title: Congenital Pulmonary Airway Malformation in an Adult Male: A Case Report with Literature Review.
abstract: Congenital pulmonary airway malformation (CPAM) is a rare cystic lung lesion formed as a result of anomalous development of airways in fetal life. Majority of the cases are recognized in neonates and infants with respiratory distress with very few presenting later in adult life. A 24-year-old male with history of three separate episodes of pneumonia in the last 6 months presented with left sided pleuritic chest pain for 4 days. He was tachycardic and tachypneic at presentation. White blood count was 14 × 10(9)/L. Chest X-ray showed left lower lobe opacity. CT angiogram of thorax showed a well-defined area of low attenuation in the left lower lobe with dedicated pulmonary arterial and venous drainage and resolving infection, suggesting CPAM. He underwent left lower lobe lobectomy. Histopathology confirmed type 2 CPAM. CPAM is a rare congenital anatomic abnormality that can present with recurrent infections in adults. As a number of cases remain asymptomatic and symptomatic cases are often missed, prevalence of CPAM might be higher than currently reported.
authors.affiliation: SUNY Upstate Medical University, East Adams Street, Syracuse, NY 13210, USA.
authors.forename: Dipti
authors.initials: D
authors.lastname: Baral
authors.affiliation: College of Medical Sciences, Bharatpur 44207, Nepal.
authors.forename: Bindu
authors.initials: B
authors.lastname: Adhikari
authors.affiliation: SUNY Upstate Medical University, East Adams Street, Syracuse, NY 13210, USA.
authors.forename: Daniel
authors.initials: D
authors.lastname: Zaccarini
authors.affiliation: College of Medical Sciences, Bharatpur 44207, Nepal.
authors.forename: Raj Man
authors.initials: RM
authors.lastname: Dongol
authors.affiliation: SUNY Upstate Medical University, East Adams Street, Syracuse, NY 13210, USA.
authors.forename: Birendra
authors.initials: B
authors.lastname: Sah