title: Prosthetic rehabilitation of hypophosphatasia with precision attachment retained unconventional partial denture: a case report.
abstract: Deficiency of the alkaline phosphatase isoenzyme can lead to a rare hereditary disorder called Hypophosphatasia. It is characterized by defective mineralization of the skeletal and dental structures of the body. Hypophophatasia is classified into six clinical forms namely, perinatal lethal, perinatal benign, infantile, childhood, adult and odontohypophosphatasia. This clinical report describes the prosthetic rehabilitation of an 18-year-old girl with Hypophosphatasia with partial anodontia and no occlusion. A precision attachment retained unconventional removable partial denture in the maxillary arch and conventional removable partial denture in the mandibular were fabricated to establish an acceptable masticatory function, speech, occlusion and aesthetics for the patient.
authors: Senior Lecturer, Department of Prosthodontics, Dr D.Y.Patil Dental College and Hospital , Navi Mumbai, Maharashtra, India .
authors: Gayatri Sheena
authors: GS
authors: Suvarna
authors: Professor, Department of Prosthodontics and Implantology, S.D.M College of Dental Sciences and Hospital , Dharwad, Karnataka, India .
authors: Ramesh Khandurao
authors: RK
authors: Nadiger
authors: Professor, Department of Prosthodontics and Implantology, S.D.M College of Dental Sciences and Hospital , Dharwad, Karnataka, India .
authors: Satyabodh Shesharaj
authors: SS
authors: Guttal
authors: Professor and Head, Department of Prosthodontics, Dr D.Y.Patil Dental College and Hospital , Navi Mumbai, Maharashtra, India .
authors: Omkar
authors: O
authors: Shetty
keywords: Hypophosphatasia; Odontohypophosphatasia; Precision attachment; Removable partial denture
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