title: Ductal stent implantation in tetralogy of fallot with aortic arch abnormality.
abstract: Stenting of patent ductus arteriosus is an alternative to palliative cardiac surgery in newborns with duct-dependent or decreased pulmonary circulation; however, the use of this technique in patients with an aortic arch abnormality presents a challenge. Tetralogy of Fallot is a congenital heart defect that is frequently associated with anomalies of the aortic arch and its branches. The association is even more common in patients with chromosome 22q11 deletion. We present the case of an 18-day-old male infant who had cyanosis and a heart murmur. After an initial echocardiographic evaluation, the patient was diagnosed with tetralogy of Fallot and right-sided aortic arch. The pulmonary annulus and the main pulmonary artery and its branches were slightly hypoplastic; the ductus arteriosus was small. Conventional and computed tomographic angiograms revealed a double aortic arch and an aberrant left subclavian artery. The right aortic arch branched into the subclavian arteries and continued into the descending aorta, whereas the left aortic arch branched into the common carotid arteries and ended with the patent ductus arteriosus. After evaluation of the ductal anatomy, we implanted a 3.5 × 15-mm coronary stent in the duct. Follow-up injections showed augmented pulmonary flow and an increase in oxygen saturation from 65% to 94%. The patient was also found to have chromosome 22q11 deletion.
authors.forename: Hasan Tahsin
authors.initials: HT
authors.lastname: Tola
authors.forename: Yakup
authors.initials: Y
authors.lastname: Ergul
authors.forename: Murat
authors.initials: M
authors.lastname: Saygi
authors.forename: Isa
authors.initials: I
authors.lastname: Ozyilmaz
authors.forename: Alper
authors.initials: A
authors.lastname: Guzeltas
authors.forename: Ender
authors.initials: E
authors.lastname: Odemis
mesh_terms: D058165:22q11 Deletion Syndrome / Q000150:complications; D001013:Aorta, Thoracic / Q000002:abnormalities*; D006348:Cardiac Surgical Procedures; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D015607:Stents; D013771:Tetralogy of Fallot / Q000150:complications / Q000601:surgery*
keywords: 22q11 deletion syndrome, infant; Chromosome deletion; chromosomes, human, pair 22; ductal stenting; ductus arteriosus, patent/therapy; infant; stents; tetralogy of Fallot