title: Idiopathic hyperammonemia after hematopoietic stem cell transplantation: A case report.
abstract: IHA is characterized by a sudden increase in plasma ammonia levels in the absence of any identifiable causes, which mostly results in intractable coma and high mortality. It has been reported in some patients after receiving intensive chemotherapy for hematological malignancy or HSCT. We describe a case of a patient with FA that developed acute idiopathic hyperammonemia after the preparative regimen for HSCT.
authors.affiliation: Pediatric BMT Unit, Medical Park Antalya Hospital, Bahçeşehir University, Antalya, Turkey.
authors.forename: Vedat
authors.initials: V
authors.lastname: Uygun
authors.forename: Gülsün
authors.initials: G
authors.lastname: Karasu
authors.forename: Hayriye
authors.initials: H
authors.lastname: Daloğlu
authors.forename: Volkan
authors.initials: V
authors.lastname: Hazar
authors.forename: Akif
authors.initials: A
authors.lastname: Yeşilipek
mesh_terms: D000641:Ammonia / Q000097:blood*; D001929:Brain Edema / Q000209:etiology; D002648:Child; D005199:Fanconi Anemia / Q000150:complications / Q000628:therapy*; D017809:Fatal Outcome; D064147:Febrile Neutropenia / Q000209:etiology; D005260:Female; D018380:Hematopoietic Stem Cell Transplantation / Q000009:adverse effects*; D006440:Hemofiltration; D006801:Humans; D022124:Hyperammonemia / Q000209:etiology*; D020300:Intracranial Hemorrhages / Q000209:etiology; D019172:Transplantation Conditioning / Q000009:adverse effects*
chemical_list: D000641:Ammonia
keywords: Fanconi anemia; hematopoietic stem cell transplantation; hyperammonemia