title: Cutaneous amyloidosis associated with autoimmune hepatitis-primary biliary cirrhosis overlap syndrome.
abstract: Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.
authors: Servicio de Gastroenterología.
authors: Emmanuel I
authors: EI
authors: González-Moreno
authors: Departamento de Medicina Interna.
authors: Carlos R
authors: CR
authors: Cámara-Lemarroy
authors: Departamento de Medicina Interna.
authors: David O
authors: DO
authors: Borjas-Almaguer
authors: Servicio de Dermatología. Hospital Universitario Dr. José E. González. Universidad Autónoma de Nuevo León. Monterrey, N.L. México.
authors: Sylvia A
authors: SA
authors: Martínez-Cabriales
authors: Servicio de Gastroenterología.
authors: Jonathan
authors: J
authors: Paz-Delgadillo
authors: Servicio de Gastroenterología.
authors: Rodrigo
authors: R
authors: Gutiérrez-Udave
authors: Servicio de Dermatología. Hospital Universitario Dr. José E. González. Universidad Autónoma de Nuevo León. Monterrey, N.L. México.
authors: Ana S
authors: AS
authors: Ayala-Cortés
authors: Servicio de Dermatología. Hospital Universitario Dr. José E. González. Universidad Autónoma de Nuevo León. Monterrey, N.L. México.
authors: Jorge
authors: J
authors: Ocampo-Candiani
authors: Servicio de Gastroenterología.
authors: Carlos A
authors: CA
authors: Cortéz-Hernández
authors: Servicio de Gastroenterología.
authors: Héctor J
authors: HJ
authors: Maldonado-Garza
mesh_terms: D000328:Adult; D028226:Amyloidosis, Familial / Q000175:diagnosis / Q000209:etiology* / Q000276:immunology; D015551:Autoimmunity; D001706:Biopsy; D003937:Diagnosis, Differential; D019693:Hepatitis, Autoimmune / Q000150:complications* / Q000175:diagnosis / Q000276:immunology; D006801:Humans; D008099:Liver / Q000473:pathology; D008105:Liver Cirrhosis, Biliary / Q000150:complications* / Q000175:diagnosis / Q000276:immunology; D008297:Male; D012867:Skin / Q000473:pathology; D012873:Skin Diseases, Genetic / Q000175:diagnosis / Q000209:etiology* / Q000276:immunology; D013577:Syndrome