title: Goldenhar Syndrome with Tessier's 7 Cleft: Report of a Case.
abstract: Goldenhar syndrome, a variant of hemifacial microsomia, is a well-known developmental anomaly of maxillofacial skeleton that is apparent at birth. The first and second branchial arch involvement during early embryonic development results in a wide spectrum of anomalies that may include macrostomia and lateral facial clefts. Though clefts of the orofacial region are among the most common congenital facial defects, the occurrence of lateral facial clefts (Tessier 7 cleft) in conditions such as the Goldenhar syndrome, is very rare (<5%). The lateral facial cleft, which results because of improper development of the perioral muscles of the face, gives an appearance of macrostomia giving rise to potential psychological, aesthetic and feeding problems. This clinical report describes the closure of a Tessier 7 cleft and the use of distraction osteogenesis to treat mandibular asymmetry in an 11-year-old female patient with Goldenhar's syndrome.
authors.affiliation: Department of Oral & Maxillofacial Surgery, AME'S Dental College Hospital & Research Centre, Raichur, 584103 Karnataka India.
authors.forename: Dinesh Singh
authors.initials: DS
authors.lastname: Chauhan
authors.affiliation: Department of Oral & Maxillofacial Surgery, AME'S Dental College Hospital & Research Centre, Raichur, 584103 Karnataka India.
authors.forename: Yadavalli
authors.initials: Y
authors.lastname: Guruprasad
keywords: Distraction osteogenesis; Goldenhar syndrome; Tessier 7 cleft
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