title: [Hearing rehabilitation in Treacher Collins Syndrome with bone anchored hearing aid].
abstract: OBJECTIVE
  To describe a case of hearing rehabilitation with bone anchored hearing aid in a patient with Treacher Collins syndrome.
  
  
  METHODS
  3 years old patient, male, with Treacher Collins syndrome and severe complications due to the syndrome, mostly related to the upper airway and hearing. He had bilateral atresia of external auditory canals, and malformation of the pinna. The initial hearing rehabilitation was with bone vibration arch, but there was poor acceptance due the discomfort caused by skull compression. It was prescribed a model of bone-anchored hearing aid, in soft band format. The results were evaluated through behavioral hearing tests and questionnaires Meaningful Use of Speech Scale (Muss) and Infant-Toddler Meaningful Auditory Integration Scale (IT-Mais).
  
  
  CONCLUSIONS
  The patient had a higher acceptance of the bone-anchored hearing aid compared to the traditional bone vibration arch. Audiological tests and the speech and auditory skills assessments also showed better communication and hearing outcomes. The bone-anchored hearing aid is a good option in hearing rehabilitation in this syndrome.
authors: Faculdade Evangélica do Paraná, Curitiba, PR, Brasil; Universidade Federal do Paraná (UFPR), Curitiba, PR, Brasil. Electronic address: jfpolanski@gmail.com.
authors: José Fernando
authors: JF
authors: Polanski
authors: Faculdade Evangélica do Paraná, Curitiba, PR, Brasil.
authors: Anna Clara
authors: AC
authors: Plawiak
authors: Universidade Tuiuti do Paraná, Curitiba, PR, Brasil.
authors: Angela
authors: A
authors: Ribas
mesh_terms: D002675:Child, Preschool; D006306:Health Surveys; D006310:Hearing Aids / Q000009:adverse effects; D006314:Hearing Loss, Conductive / Q000209:etiology / Q000534:rehabilitation*; D006320:Hearing Tests / Q000379:methods; D006801:Humans; D008297:Male; D008342:Mandibulofacial Dysostosis / Q000150:complications*; D014732:Vibration
keywords: Child; Criança; Deficiência auditiva/reabilitação; Disostose mandibulofacial; Hearing loss/rehabilitation; Mandibulofacial dysostosis