title: Desmoplastic small round cell tumor of the kidney with unusual imaging features.
abstract: Desmoplastic small round cell tumor (DSRCT) is a rare, high-grade sarcoma seen in children and young adults. DSRCT of the kidney is extremely uncommon, but has been described in both pediatric and adult populations. Here we present an unusual manifestation of renal DSRCT in a boy whose imaging studies revealed a well-circumscribed mass confined to the urinary collecting system, rather than a large aggressive-appearing mass typically associated with DSRCT, which highlights the varied clinical and imaging features of this disease.
authors.affiliation: Department of Radiology and Imaging Sciences, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: meryle.j.eklund@gmail.com.
authors.forename: Meryle J
authors.initials: MJ
authors.lastname: Eklund
authors.affiliation: Department of Pathology, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: Caitlin.cundiff@gmail.com.
authors.forename: Caitlin
authors.initials: C
authors.lastname: Cundiff
authors.affiliation: Department of Pathology and Pediatrics, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: bshehat@emory.edu.
authors.forename: Bahig M
authors.initials: BM
authors.lastname: Shehata
authors.affiliation: Department of Radiology and Imaging Sciences, Emory University and Children's Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA. Electronic address: Adina.alazraki@choa.org.
authors.forename: Adina L
authors.initials: AL
authors.lastname: Alazraki
mesh_terms: D002648:Child; D058405:Desmoplastic Small Round Cell Tumor / Q000175:diagnosis*; D003937:Diagnosis, Differential; D003952:Diagnostic Imaging / Q000379:methods*; D006801:Humans; D007668:Kidney / Q000000981:diagnostic imaging / Q000473:pathology; D007680:Kidney Neoplasms / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging / Q000379:methods*; D008297:Male; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography
keywords: Desmoplastic small round cell tumor; Pediatric radiology; Renal tumor; t(11;22) (p 13;q 12)