[Tracheobronchial prosthesis in Mounier-Kuhn syndrome: New perspectives].
BACKGROUND
Mounier-Kuhn syndrome or tracheobronchomegaly is a rare congenital condition, the management of which is complex. We report the case of a patient who was treated with interventional endoscopy.


METHODS
We describe the case of a 74-year-old man with a diagnosis of tracheobronchomegaly who was admitted in 2003 with a background of deteriorating respiratory status and the occurrence of postural syncope. He initially received a tracheobronchial silicone Y prosthesis, extended with metal prostheses at the tracheal and bronchial level. This arrangement remained stable until 2011. He then began to develop episodes of asphyxia related to posterior dislocation of the tracheobronchial prosthesis, after breakage of the metallic mesh tracheal prosthesis. A new tracheobronchial prosthesis Y was then placed, custom-made from a 3D model of the airways. This was clinically and functionally effective.


CONCLUSIONS
This case describes the management of a patient with Mounier-Kuhn syndrome by interventional bronchoscopy, with the adaptation of prosthetic materials, on an individual basis, to the anatomy of the patient's airway.
Service de pneumologie et d'oncologie thoracique, hôpital Nord, CHU de Saint-Étienne, 42055 Saint-Étienne cedex 2, France.
M
M
Sauvage
Service de chirurgie générale et thoracique, hôpital Nord, CHU de Saint-Étienne, 42055 Saint-Étienne cedex 2, France.
O
O
Tiffet
Service de pneumologie et d'oncologie thoracique, hôpital Nord, CHU de Saint-Étienne, 42055 Saint-Étienne cedex 2, France; LINA EA 4624, université Jean Monnet, 42023 Saint-Étienne, France. Electronic address: Jean.Michel.Vergnon@univ-st-etienne.fr.
J-M
JM
Vergnon
D000368:Aged; D001237:Asphyxia / Q000209:etiology; D001999:Bronchoscopy; D045422:Continuous Positive Airway Pressure; D006801:Humans; D008297:Male; D008670:Metals; D057285:Precision Medicine; D019736:Prostheses and Implants / Q000009:adverse effects; D011474:Prosthesis Design; D011475:Prosthesis Failure; D019919:Prosthesis Implantation; D012828:Silicones; D020181:Sleep Apnea, Obstructive / Q000209:etiology / Q000628:therapy; D013575:Syncope / Q000209:etiology; D014137:Tracheobronchomegaly / Q000601:surgery*
D008670:Metals; D012828:Silicones
Bronchoscopie interventionnelle; Granuloma; Granulome; Interventional bronchoscopy; Mounier-Kuhn syndrome; Prothèse silicone; Silicone prosthesis; Syndrome de Mounier-Kuhn; Tracheobronchomalacia; Trachéobronchomalacie