title: Atypical Neuroimaging Manifestations of Linear Scleroderma "en coup de sabre".
abstract: Linear scleroderma "en coup de sabre" is a subset of localized scleroderma with band-like sclerotic lesions typically involving the fronto-parietal regions of the scalp. Patients often present with neurologic symptoms. On imaging, patients may have lesions in the cerebrum ipsilateral to the scalp abnormality. Infratentorial lesions and other lesions not closely associated with the overlying scalp abnormality, such as those found in the cerebellum, have been reported, but are extremely uncommon. We present a case of an 8-year-old boy with a left fronto-parietal "en coup de sabre" scalp lesion and describe the neuroimaging findings of a progressively enlarging left cerebellar lesion discovered incidentally on routine magnetic resonance imaging. Interestingly, the patient had no neurologic symptoms given the size of the mass identified.
authors.affiliation: The Department of Radiology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
authors.forename: Andrew
authors.initials: A
authors.lastname: M Allmendinger
authors.affiliation: The Division of Plastic Surgery, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
authors.forename: Joseph
authors.initials: J
authors.lastname: A Ricci
authors.affiliation: The Department of Radiology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
authors.forename: Naman
authors.initials: N
authors.lastname: S Desai
authors.affiliation: The Department of Radiology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
authors.forename: Narayan
authors.initials: N
authors.lastname: Viswanadhan
authors.affiliation: The Division of Neuroradiology, Boston Children's Hospital, Harvard Medical School, Boston, MA, USA.
authors.forename: Diana
authors.initials: D
authors.lastname: Rodriguez
keywords: Cerebellum; Linear Scleroderma “en coup de sabre”; Localized scleroderma; MRI; Morphea