title: An unusual presentation of pediatric osteoblastoma in a patient with Klippel-Trenaunay-Weber syndrome: case report.
abstract: Osteoblastoma is an uncommon primary bone tumor that usually presents as a painful lesion in a long bone or in the spine. Osteoblastoma has been reported only twice in the literature in conjunction with systemic fibromatosis. The authors report the case of an 8-year-old girl with suspected Klippel-Trenaunay-Weber syndrome, a rare syndrome of systemic fibromatosis, who presented with a painless thoracic rib lesion that was found to be an osteoblastoma.
authors.affiliation: 1Department of Neurosurgery, Walter Reed National Military Medical Center, Bethesda, Maryland; and.
authors.forename: Scott A
authors.initials: SA
authors.lastname: Wallace
authors.affiliation: 4Surgery, Naval Medical Center San Diego, California.
authors.forename: Romeo C
authors.initials: RC
authors.lastname: Ignacio
authors.affiliation: Departments of 2 Neurosurgery.
authors.forename: Arnett
authors.initials: A
authors.lastname: Klugh
authors.affiliation: 3Pathology, and.
authors.forename: Gregory
authors.initials: G
authors.lastname: Gates
authors.affiliation: 4Surgery, Naval Medical Center San Diego, California.
authors.forename: Marion C W
authors.initials: MC
authors.lastname: Henry
mesh_terms: D001859:Bone Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000601:surgery*; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005350:Fibroma; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008279:Magnetic Resonance Imaging; D018215:Osteoblastoma / Q000150:complications / Q000175:diagnosis* / Q000601:surgery*; D012272:Ribs / Q000473:pathology / Q000601:surgery; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
keywords: KTW = Klippel-Trenaunay-Weber; Klippel-Trenaunay-Weber syndrome; oncology; osteoblastoma; pediatric; rib; spine