title: Staged biventricular repair for absent aortic valve in a neonate.
abstract: Congenitally absent aortic valve is an extremely rare and fatal cardiac malformation. We report the case of a neonate with absent aortic valve, an interrupted aortic arch, and a normal-sized left ventricle. At age 9 hours, emergency aortic valve closure and a Norwood procedure were performed to maintain coronary circulation. The patient's postoperative course was complicated because of tracheomalacia and a severely dilated aorta that were treated with reduction aortoplasty at age 4 months. Finally, a staged Yasui procedure was performed at 26 months. To our knowledge, this is the first report of a successful biventricular repair for absent aortic valve.
authors.affiliation: Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan. Electronic address: iwaki_kch@hp.pref.hyogo.jp.
authors.forename: Ryuma
authors.initials: R
authors.lastname: Iwaki
authors.affiliation: Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan.
authors.forename: Yoshihiro
authors.initials: Y
authors.lastname: Oshima
authors.affiliation: Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan.
authors.forename: Ayako
authors.initials: A
authors.lastname: Maruo
authors.affiliation: Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan.
authors.forename: Tomomi
authors.initials: T
authors.lastname: Hasegawa
authors.affiliation: Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan.
authors.forename: Hironori
authors.initials: H
authors.lastname: Matsuhisa
authors.affiliation: Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan.
authors.forename: Rei
authors.initials: R
authors.lastname: Noda
authors.affiliation: Department of Cardiovascular Surgery, Kobe Children's Hospital, Kobe, Japan.
authors.forename: Shunsuke
authors.initials: S
authors.lastname: Matsushima
mesh_terms: D001021:Aortic Valve / Q000002:abnormalities* / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods; D006330:Heart Defects, Congenital / Q000601:surgery*; D006352:Heart Ventricles / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male