title: Challenges in IPF diagnosis, current management and future perspectives: Patient case 1.
abstract: PATIENT PRESENTATION AND DIAGNOSIS: A 78-year-old female was referred to our department in April 2011 with shortness of breath. Clinical examination revealed bilateral limited crackles but no signs of finger clubbing. Lung function evaluation showed a percent predicted FVC of 78 and DLco of 67. The patient underwent HRCT imaging which showed cardinal features of a UIP pattern enabling a rapid diagnosis of IPF without the need for surgical lung biopsy.
authors.affiliation: Department of Respiratory Medicine, Mater Misericordiea University Hospital, Dublin, Ireland. redazione@mattioli1885.com.
authors.forename: Jim
authors.initials: J
authors.lastname: Egan
mesh_terms: D000368:Aged; D004417:Dyspnea / Q000175:diagnosis / Q000209:etiology; D042241:Early Diagnosis; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D054990:Idiopathic Pulmonary Fibrosis / Q000175:diagnosis / Q000000981:diagnostic imaging* / Q000188:drug therapy*; D011728:Pyridones / Q000008:administration & dosage*; D012129:Respiratory Function Tests; D018570:Risk Assessment; D013997:Time Factors; D014057:Tomography, X-Ray Computed / Q000379:methods*; D016896:Treatment Outcome
chemical_list: D011728:Pyridones; C093844:pirfenidone