title: Congenital intra-oral adhesions: a surgical approach to cleft palate lateral synechia syndrome.
abstract: An array of genetic syndromes has been associated with intra-oral adhesions in neonates. The primary medical issues arise from airway obstruction, feeding difficulties and poor oral development, specifically with cleft palate lateral synechia syndrome (CPLSS). Despite this, a paucity of data exists for the clinical management of intra-oral adhesions in this population. We report the cases of a father and daughter diagnosed with CPLSS who presented with respiratory and feeding difficulties at birth undergoing surgical correction. Early surgical ligation of intra-oral bands allows for a stabilization of the airway, improved feeding and oral development with a good long-term outcome.
authors.affiliation: Department of Otolaryngology - Head and Neck Surgery, McGill University, Montreal, Quebec, Canada. Electronic address: marco.mascarella@mail.mcgill.ca.
authors.forename: Marco A
authors.initials: MA
authors.lastname: Mascarella
authors.affiliation: Department of Otolaryngology - Head and Neck Surgery, McGill University, Montreal, Quebec, Canada.
authors.forename: Joseph
authors.initials: J
authors.lastname: Schwartz
authors.affiliation: Department of Otolaryngology - Head and Neck Surgery, McGill University, Montreal, Quebec, Canada.
authors.forename: John J
authors.initials: JJ
authors.lastname: Manoukian
mesh_terms: D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007569:Jaw Abnormalities / Q000473:pathology* / Q000601:surgery*; D009055:Mouth / Q000473:pathology*; D009056:Mouth Abnormalities / Q000473:pathology* / Q000601:surgery*
keywords: Airway obstruction; Cleft palate lateral synechia syndrome; Intra-oral adhesions