title: Primitive neuroectodermal tumour of pancreas; second case from Asia.
abstract: Primitive neuroectodermal tumours (PNETs) are malignant tumours composed of small round cells of neuroectodermal origin that affect soft tissue and bone. PNETs originating in the pancreas are extremely rare; previous to this report, only 14 cases were reported worldwide, making this case the fifteenth in the world and the second in Asia. We present the case of a painful pancreatic lump diagnosed as PNET of the pancreas after a thorough workup. The diagnosis of PNET is made according to the overall clinical picture, imaging, histopathology, cytogenetics, and immunohistochemistry, as in the case we present. It is essential to differentiate primary pancreatic PNET from a secondary involvement. A review of all of the cases diagnosed worldwide thus far is also provided.
authors.affiliation: Department of Internal Medicine, Sher-i-Kashmir Institute of Medical Sciences, Srinagar 190011, India.
authors.forename: Khalid Hamid
authors.initials: KH
authors.lastname: Changal
authors.affiliation: Department of Medical Oncology, Sher-i-Kashmir Institute of Medical Sciences, Srinagar 190011, India.
authors.forename: Mohmad Hussain
authors.initials: MH
authors.lastname: Mir
authors.affiliation: Department of Medical Oncology, Sher-i-Kashmir Institute of Medical Sciences, Srinagar 190011, India.
authors.forename: Sheikh Aejaz
authors.initials: SA
authors.lastname: Azaz
authors.affiliation: Department of Pathology, Sher-i-Kashmir Institute of Medical Sciences, Srinagar 90011, India.
authors.forename: Sumyra Khurshid
authors.initials: SK
authors.lastname: Qadri
authors.affiliation: Department of Medical Oncology, Sher-i-Kashmir Institute of Medical Sciences, Srinagar 190011, India.
authors.forename: Abdul Rashid
authors.initials: AR
authors.lastname: Lone
keywords: neuroectodermal tumors; pancreas; pancreatic neoplasms; primitive