title: Postpneumonectomy syndrome in a newborn after esophageal atresia repair.
abstract: BACKGROUND
  Postpneumonectomy syndrome (PPS) is an ominous complication, caused by mediastinal shift following massive lung resection.
  
  
  METHODS
  A neonate with oesophageal atresia and tracheo-oesophageal fistula developed acute respiratory distress shortly after surgery, despite mechanical ventilation. The patient was found to have an associated oesophageal right lung that collapsed after oesophageal atresia repair and a left pulmonary artery sling causing left main bronchus stenosis mimicking a postpneumonectomy syndrome.
  
  
  CONCLUSIONS
  We will describe the diagnostic work-up and the therapeutic measures used both in the acute phase and as definitive treatment in this challenging case.
  
  
  CONCLUSIONS
  Neonatologists and paediatric surgeons should be aware of this rare association that may cause acute life threatening and worsening of patient's clinical status. Prompt realignment of the mediastinum in the normal position is critical to obtain rapid improvement of the patient's clinical conditions.
authors.affiliation: Neonatal Surgery Unit, Department of Medical and Surgical Neonatology, Bambino Gesù Children's Hospital, IRCCS Piazza S. Onofrio 4, 00165 Rome, Italy.
authors.forename: Chiara
authors.initials: C
authors.lastname: Iacusso
authors.affiliation: Neonatal Surgery Unit, Department of Medical and Surgical Neonatology, Bambino Gesù Children's Hospital, IRCCS Piazza S. Onofrio 4, 00165 Rome, Italy.
authors.forename: Pietro
authors.initials: P
authors.lastname: Bagolan
authors.affiliation: ENT Unit, Department of Surgery and Transplantation Centre, Bambino Gesù Children's Hospital, IRCCS Piazza S. Onofrio 4, 00165 Rome, Italy.
authors.forename: Sergio
authors.initials: S
authors.lastname: Bottero
authors.affiliation: Neonatal Surgery Unit, Department of Medical and Surgical Neonatology, Bambino Gesù Children's Hospital, IRCCS Piazza S. Onofrio 4, 00165 Rome, Italy.
authors.forename: Andrea
authors.initials: A
authors.lastname: Conforti
authors.affiliation: Neonatal Surgery Unit, Department of Medical and Surgical Neonatology, Bambino Gesù Children's Hospital, IRCCS Piazza S. Onofrio 4, 00165 Rome, Italy. Electronic address: francesco.morini@opbg.net.
authors.forename: Francesco
authors.initials: F
authors.lastname: Morini
keywords: Communicating bronchopulmonary foregut malformations; Iatrogenic hydrothorax; Oesophageal atresia; Oesophageal lung; Postpneumonectomy syndrome; Pseudo-postpneumonectomy syndrome; Tissue expander
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