title: Proximal-type epithelioid sarcoma-unusual presentation: unilateral vulvar mass.
abstract: Epithelioid sarcoma of the vulva is a very rare malignant soft tissue tumour, usually initially asymptomatic, which simulates a variety of benign lesions, leading to diagnosis only at later stages. Prognosis is generally poor. We report a case of a 55-year-old postmenopausal woman, who presented with rapid growth of an asymptomatic mass located in the left labia majora. Biopsy of the lesion revealed features characteristic of proximal-type epithelioid sarcoma. Ganglionar, adrenal, pulmonary and hepatic metastases were found at thoracoabdominopelvic CT scan. During hospitalisation, the patient's clinical condition suffered rapid deterioration and she died on the 16th day of admission.
authors: Centro Materno-Infantil do Norte, Porto, Portugal.
authors: Ana Isabel
authors: AI
authors: Rodrigues
authors: Centro Materno-Infantil do Norte, Porto, Portugal.
authors: Helena Isabel
authors: HI
authors: Lopes
authors: Department of Pathology, Centro Hospitalar do Porto, Porto, Portugal.
authors: Olinda
authors: O
authors: Lima
authors: Department of Gynaecology, Centro Materno-Infantil do Norte, Porto, Portugal.
authors: Susana
authors: S
authors: Marta
mesh_terms: D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008875:Middle Aged; D009362:Neoplasm Metastasis; D011379:Prognosis; D012509:Sarcoma / Q000175:diagnosis* / Q000473:pathology; D014846:Vulvar Neoplasms / Q000175:diagnosis* / Q000473:pathology