Multifocal Endobronchial Fibromas Presenting as Unilobar Emphysema.
Tracheobronchial fibromas are very rare, locally-invasive tumors of the airways. Fewer than 30 cases have been reported within the English-speaking literature. Historically, these neoplasms have been diagnosed as isolated endobronchial masses, with affected patients presenting with wheezing, cough, stridor, hemoptysis, dyspnea, or pneumonia. We report the case of 39-year-old man with multiple, synchronous endobronchial fibromas causing unilobar emphysema. A computed tomographic scan and bronchoscopy with biopsy were performed preoperatively to diagnose these lesions in the orifices of the anterior segment and the lingula within the left upper lobe. The patient underwent successful video-assisted left upper lobectomy, without recurrence at 3 years. This is the first report of a synchronous presentation of multiple pulmonary endobronchial fibromas within the same patient and the first report of endobronchial fibroma presenting as unilobar air trapping. Recognition of the unusual presentation of this uncommon pathology can lead to timely intervention.
Division of Cardiothoracic Surgery, University of California, San Diego, La Jolla, California.
Seemal
S
Mumtaz
Division of Cardiothoracic Surgery, University of California, San Diego, La Jolla, California.
Maha
M
Alkhuziem
Division of Cardiothoracic Surgery, University of California, San Diego, La Jolla, California.
Jennifer
J
Chow
Department of Radiology, University of California, San Diego, La Jolla, California.
Andrew
A
Yen
Department of Pathology, University of California, San Diego, La Jolla, California.
Grace
G
Lin
Divison of Pulmonary and Critical Care Medicine, University of California, San Diego, La Jolla, California.
James H
JH
Harrell
Division of Cardiothoracic Surgery, University of California, San Diego, La Jolla, California. Electronic address: pthistlethwaite@ucsd.edu.
Patricia A
PA
Thistlethwaite
D000328:Adult; D001984:Bronchial Neoplasms / Q000150:complications* / Q000175:diagnosis; D005350:Fibroma / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D008297:Male; D011656:Pulmonary Emphysema / Q000209:etiology*