title: Pulmonary capillary haemangiomatosis: a rare cause of pulmonary hypertension.
abstract: Pulmonary capillary haemangiomatosis (PCH) is a rare disorder of unknown aetiology, characterised by proliferating capillaries that invade the pulmonary interstitium, alveolar septae and the pulmonary vasculature. It is often mis-diagnosed as primary pulmonary hypertension and pulmonary veno-occlusive disease. Pulmonary capillary haemangiomatosis is a locally aggressive benign vascular neoplasm of the lung. We report the case of a 19-year-old female who was referred to us in the early post-partum period with severe pulmonary artery hypertension, which was diagnosed as PCH by open lung biopsy.
authors.forename: K Anand
authors.initials: KA
authors.lastname: Babu
authors.forename: K
authors.initials: K
authors.lastname: Supraja
authors.forename: Raj B
authors.initials: RB
authors.lastname: Singh
mesh_terms: D001706:Biopsy; D003937:Diagnosis, Differential; D005260:Female; D018324:Hemangioma, Capillary / Q000175:diagnosis / Q000503:physiopathology / Q000628:therapy; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology / Q000628:therapy; D008168:Lung / Q000000981:diagnostic imaging / Q000473:pathology; D008175:Lung Neoplasms / Q000175:diagnosis / Q000503:physiopathology / Q000628:therapy; D010102:Oxygen Inhalation Therapy / Q000379:methods; D011859:Radiography; D020775:Thoracic Surgery, Video-Assisted / Q000379:methods; D055815:Young Adult