title: EEG-EMG polygraphic study of dystonia and myoclonus in a case of Creutzfeldt-Jakob disease.
abstract: We report on a patient with sporadic Creutzfeldt-Jakob disease (CJD) who showed dystonia, periodic myoclonus, and periodic sharp wave complexes (PSWCs) on EEG. The EEG-EMG polygraphic study revealed that dystonia appeared without relation to periodic myoclonus and PSWCs and that dystonia EMGs were strongly suppressed after periodic myoclonus EMGs. These findings suggest that dystonia has a pathogenesis different from that of periodic myoclonus and PSWCs, but dystonia and periodic myoclonus may be generated through the sensorimotor cortex in CJD.
authors.affiliation: Department of Neurology, Aizawa Hospital, Matsumoto, Japan.
authors.forename: Takao
authors.initials: T
authors.lastname: Hashimoto
authors.affiliation: Department of Internal Medicine, Tohmi Municipal Hospital, Tohmi, Japan.
authors.forename: Teruaki
authors.initials: T
authors.lastname: Iwahashi
authors.affiliation: Department of Medicine (Neurology and Rheumatology), Shinshu University School of Medicine, Japan.
authors.forename: Wataru
authors.initials: W
authors.lastname: Ishii
authors.affiliation: Department of Neurology, Nagano Municipal Hospital, Nagano, Japan.
authors.forename: Kanji
authors.initials: K
authors.lastname: Yamamoto
authors.affiliation: Department of Medicine (Neurology and Rheumatology), Shinshu University School of Medicine, Japan.
authors.forename: Shu-Ichi
authors.initials: S
authors.lastname: Ikeda
keywords: Creutzfeldt–Jakob disease; Dystonia; Myoclonus; Periodic sharp wave complexes