MR imaging of arrhythmogenic right ventricular dysplasia: What the radiologist needs to know.
Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is an inherited heart muscle disease that predominantly affects the right ventricle. Clinical manifestations are related to severe ventricular arrhythmia that may lead to sudden death, mostly in young patients. Magnetic resonance imaging (MRI), included in the new diagnostic criteria since 2010, aims to detect segmental and global wall motion abnormalities, reduced ejection fraction, right ventricular dilatation and right ventricular diastolic/systolic dysfunction. An MRI assessment of the right ventricle is often challenging, partly because the MRI diagnostic criteria have some limitations, and also because it requires a significant learning curve due to the low prevalence of the disease. Therefore, this article aims to review the pathophysiology of the disease, the cardiac MRI protocol, images of the various stages of this affection as well as the differential diagnosis.
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France. Electronic address: alice.tavano@ap-hm.fr.
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Tavano
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Maurel
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Gaubert
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Varoquaux
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Cassagneau
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Vidal
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Bartoli
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Moulin
Department of Radiology, université Marseille Méditerranée, hôpital universitaire de la Timone, 264, rue Saint-Pierre, 13385 Marseille cedex 5, France.
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Jacquier
D000328:Adult; D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000175:diagnosis*; D057791:Cardiac Imaging Techniques; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D011871:Radiology
Arrhythmogenic right ventricular dysplasia; Cardiac MRI; Cardiomyopathy