Re-recurrent Dermatofibrosarcomaprotuberans of the chest wall.
Dermatofibrosarcomaprotuberans is a rare, soft tissue tumour with high rate of recurrence. It is locally aggressive, with a low rate of metastasis. We describe the case of a 42 year old man who presented with a re-recurrent, large tumour situated on the anterior chest wall in the sternal region. We did a wide local excision and covered the resulting defect by using bilateral, pectoralis major myocutaneous flaps. Histopathology and immunohistochemical staining findings were consistent with the diagnosis of Dermatofibrosarcoma Protuberance. Post operatively the patient was treated with chemotherapy and radiotherapy.
Ojha Institute of Chest Disease and Dow University Hospital, Karachi, Pakistan.
Niaz
N
Hussain
Aga Khan University Hospital, Karachi, Pakistan.
Mujtaba Zaki
MZ
Naveed
Jinnah Postgraduate Medical Center, Karachi, Pakistan.
Ghulam
G
Haider
D000328:Adult; D018223:Dermatofibrosarcoma / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000000981:diagnostic imaging / Q000601:surgery*; D012878:Skin Neoplasms / Q000000981:diagnostic imaging / Q000601:surgery*; D035441:Thoracic Wall / Q000000981:diagnostic imaging / Q000601:surgery*; D014057:Tomography, X-Ray Computed
Dermatofibrosarcomaprotuberans, Chest wall, Soft tissue tumour.