Erdheim-Chester disease mimicking an intracranial trigeminal schwannoma: case report.
Erdheim-Chester disease (ECD) is non-Langerhans histiocytosis that can affect multiple organ systems. It usually affects middle-aged patients, and only a few reports of ECD in children appear in the literature. Central nervous system involvement is a common feature that usually occurs as infiltration of the hypothalamus-pituitary axis, cerebellum, and/or brainstem. Meningeal involvement occurs less commonly. In this article, the authors discuss a rare pediatric case of ECD presenting as an infiltrative mass of the trigeminal nerve and resembling the clinical and imaging features of a trigeminal schwannoma.
International Neuroscience Institute;
Maysam
M
Alimohamadi
Christian
C
Hartmann
Vincenzo
V
Paterno
Madjid
M
Samii
D000293:Adolescent; D000368:Aged; D003390:Cranial Nerve Neoplasms / Q000175:diagnosis*; D003937:Diagnosis, Differential; D031249:Erdheim-Chester Disease / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy; D005260:Female; D006801:Humans; D007249:Inflammation / Q000175:diagnosis; D008297:Male; D008875:Middle Aged; D009442:Neurilemmoma / Q000175:diagnosis*; D011159:Population Surveillance; D011379:Prognosis; D014057:Tomography, X-Ray Computed
ECD = Erdheim-Chester disease; Erdheim-Chester disease; JXG = juvenile xanthogranuloma; LCH = Langerhans cell histiocytosis; RDD = Rosai-Dorfman disease; brain tumor; histiocytosis; oncology; skull base tumor; trigeminal schwannoma