title: Epidermolysis Bullosa Pruriginosa: Case Series and Review of the Literature.
abstract: Epidermolysis bullosa (EB) pruriginosa is a rare clinical subtype of dystrophic epidermolysis bullosa (DEB) that is characterized by intense pruritus resulting in hypertrophic, lichenified, prurigo-like plaques and nodules secondary to scratching. The variability in the age of onset, rarity of intact bullae, histologic ambiguities, and close resemblance to other conditions such as acquired inflammatory dermatoses may make diagnosis difficult for this unusual condition, for which fewer than 100 cases have been documented. In this report, we describe 3 cases of EB pruriginosa and review the current literature.
authors.affiliation: McMaster University, Hamilton, Ontario, Canada whan.kim@medportal.ca.
authors.forename: Whan B
authors.initials: WB
authors.lastname: Kim
authors.affiliation: University of Toronto, Toronto, Ontario, Canada Women's College Hospital, Toronto, Ontario, Canada.
authors.forename: Afsaneh
authors.initials: A
authors.lastname: Alavi
authors.affiliation: University of Toronto, Toronto, Ontario, Canada University of Toronto Hospital for Sick Children, Toronto, Ontario, Canada.
authors.forename: Elena
authors.initials: E
authors.lastname: Pope
authors.affiliation: University of Toronto, Toronto, Ontario, Canada Sunnybrook Health Sciences Centre, Toronto, Ontario, Canada.
authors.forename: Scott
authors.initials: S
authors.lastname: Walsh
mesh_terms: D000328:Adult; D001706:Biopsy; D002648:Child; D003937:Diagnosis, Differential; D016108:Epidermolysis Bullosa Dystrophica / Q000175:diagnosis*; D005260:Female; D006801:Humans; D007866:Leg; D008297:Male; D008875:Middle Aged; D012867:Skin / Q000473:pathology*
keywords: case series; dominant dystrophic epidermolysis bullosa; epidermolysis bullosa pruriginosa; literature review