title: Meandering right pulmonary vein associated with severe and progressive "idiopathic-like" pulmonary hypertensive vascular disease.
abstract: Congenital anomalies of the pulmonary veins are rare. Meandering right pulmonary vein, considered a part of the Scimitar syndrome spectrum, is often an incidental finding during chest imaging. We present the case of a 4-year-old girl diagnosed with meandering pulmonary vein, who developed pulmonary hypertensive disease with an aggressive course, in spite of absence of hypoxia or elevated pulmonary wedge pressure.
authors.affiliation: 1Cardiology Department,Hospital Universitario Puerta de Hierro Majadahonda,Madrid,Spain.
authors.forename: Sofia
authors.identifier: http://orcid.org/0000-0003-3388-8598
authors.initials: S
authors.lastname: Cuenca
authors.affiliation: 2Pediatric Radiology Department,Hospital Universitario La Paz,Madrid,Spain.
authors.forename: Montserrat
authors.initials: M
authors.lastname: Bret
authors.affiliation: 3Pediatric Cardiology Department,Hospital Universitario Ramon y Cajal,Madrid,Spain.
authors.forename: Maria Jesus
authors.initials: MJ
authors.lastname: del Cerro
mesh_terms: D000792:Angiography; D002675:Child, Preschool; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis* / Q000209:etiology*; D033162:Incidental Findings; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D011859:Radiography; D012587:Scimitar Syndrome; D014057:Tomography, X-Ray Computed
keywords: Meandering pulmonary vein; pulmonary hypertension; scimitar syndrome