title: Desmoid Tumor of the Pancreas: Case Report and Review of a Rare Entity.
abstract: Desmoid tumors, also known as desmoid-type fibromatoses or aggressive fibromatoses, are clonal fibroblastic proliferations that arise in the deep soft tissues. They are characterized by infiltrative growth, a tendency toward local recurrence and the inability to metastasize. We present a case of a 63-year-old woman who complained of abdominal pain, and a contrast-enhanced computed tomography scan revealed a well-circumscribed tumor in the pancreatic tail, measuring 5.1 cm. A left-sided, spleen-preserving pancreatic resection was performed, and pathological analysis showed a mesenchymal tumor. The diagnosis of a pancreatic desmoid tumor was made based on the characteristic morphology and the immune phenotype of the tumor. The English-language literature on pancreatic desmoid tumors was reviewed. In total, 16 previous cases were identified.
authors.affiliation: Department of Pathology, Odense University Hospital, Odense, Denmark.
authors.forename: Roxana
authors.initials: R
authors.lastname: Gerleman
authors.affiliation: HPB Section, Department of Surgery, Odense University Hospital, Odense, Denmark.
authors.forename: Michael Bau
authors.initials: MB
authors.lastname: Mortensen
authors.affiliation: Department of Pathology, Odense University Hospital, Odense, Denmark Sonke.Detlefsen@rsyd.dk.
authors.forename: Sönke
authors.initials: S
authors.lastname: Detlefsen
mesh_terms: D014408:Biomarkers, Tumor / Q000378:metabolism; D005260:Female; D018222:Desmoid Tumors / Q000378:metabolism / Q000473:pathology*; D006801:Humans; D008875:Middle Aged; D010179:Pancreas / Q000378:metabolism / Q000473:pathology*; D010190:Pancreatic Neoplasms / Q000378:metabolism / Q000473:pathology*
chemical_list: D014408:Biomarkers, Tumor
keywords: abdominal discomfort; deep fibromatosis; desmoid tumor; pancreas; pathology