title: Common variable immunodeficiency and pulmonary amyloidosis: a case report.
abstract: Common variable immunodeficiency is the most common symptomatic primary immune deficiency characterized by hypogammaglobulinemia, recurrent infections, and increased risk of autoimmune disease and malignancy. Secondary amyloidosis develops from chronic inflammatory conditions. The co-existence of CVID (especially in patients with bronchiectasis) and secondary amyloidosis has been reported rarely. We describe the first case of pulmonary hypertension secondary to pulmonary amyloidosis in a patient with CVID.
authors.affiliation: Meram Faculty of Medicine, Department of Clinical Immunology and Allergy, Necmettin Erbakan University, Konya, 42090, Turkey.
authors.forename: Sevket
authors.initials: S
authors.lastname: Arslan
authors.forename: Ramazan
authors.initials: R
authors.lastname: Ucar
authors.forename: Dudu Mehmet
authors.initials: DM
authors.lastname: Yavsan
authors.forename: Hasan
authors.initials: H
authors.lastname: Esen
authors.forename: Emin
authors.initials: E
authors.lastname: Maden
authors.forename: Ismail
authors.initials: I
authors.lastname: Reisli
authors.forename: Ahmet Zafer
authors.initials: AZ
authors.lastname: Calıskaner
mesh_terms: D000293:Adolescent; D000686:Amyloidosis / Q000175:diagnosis / Q000209:etiology*; D001706:Biopsy; D017074:Common Variable Immunodeficiency / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D017809:Fatal Outcome; D005500:Follow-Up Studies; D006801:Humans; D008171:Lung Diseases / Q000175:diagnosis / Q000209:etiology*; D008297:Male; D013902:Radiography, Thoracic