title: Cochlear implantation in patient with Dandy-walker syndrome.
abstract: BACKGROUND
  Dandy Walker Syndrome is a congenital abnormality in the central nervous system, characterized by a deficiency in the development of middle cerebelar structures, cystic dilatation of the posterior pit communicating with the fourth ventricle and upward shift of the transverse sinuses, tentorium and dyes. Among the clinical signs are occipital protuberances, a progressive increase of the skull, bowing before the fontanels, papilledema, ataxia, gait disturbances, nystagmus, and intellectual impairment.
  
  
  OBJECTIVE
  To describe a case of female patient, 13 years old with a diagnosis of this syndrome and bilateral hearing loss underwent cochlear implant surgery under local anesthesia and sedation.
  
  
  METHODS
  CGS, 13 years old female was referred to the Otolaryngological Department of Otolaryngology Institute of Parana with a diagnosis of "Dandy-Walker syndrome" for Otolaryngological evaluation for bilateral hearing loss with no response to the use of hearing aids. Final Comments: The field of cochlear implants is growing rapidly. We believe that the presence of Dandy-Walker syndrome cannot be considered a contraindication to the performance of cochlear implant surgery, and there were no surgical complications due to neurological disorders with very favorable results for the patient who exhibits excellent discrimination. It has less need for lip reading with improvement in speech quality.
authors.affiliation: Otolaryngological Doctor at Hospital of Parana of Otolaryngology.
authors.forename: Adriana Kosma Pires
authors.initials: AK
authors.lastname: de Oliveira
authors.affiliation: Professor of Otolaryngology, Federal University of Parana. Otolaryngologist Doctor at, Hospital of Parana of Otolaryngology.
authors.forename: Rogerio
authors.initials: R
authors.lastname: Hamerschmidt
authors.affiliation: Head of the Department of Otolaryngology, Clinics Hospital, Federal University of Parana. Head of the Department of Otolaryngology, Clinics Hospital, Federal University of Parana.
authors.forename: Marcos
authors.initials: M
authors.lastname: Mocelin
authors.affiliation: Resident of Otolaryngology at the Clinics Hospital, Federal University of Parana.
authors.forename: Rodrigo K
authors.initials: RK
authors.lastname: Rezende
keywords: Dandy-Walker syndrome; cochlear implants; hearing loss