title: Chylous ascites and lymphangiectasia in focal segmental glomerulosclerosis--a rare coexistence: a case report.
abstract: BACKGROUND
  Nephrotic syndrome is considered a rare cause of chylous ascites. Intestinal lymphangiectasia in a background of chylous ascites and without any lymphatic obstruction has been reported in association with yellow nail syndrome, which is a rare clinical occurrence in itself. The existence of chylous ascites, duodenal and splenic lymphangiectasia (without any lymphatic obstruction) and nephrotic syndrome in the form of focal segmental glomerulosclerosis in the same patient makes this case the first of its kind to be reported in the literature.
  
  
  METHODS
  Here we report the case of a 54-year-old Asian man who presented with recurrent episodes of anasarca for approximately 25 years. He was subsequently found to have chylous ascites, lymphangiectasia and persistent proteinuria. A renal biopsy revealed focal segmental glomerulosclerosis, not otherwise specified. A lymphangiogram, which was performed with the purpose of addressing the intestinal lymphangiectasia, failed to demonstrate any abnormality of lymphatic channels. He was put on oral steroids with consequent remission of his oedema and proteinuria.
  
  
  CONCLUSIONS
  This case highlights the fact that duodenal and splenic lymphangiectasia can exist in a scenario of chylous ascites without any obvious obstruction of lymphatic channels and in the absence of yellow nail syndrome. This case also signifies that chylous ascites may be a rare presenting feature of nephrotic syndrome and hence this aspect should be considered while in diagnostic dilemma regarding such a clinical presentation.
authors.affiliation: Department of General Medicine, IPGMER and SSKM Hospital, Kolkata, 700020, India. durjoy21288@ymail.com.
authors.forename: Durjoy
authors.initials: D
authors.lastname: Lahiri
authors.affiliation: Department of General Medicine, IPGMER and SSKM Hospital, Kolkata, 700020, India. dr.agarwal.rakesh@hotmail.com.
authors.forename: Rakesh
authors.initials: R
authors.lastname: Agarwal
authors.affiliation: Department of General Medicine, IPGMER and SSKM Hospital, Kolkata, 700020, India. drmanojroy@gmail.com.
authors.forename: Manoj Kumar
authors.initials: MK
authors.lastname: Roy
authors.affiliation: Department of General Medicine, IPGMER and SSKM Hospital, Kolkata, 700020, India. dramrito@gmail.com.
authors.forename: Amrita
authors.initials: A
authors.lastname: Biswas
mesh_terms: D002915:Chylous Ascites / Q000175:diagnosis / Q000209:etiology*; D005923:Glomerulosclerosis, Focal Segmental / Q000150:complications*; D006801:Humans; D008200:Lymphangiectasis / Q000209:etiology*; D008297:Male; D008875:Middle Aged; D009404:Nephrotic Syndrome / Q000150:complications; D011507:Proteinuria / Q000652:urine; D014057:Tomography, X-Ray Computed