title: Uhl's anomaly: Absence of the right ventricular myocardium.
abstract: We report a case of Uhl's anomaly in a 3-week-old infant that underwent central shunt placement, patent duct us arteriosus and main pulmonary artery ligation. The infant presented with room air saturation of 43%, dilated right ventricle with decreased function and dilated right atrium. Diagnosis was established with a myocardial biopsy.
authors: Department of Pediatrics, College of Medicine, University of Florida, Jacksonville, Florida, USA.
authors: Joanna
authors: J
authors: Ganczar
authors: Department of Pediatric Cardiology, College of Medicine, University of Florida, Jacksonville, Florida, USA.
authors: Robert
authors: R
authors: English
keywords: Cyanosis in an infant; Uhl’sanomaly; right ventricular dysfunction; right-sided heart failure