title: Physical activity in youth with osteogenesis imperfecta type I.
abstract: BACKGROUND
  Individuals with Osteogenesis Imperfecta (OI) type I often show muscular weakness. However, it is unclear whether muscular weakness is a consequence of physical inactivity or a result of the disease itself. The aim was to assess muscle function in youth with OI type I and evaluate physical activity (PA).
  
  
  METHODS
  Fourteen children with OI type I (mean age [SD]: 12.75 [4.62] years) were compared to 14 age- and gender-matched controls (mean age [SD]: 12.75 [4.59] years). Muscle force and power were determined through mechanography. PA and daily energy expenditure were measured with an accelerometer and a questionnaire.
  
  
  RESULTS
  Compared to controls, children with OI type I had lower muscle force and power. OI type I children were as active as their healthy counterparts.
  
  
  CONCLUSIONS
  Children and adolescents with OI type I and their healthy counterparts did not reached daily recommendations of PA. Given their muscle function deficit, youth with OI type I would benefit to reach these recommendations to prevent precocious effect of aging on muscles.
authors.affiliation: Shriners Hospital for Children and Departement of Pediatrics, McGill University, 1529 avenue Cedar, Montréal, Québec, Canada H3G 1A6.|Centre de Recherche CHU Sainte-Justine, Centre de réadaptation Marie Enfant, 5200 rue Bélanger, Montréal, Québec, Canada H1T 1C9.|Département de Kinanthropologie, Université du Québec à Montréal, 141 Avenue du Président-Kennedy, Montréal, Québec, Canada H2X 1Y4.
authors.forename: A
authors.initials: A
authors.lastname: Pouliot-Laforte
authors.affiliation: Shriners Hospital for Children and Departement of Pediatrics, McGill University, 1529 avenue Cedar, Montréal, Québec, Canada H3G 1A6.|Centre de Recherche CHU Sainte-Justine, Centre de réadaptation Marie Enfant, 5200 rue Bélanger, Montréal, Québec, Canada H1T 1C9.
authors.forename: L-N
authors.initials: LN
authors.lastname: Veilleux
authors.affiliation: Shriners Hospital for Children and Departement of Pediatrics, McGill University, 1529 avenue Cedar, Montréal, Québec, Canada H3G 1A6.|Centre de Recherche CHU Sainte-Justine, Centre de réadaptation Marie Enfant, 5200 rue Bélanger, Montréal, Québec, Canada H1T 1C9.
authors.forename: F
authors.initials: F
authors.lastname: Rauch
authors.affiliation: Centre de Recherche CHU Sainte-Justine, Centre de réadaptation Marie Enfant, 5200 rue Bélanger, Montréal, Québec, Canada H1T 1C9.|Département de Kinanthropologie, Université du Québec à Montréal, 141 Avenue du Président-Kennedy, Montréal, Québec, Canada H2X 1Y4.
authors.forename: M
authors.initials: M
authors.lastname: Lemay
mesh_terms: D061725:Accelerometry; D000293:Adolescent; D001827:Body Height; D001835:Body Weight; D002648:Child; D004734:Energy Metabolism; D005260:Female; D006801:Humans; D008297:Male; D009043:Motor Activity; D009119:Muscle Contraction; D053580:Muscle Strength; D018908:Muscle Weakness / Q000209:etiology / Q000503:physiopathology; D018482:Muscle, Skeletal / Q000503:physiopathology; D010013:Osteogenesis Imperfecta / Q000503:physiopathology*; D011795:Surveys and Questionnaires