title: Hypoplastic Left Heart Syndrome With Right Ventricle Compression.
abstract: A male neonate presented with the aortic atresia-mitral stenosis (AA-MS) variant of hypoplastic left heart syndrome (HLHS) wherein the suprasystemic left ventricular (LV) pressure and large left ventricle shifted the intraventricular septum. A compressed right ventricle made it difficult to maintain stroke volume. To avoid high right ventricular (RV) volume load and output, we used a 2-stage Norwood-Glenn (NW-G) procedure. Bilateral pulmonary artery banding (bPAB) was performed on day of life (DOL) 4. On DOL 58, we performed percutaneous balloon dilation of the bPAB portion. At age 3 months, the NW-G procedure was performed without peripheral pulmonary hypoplasia. The patient is currently doing well.
authors.affiliation: Department of Pediatric Cardiovascular Surgery, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan. Electronic address: taifuchigami@yahoo.co.jp.
authors.forename: Tai
authors.initials: T
authors.lastname: Fuchigami
authors.affiliation: Department of Pediatric Cardiovascular Surgery, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan.
authors.forename: Masahiko
authors.initials: M
authors.lastname: Nishioka
authors.affiliation: Department of Pediatric Cardiology, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan.
authors.forename: Kazuhiro
authors.initials: K
authors.lastname: Takahashi
authors.affiliation: Department of Pediatric Cardiovascular Surgery, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan.
authors.forename: Toru
authors.initials: T
authors.lastname: Akashige
authors.affiliation: Department of Pediatric Cardiovascular Surgery, Okinawa Prefectural Nanbu Medical Center & Children's Medical Center, Arakawa, Okinawa prefecture, Japan.
authors.forename: Nobuhiro
authors.initials: N
authors.lastname: Nagata
mesh_terms: D006348:Cardiac Surgical Procedures; D006331:Heart Diseases / Q000209:etiology / Q000601:surgery; D006352:Heart Ventricles; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000150:complications* / Q000601:surgery; D007231:Infant, Newborn; D008297:Male; D011312:Pressure