title: Pulmonary manifestation of a condition resembling Kasabach-Merritt syndrome in a woman with abdominal angiomatosis associated with consumptive coagulopathy--surgical management: a case report.
abstract: BACKGROUND
  Kasabach-Merritt syndrome is a benign condition characterized by hemangiomatosis, severely disseminated intravascular consumption coagulopathy, and thrombocytopenia. The mortality rate increases from 12% to 30% in hemorrhagic cases. In general, the symptoms primarily manifest in the gastrointestinal tract, the skin, and the subcutaneous tissue. There is no publication about pulmonary manifestation of angiomatosis in combination with vascular malformation and hemoptysis. This is the first description of a Kasabach-Merritt syndrome-like condition in the lung.
  
  
  METHODS
  We present the case of a 29-year-old German woman with angiomatosis and associated pulmonary vascular malformation in her lower left lobe with a Kasabach-Merritt syndrome like condition. It was detected after hemoptysis. We also present our case observations and management.
  
  
  CONCLUSIONS
  In a case of angiomatosis with an associated pulmonary lobar vascular malformation, lobectomy can be safely performed to prevent life-threatening bleeding.
authors.affiliation: Department of Thoracic Surgery, Ruhrlandklinik-Essen, University of Duisburg-Essen, Essen, Germany. danjouma.cheufou@ruhrlandklinik.uk-essen.de.
authors.forename: Danjouma Housmanou
authors.initials: DH
authors.lastname: Cheufou
authors.affiliation: Institute of Pathology and Neuropathology, University Hospital of Essen, University of Duisburg-Essen, Essen, Germany. thomas.hager@uk-essen.de.
authors.forename: Thomas
authors.initials: T
authors.lastname: Hager
authors.affiliation: Department of Thoracic Surgery, Ruhrlandklinik-Essen, University of Duisburg-Essen, Essen, Germany. stefan.welter@ruhrlandklinik.uk-essen.de.
authors.forename: Stefan
authors.initials: S
authors.lastname: Welter
authors.affiliation: Institute of Pathology and Neuropathology, University Hospital of Essen, University of Duisburg-Essen, Essen, Germany. dirk.theegarten@uk-essen.de.
authors.forename: Dirk
authors.initials: D
authors.lastname: Theegarten
authors.affiliation: Department of Thoracic Surgery, Ruhrlandklinik-Essen, University of Duisburg-Essen, Essen, Germany. georgios.stamatis@ruhrlandklinik.uk-essen.de.
authors.forename: Georgios
authors.initials: G
authors.lastname: Stamatis
mesh_terms: D000005:Abdomen; D000328:Adult; D000798:Angiomatosis / Q000150:complications*; D003937:Diagnosis, Differential; D004211:Disseminated Intravascular Coagulation; D005260:Female; D006801:Humans; D059885:Kasabach-Merritt Syndrome / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D008168:Lung / Q000000981:diagnostic imaging / Q000601:surgery*; D011013:Pneumonectomy; D011859:Radiography; D054079:Vascular Malformations / Q000175:diagnosis / Q000601:surgery*