title: Nutritional aspects of children and adolescents with epidermolysis bullosa: literature review.
abstract: Epidermolysis Bullosa is a genetic disorder that affects mainly the skin, however, all others systems are influenced. The nutritional care of children and adolescents with Epidermolysis Bullosa is a key treatment strategy, since the energy needs are increased due to the disease's metabolism, burdening the immune system and cicatrization process, symptoms caused by the disease hinder the intake and adequate absorption of nutrients, which may result in inadequate growth and development. Because this is a rare disease, there are few professionals who know the characteristics of both the clinical evolution and nutritional and dietary treatments. This literature review discusses the latest knowledge on energy and specific nutrient requirements to the dietary treatment and monitoring of children and adolescents with Epidermolysis Bullosa.
authors.affiliation: Universidade de Brasília, Brasília, DF, Brazil.
authors.forename: Ana Paula Caio
authors.initials: AP
authors.lastname: Zidorio
authors.affiliation: Universidade de Brasília, Brasília, DF, Brazil.
authors.forename: Eliane Said
authors.initials: ES
authors.lastname: Dutra
authors.affiliation: Universidade de Brasília, Brasília, DF, Brazil.
authors.forename: Dryelle Oliveira Dias
authors.initials: DO
authors.lastname: Leão
authors.affiliation: Universidade de Brasília, Brasília, DF, Brazil.
authors.forename: Izelda Maria Carvalho
authors.initials: IM
authors.lastname: Costa
mesh_terms: D000293:Adolescent; D041923:Adolescent Development; D002648:Child; D002657:Child Development; D002149:Energy Intake; D004820:Epidermolysis Bullosa / Q000178:diet therapy* / Q000378:metabolism; D016108:Epidermolysis Bullosa Dystrophica / Q000178:diet therapy / Q000378:metabolism; D006801:Humans; D009751:Nutritional Requirements / Q000502:physiology*; D009752:Nutritional Status / Q000502:physiology*
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