title: An unusual presentation of extranodal Rosai-Dorfman disease threatening the airway.
abstract: Rosai-Dorfman disease (RDD) is a rare benign systemic histiocytic proliferation, characterized by massive lymph node enlargement and sometimes associated with extranodal involvement. Even though it is considered as a benign disease, fatalities can occur due to its unusually large size and its location. Our case highlighting a primary extranodal site of vallecula, which is extremely rare and not reported in literature before. It presented with almost complete obstructing the oropharyngeal airway creating a life threatening situation, needed emergency tracheostomy.
authors.affiliation: Department of Otorhinolaryngology, IMS and SUM Hospital, Siksha "O" Anusandhan University, K8, Kalinganagar, Bhubaneswar 751003, Odisha, India. Electronic address: santoshvoltaire@yahoo.co.in.
authors.forename: Santosh K
authors.initials: SK
authors.lastname: Swain
authors.affiliation: Department of Otorhinolaryngology, IMS and SUM Hospital, Siksha "O" Anusandhan University, K8, Kalinganagar, Bhubaneswar 751003, Odisha, India.
authors.forename: Alok
authors.initials: A
authors.lastname: Das
authors.affiliation: Department of Anesthesia, IMS and SUM Hospital, Siksha "O" Anusandhan University, K8, Kalinganagar, Bhubaneswar 751003, Odisha, India.
authors.forename: Sangeeta
authors.initials: S
authors.lastname: Sahoo
authors.affiliation: Department of Pathology, Apollo Hospital, Bhubaneswar, Odisha, India.
authors.forename: Manas R
authors.initials: MR
authors.lastname: Baisakh
authors.affiliation: Central Research Laboratory, IMS and SUM Hospital, Siksha "O" Anusandhan University, K8, Kalinganagar, Bhubaneswar 751003, Odisha, India.
authors.forename: Mahesh C
authors.initials: MC
authors.lastname: Sahu
mesh_terms: D000328:Adult; D000402:Airway Obstruction / Q000000981:diagnostic imaging* / Q000209:etiology / Q000601:surgery; D015618:Histiocytosis, Sinus / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D006801:Humans; D007828:Laryngoscopy; D008297:Male; D014057:Tomography, X-Ray Computed; D014139:Tracheostomy
keywords: Extranodal involvement; Rosai–Dorfman disease; Sinus histiocytosis; Vallecula