title: Late Peripheral Thoracic Aneurysms following Aortic Root Surgery in Patients with Loeys-Dietz Syndrome.
abstract: The Loeys-Dietz syndrome is a multisystem connective tissue disorder characterized by aortopathy, arterial tortuosity, peripheral aneurysms, and skeletal features. The peripheral arteriopathy is an important cause of morbidity and potential mortality. This report presents 2 cases: the first demonstrating a 5-cm pseudoaneurysm of the right internal mammary artery and the second demonstrating a 2.3-cm aneurysm of the left internal mammary artery, each following aortic root surgery. These were successfully treated with percutaneous techniques. No complications were seen at follow-up as long as 2 years. Patients with Loeys-Dietzs syndrome require comprehensive long-term vascular follow-up and are likely to require percutaneous vascular interventions.
authors.affiliation: Departments of Cardiology, Queen Elizabeth Hospital, Birmingham.; Departments of Cardiology, Royal Infirmary of Edinburgh, Edinburgh, United Kingdom.. Electronic address: yasoemmanuel@yahoo.co.uk.
authors.forename: Yaso
authors.initials: Y
authors.lastname: Emmanuel
authors.affiliation: Departments of Radiology, Royal Infirmary of Edinburgh, Edinburgh, United Kingdom.
authors.forename: Jim
authors.initials: J
authors.lastname: Gordon-Smith
authors.affiliation: Departments of Radiology, Royal Infirmary of Edinburgh, Edinburgh, United Kingdom.
authors.forename: Graham
authors.initials: G
authors.lastname: McKillop
authors.affiliation: Departments ofInterventional Radiology, Queen Elizabeth Hospital, Birmingham.
authors.forename: Martin
authors.initials: M
authors.lastname: Duddy
authors.affiliation: Departments of Cardiology, Queen Elizabeth Hospital, Birmingham.
authors.forename: Paul
authors.initials: P
authors.lastname: Clift
mesh_terms: D000328:Adult; D000783:Aneurysm / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D001011:Aorta / Q000601:surgery*; D005260:Female; D006801:Humans; D055947:Loeys-Dietz Syndrome / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery*; D008875:Middle Aged; D011859:Radiography; D013909:Thorax / Q000098:blood supply; D016896:Treatment Outcome; D058017:Vascular Grafting / Q000009:adverse effects*