title: Brugada syndrome in children.
abstract: Brugada syndrome is an inherited arrhythmia associated with characteristic ST elevation in the right precordial leads and sudden cardiac death. The average age of sudden cardiac death is 40 years; reported pediatric cases remain rare. Genetic testing and increased disease awareness may result in many more children being diagnosed with Brugada syndrome.
authors.affiliation: Pediatric Cardiology, Bloomberg Children's Center, Johns Hopkins Hospital, 1800 Orleans Street, Baltimore, MD 21287, USA.
authors.forename: Jane E
authors.initials: JE
authors.lastname: Crosson
authors.forename: Melanie
authors.initials: M
authors.lastname: Nies
mesh_terms: D000367:Age Factors; D001145:Arrhythmias, Cardiac / Q000175:diagnosis / Q000235:genetics / Q000503:physiopathology / Q000628:therapy; D053840:Brugada Syndrome / Q000175:diagnosis / Q000235:genetics / Q000503:physiopathology / Q000628:therapy; D000075224:Cardiac Conduction System Disease; D002648:Child; D002675:Child, Preschool; D016757:Death, Sudden, Cardiac / Q000209:etiology*; D004562:Electrocardiography / Q000379:methods; D006321:Heart / Q000503:physiopathology*; D006329:Heart Conduction System / Q000002:abnormalities* / Q000503:physiopathology; D006801:Humans
keywords: Brugada syndrome; ECG; SCN5A; ST elevation; children; defibrillator; genetic syndrome; quinidine; sudden death; ventricular tachycardia