title: Extra-hepatic biliary atresia in association with polysplenia and intestinal malrotation.
abstract: The syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in the neonatal period. Inspite of successful Kasai's portoenterostomy at 52nd day of life, the child succumbed to post-operative sepsis.
authors.affiliation: B.J.Medical College, Gujarat University, Ahmedabad, Gujarat, India.
authors.forename: Jaishri
authors.initials: J
authors.lastname: Ramji
authors.affiliation: B.J.Medical College, Gujarat University, Ahmedabad, Gujarat, India.
authors.forename: Rakesh S
authors.initials: RS
authors.lastname: Joshi
authors.affiliation: B.J.Medical College, Gujarat University, Ahmedabad, Gujarat, India.
authors.forename: Mitesh
authors.initials: M
authors.lastname: Bachani
authors.affiliation: B.J.Medical College, Gujarat University, Ahmedabad, Gujarat, India.
authors.forename: Dungarsingh
authors.initials: D
authors.lastname: Rathore
keywords: Extra-hepatic biliary atresia; Intestinal malrotation; Polysplenia