title: Living Donor Liver Transplantation for Unresectable Liver Adenomatosis Associated with Congenital Absence of Portal Vein: A Case Report and Literature Review.
abstract: BACKGROUND
  Abernethy malformation (AM), or congenital absence of portal vein (CAPV), is a very rare disease which tends to be associated with the development of benign or malignant tumors, usually in children or young adults.
  
  
  METHODS
  We report the case of a 21-year-old woman diagnosed with type Ib AM (portal vein draining directly into the inferior vena cava) and unresectable liver adenomatosis. The patient presented mild liver dysfunction and was largely asymptomatic. Living donor liver transplantation was performed using a left hemiliver graft from her mother. Postoperatively, the patient attained optimal liver function and at 9-month follow-up has returned to normal life.
  
  
  CONCLUSIONS
  We consider that living donor liver transplantation is the best therapeutic solution for AM associated with unresectable liver adenomatosis, especially because compared to receiving a whole liver graft, the waiting time on the liver transplantation list is much shorter.
authors.affiliation: "Dan Setlacec" Center of General Surgery and Liver Transplantation, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Vladislav
authors.initials: V
authors.lastname: Brasoveanu
authors.affiliation: "Dan Setlacec" Center for General Surgery and Liver Transplantation, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Mihnea Ioan
authors.initials: MI
authors.lastname: Ionescu
authors.affiliation: "Dan Setlacec" Center of General Surgery and Liver Transplantation, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Razvan
authors.initials: R
authors.lastname: Grigorie
authors.affiliation: Department of Internal Medicine, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Mariana
authors.initials: M
authors.lastname: Mihaila
authors.affiliation: "Carol Davila" University of Medicine and Pharmacy, Bucharest, Romania.
authors.forename: Nicolae
authors.initials: N
authors.lastname: Bacalbasa
authors.affiliation: Department of Radiology and Imagistics, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Radu
authors.initials: R
authors.lastname: Dumitru
authors.affiliation: Department of Morphopathology, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Vlad
authors.initials: V
authors.lastname: Herlea
authors.affiliation: Department of Morphopathology, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Andreea
authors.initials: A
authors.lastname: Iorgescu
authors.affiliation: Department of Anesthesiology, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Dana
authors.initials: D
authors.lastname: Tomescu
authors.affiliation: "Dan Setlacec" Center for General Surgery and Liver Transplantation, Fundeni Clinical Institute, Bucharest, Romania.
authors.forename: Irinel
authors.initials: I
authors.lastname: Popescu
mesh_terms: D000236:Adenoma / Q000175:diagnosis / Q000601:surgery*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008113:Liver Neoplasms / Q000150:complications* / Q000601:surgery; D016031:Liver Transplantation; D019520:Living Donors; D011169:Portal Vein / Q000002:abnormalities*; D013997:Time Factors; D054079:Vascular Malformations / Q000150:complications* / Q000601:surgery; D055815:Young Adult