Adult liver transplantation in the congenital absence of inferior vena cava.
Whereas congenital absence of inferior vena cava observed in paediatric population more often than not, as an isolated or syndromic variety, this is seldom encountered in adult liver transplant recipients. There appear few sporadic reports in the literature on experience of such anomaly in adults. Given the rarity of situation, surprising encounters of such anomalies may pose challenge to the unprepared transplant surgeon and unfavourable outcomes may even have resulted in under-reportage of this condition. In this brief report we document our recent experience with two such cases and this is supplemented with extensive reference to the literature on classification of such anomalies with the endeavour to document implications of such in the adult liver transplant setting.
The Liver Unit, Queen Elizabeth Hospital Birmingham, Edgbaston, Birmingham B15 TH, United Kingdom.
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Angelico
Birmingham Children's Hospital, Birmingham B4 6NH United Kingdom.
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Stonelake
The Liver Unit, Queen Elizabeth Hospital Birmingham, Edgbaston, Birmingham B15 TH, United Kingdom.
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Perera
The Liver Unit, Queen Elizabeth Hospital Birmingham, Edgbaston, Birmingham B15 TH, United Kingdom; Birmingham Children's Hospital, Birmingham B4 6NH United Kingdom.
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Mirza
The Liver Unit, Queen Elizabeth Hospital Birmingham, Edgbaston, Birmingham B15 TH, United Kingdom.
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Russell
The Liver Unit, Queen Elizabeth Hospital Birmingham, Edgbaston, Birmingham B15 TH, United Kingdom; Birmingham Children's Hospital, Birmingham B4 6NH United Kingdom.
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Muiesan
The Liver Unit, Queen Elizabeth Hospital Birmingham, Edgbaston, Birmingham B15 TH, United Kingdom; Birmingham Children's Hospital, Birmingham B4 6NH United Kingdom. Electronic address: Thamara.Perera@uhb.nhs.uk.
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Perera
D000328:Adult; D000367:Age Factors; D006528:Carcinoma, Hepatocellular / Q000473:pathology / Q000601:surgery*; D058625:End Stage Liver Disease / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008113:Liver Neoplasms / Q000473:pathology / Q000601:surgery*; D016031:Liver Transplantation; D008297:Male; D008875:Middle Aged; D014682:Vena Cava, Inferior / Q000002:abnormalities*
Absent inferior vena cava; Azygous system; Congenial anomalies; Heterotaxy syndrome; Liver transplant