Mechanical circulatory support after surgical repair of Bland-White-Garland syndrome. A study of three cases.
The anomalous origin of the left coronary artery arising from the pulmonary artery (ALCAPA), also known as Bland-White-Garland (BWG) syndrome, is a rare congenital heart disease. We present cases of three children in whom BWG syndrome was repaired surgically. In two of them, the left coronary artery was transplanted from the pulmonary trunk to the aorta, and in one, the Takeuchi procedure was performed. In both cases in which the left coronary artery was transplanted to the aorta, mechanical circulatory support was used after the surgery. This was due to a low ejection fraction (10%) while weaning from cardiopulmonary bypass. Although associated with numerous complications, mechanical circulatory support can be a lifesaving therapy in patients with a poor left ventricular function after the correction of BWG syndrome.
Lower Silesian Center for Heart Diseases, Wroclaw, Poland.
Girish
G
Sharma
Lower Silesian Center for Heart Diseases, Wroclaw, Poland.
Cyprian
C
Augustyn
Student Research Association operating at the Lower Silesian Center for Heart Diseases, Wroclaw, Poland.
Paweł
P
Nawrocki
Clinic of Cardiac Surgery, 1 Chair and Clinic of Cardiology, 1 Faculty of Medicine, Medical University of Warsaw, Poland.
Romuald
R
Cichoń
Bland-White-Garland syndrome; mechanical circulatory support