title: Right ventricular cardiomyopathy meeting the arrhythmogenic right ventricular dysplasia revised criteria? Don't forget sarcoidosis!
abstract: A 53-year-old woman was referred for ventricular fibrillation with resuscitation. A CT-angiography showed signs of a right ventricular enlargement without obvious cause. A cardiac MRI demonstrated a dilated and hypokinetic right ventricle with extensive late gadolinium enhancement. Arrhythmogenic right ventricular dysplasia (ARVD) was suspected according to the "revised ARVD task force criteria". An endomyocardial biopsy was inconclusive. The patient developed purulent pericarditis after epicardial ablation therapy and died of toxic shock syndrome. The post-mortem pathologic examination demonstrated sarcoidosis involving the heart, lungs, and thyroid gland.
authors.affiliation: Department of Radiology, Leiden University Medical Center, Leiden 2333 ZA, The Netherlands.
authors.forename: Sabina
authors.initials: S
authors.lastname: Vasaturo
authors.affiliation: Department of Pathology, Leiden University Medical Center, Leiden 2333 ZA, The Netherlands.
authors.forename: David E
authors.initials: DE
authors.lastname: Ploeg
authors.affiliation: Department of Radiology, Hospital General Universitario Gregorio Maranon, Madrid 28007, Spain.
authors.forename: Guadalupe
authors.initials: G
authors.lastname: Buitrago
authors.affiliation: Department of Cardiology, Leiden University Medical Center, Leiden 2333 ZA, The Netherlands.
authors.forename: Katja
authors.initials: K
authors.lastname: Zeppenfeld
authors.affiliation: Department of Pathology, Leiden University Medical Center, Leiden 2333 ZA, The Netherlands.
authors.forename: Maud
authors.initials: M
authors.lastname: Veselic-Charvat
authors.affiliation: Department of Radiology, Leiden University Medical Center, Leiden 2333 ZA, The Netherlands.
authors.forename: Lucia J M
authors.initials: LJ
authors.lastname: Kroft
mesh_terms: D019571:Arrhythmogenic Right Ventricular Dysplasia / Q000175:diagnosis*; D005260:Female; D006352:Heart Ventricles / Q000473:pathology; D006801:Humans; D008168:Lung / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D009206:Myocardium / Q000473:pathology; D012507:Sarcoidosis / Q000175:diagnosis*; D013961:Thyroid Gland / Q000473:pathology; D014693:Ventricular Fibrillation / Q000175:diagnosis / Q000209:etiology*
keywords: ARVD; Cardiomyopathy; Late enhancement; MRI; Pathology; Right ventricle; Sarcoidosis