title: Hypohidrotic ectodermal dysplasia: a clinical case with a longitudinal approach.
abstract: OBJECTIVE
  This paper describes a clinical case of a male with hypohidrotic ectodermal dysplasia submitted to rehabilitation and occlusal dental interventions with follow-up from 3 to 14 years of age.
  
  
  BACKGROUND
  Due to the severe effects on function and esthetics, the clinical manifestations of ectodermal dysplasia exert a negative impact on quality of life. However, oral rehabilitation in childhood poses a challenge due to growth and development.
  
  
  METHODS
  A male with hypohidrotic ectodermal dysplasia began dental intervention at the age of 3 years. The clinical and radiographic exams revealed the absence of several primary and permanent teeth and abnormal shape of the primary maxillary incisors. The facial characteristics were compatible with hypohidrotic ectodermal dysplasia, such as a prominent brow, everted lips, fattened bridge of the nose and small vertical facial height. The treatment proposed involved rehabilitation through successive temporary partial dentures, functional orthopedics of the jaws, esthetic reconstruction of the anterior teeth, timely occlusal intervention and preventive actions for the control of dental caries and plaque.
  
  
  CONCLUSIONS
  The present case demonstrates that early care plays a fundamental role in minimizing the biopsychosocial consequences of hypohidrotic ectodermal dysplasia and preparing the patient for future oral rehabilitation.
  
  
  CONCLUSIONS
  Although, the literature offers a number of papers describing dental treatment for ectodermal dysplasia, few cases include long-term follow-up and the use of a functional orthopedic appliance in combination with removable dentures in such patients.
authors.affiliation: Associate Professor, Department of Stomatology, Avenida Prefeito Lothario Meissner 632, Jardim Botânico, Curitiba, ParanáBrazil, Zip Code: 80210-170, Phone: 55 41 3360 4021, e-mail: fabianfraiz@gmail.com.
authors.forename: Fabian Calixto
authors.initials: FC
authors.lastname: Fraiz
authors.affiliation: Associate Professor, Department of Stomatology, Universidade Federal do Paraná, Paraná, Brazil.
authors.forename: Renato Cordeiro
authors.initials: RC
authors.lastname: Gugisch
authors.affiliation: MSc Student, Department of Stomatology, Universidade Federal do Paraná, Paraná, Brazil.
authors.forename: Bianca Lopes
authors.initials: BL
authors.lastname: Cavalcante-Leão
authors.affiliation: Pediatric Dentist, Private Practice, Curitiba, Paraná, Brazil.
authors.forename: Liliane Moreira
authors.initials: LM
authors.lastname: Macedo
mesh_terms: D000848:Anodontia / Q000628:therapy; D002675:Child, Preschool; D017742:Dental Care for Chronically Ill; D003731:Dental Caries / Q000517:prevention & control; D003773:Dental Plaque / Q000517:prevention & control; D003833:Denture, Partial, Temporary; D004476:Ectodermal Dysplasia / Q000150:complications*; D004955:Esthetics, Dental; D005500:Follow-Up Studies; D006801:Humans; D007180:Incisor / Q000002:abnormalities; D008137:Longitudinal Studies; D008297:Male; D009065:Mouth Rehabilitation / Q000379:methods*; D009971:Orthodontics, Corrective; D014094:Tooth, Deciduous / Q000002:abnormalities
keywords: Case reports; Cavalcante-Leão BL; Dental care for children; Denture; Ectodermal dysplasia; Functional. How to cite this article: Fraiz FC; Gugisch RC; Macedo LM. Hypohidrotic Ectodermal Dysplasia: A Clinical Case with a Longitudinal Approach. J Contemp Dent Pract 2014;15(6):788-791. Source of support: Nil Conflict of interest: None.; Orthodontic appliances; Partial; Temporary