Cor triatriatum: a reversible cause of severe pulmonary hypertension.
Cor triatriatum sinister is a congenital heart disorder that can lead to progressive dyspnea, pulmonary hypertension, and ultimately right ventricular (RV) failure. We report a case in which symptoms of progressive pulmonary hypertension were initially attributed to asthma, leading to a delayed diagnosis that resulted in suprasystemic pulmonary pressures and RV dysfunction. Rapid symptomatic and hemodynamic improvement was observed after surgical repair, with normalization of pulmonary artery pressures and RV function.
Division of Cardiovascular Medicine, University of Michigan Health System, Ann Arbor, Michigan, USA.
Michael J
MJ
Howe
Division of Cardiovascular Medicine, University of Michigan Health System, Ann Arbor, Michigan, USA.
Michael P
MP
Thomas
Department of Radiology, University of Michigan Health System, Ann Arbor, Michigan, USA.
Prachi P
PP
Agarwal
Division of Cardiovascular Medicine, University of Michigan Health System, Ann Arbor, Michigan, USA.
David S
DS
Bach
Division of Cardiovascular Medicine, University of Michigan Health System, Ann Arbor, Michigan, USA. Electronic address: mrubenfir@umich.edu.
Melvyn
M
Rubenfire
D000328:Adult; D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures / Q000379:methods; D003310:Cor Triatriatum / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D018450:Disease Progression; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D019028:Magnetic Resonance Imaging, Cine; D011669:Pulmonary Wedge Pressure / Q000502:physiology*; D020127:Recovery of Function; D016278:Ventricular Function, Right / Q000502:physiology