title: I-gel assisted fiberoptic intubation in a child with Morquio's syndrome.
abstract: Morquio's syndrome, also known as mucopolysaccharidosis type IV is an autosomal recessive disorder, caused by deficiency of n-acetylgalactosamine-6-sulphate. Anesthetic management of this syndrome is a great challenge, especially in pediatric age group as "cannot ventilate, cannot intubate" scenario can be encountered by anesthesiologist due to the possibility of total airway collapse. Herewith, we are reporting a case of child with Morquio's syndrome where I-gel assisted fiber-optic intubation was used for safe endotracheal intubation.
authors.affiliation: Department of Anaesthesiology and Critical Care, Indira Gandhi Medical College and Research Institute, Puducherry, India.
authors.forename: Sangeeta
authors.initials: S
authors.lastname: Dhanger
authors.affiliation: Department of Anaesthesiology and Critical Care, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
authors.forename: Sethuramachandran
authors.initials: S
authors.lastname: Adinarayanan
authors.affiliation: Department of Anaesthesiology and Critical Care, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
authors.forename: Stalin
authors.initials: S
authors.lastname: Vinayagam
authors.affiliation: Department of Anaesthesiology and Critical Care, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
authors.forename: Mohanasundaram Praveen
authors.initials: MP
authors.lastname: Kumar
keywords: Difficult airway; I-gel; Morquio's syndrome; fiber-optic bronchoscope
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