title: Syndrome in question. Immunoglobulin light chain amyloidosis.
abstract: Immunoglobulin light chain amyloidosis is the most common acquired systemic amyloidosis. Its presentation is often insidious and progressive, which may delay diagnosis. The authors describe a rare case of immunoglobulin light chain amyloidosis in a 34-year-old man with scleroderma-like manifestation substantiated by multifarious laboratory investigations and the histopathologic feature of involved skin lesions stained with Congo red and crystal violet. This helps to maintain a high clinical suspicion of the disease when confronting similar skin presentation.
authors.affiliation: Third Affiliated Hospital, Sun Yat-sen University, Guangdong, China.
authors.forename: Han
authors.initials: H
authors.lastname: Ma
authors.affiliation: First Affiliated Hospital, Sun Yat-sen University, Guangdong, China.
authors.forename: Meilan
authors.initials: M
authors.lastname: Chen
authors.affiliation: First Affiliated Hospital, Sun Yat-sen University, Guangdong, China.
authors.forename: Juan
authors.initials: J
authors.lastname: Li
authors.affiliation: First Affiliated Hospital, Sun Yat-sen University, Guangdong, China.
authors.forename: Ying
authors.initials: Y
authors.lastname: Li
authors.affiliation: Third Affiliated Hospital, Sun Yat-sen University, Guangdong, China.
authors.forename: Shu
authors.initials: S
authors.lastname: Qiu
mesh_terms: D000328:Adult; D000686:Amyloidosis / Q000276:immunology / Q000473:pathology*; D001706:Biopsy; D005434:Flow Cytometry; D006801:Humans; D007147:Immunoglobulin Light Chains; D008297:Male; D012867:Skin / Q000473:pathology; D012871:Skin Diseases / Q000276:immunology / Q000473:pathology*; D013577:Syndrome
chemical_list: D007147:Immunoglobulin Light Chains
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