title: Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome.
abstract: BACKGROUND
  Treacher-Collins syndrome is characterized by craniofacial malformations, narrowing of the external auditory canal (EAC), and, in 30% of cases, agenesis of the canal and ossicular chain defects. The use of hearing aids (HA) is not possible in cases in which agenesis or stenosis of the EAC accompanies conductive deafness. In contrast, bone conduction implants such as the Bone Anchored Hearing Aid (BAHA(®)) allow direct stimulation of the cochlea and are thus superior to conventional hearing aids in cases of severe conductive hearing loss.
  
  
  OBJECTIVE
  To present 2 cases of patients with Treacher-Collins syndrome who underwent implantation of BAHA(®).
  
  
  METHODS
  The first patient was a 52-year-old woman diagnosed with Treacher-Collins syndrome who presented with severe bilateral mixed hearing loss and a history of unsuccessful previous use of a bone contact conduction device. The BAHA(®) implantation was uneventful, and the post-operative results were good. The second patient was a 14-year-old girl who was also diagnosed with Treacher-Collins Syndrome with bilateral moderate conductive hearing loss by audiometry. The use of a bone vibrator contact device did not improve her hearing; however, implantation of a BAHA(®) resulted in a decreased gap postoperatively. Final comments: BAHA(®) hearing devices provide adequate rehabilitation and consequent improvement of the quality of life in patients with Treacher-Collins syndrome.
authors.affiliation: Resident Doctor in the Department of Otolaryngology at the Institute of Medical Assistance to the State's Public Service, Sao Paulo.
authors.forename: Alexandra Kolontai de Sousa
authors.initials: AK
authors.lastname: Oliveira
authors.affiliation: Resident Doctor in the Department of Otolaryngology at the Institute of Medical Assistance to the State's Public Service, Sao Paulo.
authors.forename: Lília Pereira Abreu
authors.initials: LP
authors.lastname: Ferro
authors.affiliation: Speech Therapist at the Institute of Medical Assistance to the State's Public Service, Sao Paulo.
authors.forename: Jaiede Nicacio
authors.initials: JN
authors.lastname: da Silva
authors.affiliation: Master of Health Sciences. Physician Assistant Hospital Service, State of São Paulo.
authors.forename: Daniel Mochida
authors.initials: DM
authors.lastname: Okada
keywords: bone conduction; conductive; hearing loss; mandibulofacial dysostosis