The risk for type B aortic dissection in Marfan syndrome.
Marfan syndrome is the most prevalent connective tissue disorder, with an autosomal dominant inheritance with variable penetrance. This paper aims to summarize epidemiology and treatment for type B dissection in Marfan patients.
Vascular and Endovascular Surgery Unit, Department of Medicine, Surgery and Neurological Sciences, University of Siena, Siena, Italy - setacci@unisi.it.
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Setacci
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Setacci
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Mazzitelli
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Ricci
D000784:Aortic Dissection / Q000175:diagnosis / Q000453:epidemiology* / Q000601:surgery; D000818:Animals; D001014:Aortic Aneurysm / Q000175:diagnosis / Q000453:epidemiology* / Q000601:surgery; D019917:Blood Vessel Prosthesis Implantation; D003952:Diagnostic Imaging / Q000379:methods; D057510:Endovascular Procedures; D020022:Genetic Predisposition to Disease; D006801:Humans; D008382:Marfan Syndrome / Q000175:diagnosis / Q000453:epidemiology* / Q000235:genetics; D010641:Phenotype; D011237:Predictive Value of Tests; D015995:Prevalence; D012307:Risk Factors; D016896:Treatment Outcome