title: Primary Ewing Sarcoma Presenting as a Vulvar Mass in an Adolescent: Case Report and Review of Literature.
abstract: BACKGROUND
  Extraosseous Ewing sarcoma (ES) tumors presenting in the genitourinary tract are highly uncommon. Few cases of primary vulvar and vaginal cases of ES have been published.
  
  
  METHODS
  A 15-year-old adolescent presented with a bothersome 5-cm mass located on her left labium minorum. Following excision, a diagnosis of a primary ES was made. The patient was treated with multiagent chemotherapy and was doing well 20 months after treatment completion.
  
  
  CONCLUSIONS
  Based on the few available case reports and our reported case, it appears that extraosseous ES arising in superficial sites such as the vulva have better prognosis and should be treated with complete excision and multiagent chemotherapy.
authors.affiliation: Cleveland Clinic, Obstetrics and Gynecology, Division of Female Pelvic Medicine and Reconstructive Surgery, Hartford, Connecticut. Electronic address: lena0605@gmail.com.
authors.forename: Elena
authors.initials: E
authors.lastname: Tunitsky-Bitton
authors.affiliation: Cleveland Clinic, Obstetrics and Gynecology, Division of Benign Gynecology, Hartford, Connecticut.
authors.forename: M Jean S
authors.initials: MJ
authors.lastname: Uy-Kroh
authors.affiliation: Cleveland Clinic, Obstetrics and Gynecology, Division of Gynecologic Oncology, Hartford, Connecticut.
authors.forename: Chad
authors.initials: C
authors.lastname: Michener
authors.affiliation: Cleveland Clinic, Obstetrics and Gynecology, Division of Female Pelvic Medicine and Reconstructive Surgery, Hartford, Connecticut.
authors.forename: Megan E
authors.initials: ME
authors.lastname: Tarr
mesh_terms: D000293:Adolescent; D004358:Drug Therapy; D005260:Female; D006801:Humans; D011379:Prognosis; D012512:Sarcoma, Ewing / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery; D014846:Vulvar Neoplasms / Q000175:diagnosis* / Q000188:drug therapy / Q000601:surgery
keywords: Extraosseous Ewing sarcoma; Neuroectodermal tumor; PNET; Vulvar mass