title: Pure Choriocarcinoma of the Ovary in Silver-Russell Syndrome.
abstract: Pure ovarian choriocarcinoma is an extremely rare malignancy that can be gestational or non-gestational in origin. Silver-Russell syndrome (SRS) is a rare congenital developmental disorder characterized by pre- and postnatal growth failure, relative macrocephaly, a triangular face, hemihypotrophy, and fifth-finger clinodactyly. We report a rare case of pure ovarian choriocarcinoma occurring in a 19-year-old woman with SRS. Following surgery, multiple chemotherapy courses were effective and she was free of disease at the 10-month follow-up.
authors.affiliation: Department of Obstetrics and Gynecology, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama 700-8558, Japan.m_tochan@yahoo.co.jp.
authors.forename: Tomoko
authors.initials: T
authors.lastname: Haruma
authors.forename: Chikako
authors.initials: C
authors.lastname: Ogawa
authors.forename: Takeshi
authors.initials: T
authors.lastname: Nishida
authors.forename: Tomoyuki
authors.initials: T
authors.lastname: Kusumoto
authors.forename: Keiichiro
authors.initials: K
authors.lastname: Nakamura
authors.forename: Noriko
authors.initials: N
authors.lastname: Seki
authors.forename: Takaaki
authors.initials: T
authors.lastname: Katayama
authors.forename: Yuji
authors.initials: Y
authors.lastname: Hiramatsu
mesh_terms: D000328:Adult; D002822:Choriocarcinoma / Q000097:blood / Q000473:pathology* / Q000628:therapy; D018997:Chorionic Gonadotropin, beta Subunit, Human / Q000097:blood; D005260:Female; D006801:Humans; D010051:Ovarian Neoplasms / Q000097:blood / Q000473:pathology* / Q000628:therapy; D011247:Pregnancy; D056730:Silver-Russell Syndrome / Q000473:pathology*
chemical_list: D018997:Chorionic Gonadotropin, beta Subunit, Human