title: Cerebral vascular findings in PAPA syndrome: cerebral arterial vasculopathy or vasculitis and a posterior cerebral artery dissecting aneurysm.
abstract: A young patient with PAPA (pyogenic arthritis, pyoderma gangrenosum, and acne) syndrome developed an unusual cerebral arterial vasculopathy/vasculitis (CAV) that resulted in subarachnoid hemorrhage from a ruptured dissecting posterior cerebral artery (PCA) aneurysm. This aneurysm was successfully treated by endovascular coil sacrifice of the affected segment of the PCA. The patient made an excellent recovery with no significant residual neurologic deficit.
authors.affiliation: Department of Neurology, Stanford University, Stanford, California, USA.
authors.forename: Kasra
authors.initials: K
authors.lastname: Khatibi
authors.affiliation: Department of Radiology, Stanford University, Stanford, California, USA.
authors.forename: Jeremy J
authors.initials: JJ
authors.lastname: Heit
authors.affiliation: Department of Radiology, Stanford University, Stanford, California, USA.
authors.forename: Nicholas A
authors.initials: NA
authors.lastname: Telischak
authors.affiliation: Department of Neurology, Stanford University, Stanford, California, USA.
authors.forename: Jorina M
authors.initials: JM
authors.lastname: Elbers
authors.affiliation: Departments of Radiology and Neurosurgery, Stanford University, Stanford, California, USA.
authors.forename: Huy M
authors.initials: HM
authors.lastname: Do
mesh_terms: D000152:Acne Vulgaris / Q000000981:diagnostic imaging* / Q000601:surgery; D000784:Aortic Dissection / Q000000981:diagnostic imaging* / Q000601:surgery; D001170:Arthritis, Infectious / Q000000981:diagnostic imaging* / Q000601:surgery; D002533:Cerebral Angiography; D003937:Diagnosis, Differential; D057510:Endovascular Procedures / Q000379:methods; D006801:Humans; D002532:Intracranial Aneurysm / Q000000981:diagnostic imaging* / Q000601:surgery; D018810:Magnetic Resonance Angiography; D055624:Methicillin-Resistant Staphylococcus aureus; D020769:Posterior Cerebral Artery / Q000000981:diagnostic imaging* / Q000601:surgery; D017511:Pyoderma Gangrenosum / Q000000981:diagnostic imaging* / Q000601:surgery; D013203:Staphylococcal Infections / Q000150:complications; D013345:Subarachnoid Hemorrhage / Q000000981:diagnostic imaging / Q000601:surgery; D016896:Treatment Outcome; D020293:Vasculitis, Central Nervous System / Q000000981:diagnostic imaging* / Q000601:surgery
keywords: Aneurysm; Angiography; Brain; Coil; Vasculitis