title: Improved pulmonary function following pirfenidone treatment in a patient with progressive interstitial lung disease associated with systemic sclerosis.
abstract: Pirfenidone is an anti-fibrotic drug which has been approved for the management of patients with Idiopathic Pulmonary Fibrosis (IPF). However, its role in interstitial lung disease (ILD) due to other causes such as systemic sclerosis (SSc) is not clear. We present a case of a patient with SSc associated ILD who showed a subjective as well as objective improvement in lung function with pirfenidone.
authors.affiliation: Department of Respiratory Medicine, PD Hinduja National Hospital and Medical Research Centre, Mumbai, Maharashtra, India.
authors.forename: Zarir F
authors.initials: ZF
authors.lastname: Udwadia
authors.affiliation: Department of Respiratory Medicine, PD Hinduja National Hospital and Medical Research Centre, Mumbai, Maharashtra, India.
authors.forename: Jai B
authors.initials: JB
authors.lastname: Mullerpattan
authors.affiliation: Department of Rheumatology, PD Hinduja National Hospital and Medical Research Centre, Mumbai, Maharashtra, India.
authors.forename: Canchi
authors.initials: C
authors.lastname: Balakrishnan
authors.affiliation: Department of Respiratory Medicine, Chair of Interstitial Lung Disease, Centre for Rare Lung Diseases, University of Modena and Reggio Emilia, Modena, Italy.
authors.forename: Luca
authors.initials: L
authors.lastname: Richeldi
keywords: Interstitial lung disease; pirfenidone; systemic sclerosis