title: A Case of Immunoglobulin G4-Related Disease with Extensive Multiorgan Involvements.
abstract: We report a case of IgG4-related disease (IgG4-RD) with multiple ten-organ involvement. This case showed many clinical findings, such as bilateral swelling of salivary and lacrimal glands, autoimmune pancreatitis, interstitial nephritis, retroperitoneal fibrosis, periaortitis, systemic swelling of lymph nodes, pulmonary lesions, splenomegaly, and jejunal lesions. He was suspected as having SLE or malignant lymphoma but diagnosed as having IgG4-RD by the elevated serum IgG4 level and histological findings from kidney and lymph node. We report a case of IgG4-RD with multiple ten-organ involvement that was successfully treated with prednisolone therapy.
authors.affiliation: Division of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, Japan.
authors.forename: Kazuhiko
authors.initials: K
authors.lastname: Higashioka
authors.affiliation: Division of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, Japan.
authors.forename: Kenji
authors.initials: K
authors.lastname: Yoshida
authors.affiliation: Division of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, Japan.
authors.forename: Kensuke
authors.initials: K
authors.lastname: Oryoji
authors.affiliation: Division of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, Japan.
authors.forename: Kazuo
authors.initials: K
authors.lastname: Kamada
authors.affiliation: Division of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, Japan.
authors.forename: Shinichi
authors.initials: S
authors.lastname: Mizuki
authors.affiliation: Department of Medicine and Biosystemic Science, Graduate School of Medical Sciences, Kyushu University, 3-1-1 Maidashi, Higashi-ku, Fukuoka 812-8582, Japan.
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Tsukamoto
authors.affiliation: Division of Rheumatology, Matsuyama Red Cross Hospital, 1 Bunkyo-tyo, Matsuyama, Ehime 790-0826, Japan.
authors.forename: Eisuke
authors.initials: E
authors.lastname: Yokota
authors.affiliation: Department of Medicine and Biosystemic Science, Graduate School of Medical Sciences, Kyushu University, 3-1-1 Maidashi, Higashi-ku, Fukuoka 812-8582, Japan.
authors.forename: Koichi
authors.initials: K
authors.lastname: Akashi