Frontal Encephalocele Associated With a Bilateral Tessier Number Three Cleft and Fraser Syndrome.
Oblique craniofacial clefts and encephaloceles are each rare conditions, and only a few instances of these findings in combination have been described. Each pathologic entity presents a unique reconstructive challenge. The authors report the case of a male infant who presented with a large right frontoencephalocele and bilateral Tessier number 3 clefts. A review of the pertinent literature, including specific considerations related to perioperative management and technical aspects of the surgical approach, is discussed.
*Division of Plastic Surgery †Division of Neurosurgery, Children's National Medical Center, Washington, DC.
Benjamin C
BC
Wood
Sojung
S
Yi
Albert K
AK
Oh
Gary F
GF
Rogers
Suresh N
SN
Magge
D003937:Diagnosis, Differential; D004210:Dissection / Q000379:methods; D004598:Electrosurgery / Q000379:methods; D004677:Encephalocele / Q000175:diagnosis* / Q000601:surgery; D058497:Fraser Syndrome / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008026:Ligation / Q000379:methods; D008297:Male; D013396:Suction / Q000379:methods; D014057:Tomography, X-Ray Computed / Q000379:methods