title: Artery fistula causing aortic regurgitation in pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries.
abstract: We report a case of aortic regurgitation (AR), coronary artery-to-pulmonary artery (CAPA) fistula, pulmonary atresia with ventricular septal defect (PA/VSD), and major aortopulmonary collateral arteries (MAPCAS). As a result of coronary steal and AR, myocardial ischemia and ventricular dysfunction occurred. When the patient was 2 months old with a body weight of 2.7 kg, we performed fistula ligation, aortic valvuloplasty, unifocalization of the MAPCAS, and right ventricle-to-pulmonary artery shunting. After the operation, the AR volume reduced, and the patient was scheduled for repair.
authors.affiliation: Department of Cardiovascular Surgery, Iwate Medical University, Morioka, Japan.
authors.forename: Tatsuya
authors.initials: T
authors.lastname: Furutake
authors.affiliation: Department of Cardiovascular Surgery, Iwate Medical University, Morioka, Japan.
authors.forename: Junichi
authors.initials: J
authors.lastname: Koizumi
authors.affiliation: Department of Cardiovascular Surgery, Iwate Medical University, Morioka, Japan.
authors.forename: Tomoyuki
authors.initials: T
authors.lastname: Iwase
authors.affiliation: Department of Cardiovascular Surgery, Iwate Medical University, Morioka, Japan.
authors.forename: Takeshi
authors.initials: T
authors.lastname: Kamada
authors.affiliation: Department of Pediatric Cardiology, Iwate Medical University, Morioka, Japan.
authors.forename: Shin
authors.initials: S
authors.lastname: Takahashi
authors.affiliation: Department of Pediatric Cardiology, Iwate Medical University, Morioka, Japan.
authors.forename: Kotaro
authors.initials: K
authors.lastname: Oyama
authors.affiliation: Department of Cardiovascular Surgery, Iwate Medical University, Morioka, Japan.
authors.forename: Hitoshi
authors.initials: H
authors.lastname: Okabayashi
authors.affiliation: Department of Cardiovascular Surgery, Iwate Medical University, Morioka, Japan. Electronic address: ikai@iwate-med.ac.jp.
authors.forename: Akio
authors.initials: A
authors.lastname: Ikai
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities*; D001022:Aortic Valve Insufficiency / Q000209:etiology*; D001159:Arterio-Arterial Fistula / Q000150:complications*; D003097:Collateral Circulation; D003324:Coronary Artery Disease / Q000150:complications*; D006343:Heart Septal Defects / Q000150:complications*; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities*; D018633:Pulmonary Atresia / Q000150:complications*