Two interesting cases of EEC syndrome.
OBJECTIVE
To report two cases of EEC syndrome with oral involvement to highlight the fact that the dental surgeon may be among the first to recognise the condition.


BACKGROUND
The EEC syndrome, a rare congenital syndrome is characterised by ectodermal dysplasia, distal limb anomaly, cleft lip and palate and lachrymal duct anomalies although the term oligosymptomatic EEC syndrome has been suggested for cases in which ectrodactyly may be absent and that such cases should not be deprived of the EEC syndrome diagnosis. It is usually inherited as an autosomal dominant trait with variable expressivity and penetrance and all these features rarely coexist in a single individual.


CONCLUSIONS
Both our cases had all three characteristic features of the EEC syndrome. Other syndromes with overlapping features such as the Rapp-Hodgkin syndrome and the AEC syndrome should be considered in the differential diagnosis of incomplete forms of EEC syndrome.


CONCLUSIONS
It is important to follow an interdisciplinary approach to attain the greatest degree of success possible in the treatment of such cases.
Professor, Department of Prosthodontics, Career Post Graduate Institute of Dental Sciences & Hospital, Lucknow, U.P. 226024, India.
Mariyam
M
Iqbal Ali
Reader, Department of Oral Medicine & Radiology, Career Post Graduate Institute of Dental Sciences & Hospital, Lucknow, India.
K
K
Aravinda
Sr Lecturer, Department of Oral Medicine & Radiology, Career Post Graduate Institute of Dental Sciences & Hospital, Lucknow, India.
Nitin Kumar
NK
Nigam
Professor & Head, Department of Oral & Maxillofacial Surgery, Career Post Graduate Institute of Dental Sciences & Hospital, Lucknow, India.
Iqbal
I
Ali
Cleft lip; EEC syndrome; Ectodermal dysplasia; Ectrodactyly