title: Neurofibromatosis type 1-associated hypertension secondary to coarctation of the thoracic aorta.
abstract: Neurofibromatosis type 1 (NF-1), also known as von Recklinghausen's disease, is an autosomal dominant genetic disorder. NF-I vasculopathy has been used to describe various vascular malformations associated with NF-1. Secondary hypertension related to NF-1 vasculopathy has been reported because of renal artery stenosis, coarctation of the abdominal aorta and other vascular lesions; however, coarctation of the thoracic aorta has seldom been reported. We report the first case, to our knowledge, of isolated coarctation of thoracic aorta in a pregnant female with NF-1. Healthcare providers caring for patients with NF-1 should be aware of associated vascular complications.
authors: Department of Nephrology , Lenox Hill Hospital , New York , NY , USA.
authors: Gaurang
authors: G
authors: Mavani
authors: Department of Medicine , Lenox Hill Hospital , New York , NY , USA.
authors: Vivek
authors: V
authors: Kesar
authors: Department of Nephrology , Lenox Hill Hospital , New York , NY , USA.
authors: Maria V
authors: MV
authors: Devita
authors: Department of Nephrology , Lenox Hill Hospital , New York , NY , USA.
authors: Jordan L
authors: JL
authors: Rosenstock
authors: Department of Nephrology , Lenox Hill Hospital , New York , NY , USA.
authors: Michael F
authors: MF
authors: Michelis
authors: Department of Nephrology , Lenox Hill Hospital , New York , NY , USA.
authors: Joshua A
authors: JA
authors: Schwimmer
keywords: NF-1; aorta; coarctation; vasculopathy