title: A new association - multiple endocrine neoplasia type 1 and malignant peripheral nerve sheath tumor.
abstract: We report a patient with multiple endocrine neoplasia type 1 (MEN-1) and an aggressive malignant peripheral nerve sheath tumor (MPNST) arising from a ganglioneuroma of the adrenal gland. Patients with MEN-1 require careful consideration of other tumor associations, including MPNST, as it can portend a poor prognosis. MEN-1 and MPNST have not been reported. We report a patient with multiple endocrine neoplasia type 1 (MEN-1) and an aggressive malignant peripheral nerve sheath tumor (MPNST) arising from a ganglioneuroma of the adrenal gland. Patients with MEN-1 require careful consideration of other tumor associations, including MPNST, as it can portend a poor prognosis. MEN-1 and MPNST have not been reported.
authors: Department of Endocrinology, Royal North Shore Hospital St Leonards, Sydney, New South Wales, 2065, Australia ; Sydney Medical School, University of Sydney Sydney, New South Wales, 2006, Australia.
authors: Veronica
authors: V
authors: Preda
authors: Department of Endocrine Surgery, Royal North Shore Hospital St Leonards, Sydney, New South Wales, 2065, Australia.
authors: Mark
authors: M
authors: Sywak
authors: Department of Endocrinology, Royal North Shore Hospital St Leonards, Sydney, New South Wales, 2065, Australia ; Sydney Medical School, University of Sydney Sydney, New South Wales, 2006, Australia.
authors: Diana
authors: D
authors: Learoyd
keywords: Adrenal; MEN-1; malignant peripheral nerve sheath tumor; neuroendocrine tumors; sarcoma