and Hospital, Sangli, Maharashtra, India.
authors.forename: SandhyaRani
authors.initials: S
authors.lastname: Huddar
mesh_terms: D002648:Child; D003029:Coagulants / Q000627:therapeutic use; D005164:Factor IX / Q000627:therapeutic use; D006406:Hematoma / Q000188:drug therapy* / Q000209:etiology; D002836:Hemophilia B / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy*; D006801:Humans; D007180:Incisor / Q000293:injuries*; D008046:Lip / Q000293:injuries*; D008297:Male
chemical_list: D003029:Coagulants; D005164:Factor IX