title: Atypical abnormal pulmonary vein drainage with atrial septal defect: surgical treatment.
abstract: Sinus venosus atrial septal defect (SV-ASD) usually coexists with partial anomalous pulmonary vein connection (PAPVC). It is a difficult diagnosis in transthoracic echocardiography (TTE) due to eccentric position of defects. We present a rare case of atypical anatomical variation in PAPVC, which was never described before. Two right pulmonary veins drained into superior vena cava, which overrode SV-ASD and interatrial septum, a third pulmonary vein into the right atrium. Complete diagnosis could not be set after TTE, nor transesophageal echocardiography, whereas angio-CT was finally conclusive. This diagnostic approach allowed the surgical planning.
authors.affiliation: 1st Chair and Department of Cardiology, Medical University of Warsaw, Warsaw, Poland.
authors.forename: Wojciech
authors.initials: W
authors.lastname: Szychta
authors.affiliation: Cardiology Division in Cardiac Surgery Dept, Policlinic of Monza, San Gaudenzio Clinic, Novara, Italy.
authors.forename: Gheorghe
authors.initials: G
authors.lastname: Cerin
authors.affiliation: Cardiology Division in Cardiac Surgery Dept, Policlinic of Monza, San Gaudenzio Clinic, Novara, Italy.
authors.forename: Bogdan Adrian
authors.initials: BA
authors.lastname: Popa
authors.affiliation: Department of Radiology, Policlinic of Monza, San Gaudenzio Clinic, Novara, Italy.
authors.forename: Armienti
authors.initials: A
authors.lastname: Felice
authors.affiliation: Departments of Cardiac Surgery, Policlinic of Monza, San Gaudenzio Clinic, Novara, Italy.
authors.forename: Guido
authors.initials: G
authors.lastname: Lanzillo
authors.affiliation: Departments of Cardiac Surgery, Policlinic of Monza, San Gaudenzio Clinic, Novara, Italy.
authors.forename: Marco
authors.initials: M
authors.lastname: Diena
authors.affiliation: 1st Chair and Department of Cardiology, Medical University of Warsaw, Warsaw, Poland.
authors.forename: Grzegorz
authors.initials: G
authors.lastname: Opolski
mesh_terms: D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000601:surgery*; D000328:Adult; D004452:Echocardiography / Q000379:methods*; D006344:Heart Septal Defects, Atrial / Q000000981:diagnostic imaging* / Q000601:surgery*; D006801:Humans; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery*; D016896:Treatment Outcome
keywords: Computed tomography; echocardiography; pulmonary arteries/veins; pulmonary vascular resistance/hypertension; septal defects