title: Choice of anesthesia in molybdenum cofactor deficiency: A case report.
abstract: Molybdenum cofactor (MC) deficiency is defined as a progressive neurodegenerative and neurometabolic disease, characterized by convulsions, severe mental and motor retardation resistant to the treatment. Patients with MC deficiency usually need at least sedation for even minor interventions such as dental examination or treatment. Sedation or general anesthesia for these patients may be complicated due to accompanying disorders. However, we were unable to find any reports on anesthetic management of patients with MC deficiency in the literature. In this article, we intend to share our experience of a patient with MC deficiency, who had undergone dental treatment under deep sedation.
authors: Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Gazi University, Ankara, Turkey.
authors: Metin
authors: M
authors: Alkan
authors: Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Gazi University, Ankara, Turkey.
authors: Gülay
authors: G
authors: Kip
authors: Department of Oral and Maxillofacial Surgery, Faculty of Dentistry, Gazi University, Ankara, Turkey.
authors: Şaziye
authors: Ş
authors: Şahin
authors: Department of Pedodontics, Faculty of Dentistry, Gazi University, Ankara, Turkey.
authors: Didem
authors: D
authors: Atabek
keywords: Deep; ketamine; molybdenum cofactor deficiency; sedation
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