title: Klippel-trénaunay syndrome - a very rare and interesting syndrome.
abstract: Klippel-Trénaunay syndrome (KTS or KT) is an infrequently seen dermatological syndrome, which is often viewed as a triad of vascular malformation (capillary malformations or port-wine brands), venous varicosity, and soft tissue and/or bony hypertrophy. We report a case of a 12-year-old male who presented to us with the symptoms of varicose plaques over both lower limbs and was diagnosed as a case of KTS. Management is normally conservative and includes stockings for compression of the branches to reduce edema because of chronic venous insufficiency; modern devices that cause on and off pneumatic compression; and rarely, surgical correction of varicose veins with lifelong follow-up. The orthopedic abnormalities are treated with epiphysiodesis in order to prevent (stop) overgrowing of limb and correction of bone deformity.
authors: Department of Neonatology, Fernandez Hospital, Hyderguda, Hyderabad, Andhra Pradesh, India.
authors: Deepak
authors: D
authors: Sharma
authors: Department of Dermatology, SMS Medical College, Jaipur, Rajasthan, India.
authors: Sachin
authors: S
authors: Lamba
authors: Department of Neonatology, Fernandez Hospital, Hyderguda, Hyderabad, Andhra Pradesh, India.
authors: Aakash
authors: A
authors: Pandita
authors: ACPM Medical College, Dhule, Maharashtra, India.
authors: Sweta
authors: S
authors: Shastri
keywords: Klippel–Trénaunay syndrome; capillary malformations; compression stockings; port-wine stains; soft tissue and/or bony hypertrophy; venous varicosity