Absence of left pulmonary artery in tetralogy of Fallot with absent pulmonary valve syndrome.
The rare combination of tetralogy of Fallot (TOF), absent pulmonary valve syndrome (APVS), and absent left pulmonary artery (ALPA) is reviewed herein. Children with TOF with APVS and ALPA should be closely monitored, even if they are asymptomatic or mildly symptomatic, and should undergo elective surgery at the end of infancy.
Mustafa Kemal
MK
Avsar
Tolga
T
Demir
Hale Bolgi
HB
Demir
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery; D000792:Angiography; D013504:Cardiovascular Surgical Procedures; D004452:Echocardiography; D017558:Elective Surgical Procedures; D005260:Female; D006352:Heart Ventricles / Q000000981:diagnostic imaging; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery; D012189:Retrospective Studies; D013577:Syndrome; D013771:Tetralogy of Fallot / Q000175:diagnosis / Q000601:surgery