title: Congenital portosystemic shunts with and without gastrointestinal bleeding - case series.
abstract: BACKGROUND
  The clinical presentation of congenital portosystemic shunt is variable and gastrointestinal bleeding is an uncommon presentation.
  
  
  OBJECTIVE
  To describe the imaging features of congenital portosystemic shunt as it presented in 11 children with (n = 6) and without gastrointestinal bleeding (n = 5).
  
  
  METHODS
  We performed a retrospective study on a clinical and imaging dataset of 11 children diagnosed with congenital portosystemic shunt.
  
  
  RESULTS
  A total of 11 children with congenital portosystemic shunt were included in this study, 7 with extrahepatic portosystemic shunts and 4 with intrahepatic portosystemic shunts. Six patients with gastrointestinal bleeding had an extrahepatic portosystemic shunt, and the imaging results showed that the shunts originated from the splenomesenteric junction (n = 5) or splenic vein (n = 1) and connected to the internal iliac vein. Among the five cases of congenital portosystemic shunt without gastrointestinal bleeding, one case was an extrahepatic portosystemic shunt and the other four were intrahepatic portosystemic shunts.
  
  
  CONCLUSIONS
  Most congenital portosystemic shunt patients with gastrointestinal bleeding had a shunt that drained portal blood into the iliac vein via an inferior mesenteric vein. This type of shunt was uncommon, but the concomitant rate of gastrointestinal bleeding with this type of shunt was high.
authors.affiliation: Department of Radiology, Children's Hospital of Fudan University, 399 Wanyuan Road, Minhang District, Shanghai, 201102, China.
authors.forename: Ying
authors.initials: Y
authors.lastname: Gong
authors.affiliation: Department of Radiology, Fudan University Shanghai Cancer Center, Shanghai, 200032, the People's Republic of China.
authors.forename: Hui
authors.initials: H
authors.lastname: Zhu
authors.affiliation: Department of Radiology, Children's Hospital of Fudan University, 399 Wanyuan Road, Minhang District, Shanghai, 201102, China.
authors.forename: Jun
authors.initials: J
authors.lastname: Chen
authors.affiliation: Department of Radiology, Children's Hospital of Fudan University, 399 Wanyuan Road, Minhang District, Shanghai, 201102, China.
authors.forename: Qi
authors.initials: Q
authors.lastname: Chen
authors.affiliation: Department of Radiology, Children's Hospital of Fudan University, 399 Wanyuan Road, Minhang District, Shanghai, 201102, China.
authors.forename: Min
authors.initials: M
authors.lastname: Ji
authors.affiliation: Department of Radiology, Children's Hospital of Fudan University, 399 Wanyuan Road, Minhang District, Shanghai, 201102, China.
authors.forename: Mier
authors.initials: M
authors.lastname: Pa
authors.affiliation: Department of Surgery, Children's Hospital of Fudan University, Shanghai, 200032, the People's Republic of China.
authors.forename: Shan
authors.initials: S
authors.lastname: Zheng
authors.affiliation: Department of Radiology, Children's Hospital of Fudan University, 399 Wanyuan Road, Minhang District, Shanghai, 201102, China. zqiao@fudan.edu.cn.
authors.forename: Zhongwei
authors.initials: Z
authors.lastname: Qiao
mesh_terms: D000792:Angiography; D002648:Child; D002675:Child, Preschool; D003113:Colonoscopy; D003287:Contrast Media; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000000981:diagnostic imaging* / Q000209:etiology*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D007472:Iohexol; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D012189:Retrospective Studies; D014057:Tomography, X-Ray Computed; D016157:Vascular Fistula / Q000151:congenital* / Q000000981:diagnostic imaging*
chemical_list: D003287:Contrast Media; D007472:Iohexol
keywords: Abernethy malformation; Child; Computed tomography angiography; Congenital portosystemic shunt; Congenital vascular disease; Magnetic resonance angiography