title: A newborn with three cochlear turns: Case report and literature review.
abstract: Objectives/Hypothesis: The human cochlea is most commonly considered to have two and a half turns. Although the causes of cochlear hypoplasia are well described, cochlear hyperplasia is a rarer entity that is poorly understood. We describe rare anatomic cochlear malformations identified in a 4-month-old male originally referred for evaluation after a failed newborn hearing screening. The full diagnostic evaluation, imaging findings, treatment, and follow-up are described in detail. Cochleae with three turns are an uncommon malformation that is not included in current classifications schemes and may represent a distinct type of anomaly not caused by developmental arrest.
authors: Department of Otolaryngology/Head and Neck Surgery, Tulane University School of Medicine.
authors: Douglas M
authors: http://orcid.org/0000-0003-3310-479X
authors: DM
authors: Hildrew
authors: Department of Otolaryngology/Head and Neck Surgery, Tulane University School of Medicine.
authors: Ashwin
authors: A
authors: Ananth
authors: Department of Otolaryngology/Head and Neck Surgery, Ochsner Health System, New Orleans, Louisiana, U.S.A.
authors: Kimsey H
authors: KH
authors: Rodriguez
mesh_terms: D001299:Audiometry; D003051:Cochlea / Q000002:abnormalities* / Q000601:surgery; D006319:Hearing Loss, Sensorineural / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D008876:Middle Ear Ventilation / Q000379:methods*; D014057:Tomography, X-Ray Computed
keywords: Three cochlear turns; cochlea; cochlear malformations; conductive hearing loss; conductive hearing loss (CHL); hearing loss; hyperplasia congenital; hyperplastic; sensorineural hearing loss; sensorineural hearing loss (SNHL)