title: Incontinentia pigmenti: a rare genodermatosis in a male child.
abstract: Incontinentia pigmenti is rare X-linked dominant disorder. There is no consistent expression of Incontinetia pigmenti in female child, but in male child, they always lead to death in utero. Vesicular, verrucous, hyperpigmented, and atrophic stages are the four stages of Incontinetia Pigmenti and it is uncommon for all stages to be seen in a same case. It is a rare genodermatosis, with only very few cases of male child with Incontinentia pigmenti have been reported. Thus, we report this case due to its extreme rarity and the child showed all the first 3 stages on followup.
authors: Assistant Professor, Department of Paediatrics, Sri Manakula Vinayagar Medical College and Hospital , Puducherry, India .
authors: Dinesh Kumar Narayana
authors: DK
authors: Swamy
authors: Associate Professor, Department of Paediatrics, Sri Manakula Vinayagar Medical College and Hospital , Puducherry, India .
authors: Arulkumaran
authors: A
authors: Arunagirinathan
authors: Post Graduate, Department of Paediatrics, Sri Manakula Vinayagar Medical College and Hospital , Puducherry, India .
authors: Revathi
authors: R
authors: Krishnakumar
authors: Post Graduate, Department of Paediatrics, Sri Manakula Vinayagar Medical College and Hospital , Puducherry, India .
authors: Sivaraman
authors: S
authors: Sangili
keywords: Eosinophilia; Genes X-Linked; Melanins; Pigmentation