title: Spinal Neurenteric Cyst in Association with Klippel-Feil Syndrome: Case Report and Literature Review.
abstract: BACKGROUND
  Spinal neurenteric cysts, also known as endodermal or enterogenous cysts, are rare epithelium-lined structures of presumed endodermal origin. Congenital vertebral anomalies are frequently seen in patients with neurenteric cysts, most typically anterior spina bifida, butterfly vertebrae, and hemivertebrae. However, few series of intraspinal neurenteric cysts accompanied by Klippel-Feil syndrome have been reported previously.
  
  
  METHODS
  Our purpose is to present the clinical, radiological, and histological results of a 29-year-old patient with a spinal neurenteric cyst associated with Klippel-Feil syndrome and to review previous reported cases of neurenteric cysts associated with Klippel-Feil syndrome. In our patient, cervical radiography demonstrated C5-T1 vertebral fusion and magnetic resonance imaging revealed a large intradural cystic mass. The cystic lesion was removed successfully, and it was histopathologically diagnosed as a neurenteric cyst.
  
  
  CONCLUSIONS
  Neurenteric cysts should always be considered in the differential diagnosis of an intraspinal cystic mass seen in the setting of vertebral anomalies.
authors: Department of Neurosurgery, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA; Department of Neurosurgery, Erasmus Medical Center, Rotterdam, The Netherlands. Electronic address: acan@mgh.harvard.edu.
authors: Anil
authors: A
authors: Can
authors: Department of Neurosurgery, Erasmus Medical Center, Rotterdam, The Netherlands.
authors: Ellianne J
authors: EJ
authors: Dos Santos Rubio
authors: Department of Radiology, Erasmus Medical Center, Rotterdam, The Netherlands.
authors: Bas
authors: B
authors: Jasperse
authors: Department of Pathology, Erasmus Medical Center, Rotterdam, The Netherlands.
authors: Robert M
authors: RM
authors: Verdijk
authors: Department of Neurosurgery, Erasmus Medical Center, Rotterdam, The Netherlands.
authors: B Sanjay
authors: BS
authors: Harhangi
mesh_terms: D000328:Adult; D002574:Cervical Vertebrae / Q000473:pathology* / Q000601:surgery*; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D007714:Klippel-Feil Syndrome / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery*; D008279:Magnetic Resonance Imaging; D008297:Male; D009436:Neural Tube Defects / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery*; D013904:Thoracic Vertebrae / Q000473:pathology* / Q000601:surgery*
keywords: Congenital cyst; Endodermal cyst; Enterogenous cyst; Klippel-Feil anomaly; Neurenteric cyst; Spinal cyst