title: Erdheim-Chester Disease: A Case Report.
abstract: BACKGROUND
  The diagnosis of Erdheim-Chester disease, a rare illness, is difficult and requires increased awareness.
  
  
  METHODS
  We report the case of a 56-year-old woman who initially presented with a mesenteric panniculitis and 8 years later developed neurological manifestations and bone lesions that led to a diagnosis of Erdheim-Chester disease.
  
  
  CONCLUSIONS
  The rather characteristic aspect of the bone lesions as well as the presence of foamy cells in involved tissue biopsies should suggest the diagnosis. No therapy is available at present but recent biological data might suggest new approaches for the understanding and therapy of this condition.
authors.affiliation: Department of Radiology, Institut Jules Bordet, Brussels, Belgium.
authors.forename: Jean
authors.initials: J
authors.lastname: Alexiou
authors.affiliation: Department of Oncology, Institut Jules Bordet, Brussels, Belgium.
authors.forename: Jean
authors.initials: J
authors.lastname: Klastersky
mesh_terms: D001706:Biopsy; D003937:Diagnosis, Differential; D031249:Erdheim-Chester Disease / Q000175:diagnosis*; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D014057:Tomography, X-Ray Computed