title: An adult case of polysplenia syndrome associated with sinus node dysfunction, dextrocardia, and systemic venous anomalies.
abstract: A 54-year-old woman was referred to our hospital for symptomatic sinus bradyarrhythmia with a sinus pause of 8 seconds. She was diagnosed with dextrocardia during childhood and discovered to have heterotaxy syndrome when she had an appendectomy during her teenager years. Chest and abdominal examinations by computed tomography showed multiple spleens located on the right side and abnormal drainages of the superior and inferior vena cava. Left isomerism was diagnosed by bilaterally bilobed lungs. Because of a patent bilateral superior vena cava, pacemaker leads were implanted using the right cephalic vein approach. Her fainting symptoms disappeared after pacemaker implantation.
authors.affiliation: Department of Cardiology, Juntendo University Nerima Hospital, Japan.
authors.forename: Kentaro
authors.initials: K
authors.lastname: Fukuda
authors.forename: Toshihito
authors.initials: T
authors.lastname: Onda
authors.forename: Yuki
authors.initials: Y
authors.lastname: Kimura
authors.forename: Seiji
authors.initials: S
authors.lastname: Miura
authors.forename: Rie
authors.initials: R
authors.lastname: Matsumori
authors.forename: Yoshiyuki
authors.initials: Y
authors.lastname: Masaki
authors.forename: Akihisa
authors.initials: A
authors.lastname: Nishino
authors.forename: Kenji
authors.initials: K
authors.lastname: Inoue
authors.forename: Yasumasa
authors.initials: Y
authors.lastname: Fujiwara
authors.forename: Masataka
authors.initials: M
authors.lastname: Sumiyoshi
mesh_terms: D001146:Arrhythmia, Sinus / Q000150:complications / Q000503:physiopathology*; D003914:Dextrocardia / Q000150:complications / Q000503:physiopathology* / Q000628:therapy; D005260:Female; D059446:Heterotaxy Syndrome / Q000000981:diagnostic imaging* / Q000503:physiopathology / Q000628:therapy; D006801:Humans; D008875:Middle Aged; D010138:Pacemaker, Artificial; D013575:Syncope / Q000209:etiology / Q000503:physiopathology* / Q000628:therapy; D014057:Tomography, X-Ray Computed; D014682:Vena Cava, Inferior / Q000002:abnormalities