title: Two-stage release in Streeter's dysplasia.
abstract: Streeter's dysplasia is a rare disorder of congenital constricting bands, occurring in 1-10 000 birth, with no sex predilection. In severe cases, it is associated with autoamputation of distal extremities such as fingers and toes. Recent advances have made it possible, in developed countries, to recognise this condition in the prenatal period and to initiate prompt intrauterine management, however, these, being uncommon procedures, need technical advances and experienced hands. In developing countries, recognition of the condition with timely management of primary and associated abnormalities required. We present a case of a 4-month-old child with type IV Streeter's dysplasia associated with right flexible clubfoot, who underwent successful two-stage release of symptomatic constricting bands from bilateral legs.
authors.affiliation: Department of General Surgery, Aga Khan University Hospital, Karachi, Sindh, Pakistan.
authors.forename: Zohaib Gulzar
authors.initials: ZG
authors.lastname: Naqvi
authors.affiliation: Department of Orthopedics, The Indus Hospital, Karachi, Sindh, Pakistan.
authors.forename: Irfan
authors.initials: I
authors.lastname: Rao
authors.affiliation: Department of General Surgery, The Indus Hospital, Karachi, Sindh, Pakistan.
authors.forename: Wahid
authors.initials: W
authors.lastname: Anwer
authors.affiliation: Department of Surgery, The Indus Hospital, Karachi, Sindh, Pakistan.
authors.forename: Tahir
authors.initials: T
authors.lastname: Yaseen
mesh_terms: D000015:Abnormalities, Multiple / Q000473:pathology / Q000601:surgery; D000652:Amniotic Band Syndrome / Q000473:pathology* / Q000601:surgery*; D003025:Clubfoot / Q000473:pathology / Q000601:surgery; D005260:Female; D005385:Fingers / Q000002:abnormalities; D006801:Humans; D007223:Infant; D007866:Leg / Q000002:abnormalities*; D008297:Male; D013577:Syndrome; D014034:Toes / Q000002:abnormalities