title: Right Aortic Arch Detected Prenatally: A Rare Case With Bilateral Arterial Duct and Nonconfluent Pulmonary Arteries.
abstract: We describe a rare case of right aortic arch (RAA) and nonconfluent pulmonary arteries. RAA and a right-sided arterial duct (AD) were identified on the prenatal scan, but a second left-sided AD and disconnection of the left pulmonary artery were missed. The missed diagnosis in fetal life adversely affected postnatal management. We suggest that fetuses with a prenatal diagnosis of RAA and right-sided AD be delivered in tertiary care centres to rule out an association with bilateral AD and nonconfluent pulmonary arteries after birth. Prompt postnatal diagnosis will enable preservation of flow in the disconnected pulmonary artery through prostaglandin E1 infusion until surgical reconstruction.
authors.affiliation: Division of Pediatric Cardiology, Azienda Ospedaliero-Universitaria Meyer, Florence, Italy.
authors.forename: Silvia
authors.initials: S
authors.lastname: Ricci
authors.affiliation: Division of Pediatric Cardiology, Azienda Ospedaliero-Universitaria Meyer, Florence, Italy; Department of Clinical and Experimental Medicine, Parma University Hospital, Parma, Italy.
authors.forename: Valentina
authors.initials: V
authors.lastname: Fainardi
authors.affiliation: Division of Pediatric Cardiology, Azienda Ospedaliero-Universitaria Meyer, Florence, Italy.
authors.forename: Gaia
authors.initials: G
authors.lastname: Spaziani
authors.affiliation: Division of Pediatric Cardiology, Azienda Ospedaliero-Universitaria Meyer, Florence, Italy.
authors.forename: Silvia
authors.initials: S
authors.lastname: Favilli
authors.affiliation: Division of Pediatric Cardiology, Azienda Ospedaliero-Universitaria Meyer, Florence, Italy. Electronic address: e.chiappa@meyer.it.
authors.forename: Enrico
authors.initials: E
authors.lastname: Chiappa
mesh_terms: D000328:Adult; D000527:Alprostadil / Q000008:administration & dosage; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000000981:diagnostic imaging; D058070:Asymptomatic Diseases; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging*; D006801:Humans; D007261:Infusions, Intra-Arterial; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011859:Radiography; D016216:Ultrasonography, Prenatal; D014665:Vasodilator Agents / Q000008:administration & dosage
chemical_list: D014665:Vasodilator Agents; D000527:Alprostadil