title: Malignant Triton Tumor of the Kidney. New Location Not Previously Reported.
abstract: Malignant triton tumor (MTT) is a variant of the peripheral nerve sheath tumor. It is very uncommon but shows an aggressive course and limited survival. Half of the cases present symptoms related to neurofibromatosis type 1 disease. There is no standardized treatment, but multimodal approach is the best option. We present the case of a primary MTT located in the kidney, in a 43-year-old woman who received neoadjuvant chemotherapy as first-line treatment followed by surgical resection and adjuvant chemotherapy.
authors.affiliation: Department of Urology, Hospital Universitari i Politècnic La Fe, Valencia, Spain.
authors.forename: Angel
authors.initials: A
authors.lastname: Gallego
authors.forename: Jose Luis
authors.initials: JL
authors.lastname: Pontones
authors.forename: David
authors.initials: D
authors.lastname: Ramos
authors.forename: Francisco
authors.initials: F
authors.lastname: Boronat
mesh_terms: D000328:Adult; D014408:Biomarkers, Tumor / Q000235:genetics; D017024:Chemotherapy, Adjuvant; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000000981:diagnostic imaging / Q000235:genetics / Q000473:pathology* / Q000628:therapy; D020360:Neoadjuvant Therapy; D009392:Nephrectomy; D010524:Peripheral Nervous System Neoplasms / Q000000981:diagnostic imaging / Q000235:genetics / Q000473:pathology* / Q000628:therapy; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
chemical_list: D014408:Biomarkers, Tumor
keywords: Kidney tumor; Malignant triton tumor; Peripheral nerve sheath tumor; Rhabdomyoblastic differentiation