title: Arrhythmias in the muscular dystrophies.
abstract: In patients with muscular dystrophies, cardiac involvement leading to cardiomyopathy and arrhythmias occurs with variable prevalence, mirroring the phenotypic variability seen among and within the various hereditary myopathies. Knowledge of the incidence of arrhythmias and predictors of sudden death in the various hereditary myopathies can help guide screening and appropriate management of these patients, thereby improving survival. The noncardiac manifestations can lead to delayed recognition of symptoms, affect the decision to implant a prophylactic device, and once a decision is made to proceed with device implant, increase peri-procedural respiratory and anesthesia-related complications.
authors.affiliation: Krannert Institute of Cardiology, Indiana University School of Medicine, Indianapolis, IN 46202, USA.
authors.forename: Archana
authors.initials: A
authors.lastname: Rajdev
authors.affiliation: William Jennings Bryan Dorn Veterans Affairs Medical Center, University of South Carolina, 6439 Garners Ferry Road, Columbia, SC 29209-1639, USA. Electronic address: wgroh@iu.edu.
authors.forename: William J
authors.initials: WJ
authors.lastname: Groh
mesh_terms: D001145:Arrhythmias, Cardiac; D006801:Humans; D009136:Muscular Dystrophies
keywords: Arrhythmia; Genetics; Implantable cardioverter-defibrillator; Muscular dystrophy; Pacemaker; Sudden cardiac death