title: Female form of persistent mullerian duct syndrome: Rare entity.
abstract: Persistent Mullerian duct syndrome (PMDS) is a rare form of Disorder of sex development in which Mullerian duct derivatives (fallopian tubes, uterus and the proximal vagina) are present in an otherwise normally differentiated 46 XY male. In the majority of cases, PMDS is a surprise finding either during orchidopexy or during inguinal hernia repair. We report a case of 4 year child with female type (Type III) PMDS. We are discussing the presentation, management and review of the literature.
authors: Department of Pediatric Surgery, Indira Gandhi Institute of Child Health, Bengaluru, Karnataka, India.
authors: Shailesh
authors: S
authors: Solanki
authors: Department of Pediatric Surgery, Indira Gandhi Institute of Child Health, Bengaluru, Karnataka, India.
authors: Gowrishankar
authors: Department of Pediatric Surgery, Indira Gandhi Institute of Child Health, Bengaluru, Karnataka, India.
authors: Vinay
authors: V
authors: Jadhav
authors: Department of Pediatric Surgery, Indira Gandhi Institute of Child Health, Bengaluru, Karnataka, India.
authors: M Narendra
authors: MN
authors: Babu
authors: Department of Pediatric Surgery, Indira Gandhi Institute of Child Health, Bengaluru, Karnataka, India.
authors: S
authors: S
authors: Ramesh
keywords: Anti Mullerian hormone; cryptorchidism; hernia uteri inguinale; persistent Mullerian duct syndrome
references: Indian J Surg. 2010 Feb;72(1):16-9
references: 23133198
references: Radiographics. 2003 Mar-Apr;23 (2):309-13
references: 12640149
references: Best Pract Res Clin Endocrinol Metab. 2011 Apr;25(2):221-38
references: 21397195
references: Br J Urol. 1997 Jan;79(1):122-6
references: 9043511
references: Clin Imaging. 2008 Jul-Aug;32(4):314-7
references: 18603188
references: Urology. 2005 Jul;66(1):194-5
references: 16009404
references: Urology. 1997 Jun;49(6):941-5
references: 9187705
references: AJR Am J Roentgenol. 2000 Jan;174(1):102-4
references: 10628462