title: [Idiopathic non-cirrhotic portal hypertension: An update].
abstract: Idiopathic non-cirrhotic portal hypertension is an under-estimated cause of portal hypertension. The diagnosis requires the exclusion of cirrhosis, common causes of chronic liver disease and venous obstruction of the portal and hepatic veins. It has been associated with various extra-hepatic conditions that are most frequently immunologic, prothrombotic, hematologic and toxic. The most frequent clinical complications are variceal hemorrhage and portal vein thrombosis. Complications of portal hypertension should be managed as in patients with cirrhosis.
authors.affiliation: AP-HP, hôpital Beaujon, centre de référence des maladies vasculaires du foie, pôle des maladies de l'appareil digestif, service d'hépatologie, DHU unity, 92118 Clichy, France.
authors.forename: Julien
authors.initials: J
authors.lastname: Bissonnette
authors.affiliation: AP-HP, hôpital Beaujon, centre de référence des maladies vasculaires du foie, pôle des maladies de l'appareil digestif, service d'hépatologie, DHU unity, 92118 Clichy, France; Université Paris Diderot, hôpital Bichat, CRI Paris-Montmartre, UMR 1149, PRES SPC, 75018 Paris, France.
authors.forename: Pierre-Emmanuel
authors.initials: PE
authors.lastname: Rautou
authors.affiliation: AP-HP, hôpital Beaujon, centre de référence des maladies vasculaires du foie, pôle des maladies de l'appareil digestif, service d'hépatologie, DHU unity, 92118 Clichy, France; Université Paris Diderot, hôpital Bichat, CRI Paris-Montmartre, UMR 1149, PRES SPC, 75018 Paris, France; Université Paris Descartes, Paris cardiovascular research center, PARCC, UMR-S970, Inserm, U970, Sorbonne Paris Cité, 75015 Paris, France. Electronic address: dominique.valla@bjn.aphp.fr.
authors.forename: Dominique-Charles
authors.initials: DC
authors.lastname: Valla
mesh_terms: D004932:Esophageal and Gastric Varices / Q000150:complications / Q000453:epidemiology / Q000628:therapy; D006471:Gastrointestinal Hemorrhage / Q000150:complications / Q000453:epidemiology / Q000628:therapy; D006801:Humans; D006975:Hypertension, Portal / Q000453:epidemiology / Q000209:etiology / Q000628:therapy*; D008103:Liver Cirrhosis / Q000150:complications / Q000453:epidemiology / Q000628:therapy; D011169:Portal Vein / Q000473:pathology; D010818:Practice Patterns, Physicians' / Q000639:trends