[Hughes-Stovin Syndrome, a case report].
The Hughes-Stovin syndrome is a rare entity characterized by deep vein thrombosis and pulmonary artery aneurysms of unknown etiology and pathogenesis. Some authors considered a variant of Behcet's disease. Its natural course is usually fatal. The symptoms are cough, dyspnea, hemoptysis, chest pain and fever. The treatment goes from steroids and cytotoxic agents to surgery. We present the case of a 41 year old man who shows dyspnea, hemoptysis, and chest pain leading to the diagnosis of deep venous thrombosis of the right leg, lung thromboembolism and pulmonary artery aneurysms. He was treated with high-dose corticosteroids and 6 cyclophosphamide pulses of 1 gram each per 6 months with complete regression of aneurysms and symptomatology.
Servicio de Clínica Médica, Hospital Británico de Buenos Aires, Argentina.
Sonia
S
Pankl
Ana
A
Meraldi
Paola
P
Pegoraro
Geofredo
G
Earsman
Julio E
JE
Bruetman
José
J
Ceresetto
Martín
M
Bosio
Gustavo
G
Lyons
Pablo
P
Young
D000328:Adult; D017542:Aneurysm, Ruptured / Q000175:diagnosis*; D001528:Behcet Syndrome / Q000175:diagnosis; D006469:Hemoptysis / Q000209:etiology; D006801:Humans; D008297:Male; D011651:Pulmonary Artery; D011655:Pulmonary Embolism / Q000175:diagnosis*; D013577:Syndrome; D020246:Venous Thrombosis / Q000175:diagnosis*
Behcet's disease; deep vein thrombosis; hemoptysis; pulmonary artery aneurysms; vasculitis