title: A case of cephalomelia discovered in a baby born in Niger.
abstract: BACKGROUND
  Subcutaneous tumors with extra limbs are very rare, and they are considered either as fetus in fetu or fetiform teratoma.
  
  
  METHODS
  We report here the case of a 6-day-old presenting a mass extending at the level of the occipital bone. This mass is developed in the extracranial region and contains two forelimbs including hands with digits. CT shows that the squamous part of the occipital bone is involved with several defects through which a part of the cerebellum herniates. The boy was operated on and the tumor was removed. The herniated region of the cerebellum has also been removed. After surgery, the boy develops normally.
  
  
  CONCLUSIONS
  This type of tumor is extremely rare and is only the second case that has been reported at this exact location. This could be the so-called céphalomélie described by Isidore Geoffroy Saint-Hilaire in a duck in his famous Treatise of Teratology (1836). The cause of this malformation is still a matter for debate.
authors.affiliation: Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger. akelani2@yahoo.fr.|Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger. akelani2@yahoo.fr.
authors.forename: A Bariath
authors.initials: AB
authors.lastname: Kelani
authors.affiliation: Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger.|Département d'Histologie et Embryologie, UAM, Niamey, Niger.
authors.forename: H
authors.initials: H
authors.lastname: Moumouni
authors.affiliation: Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger.|Service de Chirurgie Générale, Hôpital National de Niamey, Niamey, Niger.
authors.forename: H
authors.initials: H
authors.lastname: Younsa
authors.affiliation: Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger.|Service de Chirurgie Générale, Hôpital National de Niamey, Niamey, Niger.
authors.forename: L
authors.initials: L
authors.lastname: James Didier
authors.affiliation: Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger.
authors.forename: A M
authors.initials: AM
authors.lastname: Hima
authors.affiliation: Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger.
authors.forename: A
authors.initials: A
authors.lastname: Guemou
authors.affiliation: Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger.
authors.forename: A W
authors.initials: AW
authors.lastname: Issa
authors.affiliation: Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger.
authors.forename: A
authors.initials: A
authors.lastname: Ibrahim
authors.affiliation: Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger.
authors.forename: M A
authors.initials: MA
authors.lastname: Sanda
authors.affiliation: Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger.|Service de Chirurgie Générale, Hôpital National de Niamey, Niamey, Niger.
authors.forename: R
authors.initials: R
authors.lastname: Sani
authors.affiliation: Service de Neurochirurgie, Hôpital National de Niamey, Niamey, Niger.|Faculté des Sciences de la Santé, Service de Neurochirurgie, Hôpital National de Niamey (HNN), Université Abdou Moumouni (UAM), BP 12932, Niamey, Niger.
authors.forename: S
authors.initials: S
authors.lastname: Sanoussi
authors.affiliation: Sorbonne Université, UPMC Université Paris 06, UMR7622, F-75005, Paris, France.|Institut de Biologie Paris Seine (IBPS) - Developmental Biology Laboratory, UMR7622, CNRS, F-75005, Paris, France.|INSERM, ERL1156, F-75005, Paris, France.|Fédération de Neurologie, Groupe hospitalier Pitié-Salpêtrière-APHP, F-75013, Paris, France.
authors.forename: M
authors.initials: M
authors.lastname: Catala
mesh_terms: D005315:Fetal Diseases / Q000473:pathology*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D009548:Niger; D009778:Occipital Lobe / Q000002:abnormalities* / Q000473:pathology* / Q000601:surgery
keywords: Cephaloceles; Cephalomelia; Niger