title: Intrahepatic stones from congenital biliary dilatation.
abstract: BACKGROUND
  Congenital or primary intrahepatic bile duct (IHBD) dilatation is a rare disorder with symptoms of abdominal pain and hepatomegaly that usually presents in childhood and adolescence. Recurrent cholangitis, liver abscesses, septicemia, and biliary cirrhosis may result secondary to biliary sludge and hepatolithiasis.
  
  
  METHODS
  We present a case of IHBD dilatation with hepatolithiasis cured with surgical resection and discuss the management of this disease.
  
  
  CONCLUSIONS
  IHBD dilatation should be treated, as chronic biliary stasis and hepatolithiasis can lead to infection and recurrent cholangitis that can progress to cholangiocarcinoma. Treatment for IHBD dilatation usually involves multiple modalities including medical therapy, but ultimately resection of the diseased segments or lobes is required given the increased risk of malignancy.
authors.affiliation: Department of Surgery, Ochsner Clinic Foundation, New Orleans, LA.
authors.forename: Satvik
authors.initials: S
authors.lastname: Jhamb
authors.affiliation: Department of Gastroenterology, Ochsner Clinic Foundation, New Orleans, LA.
authors.forename: Christopher
authors.initials: C
authors.lastname: Decker
authors.affiliation: Department of Gastroenterology, Ochsner Clinic Foundation, New Orleans, LA.
authors.forename: Ricardo
authors.initials: R
authors.lastname: Romero
authors.affiliation: Department of Gastroenterology, Ochsner Clinic Foundation, New Orleans, LA.
authors.forename: Ramon E
authors.initials: RE
authors.lastname: Rivera
authors.affiliation: Department of Surgery, Ochsner Clinic Foundation, New Orleans, LA ; The University of Queensland School of Medicine, Ochsner Clinical School, New Orleans, LA.
authors.forename: W Charles
authors.initials: WC
authors.lastname: Conway
keywords: Bile ducts–intrahepatic; cholangiocarcinoma; cholangitis
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