Propranolol-responsive cranial nerve palsies in a patient with PHACES syndrome.
PHACES syndrome is a neurocutaneous disorder characterized by the presence of segmental hemangiomas with associated anomalies of the posterior fossa, cerebral vasculature, cardiovascular system, eyes, and ventral or midline structures. We present the first case of propranolol-responsive congenital trigeminal and facial nerve palsies secondary to an intracranial hemangioma in a patient with PHACES syndrome.
Department of Otolaryngology - Head and Neck Surgery, Oregon Health & Science University, 3181 SW Sam Jackson Park Road, PV01, Portland, OR 97239, USA. Electronic address: elrassie@ohsu.edu.
Edward
E
El Rassi
Department of Otolaryngology - Head and Neck Surgery, Oregon Health & Science University, 3181 SW Sam Jackson Park Road, PV01, Portland, OR 97239, USA.
Carol J
CJ
MacArthur
D001017:Aortic Coarctation / Q000150:complications*; D020330:Bell Palsy / Q000151:congenital / Q000188:drug therapy* / Q000209:etiology; D005124:Eye Abnormalities / Q000150:complications*; D006391:Hemangioma / Q000150:complications / Q000188:drug therapy*; D006801:Humans; D007223:Infant; D020752:Neurocutaneous Syndromes / Q000150:complications*; D011433:Propranolol / Q000627:therapeutic use*; D020433:Trigeminal Nerve Diseases / Q000151:congenital / Q000188:drug therapy* / Q000209:etiology; D014665:Vasodilator Agents / Q000627:therapeutic use*
D014665:Vasodilator Agents; D011433:Propranolol
Cranial nerve palsy; Hemangioma; PHACES syndrome; Propranolol; Vascular anomaly