title: Management of a Parturient with Diastrophic Dysplasia.
abstract: A 27-year-old primigravida patient with diastrophic dysplasia (DTD) presented to our obstetrics clinic at 8 weeks' gestational age. Diastrophic dysplasia is a rare, autosomal-recessive abnormality that presents multiple challenges to perinatal anesthetic management, including difficult airway management and relative contraindications to neuraxial anesthesia. The patient underwent elective cesarean delivery at 35 weeks' gestational age under general anesthesia. In this report, we describe our preoperative evaluation and management strategy that involved a multidisciplinary care team.
authors.affiliation: From the *Department of Anesthesiology, †Department of Otolaryngology, and ‡Department of Obstetrics and Gynecology, Dartmouth-Hitchcock Medical Center, Lebanon, New Hampshire; and §Mountain West Anesthesia, Park City, Utah.
authors.forename: Jacqueline S
authors.initials: JS
authors.lastname: Lagoy
authors.forename: Nathaniel D
authors.initials: ND
authors.lastname: Kofford
authors.forename: Benoit J
authors.initials: BJ
authors.lastname: Gosselin
authors.forename: Michelle A
authors.initials: MA
authors.lastname: Russell
authors.forename: Benjamin D
authors.initials: BD
authors.lastname: Morley
mesh_terms: D000328:Adult; D000768:Anesthesia, General; D002585:Cesarean Section / Q000379:methods*; D004392:Dwarfism; D005260:Female; D005865:Gestational Age; D006801:Humans; D007231:Infant, Newborn; D007442:Intubation, Intratracheal / Q000379:methods; D008297:Male; D036801:Parturition; D011247:Pregnancy; D011248:Pregnancy Complications; D012307:Risk Factors