PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review.
PEComas are a group of very rare mesenchymal neoplasms, which express myogenic and melanocytic markers, such as HMB-45 and actin. Situs inversus totalis represents a complete left to right side transposition of the asymmetrical thoracic and abdominal organs and incorporates dextrocardia. The presence of uterus PEComa in the setting of situs inversus totalis is extremely rare. Here, we report a case of PEComa of uterus with coexistence of situs inversus totalis and review the literatures. To the best of our knowledge this is the fist report of a uterus PEComa patient with situs inversus totalis.
Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. 1113430367@qq.com.
Yang
Y
Han
Department of General Surgery, The First Affiliated Hospital of China Medical University, Shenyang, China. 469883299@qq.com.
Ting-ting
TT
Liu
Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. qiuxueshan_1963001@hotmail.com.
Xue-shan
XS
Qiu
Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. liqingchang19720303@cmu.edu.cn.
Qing-chang
QC
Li
Department of Obstetrics and Gynecology, The First Affiliated Hospital of China Medical University, Shenyang, China. zhaoyi19791011@hotmail.com.
Yi
Y
Zhao
Department of Obstetrics and Gynecology, The First Affiliated Hospital of China Medical University, Shenyang, China. pangxy19830301@hotmail.com.
Xiao-Yan
XY
Pang
Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. wangenhua@hotmail.com.
En-hua
EH
Wang
D000328:Adult; D014408:Biomarkers, Tumor / Q000032:analysis; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D054973:Perivascular Epithelioid Cell Neoplasms / Q000150:complications* / Q000473:pathology*; D012857:Situs Inversus / Q000150:complications*; D014594:Uterine Neoplasms / Q000150:complications* / Q000473:pathology*
D014408:Biomarkers, Tumor