title: Cystic Fibrosis Papers of the Year, 2013-2014.
abstract: Studies published in the last year in the field of cystic fibrosis have provided more data on the safety and efficacy of a number of therapies, including mutation-specific drugs. There have also been a number of publications on monitoring of early lung disease including the use of lung clearance index and magnetic resonance scanning. Evidence suggests early lung changes may remain relatively static over the first year of life. There are important outcome differences across national patient registries and there is also the increasing recognition of psychological illnesses and possible drug interactions as treatment becomes more complicated and survival improves.
authors.affiliation: Consultant Respiratory Physician/Honorary Senior Clinical Lecturer, Department of Cystic Fibrosis, Royal Brompton Hospital and Imperial College, Sydney Street, London, United Kingdom, SW3 6NP. Electronic address: n.simmonds@imperial.ac.uk.
authors.forename: Nicholas J
authors.initials: NJ
authors.lastname: Simmonds
mesh_terms: D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D003550:Cystic Fibrosis / Q000175:diagnosis / Q000188:drug therapy*; D016903:Drug Monitoring / Q000379:methods*; D006801:Humans; D012042:Registries; D055815:Young Adult
keywords: Cystic fibrosis; Monitoring; Publications; Registries; Trials