title: Atypical Clival Chordoma in an Adolescent without Imaging Evidence of Bone Involvement.
abstract: Clival chordoma is a rare primary bone tumour that arises from the remnant of the notochord and typically occurs in older adults. Upon imaging, the tumour can be seen arising from the clivus and causes clival destruction. This usually provides insight for a diagnosis. Here we present a case of a non-enhancing, pre-pontine mass that was hypointense on T1W and hyperintense on T2W in an adolescent. No clival bone erosion was observed. Based on the age group, imaging findings, and lack of clival erosion, a provisional diagnosis of epidermoid cyst was made and the tumour was resected. This patient was eventually diagnosed with a clival chordoma based on histopathological examination.
authors.affiliation: Imaging Unit, Faculty of Medicine, Universiti Teknologi MARA, Jalan Hospital, 47000 Sungai Buloh, Selangor, Malaysia.
authors.forename: Hilwati
authors.initials: H
authors.lastname: Hashim
authors.affiliation: Department of Neurosurgery, Sungai Buloh Hospital, Jalan Hospital, 47000 Sungai Buloh, Selangor, Malaysia.
authors.forename: Azmin Kass
authors.initials: AK
authors.lastname: Rosman
authors.affiliation: Department of Radiology, Sungai Buloh Hospital, Jalan Hospital, 47000 Sungai Buloh, Selangor, Malaysia.
authors.forename: Aida
authors.initials: A
authors.lastname: Abdul Aziz
authors.affiliation: Imaging Unit, Faculty of Medicine, Universiti Teknologi MARA, Jalan Hospital, 47000 Sungai Buloh, Selangor, Malaysia.
authors.forename: Abdul Kadir
authors.initials: AK
authors.lastname: Roqiah
authors.affiliation: Department of Pathology, Faculty of Medicine, Universiti Teknologi MARA, Jalan Hospital, 47000 Sungai Buloh, Selangor, Malaysia.
authors.forename: Nor Salmah
authors.initials: NS
authors.lastname: Bakar
keywords: adolescent; atypical; chordoma; clivus; magnetic resonance imaging