title: Non-functional paraganglioma of retroperitoneum mimicking pancreatic mass with concurrent urinary bladder paraganglioma: an extremely rare entity.
abstract: Paragangliomas are extra-adrenal tumours of the autonomic nervous system, which rarely present as primary retroperitoneal mass mimicking pancreatic malignancy (incidence 2-8 per million populations). Urinary Bladder Paraganglioma are also extremely rare (0.06% of all Bladder Tumour and 6% of Paragangliomas) with most being malignant and high grade tumours. Non-functional varieties of both tumours are usually incidentally diagnosed. The possibility for malignant transformation in them makes surgical excision the treatment of choice. A 45-year-old lady with abdominal pain was investigated to have a complex retroperitoneal mass behind head of pancreas and a urinary bladder mass. Complete excision of retroperitoneal and bladder lesion was done. Histopathological examinations of both specimens were suggestive of Paraganglioma with no abnormal mitotic activity and capsular/vascular invasion. Although concurrent non functional paragangliomas had been reported but the synchronous non-functional paragangliomas of retroperitoneum and urinary bladder reported in this case is extremely rare and is not reported so far in English literature.
authors: Senior Resident, Department of Surgery, Lady Harding Medical College and SSKH , New Delhi, India .
authors: Ankur
authors: A
authors: Verma
authors: Post graduate Student, Department of Surgery, Lady Harding Medical College and SSKH , New Delhi, India .
authors: Diwakar
authors: D
authors: Pandey
authors: Assistant Professor, Department of Surgery, Lady Harding Medical College and SSKH , New Delhi, India .
authors: Azaz
authors: A
authors: Akhtar
authors: Associate Professor, Department of Surgery, Lady Harding Medical College and SSKH , New Delhi, India .
authors: Ashish
authors: A
authors: Arsia
authors: Associate Professor, Department of Surgery, Lady Harding Medical College and SSKH , New Delhi, India .
authors: Nain
authors: N
authors: Singh
keywords: Excision; Pancreas; Retroperitoneal mass; Synchronous