title: Intraperitoneal follicular dendritic cell sarcoma: role of chemotherapy and bone marrow allotransplantation in locally advanced disease?
abstract: We describe a case of a 44 year-old woman diagnosed with follicular dendritic cell sarcoma (FDCS). FDCS is a very rare disease affecting the dendritic antigen presenting cells and is often misdiagnosed. Surgery is considered the best treatment modality, followed by chemotherapy. In our case, surgical excision was not possible, therefore the patient received two lines of chemotherapy followed by bone marrow allotransplantation, then a third line of chemotherapy with a complete metabolic response seen on PET/computed tomography (CT) follow-up 29 months later. A review of the literature has been performed.
authors.affiliation: Department of Digestive Surgery, Medical School, Université Libre de Bruxelles, Jules Bordet Institute, Brussels, Belgium.
authors.forename: G
authors.initials: G
authors.lastname: Liberale
authors.affiliation: Department of Digestive Surgery, Medical School, Université Libre de Bruxelles, Jules Bordet Institute, Brussels, Belgium.
authors.forename: K
authors.initials: K
authors.lastname: Keriakos
authors.affiliation: Department of Medical Hematology, Medical School, Université Libre de Bruxelles, Jules Bordet Institute and CHU Brugmann, Brussels, Belgium.
authors.forename: Ma
authors.initials: M
authors.lastname: Azerad
authors.affiliation: Department of Pathology, Medical School, Université Libre de Bruxelles, Jules Bordet Institute, Brussels, Belgium.
authors.forename: N
authors.initials: N
authors.lastname: De Saint Aubain
authors.affiliation: Department of Digestive Surgery, Medical School, Université Libre de Bruxelles, Jules Bordet Institute, Brussels, Belgium.
authors.forename: I
authors.initials: I
authors.lastname: El Nakadi
keywords: bone marrow allotransplantation; chemotherapy; follicular dendritic cell sarcoma (FDCS); intraperitoneal