title: Anti-neutrophil Cytoplasmic Antibody (ANCA)-associated Vasculitis Associated with Primary Biliary Cirrhosis: A Case Report and Literature Review.
abstract: We herein report a rare case of microscopic polyangiitis with primary biliary cirrhosis (PBC) and a literature review of six previously reported cases of PBC complicated by anti-neutrophil cytoplasmic antibody-associated vasculitis. Due to the scarcity of similar reports, it was not possible to establish a true overlap syndrome or casual association. When the biliary enzyme levels are elevated in patients with vasculitis, physicians should thus be mindful of the possible coexistence of these diseases.
authors.affiliation: Division of Rheumatic Diseases, National Center for Global Health and Medicine, Japan.
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Yamashita
authors.forename: Akitake
authors.initials: A
authors.lastname: Suzuki
authors.forename: Yuko
authors.initials: Y
authors.lastname: Takahashi
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Kaneko
authors.forename: Toshikazu
authors.initials: T
authors.lastname: Kano
authors.forename: Akio
authors.initials: A
authors.lastname: Mimori
mesh_terms: D000328:Adult; D000368:Aged; D056648:Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis / Q000150:complications*; D001327:Autoimmune Diseases / Q000150:complications; D005260:Female; D006801:Humans; D008105:Liver Cirrhosis, Biliary / Q000150:complications*; D055953:Microscopic Polyangiitis / Q000150:complications; D008875:Middle Aged