title: Proposal for an algorithm for liver transplantation in Caroli's disease and syndrome: putting an uncommon effort into a common task.
abstract: Liver transplantation (LT) represents an uncommon indication for Caroli's disease (CD) or syndrome (CS). Excellent results of LT have been reported as shown by recent multicentric European and American registry reports. Clear therapeutic flowcharts to adopt in these diseases are still lacking. This review aims at analyzing highlighting recent transplant experiences in this field and also at focusing on the role of LT in case-specific comorbidities such as development of cholangiocellular cancer or renal failure are present.
authors.affiliation: Starzl Unit Abdominal Transplantation, University Hospitals Saint Luc, Université catholique Louvain, UCL, Brussels, Belgium.|Transplant Unit, Department of Surgery, University of L'Aquila, San Salvatore Hospital, L'Aquila, Italy.
authors.forename: Quirino
authors.initials: Q
authors.lastname: Lai
authors.affiliation: Starzl Unit Abdominal Transplantation, University Hospitals Saint Luc, Université catholique Louvain, UCL, Brussels, Belgium.
authors.forename: Jan
authors.initials: J
authors.lastname: Lerut
mesh_terms: D000465:Algorithms; D016767:Caroli Disease / Q000601:surgery*; D006801:Humans; D016031:Liver Transplantation; D013577:Syndrome
keywords: Caroli's disease; Caroli's syndrome; autosomal recessive polycystic kidney disease; cholangiocellular cancer; combined kidney-liver transplantation; congenital hepatic fibrosis; liver transplantation