title: Laparoscopic appendectomy in a pediatric patient with type 1 Charcot-Marie-Tooth disease.
abstract: A pediatric patient with type 1 Charcot-Marie-Tooth disease-a disorder associated with a demyelinating polyneuropathy-presented for laparoscopic appendectomy in the setting of acute appendicitis. Induction and maintenance of anesthesia were successfully managed without the use of any depolarizing or nondepolarizing neuromuscular blocking agents. The patient was successfully extubated at the completion of the procedure without any respiratory or neuromuscular sequelae, with excellent pain control and no postoperative nausea or vomiting.
authors.affiliation: Icahn School of Medicine at Mount Sinai, 1 Gustave L. Levy Place, KCC 8th Floor, Box 1010, New York, NY 10029. Electronic address: Joshua.heller@mountsinai.org.
authors.forename: Joshua A
authors.initials: JA
authors.lastname: Heller
authors.affiliation: Icahn School of Medicine at Mount Sinai, 1 Gustave L. Levy Place, KCC 8th Floor, Box 1010, New York, NY 10029.
authors.forename: Richard Y
authors.initials: RY
authors.lastname: Marn
mesh_terms: D000293:Adolescent; D000758:Anesthesia / Q000009:adverse effects / Q000379:methods*; D001062:Appendectomy / Q000379:methods*; D001064:Appendicitis / Q000601:surgery; D002607:Charcot-Marie-Tooth Disease / Q000503:physiopathology*; D006801:Humans; D010535:Laparoscopy / Q000379:methods*; D008297:Male
keywords: Charcot-Marie-Tooth disease; Neuromuscular blockade