Rare case of truncus arteriosus with anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) and unilateral left pulmonary artery agenesis.
The incidence of congenital heart disease (CHD) is 2.4-3.8/1000 live births. Up to 70.7 % of all cases of CHD are reported to be benign; complex heart anomalies are extremely rare. Our case is extremely rare, as we report three very rare findings-truncus arteriosus, anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA), and unilateral left pulmonary artery agenesis-in a single patient. Congenital complex cardiac abnormalities are very rare, and two-dimensional echocardiography screening should be supported by cardiac computed tomography (CT). We report a case of truncus arteriosus associated with ARCAPA and left pulmonary artery agenesis diagnosed by cardiac computed tomography; we believe that such an unusual case with all three of these entities has never been reported before.
Department of Radiology, Seth G.S. Medical College and K.E.M. Hospital, Room No. 107, Main Boys Hostel, Acharya Donde Marg, Parel, Mumbai, 400012, Maharashtra, India, amit3kem@gmail.com.
Kartik
K
Mittal
Amit K
AK
Dey
Rohit
R
Gadewar
Rajaram
R
Sharma
Nilesh
N
Pandit
Priya
P
Rajput
Priya
P
Hira
D003330:Coronary Vessel Anomalies / Q000000981:diagnostic imaging*; D004452:Echocardiography; D006801:Humans; D021621:Imaging, Three-Dimensional; D007223:Infant; D011651:Pulmonary Artery / Q000002:abnormalities*; D013771:Tetralogy of Fallot / Q000000981:diagnostic imaging*; D014057:Tomography, X-Ray Computed; D014338:Truncus Arteriosus / Q000002:abnormalities*