title: Cystic lung disease in birt-hogg-dubé syndrome: a case series of three patients.
abstract: Birt-Hogg-Dubé syndrome is characterized by clinical manifestations such as hamartomas of the skin, renal tumors and lung cysts with spontaneous pneumothoraces. Patients with Birt-Hogg-Dubé syndrome may present with only multiple lung cysts. We report the chest computerized tomography (CT) features of three patients with Birt-Hogg-Dubé syndrome. Each patient had multiple lung cysts of various sizes according to chest CT evaluation, most of which were located in lower lobes and related to pleura. The identification of unique characteristics in the chest CT of patients with Birt-Hogg-Dubé syndrome may provide an efficient mechanism for diagnosis.
authors.affiliation: Department of Radiology, Hacettepe University Faculty of Medicine, Ankara, Turkey.
authors.forename: Abidin
authors.initials: A
authors.lastname: Kilincer
authors.affiliation: Department of Radiology, Hacettepe University Faculty of Medicine, Ankara, Turkey.
authors.forename: Orhan Macit
authors.initials: OM
authors.lastname: Ariyurek
authors.affiliation: Department of Radiology, Pamukkale University Hospital, Denizli, Turkey.
authors.forename: Nevzat
authors.initials: N
authors.lastname: Karabulut
keywords: Birt-Hogg-Dubé syndrome; chest CT; lung cyst