title: A rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra.
abstract: Bilateral cystic nephroma is an extremely rare benign renal neoplasm. Here we present a case of bilateral cystic nephroma in a four month old boy who subsequently developed embryonal rhabdomyosarcoma of the urethra. Both tumors were successfully treated. To our knowledge this is the first reported case of this association which could be related to Dicer-1 mutation.
authors.affiliation: Department of Paediatric Surgery, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Jujju Jacob
authors.initials: JJ
authors.lastname: Kurian
authors.affiliation: Department of Paediatric Surgery, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Sudipta
authors.initials: S
authors.lastname: Sen
authors.affiliation: Department of Paediatric Surgery, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Reju Thomas
authors.initials: RT
authors.lastname: Joseph
authors.affiliation: Department of Pathology, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Mandeep Singh
authors.initials: MS
authors.lastname: Bindra
keywords: Bilateral cystic nephroma; Dicer-1 mutation; urethral embryonal rhabdomyosarcoma
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