title: A rare combination: congenital factor VII deficiency with Chiari malformation.
abstract: Congenital factor (VII) deficiency is a rare bleeding disorder. We present a patient with congenital FVII deficiency and congenital hydrocephalus who underwent a ventriculoperitoneal shunt operation and needed no prophylaxis after the procedure.
authors.affiliation: aDepartment of Pediatrics, Division of Pediatric Hematology bDepartment of Pediatrics cDepartment of Neurosurgery, Gaziantep University, Gaziantep, Turkey.
authors.forename: Ali
authors.initials: A
authors.lastname: Bay
authors.forename: Elif
authors.initials: E
authors.lastname: Aktekin
authors.forename: Ibrahim
authors.initials: I
authors.lastname: Erkutlu
mesh_terms: D001139:Arnold-Chiari Malformation / Q000150:complications / Q000188:drug therapy* / Q000473:pathology / Q000601:surgery; D001780:Blood Coagulation Tests; D005168:Factor VII Deficiency / Q000150:complications / Q000151:congenital / Q000188:drug therapy* / Q000601:surgery; D015942:Factor VIIa / Q000627:therapeutic use*; D006801:Humans; D006849:Hydrocephalus / Q000150:complications / Q000188:drug therapy* / Q000473:pathology / Q000601:surgery; D007231:Infant, Newborn; D008297:Male; D035583:Rare Diseases; D011994:Recombinant Proteins / Q000627:therapeutic use; D016896:Treatment Outcome; D017287:Ventriculoperitoneal Shunt
chemical_list: D011994:Recombinant Proteins; C103587:recombinant FVIIa; D015942:Factor VIIa