title: [Idiopathic pulmonary fibrosis: new insights].
abstract: Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive lung disease of unknown cause. IPF has a poor prognosis with a mean survival of 2 to 5 years after diagnosis. The diagnostic process is often complex and demands a multidisciplinary approach. To date, the only curative therapy available is lung transplant. New insights into the pathogenesis of IPF have brought about changes in standard treatment strategies. New drugs have recently become available and have been shown to slow down the decline in pulmonary function considerably and improve survival.
authors: Erasmus MC, afd. Longziekten, Rotterdam.
authors: Jitske W
authors: JW
authors: Kraan
authors: Bernt
authors: B
authors: van den Blink
authors: Leon M
authors: LM
authors: van den Toorn
authors: Paul
authors: P
authors: Bresser
authors: Frouke T
authors: FT
authors: van Beek
authors: Jan C
authors: JC
authors: Grutters
authors: Marlies S
authors: MS
authors: Wijsenbeek
mesh_terms: D002908:Chronic Disease; D006801:Humans; D054990:Idiopathic Pulmonary Fibrosis / Q000175:diagnosis* / Q000401:mortality / Q000601:surgery*; D008168:Lung / Q000473:pathology; D016040:Lung Transplantation; D011379:Prognosis