title: A Rare Case of Chylothorax due to Pulmonary Lymphangiectasia in a 7-Year-Old Boy.
abstract: Pulmonary lymphangiectasia (PL) is a rare condition characterized by dilatation of the lymphatic vessels. Post-neonatal PL is usually associated with pleural effusion and should therefore be suspected in the presence of chylothorax. We describe a post-neonatal manifestation of PL in a 7-year-old boy presenting chylothorax. Radiological examinations included thorax X-ray, ultrasound, and computed tomography scans. After the failure of conservative management (maintenance of the chest tube, total parenteral nutrition, administration of somatostatin synthetic analogues) we performed a thoracoscopic massive ligation of the thoracic duct's collateral along with a lung biopsy. Histology was compatible with type 1 congenital pulmonary lymphangectasia. One month after surgery a thoracoscopic pleurodesis was required for persistent chylothorax. The boy is now doing well 1 year after surgery.
authors.affiliation: Department of Pediatric Surgery, S. Orsola-Malpighi Hospital, Bologna, Italy.
authors.forename: Giovanni
authors.initials: G
authors.lastname: Ruggeri
authors.affiliation: Department of Pediatric Surgery, S. Orsola-Malpighi Hospital, Bologna, Italy.
authors.forename: Francesca
authors.initials: F
authors.lastname: Destro
authors.affiliation: Department of Pediatric Surgery, S. Orsola-Malpighi Hospital, Bologna, Italy.
authors.forename: Michela
authors.initials: M
authors.lastname: Maffi
authors.affiliation: Department of Pediatric Surgery, S. Orsola-Malpighi Hospital, Bologna, Italy.
authors.forename: Giulio
authors.initials: G
authors.lastname: Gregori
authors.affiliation: Department of Pediatric Surgery, S. Orsola-Malpighi Hospital, Bologna, Italy.
authors.forename: Mario
authors.initials: M
authors.lastname: Lima
keywords: chylothorax; pulmonary lymphangiectasia; thoracoscopy