title: Scleroderma Renal Crisis.
abstract: Scleroderma renal crisis is a rare complication of systemic sclerosis (SSc) that remains severe. Prompt recognition and initiation of therapy with an angiotensin-converting-enzyme inhibitor offer the best chance to achieve a good outcome. SSc prevalence is poorly known, with disparities among countries.
authors.affiliation: Department of Internal Medicine, Centre de Référence Maladies Systémiques et Auto-Immunes Rares, Hôpital Cochin, Assistance Publique-Hôpitaux de Paris, Université Paris Descartes, Paris, France. Electronic address: loic.guillevin@cch.aphp.fr.
authors.forename: Loïc
authors.initials: L
authors.lastname: Guillevin
authors.affiliation: Department of Internal Medicine, Centre de Référence Maladies Systémiques et Auto-Immunes Rares, Hôpital Cochin, Assistance Publique-Hôpitaux de Paris, Université Paris Descartes, Paris, France.
authors.forename: Luc
authors.initials: L
authors.lastname: Mouthon
mesh_terms: D000806:Angiotensin-Converting Enzyme Inhibitors / Q000627:therapeutic use; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011247:Pregnancy; D011248:Pregnancy Complications; D051437:Renal Insufficiency / Q000209:etiology* / Q000628:therapy; D012595:Scleroderma, Systemic / Q000150:complications* / Q000473:pathology
chemical_list: D000806:Angiotensin-Converting Enzyme Inhibitors
keywords: Acute renal failure; Angiotensin-converting-enzyme inhibitors; Arterial hypertension; Scleroderma renal crisis; Systemic sclerosis