title: Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management.
abstract: Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplantation.
authors.affiliation: Department of Anesthesia and Critical Care, Institute of Liver and Biliary Sciences, New Delhi, India.
authors.forename: Anshuman
authors.initials: A
authors.lastname: Singh
authors.affiliation: Department of Anesthesia and Critical Care, Institute of Liver and Biliary Sciences, New Delhi, India.
authors.forename: V K
authors.initials: VK
authors.lastname: Pandey
authors.affiliation: Department of Anesthesia and Critical Care, Institute of Liver and Biliary Sciences, New Delhi, India.
authors.forename: Manish
authors.initials: M
authors.lastname: Tandon
authors.affiliation: Department of Anesthesia and Critical Care, Institute of Liver and Biliary Sciences, New Delhi, India.
authors.forename: C K
authors.initials: CK
authors.lastname: Pandey
keywords: Cirrhosis; dyskeratosis congenita; liver transplant; transplant