title: An Update on Pulmonary Arterial Hypertension.
abstract: Pulmonary arterial hypertension (PAH) is a progressive disease that ultimately leads to right heart failure and death. PAH is defined as a mean pulmonary arterial pressure ≥ 25 mm Hg with a pulmonary capillary wedge pressure ≤ 15 mm Hg at rest. The diagnosis of PAH is one of exclusion; diagnostics include an extensive history, serology, chest radiograph, pulmonary function tests, ventilation/perfusion scan, transthoracic echocardiogram, and right heart catheterization. Treatment and care of patients with PAH can be complex. Therefore, the nurse practitioner is an integral member of the healthcare team caring for PAH patients, helping to ensure seamless care and support.
authors.affiliation: University of Pennsylvania, 2101 Market Street Unit 804, Philadelphia PA 19103.
authors.forename: Joanna
authors.initials: J
authors.lastname: Wapner
authors.affiliation: University of Pennsylvania, School of Nursing, Claire M. Fagin Hall, 418 Curie Blvd., Room 322, Philadelphia, Pennsylvania 19104-4217 USA.
authors.forename: Lea Ann
authors.initials: LA
authors.lastname: Matura
keywords: diagnosis; pathophysiology; pulmonary arterial hypertension; treatment