Ectopic virilising adrenocortical tumour in the spinal region in an 8 year-old boy: a case report and review of the literature.
BACKGROUND
The adrenocortical rest tumours are the very rare entity in the pediatric population. They are usually found along the gonadal descent paths (celiac axis, the broad ligamen, the adnexa of the testes or the spermatic cord). They have been also described to occur at rare ectopic sites like intracranial locations, placenta, kidney, pancreas and liver.


METHODS
Here we present a unusual case of an ectopic, virilising, primary adrenocortical tumour localized in the spinal region in a 8 years-old-boy.


CONCLUSIONS
This is the first case of functional ectopic, adrenocortical tumour localized in the spinal region in a pediatric population. We discuss here the clinical presentation and the diagnostic challenges and provide the review of the literature.
Department of Paediatrics, Medical University of Warsaw, Dzialdowska 1, 01-189, Warsaw, Poland. askorka@wum.edu.pl.
Agata
A
Skórka
Department of Endocrinology and Diabetology, The Children's Memorial Health Institute, Al. Dzieci Polskich 20 04-730, Warsaw, Poland.
Elżbieta
E
Moszczyńska
Department of Endocrinology and Diabetology, The Children's Memorial Health Institute, Al. Dzieci Polskich 20 04-730, Warsaw, Poland.
Karolina
K
Kot
Department of Neurosurgery, The Children's Memorial Health Institute, Al. Dzieci Polskich 20 04-730, Warsaw, Poland.
Marcin
M
Roszkowski
Department of Diagnostic Imaging, The Children's Memorial Health Institute, Al. Dzieci Polskich 20 04-730, Warsaw, Poland.
Elżbieta
E
Jurkiewicz
Department of Pathology, The Children's Memorial Health Institute, Al. Dzieci Polskich 20 04-730, Warsaw, Poland.
Wiesława
W
Grajkowska
Department of Pathology, The Children's Memorial Health Institute, Al. Dzieci Polskich 20 04-730, Warsaw, Poland.
Maciej
M
Pronicki
Department of Pediatrics, Endocrinology and Diabetology, Voivodship Children's Hospital, Jana Karola Chodkiewicza 44, 85-667, Bydgoszcz, Poland.
Olgierd
O
Pilecki
Department of Endocrinology and Diabetology, The Children's Memorial Health Institute, Al. Dzieci Polskich 20 04-730, Warsaw, Poland.|Faculty of Health Sciences, UJK, ul. Żeromskiego 5 25-369, Kielce, Poland.
Mieczysław
M
Szalecki
D000314:Adrenal Rest Tumor / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008297:Male; D013125:Spinal Neoplasms / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D014770:Virilism / Q000209:etiology*