title: White matter relapsing remitting disease: "Susac's syndrome"-An underdiagnosed entity.
abstract: Susac's syndrome is a treatable microangiopathy of unknown etiology affecting arterioles of the brain, retina, and cochlea. The typical clinical manifestation is the triad of encephalopathy, visual loss, and sensorineural hearing loss. One or more of these features may not be present at onset and therefore Susac's syndrome's diagnosis may be difficult. We describe the clinical presentation, diagnostic tests, and treatment of three cases diagnosed and treated at our institution.
authors: Department of Neurology, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: luschot@gmail.com.
authors: Lucia V
authors: LV
authors: Schottlaender
authors: Department of Neurology, Neuroimmunology Section, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: jcorreale@fleni.org.ar.
authors: Jorge
authors: J
authors: Correale
authors: Department of Neurology, Vascular Neurology Section, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: sameriso@fleni.org.ar.
authors: Sebastian F
authors: SF
authors: Ameriso
authors: Department of Neurology, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: javiermoschini@hotmail.com.
authors: Javier A
authors: JA
authors: Moschini
authors: Department of Neurology, Neuroimmunology Section, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: lcrivelli@fleni.org.ar.
authors: Lucia
authors: L
authors: Crivelli
authors: Department of Neurology, Neuroimaging Section, Institute for Neurological Research (FLENI) Dr Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: fmeli@fleni.org.ar.
authors: Francisco
authors: F
authors: Meli
authors: Department of Neurology, Institute for Neurological Research (FLENI) Dr. Raúl Carrea, Montañeses 2325, Belgrano, Ciudad de Buenos Aires, Argentina. Electronic address: mfiol@fleni.org.ar.
authors: Marcela P
authors: MP
authors: Fiol
keywords: Cochlea; Corpus callosum; Encephalopathy; Retina; Susac's syndrome; White matter disease