title: Pulmonary epitheloid hemangioendothelioma PET CT findings and review of literature.
abstract: We describe a case of pulmonary epitheloid hemangioendothelioma (PEH) in a 13 years old girl, the aggressive nature of the tumor in this particular case and the PET CT findings. PEH are rare tumors of vascular origin, first described by Dial and Liebow in 1975. This is an uncommon pulmonary neoplasm, 4 times more common in young women. This tumor can affect multiple organs (lung, liver, bones and soft tissue, skin, heart, central nervous system). However lung and liver represent 2 main locations. Clinical manifestations are variable; typically patients are asymptomatic, and PEH is detected on routine chest radiographs as bilateral small (1 cm or less) nodules in the lungs Diagnosis usually requires a surgical lung biopsy. The prognosis is very unpredictable, with life expectancy ranging from 1 to 15 years. The tumor is usually considered as low to intermediate grade sarcoma. There is no single effective treatment however spontaneous remissions and aggressive behavior has been described.
authors.affiliation: Dr. Imran Yaqoob Nizami, Organ Transplant Center, MBC 96, King Faisal Specialist Hospital and Research Centre, PO Box 3354 Riyadh 11211, Saudi Arabia, T: 966-11-4647272 loc 76164, F: 966-11-4647272 loc 76167, imranyaqoob@kfshrc.edu.sa.
authors.forename: Imran
authors.initials: I
authors.lastname: Nizami
authors.forename: Shamayel
authors.initials: S
authors.lastname: Mohammed
authors.forename: Mohei El Din
authors.initials: Mel D
authors.lastname: Abouzied
mesh_terms: D000293:Adolescent; D017809:Fatal Outcome; D005260:Female; D018323:Hemangioendothelioma, Epithelioid / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis* / Q000473:pathology; D064847:Multimodal Imaging; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis* / Q000473:pathology; D010997:Pleural Neoplasms / Q000175:diagnosis* / Q000473:pathology; D049268:Positron-Emission Tomography; D014057:Tomography, X-Ray Computed
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