title: [Atypical presentation of Gorham-Stout syndrome: Case report].
abstract: Gorham-Stout syndrome is an extremely rare pathology, of unknown etiology. It is characterized by proliferation of vascular channels that causes destruction and reabsorption of the bone matrix. We present a nine year-old male patient with an acute episode characterized by fever, chest pain, respiratory distress and dyspnea. The patient was submitted to computed tomography scan and a biopsy. The findings in the biopsy were multiple lytic lesions, osteolysis, and a mediastinal lymphangioma (lymphangiomatosis). The diagnosis was Gorham-Stout syndrome with atypical presentation.
authors.affiliation: Escuela de Medicina, Universidad Peruana de Ciencias Aplicadas, Lima, Perú
authors.forename: Alejandro
authors.initials: A
authors.lastname: González Luna
authors.affiliation: Escuela de Medicina, Universidad Peruana de Ciencias Aplicadas, Lima, Perú
authors.forename: Jorge Luis
authors.initials: JL
authors.lastname: Nuñez Pizarro
authors.affiliation: Escuela de Medicina, Universidad Peruana de Ciencias Aplicadas, Lima, Perú
authors.forename: Clodo Iván
authors.initials: CI
authors.lastname: Rodríguez Echegaray
mesh_terms: D002648:Child; D006801:Humans; D008297:Male; D010015:Osteolysis, Essential / Q000175:diagnosis*; D013577:Syndrome