title: Treatment of intraabdominal desmoplastic small round cell tumor with ifosfamide-based chemotherapy.
abstract: Intraabdominal desmoplastic small round cell tumor (IDSRCT) is a rare tumor with poor prognosis that usually develops in the peritoneal cavity, often in childhood and adolescence. This tumor typically arises as single or multiple masses, and is characterized by diffuse peritoneal implants and the involvement of regional lymph nodes. Because most patients are unable to achieve a complete response with chemotherapy alone, extensive efforts have been made to develop more effective chemotherapy regimens. Here, we report on a case of IDSRCT in a 33-year-old man treated with ifosfamide (IFM)-based chemotherapy. Before treatment initiation, the patient had extensive ascites in the peritoneal cavity and was experiencing abdominal fullness and anorexia. Currently, 8 months after his initial presentation, he is still undergoing chemotherapy and is in good general condition.
authors.affiliation: Department of Gastroenterology, Toyohashi Medical Center, Toyohashi, Japan.
authors.forename: Masaki
authors.initials: M
authors.lastname: Ujihara
authors.affiliation: Department of Gastroenterology, Nagoya University Graduate School of Medicine, 65 Tsurumai-cho, Showa-ku, Nagoya, Aichi, 466-8550, Japan. takafumiando-gi@umin.ac.jp.
authors.forename: Takafumi
authors.initials: T
authors.lastname: Ando
authors.affiliation: Department of Gastroenterology, Nagoya University Graduate School of Medicine, 65 Tsurumai-cho, Showa-ku, Nagoya, Aichi, 466-8550, Japan.
authors.forename: Osamu
authors.initials: O
authors.lastname: Watanabe
authors.affiliation: Department of Surgery, Toyohashi Medical Center, Toyohashi, Japan.
authors.forename: Takahiro
authors.initials: T
authors.lastname: Asada
authors.affiliation: Department of Surgery, Toyohashi Medical Center, Toyohashi, Japan.
authors.forename: Katsuya
authors.initials: K
authors.lastname: Yamashita
authors.affiliation: Department of Surgery, Toyohashi Medical Center, Toyohashi, Japan.
authors.forename: Toru
authors.initials: T
authors.lastname: Ichihara
authors.affiliation: Department of Pathology, Toyohashi Medical Center, Toyohashi, Japan.
authors.forename: Etsuko
authors.initials: E
authors.lastname: Nakamura
authors.affiliation: Department of Gastroenterology, Nagoya University Graduate School of Medicine, 65 Tsurumai-cho, Showa-ku, Nagoya, Aichi, 466-8550, Japan.
authors.forename: Hidemi
authors.initials: H
authors.lastname: Goto
keywords: Chemotherapy; Ifosfamide; Intraabdominal desmoplastic small round cell tumor