title: Myofibroma-a rare entity with unique clinical presentation.
abstract: Myofibroma and myofibromatosis is a well-recognized spindle cell neoplasm that occurs predominantly in infants and young children. They have been described under different names since 1951. These lesions are a benign fibroblast and myofibroblast proliferation containing a biphasic presentation of spindle shaped cells surrounding a central zone of less differentiated cells focally arranged in a hemangiopericytoma like pattern. Classically these lesions are described in children younger than two, with 2/3rd present at birth and rarely in adults. Controversy exists as to an autosomal dominant or recessive inheritance or to a sporadic occurrence. Presented here is a unique case of myofibroma involving the mandible in a 11 year-old male patient. Clinically it mimicked more like a beningn tumor and not exhibiting any of its classical signs. The diagnosis could be established only after complete excision of the lesion and histopathological examination. There was no recurrence after a follow up period of 4 months.
authors.affiliation: Dept of Oral & Maxillofacial Surgery, Kamineni Institute of Dental Sciences, Sreepuram, Nalgonda Dt, Narketpally, AP 508254 India.
authors.forename: V
authors.initials: V
authors.lastname: Venkatesh
authors.affiliation: Dept of Oral & Maxillofacial Surgery, Kamineni Institute of Dental Sciences, Sreepuram, Nalgonda Dt, Narketpally, AP 508254 India.
authors.forename: Batchu Pavan
authors.initials: BP
authors.lastname: Kumar
authors.affiliation: Dept of Oral & Maxillofacial Surgery, Kamineni Institute of Dental Sciences, Sreepuram, Nalgonda Dt, Narketpally, AP 508254 India.
authors.forename: K A Jeevan
authors.initials: KA
authors.lastname: Kumar
authors.affiliation: Dept of Oral & Maxillofacial Surgery, Kamineni Institute of Dental Sciences, Sreepuram, Nalgonda Dt, Narketpally, AP 508254 India.
authors.forename: A P
authors.initials: AP
authors.lastname: Mohan
keywords: Myofibroma; Smooth muscle; Spindle cell neoplasm
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