title: Nevoid Basal cell carcinoma syndrome: a case report and review.
abstract: Nevoid basal cell carcinoma syndrome, a rare autosomal dominant disorder, comprises of a number of abnormalities such as multiple nevoid basal cell carcinomas, skeletal abnormalities and multiple keratocystic odontogenic tumors. Diagnosis may be difficult because of the variability of expressivity and different ages of onset for different traits of this disorder. The dental clinician may be the first to encounter and identify this syndrome, when the multiple cysts like radiolucencies are discovered on panoramic view. This article reports a case of Nevoid basal cell carcinoma syndrome and provides an overview on diagnosis and management.
authors.affiliation: Department of Oral and Maxillofacial Surgery, Government Dental College and Hospital, RIMS, Kadapa, Andhra Pradesh India.
authors.forename: S
authors.initials: S
authors.lastname: Bala Subramanyam
authors.affiliation: Department of Oral and Maxillofacial Surgery, Government Dental College and Hospital, RIMS, Kadapa, Andhra Pradesh India.
authors.forename: D
authors.initials: D
authors.lastname: Naga Sujata
authors.affiliation: Department of General Pathology, RIMS, Kadapa, Andhra Pradesh India.
authors.forename: K
authors.initials: K
authors.lastname: Sridhar
authors.affiliation: Department of Oral and Maxillofacial Surgery, Government Dental College and Hospital, RIMS, Kadapa, Andhra Pradesh India.
authors.forename: M
authors.initials: M
authors.lastname: Pushpanjali
keywords: Goltz syndrome; Gorlin; Keratocystic odontogenic tumor; NBCCS
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