title: Unicuspid unicommissural aortic valve: an extremely rare congenital anomaly.
abstract: Unicuspid aortic valve is a rare congenital malformation that usually presents in the 3rd to 5th decade of life-and usually with severe aortic stenosis or regurgitation. It often requires surgical correction. Diagnosis can be made with 2- or 3-dimensional transthoracic or transesophageal echocardiography, cardiac computed tomography, or cardiac magnetic resonance imaging. We report the case of a 31-year-old man who presented with dyspnea on exertion due to severe aortic stenosis secondary to a unicuspid unicommissural aortic valve. After aortic valve replacement, this patient experienced complete heart block that required the placement of a permanent pacemaker.
authors.forename: Sukhjeet
authors.initials: S
authors.lastname: Singh
authors.forename: Puneet
authors.initials: P
authors.lastname: Ghayal
authors.forename: Atish
authors.initials: A
authors.lastname: Mathur
authors.forename: Margaret
authors.initials: M
authors.lastname: Mysliwiec
authors.forename: Constantinos
authors.initials: C
authors.lastname: Lovoulos
authors.forename: Pallavi
authors.initials: P
authors.lastname: Solanki
authors.forename: Marc
authors.initials: M
authors.lastname: Klapholz
authors.forename: James
authors.initials: J
authors.lastname: Maher
mesh_terms: D000328:Adult; D001021:Aortic Valve / Q000002:abnormalities* / Q000601:surgery; D001024:Aortic Valve Stenosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D008297:Male
keywords: Aortic valve/abnormalities/ultrasonography/unicuspid unicommissural; aortic valve stenosis/congenital/etiology; complete heart block; heart defects, congenital/surgery/ultrasonography; pacemaker, permanent; unicuspid aortic valve