title: Rare Presentation of Supratentorial Primitive Neuroectodermal Tumors Mimicking Bifocal Germ Cell Tumors: 2 Case Reports.
abstract: Bifocal pineal and suprasellar tumors have only been described in the context of germ cell tumors in the pediatric age group. We report 2 patients with radiologic findings of bifocal pineal and suprasellar lesions, with a histologic diagnosis of supratentorial primitive neuroectodermal tumor. The absence of diabetes insipidus and other endocrine abnormalities was noteworthy in both cases. This observation challenges previous reports on the pathognomonic value of this clinico-radiologic entity.
authors.affiliation: *Department of Pediatrics, Division of Hematology/Oncology, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok, Thailand Divisions of †Haematology/Oncology §Pathology, The Hospital for Sick Children, University of Toronto, Toronto, ON ‡Department of Haematology/Oncology, CHU de Quebec, QC, Canada.
authors.forename: Kamon
authors.initials: K
authors.lastname: Phuakpet
authors.forename: Valerie
authors.initials: V
authors.lastname: Larouche
authors.forename: Cynthia
authors.initials: C
authors.lastname: Hawkins
authors.forename: Annie
authors.initials: A
authors.lastname: Huang
authors.forename: Uri
authors.initials: U
authors.lastname: Tabori
authors.forename: Ute K
authors.initials: UK
authors.lastname: Bartels
authors.forename: Eric
authors.initials: E
authors.lastname: Bouffet
mesh_terms: D000293:Adolescent; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008297:Male; D009373:Neoplasms, Germ Cell and Embryonal / Q000473:pathology; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D018242:Neuroectodermal Tumors, Primitive / Q000473:pathology*; D010870:Pineal Gland / Q000473:pathology; D015173:Supratentorial Neoplasms / Q000473:pathology*