title: Recurrent hemoptysis and a mass in the thorax in an infant: the split notochord syndrome.
abstract: Split notochord syndrome is a rare group of developmental abnormalities caused by abnormal splitting or deviation of the notochord clinically resulting in the duplicated bowel associated with vertebral anomalies. We report on a case of 11-month-old female infant with mediastinal hyperechogenic cyst and intestinal duplication cyst associated with T5-T6 hemivertebrae, scoliosis, and nonfusion of posterior part of T6 vertebrae, presenting with severe hemoptysis and hematemesis. The cysts were surgically removed, and histopathologic analysis revealed that the mediastinal cyst was lined by gastric mucosa and intestinal one was lined with gastric mucosa including ectopic pancreatic tissue. After removal of the lesion the patient made an uneventful recovery and shows no signs of long-term pulmonary sequelae.
authors.affiliation: Department of Pediatrics, Hacettepe University Children's Hospital, Ankara, Turkey.
authors.forename: Mutlu Uysal
authors.initials: MU
authors.lastname: Yazici
authors.affiliation: Department of Pediatric Surgery, Hacettepe University Children's Hospital, Ankara, Turkey.
authors.forename: Saniye
authors.initials: S
authors.lastname: Ekinci
authors.affiliation: Department of Pediatric Allergy and Immunology, Gaziantep University, Ankara, Turkey.
authors.forename: Ozlem Keskin
authors.initials: OK
authors.lastname: Turkmen
authors.affiliation: Department of Pediatric Pulmonology, Hacettepe University School of Medicine, Ankara, Turkey.
authors.forename: Ebru Gunes
authors.initials: EG
authors.lastname: Yalcin
authors.affiliation: Department of Pediatric Surgery, Hacettepe University Children's Hospital, Ankara, Turkey.
authors.forename: Arbay O
authors.initials: AO
authors.lastname: Ciftci
authors.affiliation: Department of Pediatric Pathology, Hacettepe University, Ankara, Turkey.
authors.forename: Safak
authors.initials: S
authors.lastname: Gucer
authors.affiliation: Department of Pediatric Pathology, Hacettepe University, Ankara, Turkey.
authors.forename: Diclehan
authors.initials: D
authors.lastname: Orhan
authors.affiliation: Department of Pediatric Immunology, Hacettepe University School of Medicine, Ankara, Turkey.
authors.forename: Ilhan
authors.initials: I
authors.lastname: Tezcan
keywords: hematemesis; hemoptysis; intestinal duplication cyst; neurenteric cyst