title: Plexogenic pulmonary hypertension in systemic lupus erythematosus: Report of two cases and review of the literature.
abstract: From the autopsy records of the Mayo Clinic, two patients with systemic lupus erythematosus were identified in whom plexogenic pulmonary hypertension also developed. Both were women (23 and 30 years old). Their pulmonary artery pressures were 96/30 and 115/45 mm Hg, respectively, and their survival after the diagnosis of pulmonary hypertension was only 21 and 19 months, respectively. To our knowledge, only two other cases have been reported. Thus, plexogenic pulmonary hypertension among patients with lupus is rare but is associated with a poor prognosis.
authors.affiliation: University of South Florida, School of Medicine, Tampa, Florida, USA.
authors.forename: J
authors.initials: J
authors.lastname: Goldman
authors.affiliation: Division of Anatomic Pathology, Mayo Clinic and Mayo Foundation, Rochester, Minnesota, USA.
authors.forename: W D
authors.initials: WD
authors.lastname: Edwards