title: Hirayama disease.
abstract: This article discusses three patients with likely Hirayama disease. They have no other significant past medical history and no personal or family history of other neurological disorders. Hirayama disease is a form of cervical myelopathy attributed to forward displacement of the posterior cervical dural sac on neck flexion with resultant cord compression and/or venous congestion. It is characterized by a pure motor focal amyotrophy in the distribution of C7, C8 and T1 spinal segmental-innervated muscles and differs from other motor neuron diseases by virtue of its ultimately non-progressive course.
authors.affiliation: Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia. Electronic address: dr.ecfoster@gmail.com.
authors.forename: Emma
authors.initials: E
authors.lastname: Foster
authors.affiliation: Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia.
authors.forename: Benjamin K-T
authors.initials: BK
authors.lastname: Tsang
authors.affiliation: Department of Radiology, The Alfred Hospital, Melbourne, VIC, Australia.
authors.forename: Anthony
authors.initials: A
authors.lastname: Kam
authors.affiliation: Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia.
authors.forename: Elsdon
authors.initials: E
authors.lastname: Storey
authors.affiliation: Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia; Monash University, Melbourne, VIC, Australia.
authors.forename: Bruce
authors.initials: B
authors.lastname: Day
authors.affiliation: Department of Neurosciences, The Alfred Hospital, 55 Commercial Road, Melbourne, VIC 3004, Australia.
authors.forename: Aron
authors.initials: A
authors.lastname: Hill
mesh_terms: D000328:Adult; D002574:Cervical Vertebrae / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods; D008297:Male; D014897:Spinal Muscular Atrophies of Childhood / Q000175:diagnosis* / Q000628:therapy*; D013904:Thoracic Vertebrae / Q000473:pathology; D055815:Young Adult
keywords: Cervical myelopathy; Hirayama disease; Motor focal amyotrophy; Motor neuron disease