title: Comprehensive dental management in a Hallermann-Streiff syndrome patient with unusual radiographic appearance of teeth.
abstract: Hallermann-Streiff syndrome (HSS) is a genetic disorder characterized by proportionate dwarfism, birdlike facies, hypotrichosis, skin atrophy, dyscephaly, bilateral microphthalmia, congenital cataracts, a narrow, weak, beaked nose, a hypoplastic mandible, and orodental anomalies. Occurrence is sporadic and distinct patterns of inheritance have not been found. This case report describes the dental management of a 3-year-old girl patient with HSS, who had unusual radiographic appearance of teeth. Furthermore, dental treatments and a 30-month follow-up period of the patient with this rare tooth structure malformation have been presented.
authors.forename: O Erken
authors.initials: OE
authors.lastname: Gungor
authors.forename: B Guzel
authors.initials: BG
authors.lastname: Nur
authors.forename: H
authors.initials: H
authors.lastname: Yalcin
authors.affiliation: Department of Pedodontics, Faculty of Dentistry, Akdeniz University, Antalya, Turkey.
authors.forename: H
authors.initials: H
authors.lastname: Karayilmaz
authors.forename: E
authors.initials: E
authors.lastname: Mihci
mesh_terms: D002675:Child, Preschool; D003832:Denture, Partial, Removable; D005260:Female; D006210:Hallermann's Syndrome / Q000150:complications* / Q000000981:diagnostic imaging / Q000628:therapy; D006801:Humans; D008310:Malocclusion / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy*; D011859:Radiography