title: Sustained ventricular tachycardia in a patient with isolated non-compaction cardiomyopathy.
abstract: Isolated non-compaction of the left ventricular myocardium (INVM) was first described in 1984 as an unclassified cardiomyopathy, not being dilated, hypertrophic or restrictive. It is assumed to occur as a result of an arrest in endomyocardial morphogenesis during normal development of the heart. The disease is characterised by heart failure due to systolic and diastolic left ventricular (LV) dysfunction, systemic emboli and ventricular arrhythmias. Echocardiography has been shown to be the method of choice in diagnosis. INVM is a rare congenital cardiomyopathy and only a few cases of this condition have been reported. It is characterised by prominent and excessive trabeculation in a ventricular wall segment, with deep inter-trabecular spaces perfused from the ventricular cavity. We report a case of INVM with ventricular tachycardia induced during electrophysiological study in a 24-year-old female patient with a family history of sudden death.
authors.affiliation: Department of Cardiology, Medical Faculty, Pamukkale University, Denizli, Turkey. aliizyu@mynet.com.
authors.forename: Yusuf Izzettin
authors.initials: YI
authors.lastname: Alihanoglu
authors.affiliation: Department of Cardiology, Medical Faculty, Pamukkale University, Denizli, Turkey.
authors.forename: Ismail Dogu
authors.initials: ID
authors.lastname: Kilic
authors.affiliation: Department of Cardiology, Medical Faculty, Pamukkale University, Denizli, Turkey.
authors.forename: Bekir Serhat
authors.initials: BS
authors.lastname: Yildiz
authors.affiliation: Department of Cardiology, Nevsehir State Hospital, Nevsehir, Turkey.
authors.forename: Mustafa
authors.initials: M
authors.lastname: Kartin
authors.affiliation: Department of Cardiology, Medical Faculty, Pamukkale University, Denizli, Turkey.
authors.forename: Harun
authors.initials: H
authors.lastname: Evrengul
mesh_terms: D000328:Adult; D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000150:complications / Q000175:diagnosis*; D017180:Tachycardia, Ventricular / Q000175:diagnosis* / Q000209:etiology