title: [Infantile segmental hemangioma without facial involvement: A cutaneous marker of vascular malformations such as in PHACE syndrome?].
abstract: BACKGROUND
  Herein we report a case of a possible PHACE syndrome without hemangioma of the head but with a large segmental hemangioma of the trunk.
  
  
  METHODS
  A 17-year-old female patient with a medical history of transposition of the great arteries with ventricular septal defect diagnosed at 3 days of life and of coarctation of the aorta diagnosed at 14 years was seen in the dermatology department for a long-standing large rectangular, segmental, atrophic and telangiectasic lesion on her back. The lesion appeared to be a sequel of infantile segmental hemangioma of the trunk, and this was confirmed by history-taking.
  
  
  CONCLUSIONS
  This case raises the question of a link between infantile segmental hemangioma and underlying cardiovascular disorders. Infantile segmental hemangioma could be a marker of an underlying vascular development defect. The presence of infantile segmental hemangioma, regardless of site, should prompt vascular explorations.
authors.affiliation: Clinique dermatologique, hôpitaux universitaires de Strasbourg, université de Strasbourg, 1, place de l'Hôpital, 67000 Strasbourg, France.
authors.forename: M
authors.initials: M
authors.lastname: Huther
authors.affiliation: Cabinet de cardiologie, 1, rue du Conseil-des-Quinze, 67000 Strasbourg, France.
authors.forename: C
authors.initials: C
authors.lastname: Gronier
authors.affiliation: Clinique dermatologique, hôpitaux universitaires de Strasbourg, université de Strasbourg, 1, place de l'Hôpital, 67000 Strasbourg, France. Electronic address: dlipsker@gmail.com.
authors.forename: D
authors.initials: D
authors.lastname: Lipsker
mesh_terms: D000015:Abnormalities, Multiple / Q000209:etiology*; D000293:Adolescent; D001017:Aortic Coarctation / Q000175:diagnosis; D001415:Back; D003937:Diagnosis, Differential; D005124:Eye Abnormalities / Q000175:diagnosis; D005260:Female; D018324:Hemangioma, Capillary / Q000209:etiology*; D006801:Humans; D020752:Neurocutaneous Syndromes / Q000175:diagnosis; D012878:Skin Neoplasms / Q000209:etiology*; D013577:Syndrome; D013684:Telangiectasis / Q000209:etiology; D014188:Transposition of Great Vessels / Q000209:etiology* / Q000473:pathology
keywords: Hémangiome segmentaire; PHACE; Segmental hemangioma; Tronc; Trunk