title: Supravalvular aortic stenosis with sudden cardiac death.
abstract: Sudden cardiac death (SCD) most commonly results from previously undiagnosed congenital, acquired, or hereditary cardiac diseases. Congenital aortic valvular, subvalvular, and supravalvular disease with left ventricular outflow tract obstruction is an important preventable cause of sudden death. This report documents sudden death presumably due to acute myocardial ischemia in a young male with an undiagnosed supravalvular aortic stenosis (SVAS) due to a rare association of isolation of coronary sinuses of Valsalva. Congenital supravalvular pulmonary stenosis and mitral valvular dysplasia were also present.
authors.affiliation: Department of Pathology (Cardiovascular and Thoracic Division), Seth Gordhandas Sunderdas Medical College and King Edward Memorial Hospital, Parel, Mumbai, Maharashtra, India.
authors.forename: Pradeep
authors.initials: P
authors.lastname: Vaideeswar
authors.affiliation: Department of Pathology (Cardiovascular and Thoracic Division), Seth Gordhandas Sunderdas Medical College and King Edward Memorial Hospital, Parel, Mumbai, Maharashtra, India.
authors.forename: Preet
authors.initials: P
authors.lastname: Regi
keywords: Congenital aortic stenosis; elastin arteriopathy; sinus of Valsalva isolation; sudden cardiac death; supravalvular aortic stenosis