Peripheral and central aggressive form of Pindborg tumor of mandible - A rare case report.
BACKGROUND
The calcifying epithelial odontogenic tumor (CEOT), or Pindborg tumor, is a rare and benign odontogenic neoplasm that affects the jaw. Calcifying epithelial odontogenic tumor can be divided into 2 clinico-topographic variants: Intraosseous (central) or Extraosseous (peripheral), with an incidence of 94% and 6%, respectively. The intraosseous tumors have a predilection for the mandible, and most tumors arise in the molar and premolar region of the mandible. When present, extraosseous tumors are often located in the anterior jaw and involve the gingiva.


OBJECTIVE
In this article we present a unique rare variety of Pindborg tumor of mandible with both intraosseous & extraosseous presentation and also locally aggressive behavior.


METHODS
A 35 year old man presented with Pindborg tumor (CEOT) of mandible with both intraosseous and extraosseous variant in a single lesion, extending from right premolar region to the left molar region.


CONCLUSIONS
CEOT is an uncommon neoplasm accounting for less than 1% of all odontogenic tumors. Although CEOT is considered less aggressive clinically than typical infiltrating ameloblastoma, but our case is a rarity which was aggressive and also rapidly progressive in short duration, with intra and extraosseous presentation. Hence it was managed surgically similar to a malignant lesion.


CONCLUSIONS
Presentation of two different variants of an odontogenic tumor in a single lesion and aggressive behavior of rather slow growing tumor, mimicking malignant lesion definitely shows possibility of rare variations in different magnitude. Hence proper diagnosis for management with better prognosis of these kinds of tumors is very much essential.
Reader, Department of Oral & Maxillofacial Surgery, Yenepoya Dental College, Deralakatte, Mangalore, Karnataka, India.
K
K
Vinayakrishna
Professor & Head, Department of Oral & Maxillofacial Surgery, Government Dental College, Calicut, Kerala, India.
C S
CS
Soumithran
Professor & Head, Department of Oral & Maxillofacial Surgery, Government Dental College, Trivandrum, Kerala, India.
C R
CR
Sobhana
Asst Professor, Department of Oral & Maxillofacial Pathology, Maharashtra Institute of Dental Sciences and Research, Latur, Maharashtra, India.
Vijay
V
Biradar
Calcifying epithilial odontogenic tumor (CEOT); Extraosseous; Intraosseous; Pindborg tumor