Congenital horner syndrome with heterochromia iridis associated with ipsilateral internal carotid artery hypoplasia.
BACKGROUND
Horner syndrome (HS), also known as Claude-Bernard-Horner syndrome or oculosympathetic palsy, comprises ipsilateral ptosis, miosis, and facial anhidrosis.


METHODS
We report herein the case of a 67-year-old man who presented with congenital HS associated with ipsilateral hypoplasia of the internal carotid artery (ICA), as revealed by heterochromia iridis and confirmed by computed tomography (CT).


CONCLUSIONS
CT evaluation of the skull base is essential to establish this diagnosis and distinguish aplasia from agenesis/hypoplasia (by the absence or hypoplasia of the carotid canal) or from acquired ICA obstruction as demonstrated by angiographic CT.
Department of Radiology, Cliniques Universitaires Saint-Luc, UCL, Brussels, Belgium. fabrice.deprez@uclouvain.be.
Fabrice C
FC
Deprez
Department of Ophthalmology, Cliniques Universitaires Saint-Luc, UCL, Brussels, Belgium.
Julie
J
Coulier
Department of Radiology, Cliniques Universitaires Saint-Luc, UCL, Brussels, Belgium.
Denis
D
Rommel
Department of Ophthalmology, Cliniques Universitaires Saint-Luc, UCL, Brussels, Belgium.
Antonella
A
Boschi
computed tomography; congenital horner syndrome; heterochromia iridis; internal carotid artery agenesis