Valve Sparing Aortic Root Replacement in Children with Loeys-Dietz Syndrome.
Loeys-Dietz syndrome (LDS) is an autosomal dominant connective tissue disorder that is characterized by aggressive arterial and aortic disease, often involving the formation of aortic aneurysms. We describe the cases of two children with LDS who were diagnosed with aortic root aneurysms and successfully treated by valve-sparing aortic root replacement (VSRR) with a Valsalva graft. VSRR is a safe and suitable operation for children that avoids prosthetic valve replacement.
Department of Thoracic and Cardiovascular Surgery, Saint Carollo General Hospital.
Hyung-Tae
HT
Sim
Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine.
Dong Ju
DJ
Seo
Division of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine.
Jeong Jin
JJ
Yu
Division of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine.
Jae Suk
JS
Baek
Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine.
Hyn Woo
HW
Goo
Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine.
Jeong-Jun
JJ
Park
Aneurysm; Aorta; Aortic root; Aortic valve, surgery; Loeys-Dietz syndrome