title: A Rare Case of Aggressive Fibromatosis Infiltrating Dorsal Muscles in a 6-Year-Old Patient - CT, MRI and Elastography Evaluation.
abstract: BACKGROUND
  The term fibromatosis or desmoid tumor refers to a group of benign fibrous growths without metastatic potential but with a significant risk of local recurrence. These lesions typically present infiltrative growth pattern with local invasion of adjacent tissues. This tendency is the reason for a relatively high rate of local recurrence, even after surgical removal. Fibromatosis is a very rare condition in general population but occurs more frequently in one of the familial cancer predispositions known as familial adenomatous polyposis (FAP) or Gardner syndrome. There are two main groups of fibromatosis: superficial (small, slow-growing lesions) and deep, also known as aggressive fibromatosis (large, rapid-growing lesions).
  
  
  METHODS
  We report a case of a 6-year-old boy suffering from an aggressive form of fibromatosis. The patient developed a large pathological mass extending from the neck to the loins. After incisional biopsy and histpoathological examination of the sample, a diagnosis of aggressive fibromatosis was established. During the whole diagnostic process, different imaging techniques including CT, MRI and sonoelastography were used. As the surgical treatment was not possible, the patient was finally qualified for chemotherapy.
  
  
  CONCLUSIONS
  Eventual diagnosis of aggressive fibromatosis is based on histopathological examination. However, it is an important condition that should be included in differential diagnosis of soft-tissue masses found in diagnostic imaging. Radiologists should be careful especially in defining the margins of infiltration in case of potential surgical treatment.
authors: Department of General and Pediatric Radiology, Independent Public Clinical Hospital No. 1, Wrocław, Poland ; Department of Radiology, Wrocław Medical University, Wrocław, Poland.
authors: Aleksander
authors: A
authors: Pawluś
authors: Department of General and Pediatric Radiology, Independent Public Clinical Hospital No. 1, Wrocław, Poland.
authors: Kinga
authors: K
authors: Szymańska
authors: Department of Radiology, Wrocław Medical University, Wrocław, Poland.
authors: Krzysztof
authors: K
authors: Kaczorowski
authors: Department of General and Pediatric Radiology, Independent Public Clinical Hospital No. 1, Wrocław, Poland ; Department of Radiology, Wrocław Medical University, Wrocław, Poland.
authors: Dąbrówka
authors: D
authors: Sokołowska-Dąbek
authors: Department of General and Pediatric Radiology, Independent Public Clinical Hospital No. 1, Wrocław, Poland ; Department of Radiology, Wrocław Medical University, Wrocław, Poland.
authors: Cyprian
authors: C
authors: Olchowy
authors: Medical University of Silesia, Katowice, Poland.
authors: Bartosz D
authors: BD
authors: Markiewicz
authors: Department of General and Pediatric Radiology, Independent Public Clinical Hospital No. 1, Wrocław, Poland ; Department of Radiology, Wrocław Medical University, Wrocław, Poland.
authors: Urszula
authors: U
authors: Zaleska-Dorobisz
keywords: Diagnostic Imaging; Elasticity Imaging Techniques; Fibromatosis, Aggressive