title: Facial angioedema and systemic lupus erythematosus: case report.
abstract: Non-medication-related acquired deficiencies of C1 esterase inhibitor (C1-INH) can cause the facial acquired angioedema (AAE) seen in systemic lupus erythematosus (SLE). The defect can originate from a lymphoproliferative disease (LPD) that catabolizes C1-INH or from circulating antibodies that inactivate C1-INH. This report describes a third and rare variety of facial AAE originating in SLE in which there was no LPD or circulating antibodies to impede C1-INH activity.
authors: Resident, Department of Oral and Maxillofacial Surgery, New York-Presbyterian Medical Center (Columbia Campus), New York, NY.
authors: Daniel
authors: D
authors: Bienstock
authors: Director, Salivary Gland Center; Associate Dean and Clinical Professor, Department of Oral and Maxillofacial Surgery, Columbia University College of Dental Medicine, New York-Presbyterian Medical Center (Columbia Campus), New York, NY. Electronic address: LM7@columbia.edu.
authors: Louis
authors: L
authors: Mandel
mesh_terms: D000328:Adult; D000799:Angioedema / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D005145:Face / Q000473:pathology*; D005260:Female; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy