title: Angiokeratoma circumscriptum naeviforme with soft tissue hypertrophy and deep venous malformation: A variant of Klippel-Trenaunay syndrome?
abstract: Klippel-Trenaunay syndrome (KTS) is a cutaneous capillary malformation on a limb in association with soft tissue swelling with or without bony hypertrophy and atypical varicosity. The capillary malformation associated with KTS is port wine stain. Angiokeratoma circumscriptum naeviforme (ACN) is a congenital variant of angiokeratoma commonly present on the lower limb as a hyperkeratotic plaque. ACN is rarely associated with KTS. We report a case of ACN with soft tissue hypertrophy and deep venous malformation (possibly a variant of Klippel-Trenaunay) in a 4-year-old male child.
authors.affiliation: Department of Dermatology, Government Medical College and Hospital, Nagpur, Maharashtra, India.
authors.forename: Vaishali
authors.initials: V
authors.lastname: Wankhade
authors.affiliation: Department of Dermatology, Government Medical College and Hospital, Nagpur, Maharashtra, India.
authors.forename: Rajesh
authors.initials: R
authors.lastname: Singh
authors.affiliation: Department of Dermatology, Government Medical College and Hospital, Nagpur, Maharashtra, India.
authors.forename: Venus
authors.initials: V
authors.lastname: Sadhwani
authors.affiliation: Department of Pathology, Government Medical College and Hospital, Nagpur, Maharashtra, India.
authors.forename: Purnima
authors.initials: P
authors.lastname: Kodate
authors.affiliation: Department of Radiology, Government Medical College and Hospital, Nagpur, Maharashtra, India.
authors.forename: Amit
authors.initials: A
authors.lastname: Disawal
keywords: Angiokeratoma circumscriptum neviforme; Klippel-Trenaunay syndrome; deep venous malformation