title: Arrhythmias in left ventricular noncompaction.
abstract: Left ventricular noncompaction (LVNC) is a newly recognized form of cardiomyopathy that has been associated with heart failure, arrhythmias, thromboembolic events, and sudden death. Both ventricular and supraventricular arrhythmias are now well described as prominent clinical components of LVNC. Throughout the spectrum of age, these arrhythmias have been associated with prognosis and outcome, and their clinical management is therefore an important aspect of patient care. The risk of sudden death seems to be associated with ventricular dilation, systolic dysfunction, and the presence of arrhythmias. Proposed management strategies shown to have efficacy include antiarrhythmic therapy, ablation techniques, and implantable cardioverter-defibrillator implantation.
authors.affiliation: Section of Pediatric Cardiology, Department of Pediatrics, Baylor College of Medicine, Texas Children's Hospital, 6621 Fannin Street, Houston, TX 77030, USA.
authors.forename: Christina Y
authors.initials: CY
authors.lastname: Miyake
authors.affiliation: Section of Pediatric Cardiology, Department of Pediatrics, Baylor College of Medicine, Texas Children's Hospital, 6621 Fannin Street, Houston, TX 77030, USA. Electronic address: jjkim@texaschildrens.org.
authors.forename: Jeffrey J
authors.initials: JJ
authors.lastname: Kim
mesh_terms: D001145:Arrhythmias, Cardiac; D009202:Cardiomyopathies; D016757:Death, Sudden, Cardiac; D006330:Heart Defects, Congenital; D006333:Heart Failure; D006352:Heart Ventricles / Q000503:physiopathology; D006801:Humans
keywords: Arrhythmias; Atrial fibrillation; Cardiomyopathy; Electrocardiogram; Heart failure; Left ventricular noncompaction; Sudden death; Ventricular tachycardia