title: Congenital atresia of the left main coronary artery in an adult: A rare anomaly with an unfavorable prognosis. Review of the literature.
abstract: Congenital atresia of the left main coronary artery (LMCA) is one of the rarest congenital anomalies, which may have an unfavorable prognosis leading to myocardial ischemia, ventricle dysfunction or even sudden cardiac death. There are 34 cases of LMCA in adults reported in the literature, most of them successfully treated with coronary revascularization. We report the case of an adult with LMCA who presented with terminal heart failure that required biventricular assistance and heart transplant.
authors.affiliation: Hospital Universitario Madrid Montepríncipe. Electronic address: leireunzue@yahoo.es.
authors.forename: Leire
authors.initials: L
authors.lastname: Unzué
authors.affiliation: Hospital Universitario Madrid Montepríncipe.
authors.forename: Eulogio
authors.initials: E
authors.lastname: García
authors.affiliation: Hospital Universitario Madrid.
authors.forename: Francisco Javier
authors.initials: FJ
authors.lastname: Parra
authors.affiliation: Hospital Universitario Madrid Puerta del Sur.
authors.forename: Jesús
authors.initials: J
authors.lastname: Palomo
authors.affiliation: Hospital Universitario Madrid Montepríncipe.
authors.forename: Leticia Fernández
authors.initials: LF
authors.lastname: Friera
authors.affiliation: Hospital Universitario Madrid Montepríncipe.
authors.forename: Jorge
authors.initials: J
authors.lastname: Solís
mesh_terms: D000367:Age Factors; D000368:Aged; D002423:Cause of Death; D017023:Coronary Angiography / Q000379:methods; D003330:Coronary Vessel Anomalies / Q000175:diagnosis* / Q000401:mortality* / Q000601:surgery; D004417:Dyspnea / Q000175:diagnosis / Q000209:etiology; D006333:Heart Failure / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D016027:Heart Transplantation / Q000379:methods*; D006801:Humans; D021621:Imaging, Three-Dimensional; D019028:Magnetic Resonance Imaging, Cine / Q000379:methods; D008297:Male; D011379:Prognosis; D035583:Rare Diseases; D018570:Risk Assessment; D012737:Sex Factors; D016019:Survival Analysis; D016896:Treatment Outcome
keywords: Coronary artery anomaly; Left main coronary artery atresia