title: IgG4-related Kidney Disease in Which the Urinalysis, Kidney Function and Imaging Findings Were Normal.
abstract: IgG4-related kidney disease (IgG4RKD) is recognized as a fibroinflammatory disease characterized by storiform fibrosis, lymphoplasmacytic infiltration and a high serum IgG4 level. A renal biopsy is necessary to diagnose IgG4RKD in patients without any lesions in other organs. Nephrologists typically perform renal biopsies in patients with abnormal urinalysis, such as proteinuria or hematuria, or renal failure. However, we experienced a patient with IgG4RKD without abnormalities in the urinalysis, renal function or imaging, who had severe interstitial lesions. We therefore propose that renal biopsies should be considered if patients do not show abnormal urinalysis findings and are suspected to have IgG4RKD.
authors.affiliation: Department of Nephrology, Kobe City Medical Center West Hospital, Japan.
authors.forename: Miho
authors.initials: M
authors.lastname: Otani
authors.forename: Masahiro
authors.initials: M
authors.lastname: Morinaga
authors.forename: Yoshihiko
authors.initials: Y
authors.lastname: Nakajima
authors.forename: Hiromi
authors.initials: H
authors.lastname: Tomioka
authors.forename: Michiko
authors.initials: M
authors.lastname: Nishii
authors.forename: Yusuke
authors.initials: Y
authors.lastname: Inoue
authors.forename: Tetsuya
authors.initials: T
authors.lastname: Ikeda
authors.forename: Mai
authors.initials: M
authors.lastname: Morimoto
authors.forename: Eiji
authors.initials: E
authors.lastname: Katsuyama
authors.forename: Shinichiro
authors.initials: S
authors.lastname: Tsunoda
mesh_terms: D001327:Autoimmune Diseases / Q000175:diagnosis* / Q000276:immunology*; D001706:Biopsy; D003952:Diagnostic Imaging; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology*; D007674:Kidney Diseases / Q000175:diagnosis* / Q000276:immunology*; D007677:Kidney Function Tests; D008297:Male; D008875:Middle Aged; D016482:Urinalysis
chemical_list: D007074:Immunoglobulin G