title: Biventricular repair in a neonate with obstructive inflow cardiac rhabdomyoma and tuberous sclerosis.
abstract: A neonate with prenatally diagnosed large intracardiac rhabdomyomas and suspicion of tuberous sclerosis presented at birth with severe ductal-dependent obstruction at the tricuspid valve and an atrial septal defect (ASD). Biventricular repair at 9 days of life included tumor resection, repair of the posterior leaflet of the tricuspid valve with autologous pericardium, fenestrated ASD closure, and ductus ligation. After an uneventful postoperative recovery, follow-up echocardiography at two months showed excellent results with tricuspid valve competency and normal biventricular function. Overall prognosis will probably depend on issues pertaining to tuberous sclerosis.
authors: Pediatric and Congenital Heart Surgery, Children's Heart Center, University of Mississippi Medical Center, Jackson, MS, USA.
authors: Hunter W
authors: HW
authors: Hood
authors: Pediatric and Congenital Heart Surgery, Children's Heart Center, University of Mississippi Medical Center, Jackson, MS, USA adodgekhatami@umc.edu.
authors: Ali
authors: A
authors: Dodge-Khatami
authors: Pediatric and Fetal Cardiology, Children's Heart Center, University of Mississippi Medical Center, Jackson, MS, USA.
authors: Aimee S
authors: AS
authors: Parnell
authors: Pediatric and Congenital Heart Surgery, Children's Heart Center, University of Mississippi Medical Center, Jackson, MS, USA.
authors: Jorge D
authors: JD
authors: Salazar
mesh_terms: D004452:Echocardiography; D005260:Female; D005315:Fetal Diseases / Q000175:diagnosis; D006338:Heart Neoplasms / Q000175:diagnosis / Q000601:surgery*; D006344:Heart Septal Defects, Atrial / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008026:Ligation; D008297:Male; D010496:Pericardium / Q000637:transplantation; D011247:Pregnancy; D011296:Prenatal Diagnosis; D011379:Prognosis; D012207:Rhabdomyoma / Q000175:diagnosis / Q000601:surgery*; D014261:Tricuspid Valve / Q000601:surgery; D014264:Tricuspid Valve Stenosis / Q000601:surgery*; D014402:Tuberous Sclerosis / Q000150:complications* / Q000175:diagnosis
keywords: cardiac tumors; neonate; tricuspid valve