Cardiac Involvement in a Patient With POEMS Syndrome Detected Using Cardiac Magnetic Resonance Imaging.
We present a case of POEMS syndrome in which cardiac MRI (CMR) revealed cardiac involvement. POEMS syndrome is a very rare disease and cardiac involvement in POEMS syndrome is rarely reported. In the present case, echocardiography revealed left ventricular hypertrophy with moderately impaired systolic function and moderate pulmonary hypertension. CMR examination showed a typical circular subendocardial type of late gadolinium enhancement, which is a classic pattern of cardiac amyloidosis. The diagnosis of cardiac amyloidosis in POEMS would be helpful for further risk stratification and treatment strategies.
Division of Cardiology, West China Hospital, Sichuan University.
Guoyuan
G
Pei
Dan
D
Yang
Jiayu
J
Sun
Yong
Y
Luo
Jiaqi
J
Yan
Yucheng
Y
Chen
D000686:Amyloidosis / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology; D001706:Biopsy; D003937:Diagnosis, Differential; D019468:Disease Management; D004452:Echocardiography / Q000379:methods; D004562:Electrocardiography / Q000379:methods; D005260:Female; D005682:Gadolinium / Q000494:pharmacology*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology; D017379:Hypertrophy, Left Ventricular / Q000150:complications / Q000000981:diagnostic imaging / Q000503:physiopathology; D007089:Image Enhancement / Q000379:methods; D008279:Magnetic Resonance Imaging / Q000379:methods; D008875:Middle Aged; D016878:POEMS Syndrome / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology; D011859:Radiography; D019275:Radiopharmaceuticals / Q000494:pharmacology; D018487:Ventricular Dysfunction, Left / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology
D019275:Radiopharmaceuticals; D005682:Gadolinium