title: [Cardiac magnetic resonance in arrhythmogenic right ventricular dysplasia: report of two cases].
abstract: Arrhythmogenic right ventricular dysplasia is an inherited condition characterized by replacement of normal myocardium by fatty or fibro-fatty tissue, which mainly affects the right ventricle. The most frequent form of presentation is ventricular tachycardia or sudden death, whose origin is considered to be a product of fibrous or fatty infiltration of the myocardium. This structural damage can be detected by cardiac magnetic resonance imaging (MR). We report two patients with ventricular tachycardia due to arrhythmogenic right ventricular dysplasia. A 49 year-old female with a history of ventricular tachycardia. EKG showed epsilon waves and a prolonged QTc. Echocardiogram showed right ventricular dilatation and dysfunction. MR showed right ventricular fatty infiltration. An implantable cardioverter-defibrillator was installed to the patient. A 37 year-old male was admitted for recurrent syncope. On admission a ventricular tachycardia was detected. An echocardiogram showed right ventricular dilatation and dysfunction. MR showed a large zone of fibrosis in the right ventricle. An implantable cardioverter-defibrillator was also installed.
authors.forename: Rienzi
authors.initials: R
authors.lastname: Díaz
authors.forename: Danilo
authors.initials: D
authors.lastname: Silva
mesh_terms: D000328:Adult; D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000175:diagnosis* / Q000503:physiopathology*; D004562:Electrocardiography; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D015203:Reproducibility of Results; D018487:Ventricular Dysfunction, Left / Q000503:physiopathology; D018497:Ventricular Dysfunction, Right / Q000503:physiopathology