Cranioplasty Using a Modified Split Calvarial Graft Technique in Cleidocranial Dysplasia.
Cleidocranial dysplasia is a well-documented rare autosomal dominant skeletal dysplasia characterized by hypoplastic/aplastic clavicles, brachycephalic skull, patent sutures and fontanelles, midface hypoplasia, and abnormalities of dentition. Patients with cleidocranial dysplasia often complain about undesirable esthetic appearance of their forehead and skull. Notwithstanding many studies of molecular, genetics and skeletal abnormalities of this congenial disorder, there have been very few written reports of cranioplasty involving cleidocranial dysplasia. Thus, we report a rare case of successful cranioplasty using a modified split calvarial graft technique in patient with cleidocranial dysplasia.
Department of Neurosurgery, Cheju Halla Hospital, Jeju, Korea.
Young Taek
YT
Jung
Department of Neurosurgery, Cheju Halla Hospital, Jeju, Korea.
Jae Ik
JI
Cho
Department of Neurosurgery, Cheju Halla Hospital, Jeju, Korea.
Sang Pyung
SP
Lee
Cleidocranial dysplasia; Congenital calvarial defect; Cranioplasty; Split calvarial graft