title: Posterior reversible encephalopathy syndrome as an initial neurological manifestation of primary Sjögren's syndrome.
abstract: It is well known that patients with peripheral neuropathy along with autonomic involvement can also exhibit autonomic hyperactivity. There are rare cases in which these patients developed posterior reversible encephalopathy syndrome (PRES). Patients with primary Sjögren's syndrome (pSS) may be more likely to exhibit autonomic hypofunction rather than autonomic hyperfunction, which is a rare event. In the present work, we report the first known case of PRES as an initial neurological manifestation of pSS.
authors.affiliation: Department of Neurology, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, 29 Saemunan-ro, Jongno-gu, Seoul, 110-746, Republic of Korea.
authors.forename: Ha-Neul
authors.initials: HN
authors.lastname: Jeong
authors.affiliation: Department of Neurology, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, 29 Saemunan-ro, Jongno-gu, Seoul, 110-746, Republic of Korea. bcsuh@skku.edu.
authors.forename: Bum Chun
authors.initials: BC
authors.lastname: Suh
authors.affiliation: Department of Neurology, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, 29 Saemunan-ro, Jongno-gu, Seoul, 110-746, Republic of Korea.
authors.forename: Yong Bum
authors.initials: YB
authors.lastname: Kim
authors.affiliation: Department of Neurology, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, 29 Saemunan-ro, Jongno-gu, Seoul, 110-746, Republic of Korea.
authors.forename: Pil-Wook
authors.initials: PW
authors.lastname: Chung
authors.affiliation: Department of Neurology, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, 29 Saemunan-ro, Jongno-gu, Seoul, 110-746, Republic of Korea.
authors.forename: Heui-Soo
authors.initials: HS
authors.lastname: Moon
authors.affiliation: Department of Neurology, Kangbuk Samsung Hospital, Sungkyunkwan University School of Medicine, 29 Saemunan-ro, Jongno-gu, Seoul, 110-746, Republic of Korea.
authors.forename: Won Tae
authors.initials: WT
authors.lastname: Yoon
mesh_terms: D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D054038:Posterior Leukoencephalopathy Syndrome / Q000150:complications* / Q000175:diagnosis*; D012859:Sjogren's Syndrome / Q000150:complications* / Q000175:diagnosis*
keywords: Autonomic hyperactivity; Posterior reversible encephalopathy syndrome (PRES); Primary Sjögren’s syndrome (pSS)